(Q24621194)

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:20566636%20AND%20SRC:MED&resulttype=core&format=json

6 February 2020

title

Airway surface liquid volume regulation determines different airway phenotypes in liddle compared with betaENaC-overexpressing mice (English)

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:20566636%20AND%20SRC:MED&resulttype=core&format=json

6 February 2020

0 references

1 reference

8

1 reference

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6 February 2020

author name string

Marcus A Mall

1

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:20566636%20AND%20SRC:MED&resulttype=core&format=json

6 February 2020

Brian Button

2

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:20566636%20AND%20SRC:MED&resulttype=core&format=json

6 February 2020

Bjarki Johannesson

3

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:20566636%20AND%20SRC:MED&resulttype=core&format=json

6 February 2020

Zhe Zhou

4

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:20566636%20AND%20SRC:MED&resulttype=core&format=json

6 February 2020

Alessandra Livraghi

5

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:20566636%20AND%20SRC:MED&resulttype=core&format=json

6 February 2020

Ray A Caldwell

6

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:20566636%20AND%20SRC:MED&resulttype=core&format=json

6 February 2020

Susanne C Schubert

7

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:20566636%20AND%20SRC:MED&resulttype=core&format=json

6 February 2020

Wanda K O'Neal

9

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:20566636%20AND%20SRC:MED&resulttype=core&format=json

6 February 2020

Sylvain Pradervand

10

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:20566636%20AND%20SRC:MED&resulttype=core&format=json

6 February 2020

Edith Hummler

11

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:20566636%20AND%20SRC:MED&resulttype=core&format=json

6 February 2020

Bernard C Rossier

12

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:20566636%20AND%20SRC:MED&resulttype=core&format=json

6 February 2020

Barbara R Grubb

13

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:20566636%20AND%20SRC:MED&resulttype=core&format=json

6 February 2020

Richard C Boucher

14

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:20566636%20AND%20SRC:MED&resulttype=core&format=json

6 February 2020

language of work or name

English

0 references

publication date

21 June 2010

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:20566636%20AND%20SRC:MED&resulttype=core&format=json

Journal of Biological Chemistry

6 February 2020

published in

1 reference

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6 February 2020

volume

285

1 reference

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6 February 2020

page(s)

26945-26955

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:20566636%20AND%20SRC:MED&resulttype=core&format=json

6 February 2020

issue

35

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:20566636%20AND%20SRC:MED&resulttype=core&format=json

SPLUNC1 regulates airway surface liquid volume by protecting ENaC from proteolytic cleavage

6 February 2020

cites work

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2930694

Phosphorylation of Nedd4-2 by Sgk1 regulates epithelial Na(+) channel cell surface expression

7 April 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2930694

Evidence for periciliary liquid layer depletion, not abnormal ion composition, in the pathogenesis of cystic fibrosis airways disease

7 April 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2930694

Cell surface expression of the epithelial Na channel and a mutant causing Liddle syndrome: a quantitative approach

7 April 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2930694

Mechanism by which Liddle's syndrome mutations increase activity of a human epithelial Na+ channel

7 April 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2930694

Increased airway epithelial Na+ absorption produces cystic fibrosis-like lung disease in mice

7 April 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2930694

Epithelial sodium channel and the control of sodium balance: interaction between genetic and environmental factors

7 April 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2930694

A novel mouse Nedd4 protein suppresses the activity of the epithelial Na+ channel

7 April 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2930694

Pathophysiology of gene-targeted mouse models for cystic fibrosis

7 April 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2930694

Structure and function of the CFTR chloride channel

7 April 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2930694

Amiloride-sensitive epithelial Na+ channel is made of three homologous subunits

7 April 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2930694

Liddle's syndrome: heritable human hypertension caused by mutations in the beta subunit of the epithelial sodium channel

7 April 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2930694

Hypertension caused by a truncated epithelial sodium channel gamma subunit: genetic heterogeneity of Liddle syndrome

7 April 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2930694

Identification of the cystic fibrosis gene: genetic analysis

7 April 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2930694

ENaC at the cutting edge: regulation of epithelial sodium channels by proteases

7 April 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2930694

Cystic fibrosis: impaired bicarbonate secretion and mucoviscidosis

27 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2930694

Nav1.4 deregulation in dystrophic skeletal muscle leads to Na+ overload and enhanced cell death.

27 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2930694

Role of cilia, mucus, and airway surface liquid in mucociliary dysfunction: lessons from mouse models

27 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2930694

Soluble mediators, not cilia, determine airway surface liquid volume in normal and cystic fibrosis superficial airway epithelia

27 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2930694

Normal and cystic fibrosis airway surface liquid homeostasis. The effects of phasic shear stress and viral infections

27 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2930694

Neutrophil elastase activates near-silent epithelial Na+ channels and increases airway epithelial Na+ transport.

