(Q28277615)

Crossref

https://api.crossref.org/works/10.1007%2FS00018-010-0330-X

The regulation of catalytic activity of the menkes copper-translocating P-type ATPase. Role of high affinity copper-binding sites

21 January 2018

1 reference

12 December 2020

Imaging of the intracellular topography of copper with a fluorescent sensor and by synchrotron x-ray fluorescence microscopy

1 reference

12 December 2020

Three-dimensional structure of the human copper transporter hCTR1.

1 reference

12 December 2020

Mitochondrial free radical generation, oxidative stress, and aging

1 reference

12 December 2020

The mechanism of copper uptake mediated by human CTR1: a mutational analysis.

1 reference

12 December 2020

Essential role for Atox1 in the copper-mediated intracellular trafficking of the Menkes ATPase

1 reference

12 December 2020

Structural basis for the function of the N-terminal domain of the ATPase CopA from Bacillus subtilis

1 reference

12 December 2020

Copper homeostasis in bacteria

1 reference

12 December 2020

The copper-responsive repressor CopR of Lactococcus lactis is a 'winged helix' protein

1 reference

12 December 2020

Cu(I) binding and transfer by the N terminus of the Wilson disease protein

1 reference

12 December 2020

Amyotrophic lateral sclerosis mutations have the greatest destabilizing effect on the apo- and reduced form of SOD1, leading to unfolding and oxidative aggregation.

1 reference

12 December 2020

Spectroscopic studies of metal binding and metal selectivity in Bacillus subtilis BSco, a Homologue of the Yeast Mitochondrial Protein Sco1p

1 reference

12 December 2020

Structure of human Wilson protein domains 5 and 6 and their interplay with domain 4 and the copper chaperone HAH1 in copper uptake

1 reference

12 December 2020

Interdomain communication in calcium pump as revealed in the crystal structures with transmembrane inhibitors

1 reference

12 December 2020

Copper activation of superoxide dismutase 1 (SOD1) in vivo. Role for protein-protein interactions with the copper chaperone for SOD1

1 reference

12 December 2020

Solution structures of a cyanobacterial metallochaperone: insight into an atypical copper-binding motif

1 reference

12 December 2020

Structural model of the CopA copper ATPase of Enterococcus hirae based on chemical cross-linking

1 reference

12 December 2020

Cox11p is required for stable formation of the Cu(B) and magnesium centers of cytochrome c oxidase

1 reference

12 December 2020

Lysine-60 in copper chaperone Atox1 plays an essential role in adduct formation with a target Wilson disease domain

1 reference

12 December 2020

Structure of the ATP binding domain from the Archaeoglobus fulgidus Cu+-ATPase

1 reference

12 December 2020

Biochemical and genetic analyses of yeast and human high affinity copper transporters suggest a conserved mechanism for copper uptake

1 reference

12 December 2020

Yeast Sco1, a protein essential for cytochrome c oxidase function is a Cu(I)-binding protein.

1 reference

12 December 2020

Amyloid-like filaments and water-filled nanotubes formed by SOD1 mutant proteins linked to familial ALS

1 reference

12 December 2020

Undetectable intracellular free copper: the requirement of a copper chaperone for superoxide dismutase

1 reference

12 December 2020

Evidence for Cu(II) reduction as a component of copper uptake by Saccharomyces cerevisiae

1 reference

12 December 2020

The rate and equilibrium constants for a multistep reaction sequence for the aggregation of superoxide dismutase in amyotrophic lateral sclerosis

1 reference

12 December 2020

A physiological role for Saccharomyces cerevisiae copper/zinc superoxide dismutase in copper buffering

1 reference

12 December 2020

Solution structures of the reduced and Cu(I) bound forms of the first metal binding sequence of ATP7A associated with Menkes disease

1 reference

12 December 2020

Dephosphorylation of the calcium pump coupled to counterion occlusion

1 reference

12 December 2020

The Menkes protein (ATP7A; MNK) cycles via the plasma membrane both in basal and elevated extracellular copper using a C-terminal di-leucine endocytic signal

1 reference

12 December 2020

Mechanism of Cu+-transporting ATPases: soluble Cu+ chaperones directly transfer Cu+ to transmembrane transport sites.

