(Q46468449)

22 December 2017

title

Failure of bone morphogenetic protein receptor trafficking in pulmonary arterial hypertension: potential for rescue (English)

1 reference

22 December 2017

1 reference

arterial hypertension

1 reference

6

1 reference

22 December 2017

Nicholas W Morrell

object named as

Nicholas W Morrell

7

0 references

author name string

Anastasia Sobolewski

1

1 reference

22 December 2017

Nung Rudarakanchana

2

1 reference

22 December 2017

Paul D Upton

3

1 reference

22 December 2017

Jun Yang

4

1 reference

22 December 2017

Trina K Crilley

5

1 reference

22 December 2017

publication date

21 July 2008

1 reference

22 December 2017

published in

Human Molecular Genetics

1 reference

22 December 2017

volume

17

1 reference

22 December 2017

page(s)

3180-3190

1 reference

22 December 2017

issue

20

1 reference

22 December 2017

Distribution of obstructive intimal lesions and their cellular phenotypes in chronic pulmonary hypertension. A morphometric and immunohistochemical study

cites work

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDN214

Heterozygous germline mutations in BMPR2, encoding a TGF-beta receptor, cause familial primary pulmonary hypertension

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDN214

Familial primary pulmonary hypertension (gene PPH1) is caused by mutations in the bone morphogenetic protein receptor-II gene

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDN214

Dysfunctional Smad Signaling Contributes to Abnormal Smooth Muscle Cell Proliferation in Familial Pulmonary Arterial Hypertension

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDN214

Functional analysis of bone morphogenetic protein type II receptor mutations underlying primary pulmonary hypertension

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDN214

Functional heterogeneity of bone morphogenetic protein receptor-II mutants found in patients with primary pulmonary hypertension

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDN214

Stoichiometric imbalance in the receptor complex contributes to dysfunctional BMPR-II mediated signalling in pulmonary arterial hypertension

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDN214

Cloning and characterization of a human type II receptor for bone morphogenetic proteins

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDN214

Functional characterization of bone morphogenetic protein binding sites and Smad1/5 activation in human vascular cells

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDN214

Smad transcription factors

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDN214

Functional rescue of the constitutively internalized V2 vasopressin receptor mutant R137H by the pharmacological chaperone action of SR49059.

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDN214

Functional rescue of vasopressin V2 receptor mutants in MDCK cells by pharmacochaperones: relevance to therapy of nephrogenic diabetes insipidus

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDN214

Rescue of vasopressin V2 receptor mutants by chemical chaperones: specificity and mechanism

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDN214

Maintaining low Ca2+ level in the endoplasmic reticulum restores abnormal endogenous F508del-CFTR trafficking in airway epithelial cells.

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDN214

Calcium-pump inhibitors induce functional surface expression of Delta F508-CFTR protein in cystic fibrosis epithelial cells

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDN214

Evidence of CFTR function in cystic fibrosis after systemic administration of 4-phenylbutyrate

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDN214

Bone morphogenetic protein receptor complexes on the surface of live cells: a new oligomerization mode for serine/threonine kinase receptors

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDN214

Chemical chaperones reduce ER stress and restore glucose homeostasis in a mouse model of type 2 diabetes

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDN214

Traffic jams II: an update of diseases of intracellular transport

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDN214

Cell biology of membrane trafficking in human disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDN214

SERCA pump inhibitors do not correct biosynthetic arrest of deltaF508 CFTR in cystic fibrosis

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDN214

Thapsigargin or curcumin does not promote maturation of processing mutants of the ABC transporters, CFTR, and P-glycoprotein

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDN214

Suppressive effects of 4-phenylbutyrate on the aggregation of Pael receptors and endoplasmic reticulum stress

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDN214

Organic solutes rescue the functional defect in delta F508 cystic fibrosis transmembrane conductance regulator.

21 January 2018

1 reference

https://api.crossref.org/works/10.1093%2FHMG%2FDDN214

21 January 2018

Identifiers

DOI

10.1093/HMG/DDN214

1 reference

22 December 2017

PubMed ID

18647753

1 reference

22 December 2017