(Q43466267)

23 November 2017

1 reference

title

The prionoses and other conformational disorders (English)

1 reference

23 November 2017

1

1 reference

23 November 2017

Aucouturier P

2

1 reference

PubMed ID

9818059

23 November 2017

Soto C

series ordinal

3

1 reference

PubMed ID

9818059

23 November 2017

Frangione B

series ordinal

4

1 reference

23 November 2017

1 September 1998

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23 November 2017

1 reference

23 November 2017

5

1 reference

23 November 2017

212-224

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23 November 2017

3

1 reference

Biology of A beta amyloid in Alzheimer's disease

23 November 2017

1 reference

https://api.crossref.org/works/10.3109%2F13506129809003848

Chaperoning brain diseases.

21 January 2018

1 reference

https://api.crossref.org/works/10.3109%2F13506129809003848

21 January 2018

Conformational disease

1 reference

https://api.crossref.org/works/10.3109%2F13506129809003848

21 January 2018

Prion Protein Biology

1 reference

https://api.crossref.org/works/10.3109%2F13506129809003848

Deadly conformations--protein misfolding in prion disease

21 January 2018

1 reference

https://api.crossref.org/works/10.3109%2F13506129809003848

Degenerative disease of the central nervous system in New Guinea; the endemic occurrence of kuru in the native population

21 January 2018

1 reference

https://api.crossref.org/works/10.3109%2F13506129809003848

Experimental transmission of a Kuru-like syndrome to chimpanzees

21 January 2018

1 reference

https://api.crossref.org/works/10.3109%2F13506129809003848

Familial Gerstmann-Sträussler-Scheinker disease with neurofibrillary tangles

21 January 2018

1 reference

https://api.crossref.org/works/10.3109%2F13506129809003848

Vascular variant of prion protein cerebral amyloidosis with tau-positive neurofibrillary tangles: the phenotype of the stop codon 145 mutation in PRNP.

21 January 2018

1 reference

https://api.crossref.org/works/10.3109%2F13506129809003848

Fatal familial insomnia, a prion disease with a mutation at codon 178 of the prion protein gene

21 January 2018

1 reference

https://api.crossref.org/works/10.3109%2F13506129809003848

Fatal familial insomnia and familial Creutzfeldt-Jakob disease: disease phenotype determined by a DNA polymorphism

21 January 2018

1 reference

https://api.crossref.org/works/10.3109%2F13506129809003848

Human prion diseases and bovine spongiform encephalopathy (BSE).

21 January 2018

1 reference

https://api.crossref.org/works/10.3109%2F13506129809003848

BSE: a decade on--Part I.

21 January 2018

1 reference

https://api.crossref.org/works/10.3109%2F13506129809003848

A new variant of Creutzfeldt-Jakob disease in the UK.

21 January 2018

1 reference

https://api.crossref.org/works/10.3109%2F13506129809003848

Self-replication and scrapie

21 January 2018

1 reference

https://api.crossref.org/works/10.3109%2F13506129809003848

Novel proteinaceous infectious particles cause scrapie

21 January 2018

1 reference

https://api.crossref.org/works/10.3109%2F13506129809003848

The Ninth Datta Lecture. Molecular biology of transmissible spongiform encephalopathies

21 January 2018

1 reference

https://api.crossref.org/works/10.3109%2F13506129809003848

Does the agent of scrapie replicate without nucleic acid?

21 January 2018

1 reference

https://api.crossref.org/works/10.3109%2F13506129809003848

Inactivation of the scrapie agent by near monochromatic ultraviolet light

21 January 2018

1 reference

https://api.crossref.org/works/10.3109%2F13506129809003848

Abnormal fibrils from scrapie-infected brain

21 January 2018

1 reference

https://api.crossref.org/works/10.3109%2F13506129809003848

Conversion of alpha-helices into beta-sheets features in the formation of the scrapie prion proteins

21 January 2018

1 reference

https://api.crossref.org/works/10.3109%2F13506129809003848

Thermal stability and conformational transitions of scrapie amyloid (prion) protein correlate with infectivity

21 January 2018

1 reference

https://api.crossref.org/works/10.3109%2F13506129809003848

Molecular analysis of prion strain variation and the aetiology of 'new variant' CJD.

21 January 2018

1 reference

https://api.crossref.org/works/10.3109%2F13506129809003848

Human prion protein cDNA: molecular cloning, chromosomal mapping, and biological implications

21 January 2018

1 reference

https://api.crossref.org/works/10.3109%2F13506129809003848

A cellular gene encodes scrapie PrP 27-30 protein

21 January 2018

1 reference

https://api.crossref.org/works/10.3109%2F13506129809003848

Identification of scrapie prion protein-specific mRNA in scrapie-infected and uninfected brain

21 January 2018

1 reference

https://api.crossref.org/works/10.3109%2F13506129809003848

Synthesis and trafficking of prion proteins in cultured cells

21 January 2018

1 reference

https://api.crossref.org/works/10.3109%2F13506129809003848

Processing of a cellular prion protein: identification of N- and C-terminal cleavage sites.

