(Q48900156)

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:21916928%20AND%20SRC:MED&resulttype=core&format=json

12 February 2020

title

Cellular protein quality control and the evolution of aggregates in spinocerebellar ataxia type 3 (SCA3) (English)

1 reference

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12 February 2020

0 references

0 references

spinocerebellar ataxia

1 reference

5

1 reference

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12 February 2020

Harm H Kampinga

9

1 reference

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12 February 2020

author name string

K Seidel

1

1 reference

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12 February 2020

M Meister

2

1 reference

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12 February 2020

G J Dugbartey

3

1 reference

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12 February 2020

M P Zijlstra

4

1 reference

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12 February 2020

E R P Brunt

6

1 reference

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12 February 2020

F W van Leeuwen

7

1 reference

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12 February 2020

U Rüb

8

1 reference

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12 February 2020

W F A den Dunnen

10

1 reference

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12 February 2020

publication date

1 October 2012

1 reference

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Neuropathology and Applied Neurobiology

12 February 2020

published in

1 reference

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12 February 2020

volume

38

1 reference

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12 February 2020

issue

6

1 reference

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12 February 2020

page(s)

548-558

1 reference

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Protein fate in neurodegenerative proteinopathies: polyglutamine diseases join the (mis)fold

12 February 2020

cites work

1 reference

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Nuclear localization of ataxin-3 is required for the manifestation of symptoms in SCA3: in vivo evidence

21 January 2018

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Spinocerebellar ataxia type 3 (SCA3): thalamic neurodegeneration occurs independently from thalamic ataxin-3 immunopositive neuronal intranuclear inclusions.

21 January 2018

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Axonal inclusions in spinocerebellar ataxia type 3.

21 January 2018

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The HSP70 chaperone machinery: J proteins as drivers of functional specificity

21 January 2018

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Structural and functional diversities between members of the human HSPB, HSPH, HSPA, and DNAJ chaperone families.

21 January 2018

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In vivo chaperone activity of heat shock protein 70 and thermotolerance

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A DNAJB chaperone subfamily with HDAC-dependent activities suppresses toxic protein aggregation

21 January 2018

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Levels of DNAJB family members (HSP40) correlate with disease onset in patients with spinocerebellar ataxia type 3.

21 January 2018

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Hsp70 and hsp40 chaperones can inhibit self-assembly of polyglutamine proteins into amyloid-like fibrils

21 January 2018

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Molecular chaperones enhance the degradation of expanded polyglutamine repeat androgen receptor in a cellular model of spinal and bulbar muscular atrophy

21 January 2018

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The ubiquitin-proteasome pathway: on protein death and cell life

21 January 2018

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Immunohistochemical study of neuronal intranuclear and cytoplasmic inclusions in Machado-Joseph disease.

21 January 2018

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The ubiquitin proteasome system in Huntington's disease and the spinocerebellar ataxias

21 January 2018

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p62/SQSTM1 forms protein aggregates degraded by autophagy and has a protective effect on huntingtin-induced cell death

21 January 2018

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Signaling, polyubiquitination, trafficking, and inclusions: sequestosome 1/p62's role in neurodegenerative disease.

21 January 2018

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p62/SQSTM1 binds directly to Atg8/LC3 to facilitate degradation of ubiquitinated protein aggregates by autophagy

21 January 2018

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21 January 2018

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Polyglutamine expansion as a pathological epitope in Huntington's disease and four dominant cerebellar ataxias

21 January 2018

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Disease-specific accumulation of mutant ubiquitin as a marker for proteasomal dysfunction in the brain

21 January 2018

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Modest proteasomal inhibition by aberrant ubiquitin exacerbates aggregate formation in a Huntington disease mouse model

21 January 2018

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Inclusion body formation reduces levels of mutant huntingtin and the risk of neuronal death

21 January 2018

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21 January 2018

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21 January 2018

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21 January 2018

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21 January 2018

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