(Q80752057)

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:17680360%20AND%20SRC:MED&resulttype=core&format=json

3 January 2020

title

Inhibition of brain energy metabolism by the branched-chain amino acids accumulating in maple syrup urine disease (English)

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:17680360%20AND%20SRC:MED&resulttype=core&format=json

maple syrup urine disease

3 January 2020

main subject

1 reference

Angela M Sgaravatti

2

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:17680360%20AND%20SRC:MED&resulttype=core&format=json

3 January 2020

Rafael B Rosa

3

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:17680360%20AND%20SRC:MED&resulttype=core&format=json

3 January 2020

Patrícia F Schuck

4

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:17680360%20AND%20SRC:MED&resulttype=core&format=json

3 January 2020

Vanessa Grando

5

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:17680360%20AND%20SRC:MED&resulttype=core&format=json

3 January 2020

Anna L Schmidt

6

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:17680360%20AND%20SRC:MED&resulttype=core&format=json

3 January 2020

Gustavo C Ferreira

7

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:17680360%20AND%20SRC:MED&resulttype=core&format=json

3 January 2020

Marcos L S Perry

8

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:17680360%20AND%20SRC:MED&resulttype=core&format=json

3 January 2020

Carlos S Dutra-Filho

9

1 reference

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3 January 2020

publication date

8 August 2007

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:17680360%20AND%20SRC:MED&resulttype=core&format=json

3 January 2020

published in

Neurochemical Research

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:17680360%20AND%20SRC:MED&resulttype=core&format=json

3 January 2020

volume

33

1 reference

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3 January 2020

issue

1

1 reference

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3 January 2020

page(s)

114-124

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:17680360%20AND%20SRC:MED&resulttype=core&format=json

An evaluation of the measurement of the activities of complexes I-IV in the respiratory chain of human skeletal muscle mitochondria.

3 January 2020

cites work

1 reference

12 December 2020

Lipid peroxidation in mitochondria

1 reference

12 December 2020

Effect of alpha-ketoisocaproate and leucine on the in vivo oxidation of glutamate and glutamine in the rat brain

1 reference

12 December 2020

Maple syrup urine disease: metabolic decompensation monitored by proton magnetic resonance imaging and spectroscopy

1 reference

12 December 2020

Differential inhibitory action of nitric oxide and peroxynitrite on mitochondrial electron transport

1 reference

12 December 2020

Effects of branched chain alpha-ketoacids on the metabolism of isolated rat liver cells. III. Interactions with pyruvate dehydrogenase

1 reference

12 December 2020

Glutamate triggers rapid glucose transport stimulation in astrocytes as evidenced by real-time confocal microscopy.

1 reference

12 December 2020

Inhibition of brain glutamic acid decarboxylase by phenylalanine, valine, and leucine derivatives: a suggestion concerning the etiology of the neurological defect in phenylketonuria and branched-chain ketonuria.

1 reference

12 December 2020

Neuroenergetics: calling upon astrocytes to satisfy hungry neurons

1 reference

12 December 2020

Maple syrup urine disease: interrelations between branched-chain amino-, oxo- and hydroxyacids; implications for treatment; associations with CNS dysmyelination

1 reference

12 December 2020

Determination of blood glucose using an oxidase-peroxidase system with a non-carcinogenic chromogen

1 reference

12 December 2020

Alpha-ketoisocaproate alters the production of both lactate and aspartate from [U-13C]glutamate in astrocytes: a 13C NMR study

1 reference

12 December 2020

Elevation of amino acids in the interstitial space of the rat brain following infusion of large neutral amino and keto acids by microdialysis: alpha-ketoisocaproate infusion

1 reference

12 December 2020

Inhibition of cytochrome c oxidase activity in rat cerebral cortex and human skeletal muscle by D-2-hydroxyglutaric acid in vitro.

