(Q33745319)

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:10508741%20AND%20SRC:MED&resulttype=core&format=json

31 October 2019

review article

1 reference

title

Polyglutamine diseases: protein cleavage and aggregation (English)

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https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:10508741%20AND%20SRC:MED&resulttype=core&format=json

31 October 2019

1

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:10508741%20AND%20SRC:MED&resulttype=core&format=json

31 October 2019

Harry T. Orr

series ordinal

2

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:10508741%20AND%20SRC:MED&resulttype=core&format=json

31 October 2019

author name string

Orr HT

series ordinal

2

1 reference

29 July 2017

1 October 1999

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:10508741%20AND%20SRC:MED&resulttype=core&format=json

Current Opinion in Neurobiology

31 October 2019

published in

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:10508741%20AND%20SRC:MED&resulttype=core&format=json

31 October 2019

volume

9

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:10508741%20AND%20SRC:MED&resulttype=core&format=json

31 October 2019

page(s)

566-570

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:10508741%20AND%20SRC:MED&resulttype=core&format=json

31 October 2019

issue

5

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:10508741%20AND%20SRC:MED&resulttype=core&format=json

Intranuclear neuronal inclusions: a common pathogenic mechanism for glutamine-repeat neurodegenerative diseases?

31 October 2019

cites work

1 reference

https://api.crossref.org/works/10.1016%2FS0959-4388%2899%2900013-6

7 January 2021

Androgen receptor gene mutations in X-linked spinal and bulbar muscular atrophy

1 reference

https://api.crossref.org/works/10.1016%2FS0959-4388%2899%2900013-6

7 January 2021

Human genetic diseases due to codon reiteration: relationship to an evolutionary mechanism

1 reference

https://api.crossref.org/works/10.1016%2FS0959-4388%2899%2900013-6

7 January 2021

Glutamine repeats as polar zippers: their possible role in inherited neurodegenerative diseases

1 reference

https://api.crossref.org/works/10.1016%2FS0959-4388%2899%2900013-6

7 January 2021

Expanded polyglutamine in the Machado-Joseph disease protein induces cell death in vitro and in vivo

1 reference

https://api.crossref.org/works/10.1016%2FS0959-4388%2899%2900013-6

7 January 2021

Exon 1 of the HD gene with an expanded CAG repeat is sufficient to cause a progressive neurological phenotype in transgenic mice

1 reference

https://api.crossref.org/works/10.1016%2FS0959-4388%2899%2900013-6

7 January 2021

Ectopically expressed CAG repeats cause intranuclear inclusions and a progressive late onset neurological phenotype in the mouse.

1 reference

https://api.crossref.org/works/10.1016%2FS0959-4388%2899%2900013-6

7 January 2021

Formation of neuronal intranuclear inclusions underlies the neurological dysfunction in mice transgenic for the HD mutation

1 reference

https://api.crossref.org/works/10.1016%2FS0959-4388%2899%2900013-6

7 January 2021

Huntingtin-encoded polyglutamine expansions form amyloid-like protein aggregates in vitro and in vivo

1 reference

https://api.crossref.org/works/10.1016%2FS0959-4388%2899%2900013-6

7 January 2021

Aggregation of huntingtin in neuronal intranuclear inclusions and dystrophic neurites in brain

1 reference

https://api.crossref.org/works/10.1016%2FS0959-4388%2899%2900013-6

7 January 2021

Intranuclear inclusions of expanded polyglutamine protein in spinocerebellar ataxia type 3.

1 reference

https://api.crossref.org/works/10.1016%2FS0959-4388%2899%2900013-6

7 January 2021

Ataxin-1 with an expanded glutamine tract alters nuclear matrix-associated structures

1 reference

https://api.crossref.org/works/10.1016%2FS0959-4388%2899%2900013-6

7 January 2021

Spinocerebellar ataxia type 7 (SCA7): a neurodegenerative disorder with neuronal intranuclear inclusions.

1 reference

https://api.crossref.org/works/10.1016%2FS0959-4388%2899%2900013-6

7 January 2021

Nuclear inclusions of the androgen receptor protein in spinal and bulbar muscular atrophy.

1 reference

https://api.crossref.org/works/10.1016%2FS0959-4388%2899%2900013-6

7 January 2021

Intranuclear neuronal inclusions in Huntington's disease and dentatorubral and pallidoluysian atrophy: correlation between the density of inclusions and IT15 CAG triplet repeat length

1 reference

https://api.crossref.org/works/10.1016%2FS0959-4388%2899%2900013-6

7 January 2021

Are neuronal intranuclear inclusions the common neuropathology of triplet-repeat disorders with polyglutamine-repeat expansions?