1 reference

12 December 2020

Oxidative switches in functioning of mammalian copper chaperone Cox17

1 reference

12 December 2020

A C-terminal domain of the membrane copper pump Ctr1 exchanges copper(I) with the copper chaperone Atx1

1 reference

12 December 2020

C-terminal domain of the membrane copper transporter Ctr1 from Saccharomyces cerevisiae binds four Cu(I) ions as a cuprous-thiolate polynuclear cluster: sub-femtomolar Cu(I) affinity of three proteins involved in copper trafficking

1 reference

12 December 2020

Cellular multitasking: the dual role of human Cu-ATPases in cofactor delivery and intracellular copper balance

1 reference

12 December 2020

Folding studies of Cox17 reveal an important interplay of cysteine oxidation and copper binding

1 reference

12 December 2020

High yield heterologous expression of wild-type and mutant Cu+-ATPase (ATP7B, Wilson disease protein) for functional characterization of catalytic activity and serine residues undergoing copper-dependent phosphorylation

1 reference

12 December 2020

The whole structure of the 13-subunit oxidized cytochrome c oxidase at 2.8 A

1 reference

12 December 2020

Mechanism of Cu,Zn-superoxide dismutase activation by the human metallochaperone hCCS.

1 reference

12 December 2020

Development of a generic approach to native metalloproteomics: application to the quantitative identification of soluble copper proteins in Escherichia coli

1 reference

12 December 2020

characterization of the cytochrome c oxidase assembly factor Cox19 of Saccharomyces cerevisiae

1 reference

12 December 2020

Characterization of the binding interface between the copper chaperone Atx1 and the first cytosolic domain of Ccc2 ATPase

1 reference

12 December 2020

SCO1 and SCO2 act as high copy suppressors of a mitochondrial copper recruitment defect in Saccharomyces cerevisiae

1 reference

12 December 2020

Oxygen and the copper chaperone CCS regulate posttranslational activation of Cu,Zn superoxide dismutase

1 reference

12 December 2020

A widespread transposable element masks expression of a yeast copper transport gene.

1 reference

12 December 2020

Mechanisms for copper acquisition, distribution and regulation

1 reference

12 December 2020

A NMR study of the interaction of a three-domain construct of ATP7A with copper(I) and copper(I)-HAH1: the interplay of domains

1 reference

12 December 2020

Human SCO1 and SCO2 have independent, cooperative functions in copper delivery to cytochrome c oxidase

1 reference

12 December 2020

Identification and functional expression of HAH1, a novel human gene involved in copper homeostasis

1 reference

12 December 2020

Metal Binding Domains 3 and 4 of the Wilson Disease Protein: Solution Structure and Interaction with the Copper(I) Chaperone HAH1 † ‡

1 reference

12 December 2020

Solution structure of Cox11, a novel type of beta-immunoglobulin-like fold involved in CuB site formation of cytochrome c oxidase

1 reference

12 December 2020

Structure of the two transmembrane Cu+ transport sites of the Cu+ -ATPases

1 reference

12 December 2020

Activation by adenosine triphosphate in the phosphorylation kinetics of sodium and potassium ion transport adenosine triphosphatase

1 reference

12 December 2020

Copper-mediated homo-dimerisation for the HAH1 metallochaperone

1 reference

12 December 2020

Supercomplexes in the respiratory chains of yeast and mammalian mitochondria

1 reference

12 December 2020

The delivery of copper for thylakoid import observed by NMR.

1 reference

12 December 2020

Solution structure of the Cu(I) and apo forms of the yeast metallochaperone, Atx1

1 reference

12 December 2020

Solution structure of Sco1: a thioredoxin-like protein Involved in cytochrome c oxidase assembly

1 reference

12 December 2020

Hepatocyte-specific localization and copper-dependent trafficking of the Wilson's disease protein in the liver

1 reference

12 December 2020

Copper-induced trafficking of the cU-ATPases: a key mechanism for copper homeostasis

1 reference

12 December 2020

Mutations of the SCO1 gene in mitochondrial cytochrome c oxidase deficiency with neonatal-onset hepatic failure and encephalopathy.

