(Q55881299)

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Cystic fibrosis

scientific article published in The Lancet

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27 January 2020

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Europe PubMed Central

Cystic fibrosis (English)

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Europe PubMed Central

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27 January 2020

cystic fibrosis

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author name string

Brian P O'Sullivan

1

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27 January 2020

Steven D Freedman

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4 May 2009

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Europe PubMed Central

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27 January 2020

1 reference

Europe PubMed Central

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27 January 2020

373

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Europe PubMed Central

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27 January 2020

1891-1904

1 reference

Europe PubMed Central

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27 January 2020

9678

1 reference

Europe PubMed Central

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27 January 2020

Cystic fibrosis mortality and survival in the UK: 1947-2003

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

CFTR regulates outwardly rectifying chloride channels through an autocrine mechanism involving ATP

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

CFTR as a cAMP-dependent regulator of sodium channels

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

The cystic fibrosis transmembrane conductance regulator: an intriguing protein with pleiotropic functions

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

CFTR: more than just a chloride channel

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Cystic fibrosis: impaired bicarbonate secretion and mucoviscidosis

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Spatial patterns of cystic fibrosis mutation spectra in European populations

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Genetic modifiers of lung disease in cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Interactions between secondhand smoke and genes that affect cystic fibrosis lung disease

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Relative contribution of genetic and nongenetic modifiers to intestinal obstruction in cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Geographic distribution and regional origin of 272 cystic fibrosis mutations in European populations. The Biomed CF Mutation Analysis Consortium

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Cystic fibrosis: a worldwide analysis of CFTR mutations--correlation with incidence data and application to screening

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Consensus on the use and interpretation of cystic fibrosis mutation analysis in clinical practice

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

The prevalence of cystic fibrosis in the European Union

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Spectrum of CFTR mutations in Mexican cystic fibrosis patients: identification of five novel mutations (W1098C, 846delT, P750L, 4160insGGGG and 297-1G-->A)

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

The estimated incidence of cystic fibrosis in Japan

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Evidence for periciliary liquid layer depletion, not abnormal ion composition, in the pathogenesis of cystic fibrosis airways disease

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

A physical linkage between cystic fibrosis airway surface dehydration and Pseudomonas aeruginosa biofilms.

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Airway surface dehydration in cystic fibrosis: pathogenesis and therapy

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Effects of reduced mucus oxygen concentration in airway Pseudomonas infections of cystic fibrosis patients

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Cystic fibrosis airway epithelia fail to kill bacteria because of abnormal airway surface fluid.

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Loss of CFTR chloride channels alters salt absorption by cystic fibrosis airway epithelia in vitro.

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Human beta-defensin-1 is a salt-sensitive antibiotic in lung that is inactivated in cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Pathological regulation of arachidonic acid release in cystic fibrosis: the putative basic defect

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Inflammation and infection in naive human cystic fibrosis airway grafts

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Defective lipoxin-mediated anti-inflammatory activity in the cystic fibrosis airway

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Innate immune response in CF airway epithelia: hyperinflammatory?

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Association of cystic fibrosis with abnormalities in fatty acid metabolism.

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Interleukin 8 secretion from monocytes of subjects heterozygous for the deltaF508 cystic fibrosis transmembrane conductance regulator gene mutation is altered

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Cytokine levels in sputum of cystic fibrosis patients before and after antibiotic therapy.

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Dysregulated interleukin-8 secretion and NF-kappaB activity in human cystic fibrosis nasal epithelial cells

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

The inflammatory role of platelets in cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Exaggerated apoptosis and NF-kappaB activation in pancreatic and tracheal cystic fibrosis cells.

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Altered respiratory epithelial cell cytokine production in cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Cystic fibrosis epithelial cells have a receptor for pathogenic bacteria on their apical surface

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Airway epithelial control of Pseudomonas aeruginosa infection in cystic fibrosis.

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Cystic fibrosis: terminology and diagnostic algorithms

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Guidelines for diagnosis of cystic fibrosis in newborns through older adults: Cystic Fibrosis Foundation consensus report

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Diagnostic sweat testing: the Cystic Fibrosis Foundation guidelines.

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Diagnosis of cystic fibrosis by sweat testing: age-specific reference intervals

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Nonclassic cystic fibrosis and CFTR-related diseases

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Primary sclerosing cholangitis in childhood is associated with abnormalities in cystic fibrosis-mediated chloride channel function

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Understanding newborn screening system issues with emphasis on cystic fibrosis screening

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Guidelines for implementation of cystic fibrosis newborn screening programs: Cystic Fibrosis Foundation workshop report.

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Nutritional benefits of neonatal screening for cystic fibrosis. Wisconsin Cystic Fibrosis Neonatal Screening Study Group

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Early diagnosis of cystic fibrosis through neonatal screening prevents severe malnutrition and improves long-term growth. Wisconsin Cystic Fibrosis Neonatal Screening Study Group.

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Growth and nutritional indexes in early life predict pulmonary function in cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Infant care patterns at epidemiologic study of cystic fibrosis sites that achieve superior childhood lung function.

