(Q34336466)

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Systemic administration of tripeptidyl peptidase I in a mouse model of late infantile neuronal ceroid lipofuscinosis: effect of glycan modification

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scholarly article

1 reference

Europe PubMed Central

PubMed publication ID

1 August 2017

Systemic administration of tripeptidyl peptidase I in a mouse model of late infantile neuronal ceroid lipofuscinosis: effect of glycan modification (English)

1 reference

Europe PubMed Central

PubMed publication ID

1 August 2017

Infantile neuronal ceroid lipofuscinosis

0 references

Jansky–Bielschowsky disease

1 reference

based on heuristic

inferred from title

author name string

Yu Meng

1

1 reference

Europe PubMed Central

PubMed publication ID

1 August 2017

Istvan Sohar

2

1 reference

Europe PubMed Central

PubMed publication ID

1 August 2017

Lingling Wang

3

1 reference

Europe PubMed Central

PubMed publication ID

1 August 2017

David E Sleat

4

1 reference

Europe PubMed Central

PubMed publication ID

1 August 2017

Peter Lobel

5

1 reference

Europe PubMed Central

PubMed publication ID

1 August 2017

language of work or name

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publication date

6 July 2012

1 reference

Europe PubMed Central

PubMed publication ID

1 August 2017

1 reference

Europe PubMed Central

PubMed publication ID

1 August 2017

7

1 reference

Europe PubMed Central

PubMed publication ID

1 August 2017

7

1 reference

Europe PubMed Central

PubMed publication ID

1 August 2017

e40509

1 reference

Europe PubMed Central

PubMed publication ID

1 August 2017

copyright license

Creative Commons Attribution 4.0 International

6 July 2012

1 reference

April 2022 Public Data File from Crossref

copyright status

0 references

Large-volume intrathecal enzyme delivery increases survival of a mouse model of late infantile neuronal ceroid lipofuscinosis

1 reference

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Impact of high-dose, chemically modified sulfamidase on pathology in a murine model of MPS IIIA.

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Replacing the enzyme alpha-L-iduronidase at birth ameliorates symptoms in the brain and periphery of dogs with mucopolysaccharidosis type I.

1 reference

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Early versus late treatment of spinal cord compression with long-term intrathecal enzyme replacement therapy in canine mucopolysaccharidosis type I.

1 reference

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Crystal Structure and Autoactivation Pathway of the Precursor Form of Human Tripeptidyl-peptidase 1, the Enzyme Deficient in Late Infantile Ceroid Lipofuscinosis

1 reference

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Mannose 6-phosphate receptor-mediated transport of sulfamidase across the blood-brain barrier in the newborn mouse

1 reference

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Residual levels of tripeptidyl-peptidase I activity dramatically ameliorate disease in late-infantile neuronal ceroid lipofuscinosis

1 reference

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Chemically modified beta-glucuronidase crosses blood-brain barrier and clears neuronal storage in murine mucopolysaccharidosis VII.

1 reference

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Intrathecal enzyme replacement therapy: successful treatment of brain disease via the cerebrospinal fluid

1 reference

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Enzyme replacement for lysosomal diseases

1 reference

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Overcoming the blood-brain barrier with high-dose enzyme replacement therapy in murine mucopolysaccharidosis VII.

1 reference

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A mouse model of classical late-infantile neuronal ceroid lipofuscinosis based on targeted disruption of the CLN2 gene results in a loss of tripeptidyl-peptidase I activity and progressive neurodegeneration

1 reference

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6 July 2018

Developmentally regulated mannose 6-phosphate receptor-mediated transport of a lysosomal enzyme across the blood-brain barrier

1 reference

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6 July 2018

Enzyme replacement and enhancement therapies for lysosomal diseases

1 reference

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6 July 2018

Production and characterization of recombinant human CLN2 protein for enzyme-replacement therapy in late infantile neuronal ceroid lipofuscinosis

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3391252

6 July 2018

The human CLN2 protein/tripeptidyl-peptidase I is a serine protease that autoactivates at acidic pH

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3391252

6 July 2018

Classical late infantile neuronal ceroid lipofuscinosis fibroblasts are deficient in lysosomal tripeptidyl peptidase I

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3391252

6 July 2018

Association of mutations in a lysosomal protein with classical late-infantile neuronal ceroid lipofuscinosis

1 reference

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6 July 2018

Heparanases and tumor metastasis

1 reference

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6 July 2018

Elimination of lysosomal storage in brains of MPS VII mice treated by intrathecal administration of an adeno-associated virus vector

1 reference

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21 January 2018

Distribution of acid sphingomyelinase in rodent and non-human primate brain after intracerebroventricular infusion.

1 reference

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21 January 2018

Intraventricular enzyme replacement improves disease phenotypes in a mouse model of late infantile neuronal ceroid lipofuscinosis

1 reference

https://api.crossref.org/works/10.1371%2FJOURNAL.PONE.0040509

21 January 2018

Intracerebroventricular infusion of acid sphingomyelinase corrects CNS manifestations in a mouse model of Niemann-Pick A disease

1 reference

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21 January 2018

Enzyme-replacement therapy from birth delays the development of behavior and learning problems in mucopolysaccharidosis type IIIA mice

1 reference

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21 January 2018

Enzyme replacement in murine mucopolysaccharidosis type VII: neuronal and glial response to beta-glucuronidase requires early initiation of enzyme replacement therapy.

1 reference

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Reversal of peripheral and central neural storage and ataxia after recombinant enzyme replacement therapy in alpha-mannosidosis mice

1 reference

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Soluble Insulin-like Growth Factor II/Mannose 6-Phosphate Receptor Carries Multiple High Molecular Weight Forms of Insulin-like Growth Factor II in Fetal Bovine Serum

1 reference

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Influence of the carbohydrate moiety on the stability of glycoproteins

1 reference

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Enzyme-based diagnosis of classical late infantile neuronal ceroid lipofuscinosis: comparison of tripeptidyl peptidase I and pepstatin-insensitive protease assays

1 reference

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12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Intrathecal enzyme replacement therapy reduces lysosomal storage in the brain and meninges of the canine model of MPS I

1 reference

https://pubmed.ncbi.nlm.nih.gov/22792360

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

An assay to detect glycoproteins that contain mannose 6-phosphate

1 reference

https://pubmed.ncbi.nlm.nih.gov/22792360

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Repeated intrathecal injections of recombinant human 4-sulphatase remove dural storage in mature mucopolysaccharidosis VI cats primed with a short-course tolerisation regimen

1 reference

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inferred from PubMed ID database lookup

Highly phosphomannosylated enzyme replacement therapy for GM2 gangliosidosis

1 reference

https://pubmed.ncbi.nlm.nih.gov/22792360

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Identifiers

10.1371/JOURNAL.PONE.0040509

1 reference

Europe PubMed Central

PubMed publication ID

1 August 2017

2012PLoSO...740509M

0 references

PMC publication ID

1 reference

Europe PubMed Central

PubMed publication ID

1 August 2017

PubMed publication ID

1 reference

Europe PubMed Central

PubMed publication ID

1 August 2017

ResearchGate publication ID

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