1 reference

https://api.crossref.org/works/10.1016%2FS0959-4388%2899%2900013-6

7 January 2021

Glutamine repeats and neurodegenerative diseases: molecular aspects

1 reference

https://api.crossref.org/works/10.1016%2FS0959-4388%2899%2900013-6

7 January 2021

Chaperone suppression of aggregation and altered subcellular proteasome localization imply protein misfolding in SCA1.

1 reference

https://api.crossref.org/works/10.1016%2FS0959-4388%2899%2900013-6

7 January 2021

Evidence for proteasome involvement in polyglutamine disease: localization to nuclear inclusions in SCA3/MJD and suppression of polyglutamine aggregation in vitro

1 reference

https://api.crossref.org/works/10.1016%2FS0959-4388%2899%2900013-6

7 January 2021

Polyglutamine-expanded androgen receptors form aggregates that sequester heat shock proteins, proteasome components and SRC-1, and are suppressed by the HDJ-2 chaperone

1 reference

https://api.crossref.org/works/10.1016%2FS0959-4388%2899%2900013-6

7 January 2021

Length of huntingtin and its polyglutamine tract influences localization and frequency of intracellular aggregates

1 reference

https://api.crossref.org/works/10.1016%2FS0959-4388%2899%2900013-6

7 January 2021

Cleavage, aggregation and toxicity of the expanded androgen receptor in spinal and bulbar muscular atrophy

1 reference

https://api.crossref.org/works/10.1016%2FS0959-4388%2899%2900013-6

7 January 2021

The influence of huntingtin protein size on nuclear localization and cellular toxicity.

1 reference

https://api.crossref.org/works/10.1016%2FS0959-4388%2899%2900013-6

7 January 2021

Recruitment and the role of nuclear localization in polyglutamine-mediated aggregation

1 reference

https://api.crossref.org/works/10.1016%2FS0959-4388%2899%2900013-6

7 January 2021

A cellular model that recapitulates major pathogenic steps of Huntington's disease

1 reference

https://api.crossref.org/works/10.1016%2FS0959-4388%2899%2900013-6

7 January 2021

Protease activation during apoptosis: death by a thousand cuts?

1 reference

https://api.crossref.org/works/10.1016%2FS0959-4388%2899%2900013-6

7 January 2021

Cleavage of huntingtin by apopain, a proapoptotic cysteine protease, is modulated by the polyglutamine tract

1 reference

https://api.crossref.org/works/10.1016%2FS0959-4388%2899%2900013-6

7 January 2021

Caspase cleavage of gene products associated with triplet expansion disorders generates truncated fragments containing the polyglutamine tract

1 reference

https://api.crossref.org/works/10.1016%2FS0959-4388%2899%2900013-6

7 January 2021

Mutant huntingtin expression in clonal striatal cells: dissociation of inclusion formation and neuronal survival by caspase inhibition.

1 reference

https://api.crossref.org/works/10.1016%2FS0959-4388%2899%2900013-6

7 January 2021

Inhibition of caspase-1 slows disease progression in a mouse model of Huntington's disease

1 reference

https://api.crossref.org/works/10.1016%2FS0959-4388%2899%2900013-6

7 January 2021

Huntingtin acts in the nucleus to induce apoptosis but death does not correlate with the formation of intranuclear inclusions.

1 reference

https://api.crossref.org/works/10.1016%2FS0959-4388%2899%2900013-6

7 January 2021

Expression of ataxin-2 in brains from normal individuals and patients with Alzheimer's disease and spinocerebellar ataxia 2.

1 reference

https://api.crossref.org/works/10.1016%2FS0959-4388%2899%2900013-6

7 January 2021

Ataxin-1 nuclear localization and aggregation: role in polyglutamine-induced disease in SCA1 transgenic mice.

1 reference

https://api.crossref.org/works/10.1016%2FS0959-4388%2899%2900013-6

7 January 2021

Behavioural abnormalities and selective neuronal loss in HD transgenic mice expressing mutated full-length HD cDNA.

1 reference

https://api.crossref.org/works/10.1016%2FS0959-4388%2899%2900013-6

7 January 2021

A YAC mouse model for Huntington's disease with full-length mutant huntingtin, cytoplasmic toxicity, and selective striatal neurodegeneration.

1 reference

https://api.crossref.org/works/10.1016%2FS0959-4388%2899%2900013-6

7 January 2021

SAPKs and transcription factors do the nucleocytoplasmic tango

1 reference

https://api.crossref.org/works/10.1016%2FS0959-4388%2899%2900013-6

7 January 2021

10.1016/S0959-4388(99)00013-6

Identifiers

DOI

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:10508741%20AND%20SRC:MED&resulttype=core&format=json

31 October 2019

1 reference