(Q51973005)

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:17681480%20AND%20SRC:MED&resulttype=core&format=json

3 January 2020

title

Improvement in behaviour after substrate deprivation therapy with rhodamine B in a mouse model of MPS IIIA (English)

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:17681480%20AND%20SRC:MED&resulttype=core&format=json

3 January 2020

5

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3 January 2020

author name string

Ainslie L K Roberts

1

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:17681480%20AND%20SRC:MED&resulttype=core&format=json

3 January 2020

Matthew H Rees

2

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:17681480%20AND%20SRC:MED&resulttype=core&format=json

3 January 2020

Sonja Klebe

3

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:17681480%20AND%20SRC:MED&resulttype=core&format=json

3 January 2020

Janice M Fletcher

4

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:17681480%20AND%20SRC:MED&resulttype=core&format=json

3 January 2020

publication date

6 August 2007

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:17681480%20AND%20SRC:MED&resulttype=core&format=json

Molecular Genetics and Metabolism

3 January 2020

published in

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:17681480%20AND%20SRC:MED&resulttype=core&format=json

3 January 2020

volume

92

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:17681480%20AND%20SRC:MED&resulttype=core&format=json

3 January 2020

issue

1-2

1 reference

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3 January 2020

page(s)

115-121

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:17681480%20AND%20SRC:MED&resulttype=core&format=json

Cloning of the sulphamidase gene and identification of mutations in Sanfilippo A syndrome

3 January 2020

cites work

1 reference

https://api.crossref.org/works/10.1016%2FJ.YMGME.2007.06.016

A novel missense mutation in lysosomal sulfamidase is the basis of MPS III A in a spontaneous mouse mutant

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.YMGME.2007.06.016

A mouse model for mucopolysaccharidosis type III A (Sanfilippo syndrome).

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.YMGME.2007.06.016

Inhibition of glycosaminoglycan synthesis using rhodamine B in a mouse model of mucopolysaccharidosis type IIIA.

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.YMGME.2007.06.016

Enzyme-replacement therapy from birth delays the development of behavior and learning problems in mucopolysaccharidosis type IIIA mice

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.YMGME.2007.06.016

Development of motor deficits in a murine model of mucopolysaccharidosis type IIIA (MPS-IIIA).

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.YMGME.2007.06.016

Characterization of a C57BL/6 congenic mouse strain of mucopolysaccharidosis type IIIA.

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.YMGME.2007.06.016

Enzyme-replacement therapy in mucopolysaccharidosis I.

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.YMGME.2007.06.016

Enzyme replacement therapy in mucopolysaccharidosis VI (Maroteaux-Lamy syndrome).

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.YMGME.2007.06.016

Intracerebral injection of sulfamidase delays neuropathology in murine MPS-IIIA.

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.YMGME.2007.06.016

Improved behavior and neuropathology in the mouse model of Sanfilippo type IIIB disease after adeno-associated virus-mediated gene transfer in the striatum.

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.YMGME.2007.06.016

Significantly increased lifespan and improved behavioral performances by rAAV gene delivery in adult mucopolysaccharidosis IIIB mice

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.YMGME.2007.06.016

Neurological correction of lysosomal storage in a mucopolysaccharidosis IIIB mouse model by adeno-associated virus-mediated gene delivery

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.YMGME.2007.06.016

Adeno-associated virus type 5 reduces learning deficits and restores glutamate receptor subunit levels in MPS VII mice CNS.

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.YMGME.2007.06.016

Transduction of brain by herpes simplex virus vectors

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.YMGME.2007.06.016

Widespread correction of lysosomal storage in the mucopolysaccharidosis type VII mouse brain with a herpes simplex virus type 1 vector expressing beta-glucuronidase

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.YMGME.2007.06.016

Genetic correction of the fetal brain increases the lifespan of mice with the severe multisystemic disease mucopolysaccharidosis type VII.

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.YMGME.2007.06.016

Functional correction of established central nervous system deficits in an animal model of lysosomal storage disease with feline immunodeficiency virus-based vectors

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.YMGME.2007.06.016

Intracranial injection of recombinant adeno-associated virus improves cognitive function in a murine model of mucopolysaccharidosis type VII.

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.YMGME.2007.06.016

Widespread correction of lysosomal storage following intrahepatic injection of a recombinant adeno-associated virus in the adult MPS VII mouse

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.YMGME.2007.06.016

Overcoming the blood-brain barrier with high-dose enzyme replacement therapy in murine mucopolysaccharidosis VII.

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.YMGME.2007.06.016

Rhodamine B inhibition of glycosaminoglycan production by cultured human lip fibroblasts.

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.YMGME.2007.06.016

Augmented memory loss in aging mice after one embryonic exposure to alcohol.

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.YMGME.2007.06.016

Prenatal zinc treatment at the time of acute ethanol exposure limits spatial memory impairments in mouse offspring

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.YMGME.2007.06.016

Genistein-mediated inhibition of glycosaminoglycan synthesis as a basis for gene expression-targeted isoflavone therapy for mucopolysaccharidoses

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.YMGME.2007.06.016

Enzyme replacement therapy for murine mucopolysaccharidosis type VII leads to improvements in behavior and auditory function

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.YMGME.2007.06.016

Developmentally regulated mannose 6-phosphate receptor-mediated transport of a lysosomal enzyme across the blood-brain barrier

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.YMGME.2007.06.016

Prediction of Sanfilippo phenotype severity from immunoquantification of heparan-N-sulfamidase in cultured fibroblasts from mucopolysaccharidosis type IIIA patients

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.YMGME.2007.06.016

Expression and characterization of wild type and mutant recombinant human sulfamidase. Implications for Sanfilippo (Mucopolysaccharidosis IIIA) syndrome

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.YMGME.2007.06.016

Behavioral tests of hippocampal function: simple paradigms complex problems

7 January 2021

1 reference

https://api.crossref.org/works/10.1016%2FJ.YMGME.2007.06.016

10.1016/J.YMGME.2007.06.016

7 January 2021

Identifiers

DOI

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:17681480%20AND%20SRC:MED&resulttype=core&format=json

3 January 2020

1 reference