(Q28362315)

English

A novel pathway for biosynthesis of cholestanol with 7 alpha-hydroxylated C27-steroids as intermediates, and its importance for the accumulation of cholestanol in cerebrotendinous xanthomatosis

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scholarly article

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A novel pathway for biosynthesis of cholestanol with 7 alpha-hydroxylated C27-steroids as intermediates, and its importance for the accumulation of cholestanol in cerebrotendinous xanthomatosis (English)

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cerebrotendinous xanthomatosis

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based on heuristic

inferred from title

Ingemar Björkhem

2

object named as

I Björkhem

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author name string

S Skrede

1

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M S Buchmann

3

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G Hopen

4

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O Fausa

5

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language of work or name

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publication date

February 1985

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Journal of Clinical Investigation

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75

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2

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448-55

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Cerebrotendinous xanthomatosis: a defect in mitochondrial 26-hydroxylation required for normal biosynthesis of cholic acid

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=423517

20 March 2017

Studies on the biosynthesis of 5-alpha-cholestan-3-beta-ol. I. Cholestenone 5-alpha-reductase of rat liver

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=423517

20 March 2017

Biosynthesis of 5 -cholestan-3 -ol in cerebrotendinous xanthomatosis

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=423517

20 March 2017

Role of the 26-hydroxylase in the biosynthesis of bile acids in the normal state and in cerebrotendinous xanthomatosis. An in vivo study

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=423517

29 September 2017

A biochemical abnormality in cerebrotendinous xanthomatosis. Impairment of bile acid biosynthesis associated with incomplete degradation of the cholesterol side chain

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=423517

29 September 2017

The metabolism of cholestanol, cholesterol, and bile acids in cerebrotendinous xanthomatosis

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=423517

29 September 2017

Cholic acid biosynthesis: the enzymatic defect in cerebrotendinous xanthomatosis

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=423517

29 September 2017

Assay of intermediates in bile acid biosynthesis using isotope dilution--mass spectrometry: hepatic levels in the normal state and in cerebrotendinous xanthomatosis

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=423517

2 June 2018

Diagnosis of cerebrotendinous xanthomatosis (CTX) and effect of chenodeoxycholic acid therapy by analysis of urine using capillary gas chromatography

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=423517

2 June 2018

Isolation of 5 alpha-cholestane-3 beta, 7 alpha-diol from bile of patients with cerebrotendinous xanthomatosis. Inefficiency of this steroid as a precursor to cholestanol.

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=423517

2 June 2018

Cholestanol deposition in cerebrotendinous xanthomatosis. A possible mechanism.

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=423517

2 June 2018

Determination of hepatic cholesterol 7alpha-hydroxylase activity in man

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=423517

2 June 2018

Biosynthesis of cholestanol: conversion of cholesterol into 4-cholesten-3-one by rat liver microsomes.

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=423517

2 June 2018

Cerebrotendinous xanthomatosis (cholestanolosis). Investigations on two sisters and their family

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=423517

2 June 2018

Gas-liquid chromatographic assay of serum bile acids

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=423517

2 June 2018

Cerebrotendinous xanthomatosis. The storage of cholestanol within the nervous system

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=423517

27 November 2018

Mechanism of Microbial Transformation of Cholesterol into Coprostanol

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=423517

27 November 2018

Conversion of cholesterol injected into man to cholestanol via a 3-ketonic intermediate

1 reference

https://pubmed.ncbi.nlm.nih.gov/3919058

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

METABOLISM OF CHOLESTA-4,7-DIEN-3-ONE AND CHOLESTA-4,6-DIEN-3-ONE BY MOUSE LIVER MICROSOMES

1 reference

https://pubmed.ncbi.nlm.nih.gov/3919058

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

On the conversion of cholesterol to 7-alpha,12-alpha-dihydroxycholest-4-en-3-one. Bile acids and steroids 168

1 reference

https://pubmed.ncbi.nlm.nih.gov/3919058

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Biosynthesis of cholestanol: 5-alpha-cholestan-3-one reductase of rat liver

1 reference

https://pubmed.ncbi.nlm.nih.gov/3919058

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Two patterns of neutral steroid conversion in the feces of normal North Americans

1 reference

https://pubmed.ncbi.nlm.nih.gov/3919058

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Biosynthesis of cholestanol from intestinal 7 alpha-hydroxy-4-cholesten-3-one

1 reference

https://pubmed.ncbi.nlm.nih.gov/3919058

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

A rapid method for the quantitative extraction of bile acids and their conjugates from serum using commercially available reverse-phase octadecylsilane bonded silica cartridges

1 reference

https://pubmed.ncbi.nlm.nih.gov/3919058

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Identifiers

10.1172/JCI111719

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