1 reference

12 December 2020

Characterization of COX17, a yeast gene involved in copper metabolism and assembly of cytochrome oxidase

1 reference

12 December 2020

Selenocysteine positional variants reveal contributions to copper binding from cysteine residues in domains 2 and 3 of human copper chaperone for superoxide dismutase.

1 reference

12 December 2020

Mechanism of CuA assembly

1 reference

12 December 2020

Human Sco1 and Sco2 function as copper-binding proteins

1 reference

12 December 2020

A hemizygous SCO2 mutation in an early onset rapidly progressive, fatal cardiomyopathy

1 reference

12 December 2020

Metallochaperones and metal-transporting ATPases: a comparative analysis of sequences and structures

1 reference

12 December 2020

Structures of Metal Sites of Oxidized Bovine Heart Cytochrome c Oxidase at 2.8 Å

1 reference

12 December 2020

Metalloregulation of FRE1 and FRE2 homologs in Saccharomyces cerevisiae.

1 reference

12 December 2020

An NMR study of the interaction between the human copper(I) chaperone and the second and fifth metal-binding domains of the Menkes protein

1 reference

12 December 2020

ATP-induced conformational changes of the nucleotide-binding domain of Na,K-ATPase

1 reference

12 December 2020

Examination of the role of arginine-143 in the human copper and zinc superoxide dismutase by site-specific mutagenesis

1 reference

12 December 2020

Isolation of a candidate gene for Menkes disease that encodes a potential heavy metal binding protein

1 reference

12 December 2020

The Wilson disease gene: spectrum of mutations and their consequences

1 reference

12 December 2020

Response of gram-positive bacteria to copper stress.

1 reference

12 December 2020

Intracellular trafficking of the human Wilson protein: the role of the six N-terminal metal-binding sites.

1 reference

12 December 2020

Purification and characterization of yeast Sco1p, a mitochondrial copper protein

1 reference

12 December 2020

Molecular immunocytochemistry of the CuZn superoxide dismutase in rat hepatocytes

1 reference

12 December 2020

Familial amyotrophic lateral sclerosis mutants of copper/zinc superoxide dismutase are susceptible to disulfide reduction

1 reference

12 December 2020

A copper metallochaperone for photosynthesis and respiration reveals metal-specific targets, interaction with an importer, and alternative sites for copper acquisition

1 reference

12 December 2020

X-ray crystallographic and analytical ultracentrifugation analyses of truncated and full-length yeast copper chaperones for SOD (LYS7): a dimer-dimer model of LYS7-SOD association and copper delivery

1 reference

12 December 2020

Novel role of antioxidant-1 (Atox1) as a copper-dependent transcription factor involved in cell proliferation

1 reference

12 December 2020

A hint for the function of human Sco1 from different structures

1 reference

12 December 2020

Zn, Cu and Co in cyanobacteria: selective control of metal availability

1 reference

12 December 2020

Metal-free superoxide dismutase forms soluble oligomers under physiological conditions: a possible general mechanism for familial ALS

1 reference

12 December 2020

Mitochondrial matrix copper complex used in metallation of cytochrome oxidase and superoxide dismutase

1 reference

12 December 2020

Mechanisms for activating Cu- and Zn-containing superoxide dismutase in the absence of the CCS Cu chaperone

1 reference

12 December 2020

Mutant SOD1 in neuronal mitochondria causes toxicity and mitochondrial dynamics abnormalities

1 reference

12 December 2020

Redox susceptibility of SOD1 mutants is associated with the differential response to CCS over-expression in vivo

1 reference

12 December 2020

Structural changes in the calcium pump accompanying the dissociation of calcium

1 reference

12 December 2020

Characterization of YpmQ, an accessory protein required for the expression of cytochrome c oxidase in Bacillus subtilis

1 reference

12 December 2020

Oxidation-induced misfolding and aggregation of superoxide dismutase and its implications for amyotrophic lateral sclerosis

1 reference

12 December 2020

Essential Cys-Pro-Cys motif of Caenorhabditis elegans copper transport ATPase

1 reference

12 December 2020

Factors controlling the uptake of yeast copper/zinc superoxide dismutase into mitochondria.