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

The influence of newborn screening for cystic fibrosis on pulmonary outcomes in new South Wales

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Neonatal screening for cystic fibrosis is beneficial even in the context of modern treatment.

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Economic implications of newborn screening for cystic fibrosis: a cost of illness retrospective cohort study

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

CYSTIC FIBROSIS OF THE PANCREAS AND ITS RELATION TO CELIAC DISEASE

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Consensus report on nutrition for pediatric patients with cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Patterns of GI disease in adulthood associated with mutations in the CFTR gene

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Pseudomonas acquisition in young patients with cystic fibrosis: pathophysiology, diagnosis, and management

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Longitudinal assessment of Pseudomonas aeruginosa in young children with cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Cleavage of CXCR1 on neutrophils disables bacterial killing in cystic fibrosis lung disease

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Eradication of early Pseudomonas aeruginosa infection

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Early eradication therapy against Pseudomonas aeruginosa in cystic fibrosis patients.

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Risk factors for rate of decline in forced expiratory volume in one second in children and adolescents with cystic fibrosis.

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Acceleration of lung disease in children with cystic fibrosis after Pseudomonas aeruginosa acquisition

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Approach to eradication of initial Pseudomonas aeruginosa infection in children with cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Prospective evaluation of emerging bacteria in cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Epidemiology ofBurkholderia cepaciacomplex colonisation in cystic fibrosis patients

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Burkholderia cenocepacia lipopolysaccharide, lipid A, and proinflammatory activity.

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Burkholderia cenocepacia and Burkholderia multivorans: influence on survival in cystic fibrosis.

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Impact of Burkholderia dolosa on lung function and survival in cystic fibrosis.

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Persistent methicillin-resistant Staphylococcus aureus and rate of FEV1 decline in cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Association between Stenotrophomonas maltophilia and lung function in cystic fibrosis.

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Nontuberculous mycobacteria. I: multicenter prevalence study in cystic fibrosis.

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Multicenter cross-sectional study of nontuberculous mycobacterial infections among cystic fibrosis patients, Israel

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Allergic bronchopulmonary aspergillosis in cystic fibrosis--state of the art: Cystic Fibrosis Foundation Consensus Conference

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Allergic bronchopulmonary aspergillosis in cystic fibrosis. A European epidemiological study. Epidemiologic Registry of Cystic Fibrosis.

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Epidemiology of cystic fibrosis-related diabetes

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Glucose tolerance, insulin secretion, and insulin sensitivity in children and adolescents with cystic fibrosis and no prior history of diabetes

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Diabetes is associated with dramatically decreased survival in female but not male subjects with cystic fibrosis.

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Management of cystic fibrosis-related diabetes

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Guide to bone health and disease in cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Cystic Fibrosis Adult Care

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Impact of pregnancy on women with cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Factors influencing outcomes in cystic fibrosis: a center-based analysis.

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Cystic fibrosis pulmonary guidelines: chronic medications for maintenance of lung health.

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

A multicenter study of alternate-day prednisone therapy in patients with cystic fibrosis. Cystic Fibrosis Foundation Prednisone Trial Group

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Multicenter Randomized Controlled Trial of Withdrawal of Inhaled Corticosteroids in Cystic Fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Intravenous colistin sulphomethate in acute respiratory exacerbations in adult patients with cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Colistin inhalation therapy in cystic fibrosis patients with chronic Pseudomonas aeruginosa lung infection

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

A randomised clinical trial of nebulised tobramycin or colistin in cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Restoring airway surface liquid in cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

A controlled trial of long-term inhaled hypertonic saline in patients with cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Mucus clearance and lung function in cystic fibrosis with hypertonic saline

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Pilot study of safety and tolerability of inhaled hypertonic saline in infants with cystic fibrosis.

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Erythromycin and diffuse panbronchiolitis

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Effect of clarithromycin on airway obstruction and inflammatory markers in induced sputum in cystic fibrosis: a pilot study

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Long term azithromycin in children with cystic fibrosis: a randomised, placebo-controlled crossover trial

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Effect of long term treatment with azithromycin on disease parameters in cystic fibrosis: a randomised trial.

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Azithromycin in patients with cystic fibrosis chronically infected with Pseudomonas aeruginosa: a randomized controlled trial

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Ribosome protection prevents azithromycin-mediated quorum-sensing modulation and stationary-phase killing of Pseudomonas aeruginosa

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Macrolide activities beyond their antimicrobial effects: macrolides in diffuse panbronchiolitis and cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Effect of high-dose ibuprofen in patients with cystic fibrosis.

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

High-dose ibuprofen in cystic fibrosis: Canadian safety and effectiveness trial

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Use of high-dose ibuprofen in a pediatric cystic fibrosis center

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Antibiotic prophylaxis in infants and young children with cystic fibrosis: a randomized controlled trial

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Neonatal screening for cystic fibrosis in Wales and the West Midlands: clinical assessment after five years of screening

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Prognosis in cystic fibrosis treated with continuous flucloxacillin from the neonatal period

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Prophylactic antibiotics in cystic fibrosis: a conviction without evidence?