27 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2930694

Concerted action of ENaC, Nedd4-2, and Sgk1 in transepithelial Na(+) transport

27 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2930694

Death by necrosis. Uncontrollable catastrophe, or is there order behind the chaos?

27 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2930694

Mucus clearance as a primary innate defense mechanism for mammalian airways

27 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2930694

Electrolyte transport in the mammalian colon: mechanisms and implications for disease

27 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2930694

Regulation of the epithelial sodium channel by serine proteases in human airways

27 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2930694

Defective regulation of the epithelial Na+ channel by Nedd4 in Liddle's syndrome.

27 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2930694

Epithelial sodium channel regulated by aldosterone-induced protein sgk.

27 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2930694

Salt restriction induces pseudohypoaldosteronism type 1 in mice expressing low levels of the beta-subunit of the amiloride-sensitive epithelial sodium channel

27 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2930694

The amiloride-inhibitable Na+ conductance is reduced by the cystic fibrosis transmembrane conductance regulator in normal but not in cystic fibrosis airways.

27 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2930694

Abnormalities of nasal potential difference measurement in Liddle's syndrome

27 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2930694

An epithelial serine protease activates the amiloride-sensitive sodium channel

27 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2930694

Diversity of channels generated by different combinations of epithelial sodium channel subunits

27 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2930694

Na+ transport in cystic fibrosis respiratory epithelia. Abnormal basal rate and response to adenylate cyclase activation

27 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2930694

An animal model for cystic fibrosis made by gene targeting

27 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2930694

CFTR as a cAMP-dependent regulator of sodium channels

27 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2930694

Modelling dysregulated Na+ absorption in airway epithelial cells with mucosal nystatin treatment

27 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2930694

Characterization of wild-type and deltaF508 cystic fibrosis transmembrane regulator in human respiratory epithelia

30 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2930694

Subunit composition determines the single channel kinetics of the epithelial sodium channel

30 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2930694

Wild type but not deltaF508 CFTR inhibits Na+ conductance when coexpressed in Xenopus oocytes.

30 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2930694

Anomalies in ion transport in CF mouse tracheal epithelium

30 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2930694

Transcellular sodium transport in cultured cystic fibrosis human nasal epithelium

30 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2930694

Demonstration That CFTR Is a Chloride Channel by Alteration of Its Anion Selectivity

30 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2930694

Development of chronic bronchitis and emphysema in beta-epithelial Na+ channel-overexpressing mice.

30 May 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M110.151803

Dysfunction of the epithelial sodium channel expressed in the kidney of a mouse model for Liddle syndrome

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M110.151803

Aldosterone responsiveness of the epithelial sodium channel (ENaC) in colon is increased in a mouse model for Liddle's syndrome.

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M110.151803

Cleavage in the {gamma}-subunit of the epithelial sodium channel (ENaC) plays an important role in the proteolytic activation of near-silent channels

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M110.151803

Cystic fibrosis transmembrane conductance regulator inhibits epithelial Na+ channels carrying Liddle's syndrome mutations.

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M110.151803

The cytosolic termini of the beta- and gamma-ENaC subunits are involved in the functional interactions between cystic fibrosis transmembrane conductance regulator and epithelial sodium channel.

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M110.151803

The DeltaF508 mutation results in loss of CFTR function and mature protein in native human colon

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M110.151803

Airway surface liquid volume regulates ENaC by altering the serine protease-protease inhibitor balance: a mechanism for sodium hyperabsorption in cystic fibrosis.

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M110.151803

Preventive but not late amiloride therapy reduces morbidity and mortality of lung disease in betaENaC-overexpressing mice.

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M110.151803

Conditional gene expression in the respiratory epithelium of the mouse.

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M110.151803

Dopamine activates amiloride-sensitive sodium channels in alveolar type I cells in lung slice preparations

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M110.151803

Hyperabsorption of Na+ and raised Ca(2+)-mediated Cl- secretion in nasal epithelia of CF mice.

21 January 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2930694

beta-Liddle mutation of the epithelial sodium channel increases alveolar fluid clearance and reduces the severity of hydrostatic pulmonary oedema in mice

28 November 2018

1 reference

12 December 2020

A mouse model for Liddle's syndrome

1 reference

12 December 2020

Mineralocorticoid regulation of epithelial Na+ channels is maintained in a mouse model of Liddle's syndrome

1 reference

12 December 2020

Abnormal Ion Permeation Through Cystic Fibrosis Respiratory Epithelium

1 reference

12 December 2020

Intracellular Cl- activity and cellular Cl- pathways in cultured human airway epithelium

1 reference

12 December 2020

Regulation of Caenorhabditis elegans degenerin proteins by a putative extracellular domain

1 reference

12 December 2020

Identifiers

DOI

10.1074/JBC.M110.151803

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:20566636%20AND%20SRC:MED&resulttype=core&format=json

6 February 2020

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:20566636%20AND%20SRC:MED&resulttype=core&format=json

6 February 2020

1 reference