(Q33778431)

29 July 2017

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title

Terminal glycosylation in cystic fibrosis (English)

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29 July 2017

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1

T F Scanlin

1 reference

29 July 2017

M C Glick

2

1 reference

PubMed ID

10571016

29 July 2017

language of work or name

English

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publication date

1 October 1999

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Biochimica et Biophysica Acta

29 July 2017

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29 July 2017

1455

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29 July 2017

2-3

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29 July 2017

241-253

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Pseudomonas aeruginosa II lectin stops human ciliary beating: therapeutic implications of fucose

29 July 2017

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

Differential Concanavalin A binding of cystic fibrosis and normal liver α-L-fucosidase

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

Defective acidification of intracellular organelles in cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

Defective acidification of the biosynthetic pathway in cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

The mechanism underlying cystic fibrosis transmembrane conductance regulator transport from the endoplasmic reticulum to the proteasome includes Sec61beta and a cytosolic, deglycosylated intermediary

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

Decreased sialic acid and altered binding to lectins of purified α2-macroglobulin from patients with cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

Pericellular glycoconjugates of cultured fibroblasts from control and cystic fibrosis patients

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

Regulation of plasma membrane recycling by CFTR.

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

Altered carbohydrate composition of salivary mucins from patients with cystic fibrosis and the adhesion of Pseudomonas aeruginosa

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

Respiratory mucous secretions in patients with cystic fibrosis: relationship between levels of highly sulfated mucin component and severity of the disease

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

Increased sulfation of glycoconjugates by cultured nasal epithelial cells from patients with cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

Defective intracellular transport and processing of CFTR is the molecular basis of most cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

Study of the Oligosaccharide Units from Mucus Glycoproteins of Meconium from Normal Infants and from Cases of Cystic Fibrosis with Meconium Ileus

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

Molecular pathophysiology of cystic fibrosis based on the rescued knockout mouse model.

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

Cystic fibrosis: molecular biology and therapeutic implications

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

Transfer of genes to humans: early lessons and obstacles to success

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

CFTR gene transfer reduces the binding of Pseudomonas aeruginosa to cystic fibrosis respiratory epithelium

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

Processing of mutant cystic fibrosis transmembrane conductance regulator is temperature-sensitive

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

Differential binding of Pseudomonas aeruginosa to normal and cystic fibrosis tracheobronchial mucins

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

Heterologous expression of delta F508 CFTR results in decreased sialylation of membrane glycoconjugates

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

Correction of the cystic fibrosis defect in vitro by retrovirus-mediated gene transfer

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

Chloride Conductance Expressed by ΔF508 and Other Mutant CFTRs In Xenopus Oocytes

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

Glycan microheterogeneity of alpha 1-antitrypsin in serum and meconium from normal and cystic fibrosis patients by crossed immunoaffinoelectrophoresis with different lectins (Con A, LCA, WGA)

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

Gene transfer by DNA/glycosylated polylysine complexes into human blood monocyte-derived macrophages

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

Cystic fibrosis heterozygote resistance to cholera toxin in the cystic fibrosis mouse model

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

Sorting mechanisms regulating membrane protein traffic in the apical transcytotic pathway of polarized MDCK cells

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

Pseudomonas aeruginosa lectins

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

Expression and characterization of the cystic fibrosis transmembrane conductance regulator.

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

Characterization of human tracheal epithelial cells transformed by an origin-defective simian virus 40.

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

Intracellular retention of lysosomal enzymes in cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

Preparation of isolated surface membranes from cystic fibrosis airway epithelial cells

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

Glucose trimming and reglucosylation determine glycoprotein association with calnexin in the endoplasmic reticulum

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

Organ-specific over-sulfation of glycosaminoglycans and altered extracellular matrix in a mouse model of cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

Cystic fibrosis epithelial cells have a receptor for pathogenic bacteria on their apical surface

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

Multiple proteolytic systems, including the proteasome, contribute to CFTR processing.

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

Persistence of abnormal chloride conductance regulation in transformed cystic fibrosis epithelia.

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

Molecular defect in processing alpha-fucosidase in fucosidosis

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

Identification of the cystic fibrosis gene: genetic analysis

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

Gluconoylated and glycosylated polylysines as vectors for gene transfer into cystic fibrosis airway epithelial cells

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

Enhanced efficiency of lactosylated poly-L-lysine-mediated gene transfer into cystic fibrosis airway epithelial cells

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

High-efficiency transfer of cystic fibrosis transmembrane conductance regulator cDNA into cystic fibrosis airway cells in culture using lactosylated polylysine as a vector.