1 reference

12 December 2020

Yeast contain a non-proteinaceous pool of copper in the mitochondrial matrix

1 reference

12 December 2020

Activation of CuZn superoxide dismutases from Caenorhabditis elegans does not require the copper chaperone CCS.

1 reference

12 December 2020

A P-type ATPase importer that discriminates between essential and toxic transition metals

1 reference

12 December 2020

Essential role of Mia40 in import and assembly of mitochondrial intermembrane space proteins

1 reference

12 December 2020

Specific copper transfer from the Cox17 metallochaperone to both Sco1 and Cox11 in the assembly of yeast cytochrome C oxidase.

1 reference

12 December 2020

COX23, a homologue of COX17, is required for cytochrome oxidase assembly

1 reference

12 December 2020

Mitochondrial ATP-independent chaperones

1 reference

12 December 2020

The unusually stable quaternary structure of human Cu,Zn-superoxide dismutase 1 is controlled by both metal occupancy and disulfide status

1 reference

12 December 2020

Cyclic AMP-dependent protein kinase controls energy interconversion during the catalytic cycle of the yeast copper-ATPase.

1 reference

12 December 2020

Mitochondrial copper metabolism and delivery to cytochrome c oxidase

1 reference

12 December 2020

Occurrence of copper proteins through the three domains of life: a bioinformatic approach

1 reference

12 December 2020

Crystal structure of the calcium pump with a bound ATP analogue

1 reference

12 December 2020

Posttranslational modifications in Cu,Zn-superoxide dismutase and mutations associated with amyotrophic lateral sclerosis.

1 reference

12 December 2020

Mitochondrial copper metabolism in yeast: interaction between Sco1p and Cox2p

1 reference

12 December 2020

Mechanisms for protection against copper toxicity

1 reference

12 December 2020

Ctr1 drives intestinal copper absorption and is essential for growth, iron metabolism, and neonatal cardiac function

1 reference

12 December 2020

A fraction of yeast Cu,Zn-superoxide dismutase and its metallochaperone, CCS, localize to the intermembrane space of mitochondria. A physiological role for SOD1 in guarding against mitochondrial oxidative damage.

1 reference

12 December 2020

Heterodimer formation between superoxide dismutase and its copper chaperone

1 reference

12 December 2020

Mitochondrial protein import: precursor oxidation in a ternary complex with disulfide carrier and sulfhydryl oxidase

1 reference

12 December 2020

Structure of a Copper Pump Suggests a Regulatory Role for Its Metal-Binding Domain

1 reference

12 December 2020

Solution structures of the actuator domain of ATP7A and ATP7B, the Menkes and Wilson disease proteins

1 reference

12 December 2020

A structural perspective on copper uptake in eukaryotes

1 reference

12 December 2020

Sulfate acts as phosphate analog on the monomeric catalytic fragment of the CPx-ATPase CopB from Sulfolobus solfataricus

1 reference

12 December 2020

The different intermolecular interactions of the soluble copper-binding domains of the menkes protein, ATP7A.

1 reference

12 December 2020

NMDA receptor activation mediates copper homeostasis in hippocampal neurons

1 reference

12 December 2020

Mitochondrial copper(I) transfer from Cox17 to Sco1 is coupled to electron transfer

1 reference

12 December 2020

The human cytochrome c oxidase assembly factors SCO1 and SCO2 have regulatory roles in the maintenance of cellular copper homeostasis

1 reference

12 December 2020

Cell-specific trafficking suggests a new role for renal ATP7B in the intracellular copper storage

1 reference

12 December 2020

Solution structure of the apo and copper(I)-loaded human metallochaperone HAH1

1 reference

12 December 2020

Mitochondrial superoxide simutase. Site of synthesis and intramitochondrial localization

1 reference

12 December 2020

Copper binding to the N-terminal metal-binding sites or the CPC motif is not essential for copper-induced trafficking of the human Wilson protein (ATP7B)

1 reference

12 December 2020

X-ray absorption spectroscopy of the copper chaperone HAH1 reveals a linear two-coordinate Cu(I) center capable of adduct formation with exogenous thiols and phosphines

1 reference

12 December 2020

Catch me if you can! Oxidative protein trapping in the intermembrane space of mitochondria

1 reference

12 December 2020

Mutations in copper-zinc superoxide dismutase that cause amyotrophic lateral sclerosis alter the zinc binding site and the redox behavior of the protein

1 reference

12 December 2020

Solution structure and backbone dynamics of the Cu(I) and apo forms of the second metal-binding domain of the Menkes protein ATP7A

1 reference

12 December 2020

Cysteine-to-serine mutants of the human copper chaperone for superoxide dismutase reveal a copper cluster at a domain III dimer interface.