1 reference

12 December 2020

Inhibition of mitochondrial pyruvate transport by phenylpyruvate and alpha-ketoisocaproate

1 reference

12 December 2020

Interrelationships of leucine and glutamate metabolism in cultured astrocytes

1 reference

12 December 2020

Creatine and antioxidant treatment prevent the inhibition of creatine kinase activity and the morphological alterations of C6 glioma cells induced by the branched-chain alpha-keto acids accumulating in maple syrup urine disease

1 reference

12 December 2020

Differential investigation of the capacity of succinate oxidation in human skeletal muscle

1 reference

12 December 2020

Inhibition of acetylcholine synthesis and of carbohydrate utilization by maple-syrup-urine disease metabolites

1 reference

12 December 2020

Inhibition of glutamate uptake into synaptic vesicles of rat brain by the metabolites accumulating in maple syrup urine disease

1 reference

12 December 2020

Localization of endogenous ATPases at the nerve terminal

1 reference

12 December 2020

Control of pyruvate and beta-hydroxybutyrate utilization in rat brain mitochondria and its relevance to phenylketonuria and maple syrup urine disease

1 reference

12 December 2020

Leucine inhibits oxidation of glucose and pyruvate in skeletal muscles during fasting

1 reference

12 December 2020

Branched chain amino acids induce apoptosis in neural cells without mitochondrial membrane depolarization or cytochrome c release: implications for neurological impairment associated with maple syrup urine disease

1 reference

12 December 2020

Abnormal protein and lipid compositions of the cerebral myelin of a patient with maple syrup urine disease

1 reference

12 December 2020

1 reference

12 December 2020

Creatine kinase activity from rat brain is inhibited by branched-chain amino acids in vitro.

1 reference

12 December 2020

Influence of alpha-ketoacids on the respiration of brain in vitro.

1 reference

12 December 2020

Effects of methylmalonate and propionate on uptake of glucose and ketone bodies in vitro by brain of developing rats

1 reference

12 December 2020

Function of leucine in excitatory neurotransmitter metabolism in the central nervous system

1 reference

12 December 2020

Induction of oxidative stress in rat brain by the metabolites accumulating in maple syrup urine disease.

1 reference

12 December 2020

So-called thiamin-responsive maple syrup urine disease: 15-year follow-up of the original patient

1 reference

12 December 2020

Biochemical and molecular investigations in respiratory chain deficiencies

1 reference

12 December 2020

Mitochondrial function is differentially affected upon oxidative stress

1 reference

12 December 2020

Isoleucine, a blood glucose-lowering amino acid, increases glucose uptake in rat skeletal muscle in the absence of increases in AMP-activated protein kinase activity

1 reference

12 December 2020

Serotonin Depletion by Dietary Leucine

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12 December 2020

Myelin proteins: degradation in rat brain initiated by metabolites causative of maple syrup urine disease

1 reference

12 December 2020

Stimulation of lipid peroxidation in vitro in rat brain by the metabolites accumulating in maple syrup urine disease

1 reference

12 December 2020

Inhibition of brain energy metabolism by the alpha-keto acids accumulating in maple syrup urine disease

1 reference

12 December 2020

2-Hydroxybutyrate and 4-hydroxybutyrate inhibit CO2 formation from labeled substrates by rat cerebral cortex

1 reference

12 December 2020

Selective inactivation of alpha-ketoglutarate dehydrogenase and pyruvate dehydrogenase: reaction of lipoic acid with 4-hydroxy-2-nonenal

1 reference

12 December 2020

Protein measurement with the Folin phenol reagent

1 reference

12 December 2020

Inactivation of the 2-ketoglutarate and pyruvate dehydrogenase complexes of beef heart by branched chain keto acids.

1 reference

12 December 2020

Effect of succinate on mitochondrial lipid peroxidation. 2. The protective effect of succinate against functional and structural changes induced by lipid peroxidation

1 reference

12 December 2020

Maple syrup urine disease: diffusion MRI, and proton MR spectroscopy findings

1 reference

12 December 2020

A chemically-induced acute model of maple syrup urine disease in rats for neurochemical studies

1 reference

12 December 2020

MR diffusion imaging and MR spectroscopy of maple syrup urine disease during acute metabolic decompensation

1 reference

12 December 2020

Reduction of large neutral amino acid levels in plasma and brain of hyperleucinemic rats.

1 reference

12 December 2020

MAPLE SYRUP URINE DISEASE, WITH PARTICULAR REFERENCE TO DIETOTHERAPY

1 reference

12 December 2020