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Frequent antibiotic therapy improves survival of cystic fibrosis patients with chronic Pseudomonas aeruginosa infection

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Reduction of sputum Pseudomonas aeruginosa density by antibiotics improves lung function in cystic fibrosis more than do bronchodilators and chest physiotherapy alone

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Predictors of pulmonary exacerbations in patients with cystic fibrosis infected with multi-resistant bacteria.

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Exacerbations in cystic fibrosis. 1: Epidemiology and pathogenesis

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Exacerbations in cystic fibrosis: 2 . prevention.

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Exacerbations in cystic fibrosis: 3--Management.

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Antibiotic therapy against Pseudomonas aeruginosa in cystic fibrosis: a European consensus.

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Long term clinical outcome of home and hospital intravenous antibiotic treatment in adults with cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Home versus hospital intravenous antibiotic therapy for acute pulmonary exacerbations in children with cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Chest physiotherapy compared to no chest physiotherapy for cystic fibrosis.

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Evidence for physical therapies (airway clearance and physical training) in cystic fibrosis: an overview of five Cochrane systematic reviews

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Nonpharmacologic airway clearance therapies: ACCP evidence-based clinical practice guidelines

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Chest physiotherapy in infants with cystic fibrosis: to tip or not? A five-year study

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Physical training for cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Lung transplantation and survival in children with cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Solid benefit of lung transplantation for some children with cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Lung transplantation in children with cystic fibrosis: a view from Europe.

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Advances in lung transplantation for patients who have cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Registry of the International Society for Heart and Lung Transplantation: twenty-fourth official adult lung and heart-lung transplantation report-2007.

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Impact ofBurkholderiaInfection on Lung Transplantation in Cystic Fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Randomised placebo controlled trial of non-invasive ventilation for hypercapnia in cystic fibrosis.

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

A comparison of survival, growth, and pulmonary function in patients with cystic fibrosis in Boston and Toronto

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Longitudinal changes in growth parameters are correlated with changes in pulmonary function in children with cystic fibrosis.

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Comparison of monoclonal and polyclonal ELISAs for fecal elastase in patients with cystic fibrosis and pancreatic insufficiency

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Survey of breast-feeding practices and outcomes in the cystic fibrosis population

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

From registry to quality management: the German Cystic Fibrosis Quality Assessment project 1995 2006.

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Patient registry analyses: seize the data, but caveat lector

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Production of CFTR-null and CFTR-DeltaF508 heterozygous pigs by adeno-associated virus-mediated gene targeting and somatic cell nuclear transfer

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Adeno-associated virus-targeted disruption of the CFTR gene in cloned ferrets.

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Disruption of the CFTR gene produces a model of cystic fibrosis in newborn pigs

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

PTC124 targets genetic disorders caused by nonsense mutations

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

PTC124 is an orally bioavailable compound that promotes suppression of the human CFTR-G542X nonsense allele in a CF mouse model

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Effectiveness of PTC124 treatment of cystic fibrosis caused by nonsense mutations: a prospective phase II trial

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

CFTR and chaperones: processing and degradation.

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Sick chaperones, cellular stress, and disease

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Sodium 4-phenylbutyrate downregulates Hsc70: implications for intracellular trafficking of DeltaF508-CFTR

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Defective function of the cystic fibrosis-causing missense mutation G551D is recovered by genistein

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Curcumin, a major constituent of turmeric, corrects cystic fibrosis defects

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Hsp90 cochaperone Aha1 downregulation rescues misfolding of CFTR in cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Molecular targeting of CFTR as a therapeutic approach to cystic fibrosis.

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Emerging drug treatments for cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Preclinical evidence that sildenafil and vardenafil activate chloride transport in cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Inhalation of Moli1901 in patients with cystic fibrosis.

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Phase 2 randomized safety and efficacy trial of nebulized denufosol tetrasodium in cystic fibrosis.

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Administration of an adenovirus containing the human CFTR cDNA to the respiratory tract of individuals with cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Aerosol and lobar administration of a recombinant adenovirus to individuals with cystic fibrosis. I. Methods, safety, and clinical implications

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Physical and biological barriers to viral vector-mediated delivery of genes to the airway epithelium

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Correlation between DNA transfer and cystic fibrosis airway epithelial cell correction after recombinant adeno-associated virus serotype 2 gene therapy

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Repeated Aerosolized AAV-CFTR for Treatment of Cystic Fibrosis: A Randomized Placebo-Controlled Phase 2B Trial

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Effect of Pseudomonas-induced chronic lung inflammation on specific cytotoxic T-cell responses to adenoviral vectors in mice

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Gene therapy progress and prospects: cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0140-6736%2809%2960327-5

7 January 2021

based on heuristic

inferred from DOI database lookup

Identifiers

10.1016/S0140-6736(09)60327-5

1 reference

Europe PubMed Central

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:19403164%20AND%20SRC:MED&resulttype=core&format=json

27 January 2020

1 reference

Europe PubMed Central

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:19403164%20AND%20SRC:MED&resulttype=core&format=json

27 January 2020

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