(Q43510340)

English

A 7-kDa prion protein (PrP) fragment, an integral component of the PrP region required for infectivity, is the major amyloid protein in Gerstmann-Sträussler-Scheinker disease A117V.

scientific article published on 21 November 2000

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scholarly article

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Europe PubMed Central

PubMed publication ID

24 November 2017

A 7-kDa prion protein (PrP) fragment, an integral component of the PrP region required for infectivity, is the major amyloid protein in Gerstmann-Sträussler-Scheinker disease A117V. (English)

1 reference

Europe PubMed Central

PubMed publication ID

24 November 2017

prion protein family

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inferred from title

Giorgio Giaccone

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G Giaccone

6

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ORCID Public Data File 2021

author name string

F Tagliavini

1

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Europe PubMed Central

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24 November 2017

P M Lievens

2

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24 November 2017

C Tranchant

3

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Europe PubMed Central

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24 November 2017

J M Warter

4

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Europe PubMed Central

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24 November 2017

M Mohr

5

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24 November 2017

F Perini

7

1 reference

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24 November 2017

G Rossi

8

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24 November 2017

M Salmona

9

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24 November 2017

P Piccardo

10

1 reference

Europe PubMed Central

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24 November 2017

B Ghetti

11

1 reference

Europe PubMed Central

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24 November 2017

R C Beavis

12

1 reference

Europe PubMed Central

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24 November 2017

O Bugiani

13

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24 November 2017

B Frangione

14

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24 November 2017

F Prelli

15

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24 November 2017

language of work or name

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publication date

21 November 2000

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24 November 2017

Journal of Biological Chemistry

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24 November 2017

276

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24 November 2017

8

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24 November 2017

6009-6015

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Europe PubMed Central

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24 November 2017

Über eine eigenartige hereditär- familiäre Erkrankung des Zentralnervensystems

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M007062200

21 January 2018

Linkage of a prion protein missense variant to Gerstmann-Sträussler syndrome

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M007062200

21 January 2018

Pro----leu change at position 102 of prion protein is the most common but not the sole mutation related to Gerstmann-Sträussler syndrome

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M007062200

21 January 2018

A prion protein variant in a family with the telencephalic form of Gerstmann-Straussler-Scheinker syndrome

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M007062200

21 January 2018

Linkage of the Indiana kindred of Gerstmann-Sträussler-Scheinker disease to the prion protein gene

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M007062200

21 January 2018

Mutant prion proteins in Gerstmann-Sträussler-Scheinker disease with neurofibrillary tangles

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M007062200

21 January 2018

Novel missense variants of prion protein in Creutzfeldt-Jakob disease or Gerstmann-Sträussler syndrome

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M007062200

21 January 2018

Phenotypic variability of Gerstmann-Sträussler-Scheinker disease is associated with prion protein heterogeneity.

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M007062200

21 January 2018

Gerstmann-Sträussler-Scheinker disease: immunohistological and experimental studies

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M007062200

21 January 2018

Prion protein preamyloid and amyloid deposits in Gerstmann-Sträussler-Scheinker disease, Indiana kindred

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M007062200

21 January 2018

Prion protein amyloidosis

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M007062200

21 January 2018

Molecular biology of prion diseases

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M007062200

21 January 2018

Identification of the prion protein allotypes which accumulate in the brain of sporadic and familial Creutzfeldt-Jakob disease patients.

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M007062200

21 January 2018

Insoluble wild-type and protease-resistant mutant prion protein in brains of patients with inherited prion disease

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M007062200

21 January 2018

Immunochemical, molecular genetic, and transmission studies on a case of Gerstmann-Straussler-Scheinker syndrome

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M007062200

21 January 2018

Endogenous proteolytic cleavage of normal and disease-associated isoforms of the human prion protein in neural and non-neural tissues

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M007062200

21 January 2018

Structural characterization of protein tryptic peptides via liquid chromatography/mass spectrometry and collision-induced dissociation of their doubly charged molecular ions

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M007062200

21 January 2018

Synthetic peptides homologous to prion protein residues 106-147 form amyloid-like fibrils in vitro

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M007062200

21 January 2018

Proteinase-K-resistant prion protein isoforms in Gerstmann-Sträussler-Scheinker disease (Indiana kindred).

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M007062200

21 January 2018

Different patterns of truncated prion protein fragments correlate with distinct phenotypes in P102L Gerstmann-Sträussler-Scheinker disease

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M007062200

21 January 2018

A transmembrane form of the prion protein in neurodegenerative disease

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M007062200

21 January 2018

Biogenesis and transmembrane orientation of the cellular isoform of the scrapie prion protein [published errratum appears in Mol Cell Biol 1987 May;7(5):2035]

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M007062200

21 January 2018

Evidence for a secretory form of the cellular prion protein.

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M007062200

21 January 2018

Unusual topogenic sequence directs prion protein biogenesis

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M007062200

21 January 2018

Transmissible and genetic prion diseases share a common pathway of neurodegeneration

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M007062200

21 January 2018

NMR solution structure of the human prion protein

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M007062200

21 January 2018

An amber mutation of prion protein in Gerstmann-Sträussler syndrome with mutant PrP plaques

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M007062200

21 January 2018

Vascular variant of prion protein cerebral amyloidosis with tau-positive neurofibrillary tangles: the phenotype of the stop codon 145 mutation in PRNP.

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M007062200

21 January 2018

Predicted alpha-helical regions of the prion protein when synthesized as peptides form amyloid

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M007062200

21 January 2018

Conformational transitions in peptides containing two putative alpha-helices of the prion protein.

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M007062200

21 January 2018

Purification and structural studies of a major scrapie prion protein

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M007062200

21 January 2018

Recombinant scrapie-like prion protein of 106 amino acids is soluble

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M007062200

21 January 2018

Prion protein of 106 residues creates an artifical transmission barrier for prion replication in transgenic mice

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M007062200

21 January 2018

A synthetic peptide initiates Gerstmann-Sträussler-Scheinker (GSS) disease in transgenic mice

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M007062200

21 January 2018

Identifiers

10.1074/JBC.M007062200

1 reference

Europe PubMed Central

PubMed publication ID

24 November 2017

PubMed publication ID

1 reference

Europe PubMed Central

PubMed publication ID

24 November 2017

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