(Q33409285)

26 July 2017

title

Complement activation associated with ADAMTS13 deficiency in human and murine thrombotic microangiopathy (English)

1 reference

26 July 2017

8

Diana Karpman

1 reference

26 July 2017

Johan Rebetz

4

0 references

author name string

Ramesh Tati

1

1 reference

26 July 2017

Ann-Charlotte Kristoffersson

2

1 reference

26 July 2017

Anne-Lie Ståhl

3

1 reference

26 July 2017

Li Wang

5

1 reference

26 July 2017

Christoph Licht

6

1 reference

26 July 2017

David Motto

7

1 reference

26 July 2017

language of work or name

English

0 references

publication date

22 July 2013

1 reference

26 July 2017

published in

Journal of Immunology

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26 July 2017

volume

191

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26 July 2017

issue

5

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26 July 2017

page(s)

2184-2193

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Assembly and activation of alternative complement components on endothelial cell-anchored ultra-large von Willebrand factor links complement and hemostasis-thrombosis

26 July 2017

cites work

1 reference

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Complement activation in thrombotic microangiopathies

28 July 2018

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STEC-HUS, atypical HUS and TTP are all diseases of complement activation

28 July 2018

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28 July 2018

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28 July 2018

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Phenotypic expression of ADAMTS13 in glomerular endothelial cells

28 July 2018

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Alternative pathway activation of complement by Shiga toxin promotes exuberant C3a formation that triggers microvascular thrombosis

28 July 2018

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28 July 2018

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Shiga toxin B subunits induce VWF secretion by human endothelial cells and thrombotic microangiopathy in ADAMTS13-deficient mice

28 July 2018

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28 July 2018

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Shiga toxin and lipopolysaccharide induce platelet-leukocyte aggregates and tissue factor release, a thrombotic mechanism in hemolytic uremic syndrome

28 July 2018

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Biologically active ADAMTS13 is expressed in renal tubular epithelial cells.

28 July 2018

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Pathological aspects of membranoproliferative glomerulonephritis (MPGN) and haemolytic uraemic syndrome (HUS) / thrombocytic thrombopenic purpura (TTP).

28 July 2018

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28 July 2018

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Molecular basis of ADAMTS13 dysfunction in thrombotic thrombocytopenic purpura

28 July 2018

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28 July 2018

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Factor H dysfunction in patients with atypical hemolytic uremic syndrome contributes to complement deposition on platelets and their activation

28 July 2018

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Podocytes express ADAMTS13 in normal renal cortex and in patients with thrombotic thrombocytopenic purpura

28 July 2018

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ADAMTS13 phenotype in plasma from normal individuals and patients with thrombotic thrombocytopenic purpura

28 July 2018

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A common origin of the 4143insA ADAMTS13 mutation

28 July 2018

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A classification of hemolytic uremic syndrome and thrombotic thrombocytopenic purpura and related disorders

28 July 2018

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Shigatoxin triggers thrombotic thrombocytopenic purpura in genetically susceptible ADAMTS13-deficient mice

28 July 2018

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Hemolytic uremic syndrome-associated Shiga toxins promote endothelial-cell secretion and impair ADAMTS13 cleavage of unusually large von Willebrand factor multimers

28 July 2018

1 reference

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Endothelial microparticles induce formation of platelet aggregates via a von Willebrand factor/ristocetin dependent pathway, rendering them resistant to dissociation

28 July 2018

1 reference

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Vascular wall shear stress: basic principles and methods

28 July 2018

1 reference

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Complement activation: the missing link between ADAMTS-13 deficiency and microvascular thrombosis of thrombotic microangiopathies

28 July 2018

2 references

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3750088

28 July 2018

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Endothelial microparticles released in thrombotic thrombocytopenic purpura express von Willebrand factor and markers of endothelial activation

31 October 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3750088

Mutation analysis and clinical implications of von Willebrand factor-cleaving protease deficiency

28 July 2018

1 reference

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Mutations in factor H reduce binding affinity to C3b and heparin and surface attachment to endothelial cells in hemolytic uremic syndrome

28 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3750088

ADAMTS-13 rapidly cleaves newly secreted ultralarge von Willebrand factor multimers on the endothelial surface under flowing conditions

28 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3750088

Mutations in a member of the ADAMTS gene family cause thrombotic thrombocytopenic purpura

28 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3750088

Thrombotic microangiopathy, hemolytic uremic syndrome, and thrombotic thrombocytopenic purpura

28 July 2018

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Elevated endothelial microparticles in thrombotic thrombocytopenic purpura: findings from brain and renal microvascular cell culture and patients with active disease

28 July 2018

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Characterization of platelet glycoproteins and platelet/endothelial cell antibodies in patients with thrombotic thrombocytopenic purpura

28 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3750088

Hypocomplementemia discloses genetic predisposition to hemolytic uremic syndrome and thrombotic thrombocytopenic purpura: role of factor H abnormalities. Italian Registry of Familial and Recurrent Hemolytic Uremic Syndrome/Thrombotic [...]

28 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3750088

Antibodies to von Willebrand factor-cleaving protease in acute thrombotic thrombocytopenic purpura

28 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3750088

The cytolytically inactive terminal complement complex activates endothelial cells to express adhesion molecules and tissue factor procoagulant activity

28 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3750088

Deficient activity of von Willebrand factor-cleaving protease in chronic relapsing thrombotic thrombocytopenic purpura.

28 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3750088

Increased platelet retention in familial recurrent thrombotic thrombocytopenic purpura

28 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3750088

Complement in thrombotic thrombocytopenic purpura

28 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3750088

Thrombotic thrombocytopenic purpura: report of a case with possible immune etiology

28 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3750088

Involvement of large plasma von Willebrand factor (vWF) multimers and unusually large vWF forms derived from endothelial cells in shear stress-induced platelet aggregation

28 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3750088

Antigen retrieval in formalin-fixed, paraffin-embedded tissues: an enhancement method for immunohistochemical staining based on microwave oven heating of tissue sections

28 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3750088

Shiga toxin-associated hemolytic uremic syndrome: combined cytotoxic effects of shiga toxin and lipopolysaccharide (endotoxin) on human vascular endothelial cells in vitro.

28 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3750088

Thrombotic Thrombocytopenic Purpura with C′3Vascular Deposits: Report of a Case

28 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3750088

Phenotypic expression of factor H mutations in patients with atypical hemolytic uremic syndrome.

28 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3750088

Cleavage of von Willebrand factor by ADAMTS-13 on endothelial cells

31 October 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3750088

Fluid shear stress modulates von Willebrand factor release from human vascular endothelium

31 October 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3750088

Initiation of platelet adhesion by arrest onto fibrinogen or translocation on von Willebrand factor

31 October 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3750088

Complement peptides C3a- and C5a-induced mediator release from dissociated human skin mast cells

31 October 2018

1 reference

12 December 2020

Hirudin versus heparin for use in whole blood in vitro biocompatibility models

1 reference

12 December 2020

Successful management of a planned pregnancy in severe congenital thrombotic thrombocytopaenic purpura: the Upshaw-Schulman syndrome

1 reference

12 December 2020

Eculizumab in the treatment of refractory idiopathic thrombotic thrombocytopenic purpura

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12 December 2020

Identifiers

DOI

10.4049/JIMMUNOL.1301221

1 reference

26 July 2017

1 reference

26 July 2017

1 reference