(Q48975079)

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:15758154%20AND%20SRC:MED&resulttype=core&format=json

9 January 2020

title

Mutant superoxide dismutase 1 forms aggregates in the brain mitochondrial matrix of amyotrophic lateral sclerosis mice (English)

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:15758154%20AND%20SRC:MED&resulttype=core&format=json

amyotrophic lateral sclerosis

9 January 2020

main subject

0 references

2

M Flint Beal

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:15758154%20AND%20SRC:MED&resulttype=core&format=json

9 January 2020

author name string

Chetan Vijayvergiya

series ordinal

1

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:15758154%20AND%20SRC:MED&resulttype=core&format=json

9 January 2020

Jochen Buck

series ordinal

3

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https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:15758154%20AND%20SRC:MED&resulttype=core&format=json

9 January 2020

Giovanni Manfredi

series ordinal

4

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:15758154%20AND%20SRC:MED&resulttype=core&format=json

9 January 2020

language of work or name

English

0 references

publication date

1 March 2005

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:15758154%20AND%20SRC:MED&resulttype=core&format=json

9 January 2020

published in

Journal of Neuroscience

1 reference

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9 January 2020

volume

25

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9 January 2020

issue

10

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9 January 2020

page(s)

2463-2470

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:15758154%20AND%20SRC:MED&resulttype=core&format=json

Variation in the biochemical/biophysical properties of mutant superoxide dismutase 1 enzymes and the rate of disease progression in familial amyotrophic lateral sclerosis kindreds.

9 January 2020

cites work

1 reference

12 December 2020

Formation of high molecular weight complexes of mutant Cu, Zn-superoxide dismutase in a mouse model for familial amyotrophic lateral sclerosis.

1 reference

12 December 2020

Mitochondrial and peroxisomal targeting of 2-methylacyl-CoA racemase in humans

1 reference

12 December 2020

Human Cu/Zn superoxide dismutase (SOD1) overexpression in mice causes mitochondrial vacuolization, axonal degeneration, and premature motoneuron death and accelerates motoneuron disease in mice expressing a familial amyotrophic lateral sclerosis mut

1 reference

12 December 2020

Isolation and subfractionation of mitochondria from animal cells and tissue culture lines

1 reference

12 December 2020

A fraction of yeast Cu,Zn-superoxide dismutase and its metallochaperone, CCS, localize to the intermembrane space of mitochondria. A physiological role for SOD1 in guarding against mitochondrial oxidative damage.

1 reference

12 December 2020

Subcellular distribution of superoxide dismutases (SOD) in rat liver: Cu,Zn-SOD in mitochondria

1 reference

12 December 2020

CuZn superoxide dismutase (SOD1) accumulates in vacuolated mitochondria in transgenic mice expressing amyotrophic lateral sclerosis-linked SOD1 mutations

1 reference

12 December 2020

Histological evidence of protein aggregation in mutant SOD1 transgenic mice and in amyotrophic lateral sclerosis neural tissues

1 reference

12 December 2020

Decreased metallation and activity in subsets of mutant superoxide dismutases associated with familial amyotrophic lateral sclerosis.

1 reference

12 December 2020

A quantitative histochemical assay for activities of mitochondrial electron transport chain complexes in mouse spinal cord sections.

1 reference

12 December 2020

Mutant Cu, Zn superoxide dismutase that causes motoneuron degeneration is present in mitochondria in the CNS

1 reference

12 December 2020

Mutant SOD1 causes motor neuron disease independent of copper chaperone-mediated copper loading

1 reference

12 December 2020

High molecular weight complexes of mutant superoxide dismutase 1: age-dependent and tissue-specific accumulation

1 reference

12 December 2020

Mutated human SOD1 causes dysfunction of oxidative phosphorylation in mitochondria of transgenic mice.

1 reference

12 December 2020

Amyotrophic lateral sclerosis: a proposed mechanism

1 reference

12 December 2020

Familial amyotrophic lateral sclerosis mutants of copper/zinc superoxide dismutase are susceptible to disulfide reduction

1 reference

12 December 2020

Factors controlling the uptake of yeast copper/zinc superoxide dismutase into mitochondria.

1 reference

12 December 2020

ALS-associated mutant SOD1G93A causes mitochondrial vacuolation by expansion of the intermembrane space and by involvement of SOD1 aggregation and peroxisomes

1 reference

12 December 2020

Mechanisms for activating Cu- and Zn-containing superoxide dismutase in the absence of the CCS Cu chaperone

1 reference

12 December 2020

Toxicity of familial ALS-linked SOD1 mutants from selective recruitment to spinal mitochondria.

1 reference

12 December 2020

Amyotrophic lateral sclerosis-associated SOD1 mutant proteins bind and aggregate with Bcl-2 in spinal cord mitochondria

1 reference

12 December 2020

Hepatocyte differentiation and liver progenitor cells

1 reference

12 December 2020

The carboxyl-terminal two-thirds of the ADP/ATP carrier polypeptide contains sufficient information to direct translocation into mitochondria

1 reference

12 December 2020

Superoxide dismutase. Organelle specificity.

1 reference

12 December 2020

Superoxide dismutase: improved assays and an assay applicable to acrylamide gels

1 reference

12 December 2020

Isolation of intracellular membranes by means of sodium carbonate treatment: application to endoplasmic reticulum

1 reference

12 December 2020

An adverse property of a familial ALS-linked SOD1 mutation causes motor neuron disease characterized by vacuolar degeneration of mitochondria

1 reference

12 December 2020

Superoxide dismutase 1 with mutations linked to familial amyotrophic lateral sclerosis possesses significant activity

1 reference

12 December 2020

Mitochondrial Mas70p signal anchor sequence. Mutations in the transmembrane domain that disrupt dimerization but not targeting or membrane insertion

1 reference

12 December 2020

Motor neuron degeneration in mice that express a human Cu,Zn superoxide dismutase mutation

1 reference

12 December 2020

Mutations in Cu/Zn superoxide dismutase gene are associated with familial amyotrophic lateral sclerosis

1 reference

12 December 2020

Motor neurons in Cu/Zn superoxide dismutase-deficient mice develop normally but exhibit enhanced cell death after axonal injury

1 reference

12 December 2020

Isolation, mapping, and genomic structure of an X-linked gene for a subunit of human mitochondrial complex I.

1 reference

12 December 2020

ALS-linked SOD1 mutant G85R mediates damage to astrocytes and promotes rapidly progressive disease with SOD1-containing inclusions.

1 reference

12 December 2020

Aggregation of mutant Cu/Zn superoxide dismutase proteins in a culture model of ALS

1 reference

12 December 2020

Aggregation and Motor Neuron Toxicity of an ALS-Linked SOD1 Mutant Independent from Wild-Type SOD1

1 reference

12 December 2020

Formation of granular cytoplasmic aggregates in COS7 cells expressing mutant Cu/Zn superoxide dismutase associated with familial amyotrophic lateral sclerosis

1 reference

12 December 2020

10.1523/JNEUROSCI.4385-04.2005

Identifiers

DOI

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:15758154%20AND%20SRC:MED&resulttype=core&format=json

9 January 2020

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:15758154%20AND%20SRC:MED&resulttype=core&format=json

9 January 2020

PubMed publication ID

15758154

1 reference