1 reference

12 December 2020

Role of the N-Terminal Tail of Metal-Transporting P1B-type ATPases from Genome-Wide Analysis and Molecular Dynamics Simulations

1 reference

12 December 2020

Modeling Protein−Protein Complexes Involved in the CytochromecOxidase Copper-Delivery Pathway

1 reference

12 December 2020

Two Menkes-type atpases supply copper for photosynthesis in Synechocystis PCC 6803.

1 reference

12 December 2020

PrrC from Rhodobacter sphaeroides, a homologue of eukaryotic Sco proteins, is a copper-binding protein and may have a thiol-disulfide oxidoreductase activity.

1 reference

12 December 2020

Copper-regulated trafficking of the Menkes disease copper ATPase is associated with formation of a phosphorylated catalytic intermediate

1 reference

12 December 2020

Copper homeostasis in Enterococcus hirae

1 reference

12 December 2020

Copper(I)-mediated protein-protein interactions result from suboptimal interaction surfaces

1 reference

12 December 2020

The Binding Mode of ATP Revealed by the Solution Structure of the N-domain of Human ATP7A

1 reference

12 December 2020

Chaperone-mediated Cu+ delivery to Cu+ transport ATPases: requirement of nucleotide binding

1 reference

12 December 2020

Suppression mechanisms of COX assembly defects in yeast and human: insights into the COX assembly process

1 reference

12 December 2020

Cytochrome c oxidase deficiency

1 reference

12 December 2020

Chimeras of P-type ATPases and their transcriptional regulators: contributions of a cytosolic amino-terminal domain to metal specificity

1 reference

12 December 2020

The Saccharomyces cerevisiae copper transport protein (Ctr1p). Biochemical characterization, regulation by copper, and physiologic role in copper uptake.

1 reference

12 December 2020

Bioinformatic characterization of p-type ATPases encoded within the fully sequenced genomes of 26 eukaryotes

1 reference

12 December 2020

Biogenesis of cytochrome c oxidase--in vitro approaches to study cofactor insertion into a bacterial subunit I.

1 reference

12 December 2020

A structural-dynamical characterization of human Cox17

1 reference

12 December 2020

Metallochaperones, an intracellular shuttle service for metal ions

1 reference

12 December 2020

Multiple protein domains contribute to the action of the copper chaperone for superoxide dismutase

1 reference

12 December 2020

Solution structure of the N-domain of Wilson disease protein: distinct nucleotide-binding environment and effects of disease mutations

1 reference

12 December 2020

Human SCO2 is required for the synthesis of CO II and as a thiol-disulphide oxidoreductase for SCO1.

1 reference

12 December 2020

Different regulation of wild-type and mutant Cu,Zn superoxide dismutase localization in mammalian mitochondria

1 reference

12 December 2020

The copper chaperone CCS is abundant in neurons and astrocytes in human and rodent brain

1 reference

12 December 2020

Biochemical characterization of the human copper transporter Ctr1

1 reference

12 December 2020

The disulfide relay system of mitochondria is required for the biogenesis of mitochondrial Ccs1 and Sod1.

1 reference

12 December 2020

A copper(I) protein possibly involved in the assembly of CuA center of bacterial cytochrome c oxidase

1 reference

12 December 2020

Structure of the actuator domain from the Archaeoglobus fulgidus Cu(+)-ATPase

1 reference

12 December 2020

Cytochrome oxidase assembly in yeast requires the product of COX11, a homolog of the P. denitrificans protein encoded by ORF3.

