(Q43636858)

25 November 2017

Evidence that systemic gentamicin suppresses premature stop mutations in patients with cystic fibrosis (English)

1 reference

25 November 2017

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12

Sorscher EJ

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25 November 2017

Clancy JP

1

1 reference

25 November 2017

Bebök Z

2

1 reference

25 November 2017

Ruiz F

3

1 reference

25 November 2017

King C

4

1 reference

25 November 2017

Jones J

5

1 reference

25 November 2017

Walker L

6

1 reference

25 November 2017

Greer H

7

1 reference

25 November 2017

Hong J

8

1 reference

25 November 2017

Wing L

9

1 reference

25 November 2017

Macaluso M

10

1 reference

25 November 2017

Lyrene R

11

1 reference

25 November 2017

Bedwell DM

13

1 reference

25 November 2017

language of work or name

English

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publication date

1 June 2001

1 reference

American Journal of Respiratory and Critical Care Medicine

25 November 2017

1 reference

25 November 2017

163

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25 November 2017

7

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25 November 2017

1683-1692

1 reference

Identification of the cystic fibrosis gene: cloning and characterization of complementary DNA

25 November 2017

1 reference

https://api.crossref.org/works/10.1164%2FAJRCCM.163.7.2004001

Demonstration That CFTR Is a Chloride Channel by Alteration of Its Anion Selectivity

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FAJRCCM.163.7.2004001

Purification and functional reconstitution of the cystic fibrosis transmembrane conductance regulator (CFTR)

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FAJRCCM.163.7.2004001

Phosphorylation of the R domain by cAMP-dependent protein kinase regulates the CFTR chloride channel

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FAJRCCM.163.7.2004001

CFTR regulates outwardly rectifying chloride channels through an autocrine mechanism involving ATP

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FAJRCCM.163.7.2004001

CFTR as a cAMP-dependent regulator of sodium channels

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FAJRCCM.163.7.2004001

Genotype-phenotype correlations in cystic fibrosis

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FAJRCCM.163.7.2004001

Severe deficiency of cystic fibrosis transmembrane conductance regulator messenger RNA carrying nonsense mutations R553X and W1316X in respiratory epithelial cells of patients with cystic fibrosis

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FAJRCCM.163.7.2004001

Suppression of a CFTR premature stop mutation in a bronchial epithelial cell line

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FAJRCCM.163.7.2004001

Aminoglycoside antibiotics restore dystrophin function to skeletal muscles of mdx mice

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FAJRCCM.163.7.2004001

Long-term culture of normal and cystic fibrosis epithelial cells grown under serum-free conditions

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FAJRCCM.163.7.2004001

Cystic fibrosis transmembrane conductance regulator (CFTR) nucleotide-binding domain 1 (NBD-1) and CFTR truncated within NBD-1 target to the epithelial plasma membrane and increase anion permeability

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FAJRCCM.163.7.2004001

In vivo nasal potential difference: techniques and protocols for assessing efficacy of gene transfer in cystic fibrosis

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FAJRCCM.163.7.2004001

Relationship between airway ion transport and a mild pulmonary disease mutation in CFTR.

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FAJRCCM.163.7.2004001

DeltaF508 CFTR protein expression in tissues from patients with cystic fibrosis

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FAJRCCM.163.7.2004001

Nasal application of the cationic liposome DC-Chol:DOPE does not alter ion transport, lung function or bacterial growth

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FAJRCCM.163.7.2004001

Adenovirus-mediated gene transfer transiently corrects the chloride transport defect in nasal epithelia of patients with cystic fibrosis.

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FAJRCCM.163.7.2004001

Cationic lipid-mediated CFTR gene transfer to the lungs and nose of patients with cystic fibrosis: a double-blind placebo-controlled trial.

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FAJRCCM.163.7.2004001

A placebo-controlled study of liposome-mediated gene transfer to the nasal epithelium of patients with cystic fibrosis.

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FAJRCCM.163.7.2004001

Comparison of DNA-lipid complexes and DNA alone for gene transfer to cystic fibrosis airway epithelia in vivo

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FAJRCCM.163.7.2004001

Efficiency of gene transfer for restoration of normal airway epithelial function in cystic fibrosis

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FAJRCCM.163.7.2004001

In vitro assessment of variables affecting the efficiency and efficacy of adenovirus-mediated gene transfer to cystic fibrosis airway epithelia

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FAJRCCM.163.7.2004001

Liposome-mediated CFTR gene transfer to the nasal epithelium of patients with cystic fibrosis

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FAJRCCM.163.7.2004001

10.1164/AJRCCM.163.7.2004001

21 January 2018

Identifiers

DOI

1 reference

25 November 2017

1 reference