21 January 2018

1 reference

https://api.crossref.org/works/10.3109%2F13506129809003848

An amber mutation of prion protein in Gerstmann-Sträussler syndrome with mutant PrP plaques

21 January 2018

1 reference

https://api.crossref.org/works/10.3109%2F13506129809003848

Linkage of the Indiana kindred of Gerstmann-Sträussler-Scheinker disease to the prion protein gene

21 January 2018

1 reference

https://api.crossref.org/works/10.3109%2F13506129809003848

Mutant prion proteins in Gerstmann-Sträussler-Scheinker disease with neurofibrillary tangles

21 January 2018

1 reference

https://api.crossref.org/works/10.3109%2F13506129809003848

Normal development and behaviour of mice lacking the neuronal cell-surface PrP protein

21 January 2018

1 reference

https://api.crossref.org/works/10.3109%2F13506129809003848

129/Ola mice carrying a null mutation in PrP that abolishes mRNA production are developmentally normal.

21 January 2018

1 reference

https://api.crossref.org/works/10.3109%2F13506129809003848

Prion protein is necessary for normal synaptic function.

21 January 2018

1 reference

https://api.crossref.org/works/10.3109%2F13506129809003848

Mice deficient for prion protein exhibit normal neuronal excitability and synaptic transmission in the hippocampus

21 January 2018

1 reference

https://api.crossref.org/works/10.3109%2F13506129809003848

Loss of cerebellar Purkinje cells in aged mice homozygous for a disrupted PrP gene.

21 January 2018

1 reference

https://api.crossref.org/works/10.3109%2F13506129809003848

Mice devoid of PrP are resistant to scrapie

21 January 2018

1 reference

https://api.crossref.org/works/10.3109%2F13506129809003848

Ablation of the prion protein (PrP) gene in mice prevents scrapie and facilitates production of anti-PrP antibodies

21 January 2018

1 reference

https://api.crossref.org/works/10.3109%2F13506129809003848

Interactions between wild-type and mutant prion proteins modulate neurodegeneration in transgenic mice.

21 January 2018

1 reference

https://api.crossref.org/works/10.3109%2F13506129809003848

Serial transmission in rodents of neurodegeneration from transgenic mice expressing mutant prion protein

21 January 2018

1 reference

https://api.crossref.org/works/10.3109%2F13506129809003848

Prions, beta-sheets and transmissible dementias: is there still something missing?

21 January 2018

1 reference

https://api.crossref.org/works/10.3109%2F13506129809003848

Molecular basis of phenotypic variability in sporadic Creutzfeldt-Jakob disease

21 January 2018

1 reference

https://api.crossref.org/works/10.3109%2F13506129809003848

21 January 2018

Typing prion isoforms.

1 reference

https://api.crossref.org/works/10.3109%2F13506129809003848

Apolipoprotein E: a pathological chaperone protein in patients with cerebral and systemic amyloid

21 January 2018

1 reference

https://api.crossref.org/works/10.3109%2F13506129809003848

Is Alzheimer's disease an apolipoprotein E amyloidosis?

21 January 2018

1 reference

https://api.crossref.org/works/10.3109%2F13506129809003848

Gene dose of apolipoprotein E type 4 allele and the risk of Alzheimer's disease in late onset families

21 January 2018

1 reference

https://api.crossref.org/works/10.3109%2F13506129809003848

Apolipoprotein E: high-avidity binding to beta-amyloid and increased frequency of type 4 allele in late-onset familial Alzheimer disease

21 January 2018

1 reference

https://api.crossref.org/works/10.3109%2F13506129809003848

Lack of apolipoprotein E dramatically reduces amyloid beta-peptide deposition.

21 January 2018

1 reference

https://api.crossref.org/works/10.3109%2F13506129809003848

Transmission of Creutzfeldt-Jakob disease from humans to transgenic mice expressing chimeric human-mouse prion protein

21 January 2018

1 reference

https://api.crossref.org/works/10.3109%2F13506129809003848

Prion propagation in mice expressing human and chimeric PrP transgenes implicates the interaction of cellular PrP with another protein

21 January 2018

1 reference

https://api.crossref.org/works/10.3109%2F13506129809003848

Potent inhibition of scrapie-associated PrP accumulation by congo red

21 January 2018

1 reference

https://api.crossref.org/works/10.3109%2F13506129809003848

Effectiveness of anthracycline against experimental prion disease in Syrian hamsters.