1 reference

12 December 2020

Biochemical aspects of active transport

1 reference

12 December 2020

Oxygen-induced maturation of SOD1: a key role for disulfide formation by the copper chaperone CCS.

1 reference

12 December 2020

Cox17 Is Functional When Tethered to the Mitochondrial Inner Membrane

1 reference

12 December 2020

Erv1 mediates the Mia40-dependent protein import pathway and provides a functional link to the respiratory chain by shuttling electrons to cytochrome c.

1 reference

12 December 2020

Superoxide dismutase. An enzymic function for erythrocuprein (hemocuprein)

1 reference

12 December 2020

Evolution of substrate specificities in the P-type ATPase superfamily.

1 reference

12 December 2020

Conserved patterns in the Cu,Zn superoxide dismutase family.

1 reference

12 December 2020

Solution structure of the yeast copper transporter domain Ccc2a in the apo and Cu(I)-loaded states

1 reference

12 December 2020

Mapping the functional interaction of Sco1 and Cox2 in cytochrome oxidase biogenesis

1 reference

12 December 2020

The holo-form of the nucleotide binding domain of the KdpFABC complex from Escherichia coli reveals a new binding mode

1 reference

12 December 2020

Copper exposure induces trafficking of the menkes protein in intestinal epithelium of ATP7A transgenic mice

1 reference

12 December 2020

Phosphorylation regulates copper-responsive trafficking of the Menkes copper transporting P-type ATPase.

1 reference

12 December 2020

Understanding how cells allocate metals using metal sensors and metallochaperones

1 reference

12 December 2020

The distinct roles of the N-terminal copper-binding sites in regulation of catalytic activity of the Wilson's disease protein

1 reference

12 December 2020

Domain organization and movements in heavy metal ion pumps: papain digestion of CopA, a Cu+-transporting ATPase

1 reference

12 December 2020

Identification of a disulfide switch in BsSco, a member of the Sco family of cytochrome c oxidase assembly proteins

1 reference

12 December 2020

Functional roles of metal binding domains of the Archaeoglobus fulgidus Cu(+)-ATPase CopA.

1 reference

12 December 2020

A pivotal role of Zn-binding residues in the function of the copper chaperone for SOD1

1 reference

12 December 2020

A multinuclear copper(I) cluster forms the dimerization interface in copper-loaded human copper chaperone for superoxide dismutase

1 reference

12 December 2020

Subcellular distribution of superoxide dismutases (SOD) in rat liver: Cu,Zn-SOD in mitochondria

1 reference

12 December 2020

The mitochondrial copper metallochaperone Cox17 exists as an oligomeric, polycopper complex.

1 reference

12 December 2020

Evidence for the association of yeast mitochondrial ribosomes with Cox11p, a protein required for the Cu(B) site formation of cytochrome c oxidase

1 reference

12 December 2020

Energetics of copper trafficking between the Atx1 metallochaperone and the intracellular copper transporter, Ccc2

1 reference

12 December 2020

Copper redistribution in Atox1-deficient mouse fibroblast cells

1 reference

12 December 2020

A structural characterization of human SCO2

1 reference

12 December 2020

Copper transport activity of yeast Ctr1 is down-regulated via its C terminus in response to excess copper

1 reference

12 December 2020

NMR structural analysis of the soluble domain of ZiaA-ATPase and the basis of selective interactions with copper metallochaperone Atx1

1 reference

12 December 2020

Nucleotide recognition by CopA, a Cu+-transporting P-type ATPase

1 reference

12 December 2020

MIA40 is an oxidoreductase that catalyzes oxidative protein folding in mitochondria

1 reference

12 December 2020

The Atx1-Ccc2 complex is a metal-mediated protein-protein interaction

1 reference

12 December 2020

Cu/Zn superoxide dismutase-like immunoreactivity in Lewy body-like inclusions of sporadic amyotrophic lateral sclerosis

1 reference

12 December 2020

p53 regulates mitochondrial respiration

1 reference

12 December 2020

Evidence for a novel role of copper-zinc superoxide dismutase in zinc metabolism

1 reference

12 December 2020

Copper acquisition is mediated by YcnJ and regulated by YcnK and CsoR in Bacillus subtilis

1 reference

12 December 2020

Molecular characterization of a copper transport protein in S. cerevisiae: an unexpected role for copper in iron transport

1 reference

12 December 2020

Solution structure and intermolecular interactions of the third metal-binding domain of ATP7A, the Menkes disease protein.