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

Pseudomonas aeruginosa and Pseudomonas cepacia isolated from cystic fibrosis patients bind specifically to gangliotetraosylceramide (asialo GM1) and gangliotriaosylceramide (asialo GM2)

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

Constitutive mucin secretion linked to CFTR expression

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

Lack of proteolytic processing of alpha-L-fucosidase in human skin fibroblasts

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

The cystic fibrosis mutation (delta F508) does not influence the chloride channel activity of CFTR.

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

Brefeldin A's effects on endosomes, lysosomes, and the TGN suggest a general mechanism for regulating organelle structure and membrane traffic

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

Selectin ligands, leukocyte trafficking, and fucosyltransferase genes

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

The carbohydrate content of IgG from patients with cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

Cellular localisation of the most common mutant form of the CF gene protein, delta F508-CFTR.

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

Correction of the apical membrane chloride permeability defect in polarized cystic fibrosis airway epithelia following retroviral-mediated gene transfer

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

Mutant (delta F508) cystic fibrosis transmembrane conductance regulator Cl- channel is functional when retained in endoplasmic reticulum of mammalian cells.

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

Increased Heparin Binding in Cystic Fibrosis: A Reflection of Altered Glycoprotein Biosynthesis?

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

Cooperation of c-raf-1 and c-myc protooncogenes in the neoplastic transformation of simian virus 40 large tumor antigen-immortalized human bronchial epithelial cells

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

Rapid endocytosis of the cystic fibrosis transmembrane conductance regulator chloride channel

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

Identification of the cystic fibrosis gene: cloning and characterization of complementary DNA

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

Identification of the cystic fibrosis gene: chromosome walking and jumping

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

Epithelial mucous glycoproteins and cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

Gene therapy for cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

CFTR protein is involved in the efflux of neutral amino acids

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

In vitro pharmacologic restoration of CFTR-mediated chloride transport with sodium 4-phenylbutyrate in cystic fibrosis epithelial cells containing delta F508-CFTR.

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

Pseudomonas aeruginosa pili bind to asialoGM1 which is increased on the surface of cystic fibrosis epithelial cells

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

Cotranslational ubiquitination of cystic fibrosis transmembrane conductance regulator in vitro

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

Abnormal distribution of α-L-fucosidase in cystic fibrosis: Increased activity in skin fibroblasts

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

Abnormal distribution of alpha-L-fucosidase in cystic fibrosis: decreased activity in serum

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

Glycoproteins in culture medium: a comparison from cystic fibrosis and control skin fibroblasts

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

Altered fucosylation of membrane glycoproteins from cystic fibrosis fibroblasts

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

Interactions between glycoconjugates from human respiratory airways and Pseudomonas aeruginosa

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

Evidence against defective trans-Golgi acidification in cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

Pathogenesis of bacterial bronchitis in cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

Abnormal fucosylation of ileal mucus in cystic fibrosis: I. A histochemical study using peroxidase labelled lectins

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

Ultrastructure and function of alveolar macrophages from cystic fibrosis patients

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

Different O-glycosylation of respiratory mucin glycopeptides from a patient with cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

Primary-structure determination of fourteen neutral oligosaccharides derived from bronchial-mucus glycoproteins of patients suffering from cystic fibrosis, employing 500-MHz 1H-NMR spectroscopy

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

Gene therapy -- promises, problems and prospects

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

Targeted gene delivery with a low molecular weight glycopeptide carrier

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

Additional fucosyl residues on membrane glycoproteins but not a secreted glycoprotein from cystic fibrosis fibroblasts

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

Degradation of CFTR by the ubiquitin-proteasome pathway

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

Turnover of the cystic fibrosis transmembrane conductance regulator (CFTR): slow degradation of wild-type and delta F508 CFTR in surface membrane preparations of immortalized airway epithelial cells

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

Molecular mechanisms of CFTR chloride channel dysfunction in cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

Human intestinal mucin in cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

The common variant of cystic fibrosis transmembrane conductance regulator is recognized by hsp70 and degraded in a pre-Golgi nonlysosomal compartment

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

Binding of Pseudomonas aeruginosa to respiratory epithelial cells from patients with various mutations in the cystic fibrosis transmembrane regulator

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

A Cystic Fibrosis Bronchial Epithelial Cell Line: Immortalization by Adeno-12-SV40 Infection

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

Genotypic analysis of respiratory mucous sulfation defects in cystic fibrosis.

1 reference

https://api.crossref.org/works/10.1016%2FS0925-4439%2899%2900059-9

7 January 2021

10.1016/S0925-4439(99)00059-9

Identifiers

DOI

1 reference

29 July 2017

1 reference

PubMed ID

10571016