(Q47833285)

6 February 2018

title

Identification of the peroxisomal beta-oxidation enzymes involved in the degradation of long-chain dicarboxylic acids (English)

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6 February 2018

hydroxysteroid 17-beta dehydrogenase 4

main subject

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Enoyl-CoA hydratase and 3-hydroxyacyl CoA dehydrogenase

GOA release 2020-03-11

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long-chain-3-hydroxyacyl-CoA dehydrogenase activity

GOA release 2020-03-11

1 reference

GOA release 2020-03-11

4

Ronald J A Wanders

1 reference

6 February 2018

Sacha Ferdinandusse

1

object named as

Sacha Ferdinandusse

1 reference

6 February 2018

author name string

Simone Denis

2

1 reference

6 February 2018

Carlo W T Van Roermund

3

1 reference

6 February 2018

Georges Dacremont

5

1 reference

6 February 2018

publication date

1 April 2004

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6 February 2018

Journal of Lipid Research

published in

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6 February 2018

volume

45

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6 February 2018

issue

6

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6 February 2018

page(s)

1104-1111

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6 February 2018

The microsomal dicarboxylyl-CoA synthetase

cites work

1 reference

https://api.crossref.org/works/10.1194%2FJLR.M300512-JLR200

Peroxisomal and mitochondrial beta-oxidation of monocarboxylyl-CoA, omega-hydroxymonocarboxylyl-CoA and dicarboxylyl-CoA esters in tissues from untreated and clofibrate-treated rats

21 January 2018

1 reference

https://api.crossref.org/works/10.1194%2FJLR.M300512-JLR200

Products and intermediates of the beta-oxidation of [U-14C]hexadecanedionoyl-mono-CoA by rat liver peroxisomes and mitochondria

21 January 2018

1 reference

https://api.crossref.org/works/10.1194%2FJLR.M300512-JLR200

Characteristic acylcarnitine profiles in inherited defects of peroxisome biogenesis: a novel tool for screening diagnosis using tandem mass spectrometry

21 January 2018

1 reference

https://api.crossref.org/works/10.1194%2FJLR.M300512-JLR200

Rhizomelic chondrodysplasia punctata is caused by deficiency of human PEX7, a homologue of the yeast PTS2 receptor

21 January 2018

1 reference

https://api.crossref.org/works/10.1194%2FJLR.M300512-JLR200

Rhizomelic chondrodysplasia punctata is a peroxisomal protein targeting disease caused by a non-functional PTS2 receptor

21 January 2018

1 reference

https://api.crossref.org/works/10.1194%2FJLR.M300512-JLR200

Human PEX7 encodes the peroxisomal PTS2 receptor and is responsible for rhizomelic chondrodysplasia punctata

21 January 2018

1 reference

https://api.crossref.org/works/10.1194%2FJLR.M300512-JLR200

The mitochondrial carnitine palmitoyltransferase system. From concept to molecular analysis

21 January 2018

1 reference

https://api.crossref.org/works/10.1194%2FJLR.M300512-JLR200

Disorders of mitochondrial fatty acyl-CoA beta-oxidation

21 January 2018

1 reference

https://api.crossref.org/works/10.1194%2FJLR.M300512-JLR200

X-linked adrenoleukodystrophy: genes, mutations, and phenotypes

21 January 2018

1 reference

https://api.crossref.org/works/10.1194%2FJLR.M300512-JLR200

Large deletion of the peroxisomal acyl-CoA oxidase gene in pseudoneonatal adrenoleukodystrophy

21 January 2018

1 reference

https://api.crossref.org/works/10.1194%2FJLR.M300512-JLR200

Peroxisomal D-hydroxyacyl-CoA dehydrogenase deficiency: resolution of the enzyme defect and its molecular basis in bifunctional protein deficiency

21 January 2018

1 reference

https://api.crossref.org/works/10.1194%2FJLR.M300512-JLR200

Rhizomelic chondrodysplasia punctata, a peroxisomal biogenesis disorder caused by defects in Pex7p, a peroxisomal protein import receptor: a minireview

21 January 2018

1 reference

https://api.crossref.org/works/10.1194%2FJLR.M300512-JLR200

PCR-synthesis of marker cassettes with long flanking homology regions for gene disruptions in S. cerevisiae

21 January 2018

1 reference

https://api.crossref.org/works/10.1194%2FJLR.M300512-JLR200

Enoyl-CoA hydratase deficiency: identification of a new type of D-bifunctional protein deficiency

21 January 2018

1 reference

https://api.crossref.org/works/10.1194%2FJLR.M300512-JLR200

Peroxisomal straight-chain Acyl-CoA oxidase and D-bifunctional protein are essential for the retroconversion step in docosahexaenoic acid synthesis

21 January 2018

1 reference

https://api.crossref.org/works/10.1194%2FJLR.M300512-JLR200

Identification of the peroxisomal beta-oxidation enzymes involved in the degradation of leukotrienes.

21 January 2018

1 reference

https://api.crossref.org/works/10.1194%2FJLR.M300512-JLR200

Physiological role of D-3-hydroxyacyl-CoA dehydratase/D-3-hydroxyacyl-CoA dehydrogenase bifunctional protein

21 January 2018

1 reference

https://api.crossref.org/works/10.1194%2FJLR.M300512-JLR200

Absence of spontaneous peroxisome proliferation in enoyl-CoA Hydratase/L-3-hydroxyacyl-CoA dehydrogenase-deficient mouse liver. Further support for the role of fatty acyl CoA oxidase in PPARalpha ligand metabolism

21 January 2018

1 reference

https://api.crossref.org/works/10.1194%2FJLR.M300512-JLR200

The use of Pseudomonas acyl-CoA synthetase to form acyl-CoAs from dicarboxylic fatty acids

21 January 2018

1 reference

https://api.crossref.org/works/10.1194%2FJLR.M300512-JLR200

10.1194/JLR.M300512-JLR200

21 January 2018

Identifiers

DOI

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6 February 2018

PubMed ID

15060085

1 reference

6 February 2018