21 January 2018

1 reference

https://api.crossref.org/works/10.3109%2F13506129809003848

Thermodynamic beta-sheet propensities measured using a zinc-finger host peptide.

21 January 2018

1 reference

https://api.crossref.org/works/10.3109%2F13506129809003848

Mutations and off-pathway aggregation of proteins

21 January 2018

1 reference

https://api.crossref.org/works/10.3109%2F13506129809003848

Beta-sheet breaker peptides inhibit fibrillogenesis in a rat brain model of amyloidosis: implications for Alzheimer's therapy.

21 January 2018

1 reference

https://api.crossref.org/works/10.3109%2F13506129809003848

The Hsp70 and Hsp60 chaperone machines

21 January 2018

1 reference

https://api.crossref.org/works/10.3109%2F13506129809003848

Principles that govern the folding of protein chains

21 January 2018

1 reference

https://api.crossref.org/works/10.3109%2F13506129809003848

Mad cows meet psi-chotic yeast: the expansion of the prion hypothesis

21 January 2018

1 reference

https://api.crossref.org/works/10.3109%2F13506129809003848

The protein product of the het-s heterokaryon incompatibility gene of the fungus Podospora anserina behaves as a prion analog

21 January 2018

1 reference

https://api.crossref.org/works/10.3109%2F13506129809003848

Mutation of the Alzheimer's disease amyloid gene in hereditary cerebral hemorrhage, Dutch type.

21 January 2018

1 reference

https://api.crossref.org/works/10.3109%2F13506129809003848

Peptides homologous to the amyloid protein of Alzheimer's disease containing a glutamine for glutamic acid substitution have accelerated amyloid fibril formation.

21 January 2018

1 reference

https://api.crossref.org/works/10.3109%2F13506129809003848

Effects of the mutations Glu22 to Gln and Ala21 to Gly on the aggregation of a synthetic fragment of the Alzheimer's amyloid beta/A4 peptide.

21 January 2018

1 reference

https://api.crossref.org/works/10.3109%2F13506129809003848

Expression of a normal and variant Alzheimer's beta-protein gene in amyloid of hereditary cerebral hemorrhage, Dutch type: DNA and protein diagnostic assays.

21 January 2018

1 reference

https://api.crossref.org/works/10.3109%2F13506129809003848

Genetic predisposition to iatrogenic Creutzfeldt-Jakob disease

21 January 2018

1 reference

https://api.crossref.org/works/10.3109%2F13506129809003848

NMR structure of the mouse prion protein domain PrP(121-231)

21 January 2018

1 reference

https://api.crossref.org/works/10.3109%2F13506129809003848

Prion protein NMR structure and species barrier for prion diseases

21 January 2018

1 reference

https://api.crossref.org/works/10.3109%2F13506129809003848

NMR characterization of the full-length recombinant murine prion protein, mPrP(23-231).

21 January 2018

1 reference

https://api.crossref.org/works/10.3109%2F13506129809003848

Transmissible familial Creutzfeldt-Jakob disease associated with five, seven, and eight extra octapeptide coding repeats in the PRNP gene

21 January 2018

1 reference

https://api.crossref.org/works/10.3109%2F13506129809003848

An in-frame insertion in the prion protein gene in familial Creutzfeldt-Jakob disease

21 January 2018

1 reference

https://api.crossref.org/works/10.3109%2F13506129809003848

Linkage of a prion protein missense variant to Gerstmann-Sträussler syndrome

21 January 2018

1 reference

https://api.crossref.org/works/10.3109%2F13506129809003848

Mutations in familial Creutzfeldt-Jakob disease and Gerstmann-Sträussler-Scheinker's syndrome

21 January 2018

1 reference

https://api.crossref.org/works/10.3109%2F13506129809003848

Novel missense variants of prion protein in Creutzfeldt-Jakob disease or Gerstmann-Sträussler syndrome

21 January 2018

1 reference

https://api.crossref.org/works/10.3109%2F13506129809003848

Mutation in codon 200 of scrapie amyloid protein gene in two clusters of Creutzfeldt-Jakob disease in Slovakia

21 January 2018

1 reference

https://api.crossref.org/works/10.3109%2F13506129809003848

Mutation of the prion protein in Libyan Jews with Creutzfeldt-Jakob disease

21 January 2018

1 reference

https://api.crossref.org/works/10.3109%2F13506129809003848

Altered circadian activity rhythms and sleep in mice devoid of prion protein

21 January 2018

1 reference

https://api.crossref.org/works/10.3109%2F13506129809003848

BSE transmission to macaques

21 January 2018

1 reference

https://api.crossref.org/works/10.3109%2F13506129809003848

10.3109/13506129809003848

21 January 2018

Identifiers

DOI

1 reference

23 November 2017

1 reference

PubMed ID

9818059