1 reference

12 December 2020

Isolated cytochrome c oxidase deficiency in G93A SOD1 mice overexpressing CCS protein

1 reference

12 December 2020

Molecular genetics and pathophysiology of Menkes disease

1 reference

12 December 2020

Activation of Cu,Zn-superoxide dismutase in the absence of oxygen and the copper chaperone CCS.

1 reference

12 December 2020

Heterodimeric structure of superoxide dismutase in complex with its metallochaperone

1 reference

12 December 2020

Metal-ion regulation of gene expression in yeast.

1 reference

12 December 2020

The copper-transporting ATPases, menkes and wilson disease proteins, have distinct roles in adult and developing cerebellum

1 reference

12 December 2020

Characterization of COX19, a widely distributed gene required for expression of mitochondrial cytochrome oxidase

1 reference

12 December 2020

Oligomerization of mutant SOD1 in mitochondria of motoneuronal cells drives mitochondrial damage and cell toxicity

1 reference

12 December 2020

A limited role for disulfide cross-linking in the aggregation of mutant SOD1 linked to familial amyotrophic lateral sclerosis.

1 reference

12 December 2020

SOD1 and amyotrophic lateral sclerosis: mutations and oligomerization

1 reference

12 December 2020

Role of the copper-binding domain in the copper transport function of ATP7B, the P-type ATPase defective in Wilson disease

1 reference

12 December 2020

A novel copper site in a cyanobacterial metallochaperone

1 reference

12 December 2020

SCO1, a yeast nuclear gene essential for accumulation of mitochondrial cytochrome c oxidase subunit II.

1 reference

12 December 2020

An NMR study of the interaction of the N-terminal cytoplasmic tail of the Wilson disease protein with copper(I)-HAH1.

1 reference

12 December 2020

"Pulling the plug" on cellular copper: the role of mitochondria in copper export

1 reference

12 December 2020

Structural and dynamic aspects related to oligomerization of apo SOD1 and its mutants

1 reference

12 December 2020

Biology, structure and mechanism of P-type ATPases

1 reference

12 December 2020

An atomic-level investigation of the disease-causing A629P mutant of the Menkes protein, ATP7A.

1 reference

12 December 2020

The copper chaperone for superoxide dismutase

1 reference

12 December 2020

The Wilson disease gene is a putative copper transporting P-type ATPase similar to the Menkes gene

1 reference

12 December 2020

Functional analysis of the domains in Cox11.

1 reference

12 December 2020

The functions of Sco proteins from genome-based analysis

1 reference

12 December 2020

Yeast Cox11, a protein essential for cytochrome c oxidase assembly, is a Cu(I)-binding protein.

1 reference

12 December 2020

Structural basis for copper transfer by the metallochaperone for the Menkes/Wilson disease proteins

1 reference

12 December 2020

Human Sco1 functional studies and pathological implications of the P174L mutant

1 reference

12 December 2020

A disulfide relay system in the intermembrane space of mitochondria that mediates protein import

1 reference

12 December 2020

The right to choose: multiple pathways for activating copper,zinc superoxide dismutase

1 reference

12 December 2020

The Lys1010-Lys1325 fragment of the Wilson's disease protein binds nucleotides and interacts with the N-terminal domain of this protein in a copper-dependent manner

1 reference

12 December 2020

Overexpression of CCS in G93A-SOD1 mice leads to accelerated neurological deficits with severe mitochondrial pathology

1 reference

12 December 2020

Identification of the transmembrane metal binding site in Cu+-transporting PIB-type ATPases

1 reference

12 December 2020

Role of free radicals and catalytic metal ions in human disease: an overview

1 reference

12 December 2020

Solution structure of the fourth metal-binding domain from the Menkes copper-transporting ATPase

1 reference

12 December 2020

Protein-folding location can regulate manganese-binding versus copper- or zinc-binding

1 reference

12 December 2020