(Q34509452)

2 August 2017

title

Copper and zinc metallation status of copper-zinc superoxide dismutase from amyotrophic lateral sclerosis transgenic mice. (English)

1 reference

amyotrophic lateral sclerosis

2 August 2017

main subject

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10

Julian P Whitelegge

1 reference

2 August 2017

Herman L Lelie

1

1 reference

2 August 2017

Amir Liba

2

1 reference

2 August 2017

Megan W Bourassa

3

1 reference

2 August 2017

Madhuri Chattopadhyay

4

1 reference

2 August 2017

Pik K Chan

5

1 reference

2 August 2017

Edith B Gralla

6

1 reference

2 August 2017

Lisa M Miller

7

1 reference

2 August 2017

David R Borchelt

8

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2 August 2017

Joan Selverstone Valentine

9

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2 August 2017

language of work or name

English

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publication date

10 November 2010

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Journal of Biological Chemistry

2 August 2017

published in

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2 August 2017

volume

286

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2 August 2017

issue

4

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2 August 2017

page(s)

2795-2806

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Cu,Zn-superoxide dismutase increases toxicity of mutant and zinc-deficient superoxide dismutase by enhancing protein stability.

2 August 2017

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Initiation and elongation in fibrillation of ALS-linked superoxide dismutase

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Metalation of the amyotrophic lateral sclerosis mutant glycine 37 to arginine superoxide dismutase (SOD1) apoprotein restores its structural and dynamical properties in solution to those of metalated wild-type SOD1.

7 July 2018

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Metal-free superoxide dismutase forms soluble oligomers under physiological conditions: a possible general mechanism for familial ALS

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7 July 2018

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7 July 2018

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ALS mutants of human superoxide dismutase form fibrous aggregates via framework destabilization

7 July 2018

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From Charcot to Lou Gehrig: deciphering selective motor neuron death in ALS

7 July 2018

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Formation of high molecular weight complexes of mutant Cu, Zn-superoxide dismutase in a mouse model for familial amyotrophic lateral sclerosis.

7 July 2018

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Copper(2+) binding to the surface residue cysteine 111 of His46Arg human copper-zinc superoxide dismutase, a familial amyotrophic lateral sclerosis mutant

7 July 2018

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Loss of in vitro metal ion binding specificity in mutant copper-zinc superoxide dismutases associated with familial amyotrophic lateral sclerosis

7 July 2018

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7 July 2018

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7 July 2018

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Superoxide dismutase 1 with mutations linked to familial amyotrophic lateral sclerosis possesses significant activity

7 July 2018

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7 July 2018

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7 July 2018

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7 July 2018

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Differential scanning calorimetry of Cu,Zn-superoxide dismutase, the apoprotein, and its zinc-substituted derivatives

7 July 2018

1 reference

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Levels of lead, cadmium, zinc and copper in the blood of an urban population

7 July 2018

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Determination of manganese concentrations in the spinal cords from amyotrophic lateral sclerosis patients by inductively coupled plasma emission spectroscopy.

7 July 2018

1 reference

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7 July 2018

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7 July 2018

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Clinical features of amyotrophic lateral sclerosis according to the El Escorial and Airlie House diagnostic criteria: A population-based study

7 July 2018

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Lead exposure and amyotrophic lateral sclerosis.

21 January 2018

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Blood levels of toxic and essential metals in motor neuron disease.

21 January 2018

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Oxidative stress and metal content in blood and cerebrospinal fluid of amyotrophic lateral sclerosis patients with and without a Cu, Zn-superoxide dismutase mutation

21 January 2018

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https://api.crossref.org/works/10.1074%2FJBC.M110.186999

Copper-binding-site-null SOD1 causes ALS in transgenic mice: aggregates of non-native SOD1 delineate a common feature

21 January 2018

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Familial amyotrophic lateral sclerosis-associated mutations decrease the thermal stability of distinctly metallated species of human copper/zinc superoxide dismutase

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M110.186999

An intersubunit disulfide bond prevents in vitro aggregation of a superoxide dismutase-1 mutant linked to familial amytrophic lateral sclerosis

21 January 2018

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Amyotrophic lateral sclerosis mutations have the greatest destabilizing effect on the apo- and reduced form of SOD1, leading to unfolding and oxidative aggregation.

21 January 2018

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Fibrillar inclusions and motor neuron degeneration in transgenic mice expressing superoxide dismutase 1 with a disrupted copper-binding site

21 January 2018

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Tissue-specific alterations in zinc transporter expression in intestine and liver reflect a threshold for homeostatic compensation during dietary zinc deficiency in weanling rats

21 January 2018

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Concentrations of Cd, Co, Cu, Fe, Mn, Rb, V, and Zn in formalin-fixed brain tissue in amyotrophic lateral sclerosis and Parkinsonism-dementia complex of Guam determined by High-resolution ICP-MS.

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M110.186999

Quantification of trace elements in normal human brain by inductively coupled plasma atomic emission spectrometry.

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M110.186999

High molecular weight complexes of mutant superoxide dismutase 1: age-dependent and tissue-specific accumulation

21 January 2018

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https://api.crossref.org/works/10.1074%2FJBC.M110.186999

Oxygen-induced maturation of SOD1: a key role for disulfide formation by the copper chaperone CCS.

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M110.186999

Dysregulation of intracellular copper trafficking pathway in a mouse model of mutant copper/zinc superoxide dismutase-linked familial amyotrophic lateral sclerosis.

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M110.186999

Accumulation of labile zinc in neurons and astrocytes in the spinal cords of G93A SOD-1 transgenic mice

21 January 2018

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https://api.crossref.org/works/10.1074%2FJBC.M110.186999

Effect of zinc exposure on HNE and GLT-1 in spinal cord culture

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M110.186999

Implementation of X-ray fluorescence microscopy for investigation of elemental abnormalities in amyotrophic lateral sclerosis.

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M110.186999

Studies on amyotrophic lateral sclerosis by neutron activation analysis--2. Comparative study of analytical results on Guam PD, Japanese ALS and Alzheimer disease cases.

21 January 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3024775

ALS and mercury intoxication: A relationship?

27 October 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M110.186999

Toxic and essential metals in liver, kidney and muscle of pigs at slaughter in Galicia, north-west Spain

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M110.186999

Variable Metallation of Human Superoxide Dismutase: Atomic Resolution Crystal Structures of Cu–Zn, Zn–Zn and As-isolated Wild-type Enzymes

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M110.186999

Estimation of Zinc in Biological Specimens: Determination of Zinc-65

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M110.186999

Genetically Decreased Spinal Cord Copper Concentration Prolongs Life in a Transgenic Mouse Model of Amyotrophic Lateral Sclerosis

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M110.186999

Structural analyses of various Cu2+, Zn2+-superoxide dismutases by differential scanning calorimetry and Raman spectroscopy

21 January 2018

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12 December 2020

Studies on amyotrophic lateral sclerosis by neutron activation analysis. 3. Systematic analysis of metals on Guamanian ALS and PD cases

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12 December 2020

Regional interrelationships of zinc, copper, and lead in the brain following lead intoxication

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12 December 2020

Neutron Activation Analysis of Trace Elements in Motor Neuron Disease Spinal Cord

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12 December 2020

Metallothionein in amyotrophic lateral sclerosis

1 reference

12 December 2020

Spectrophotometric assay for superoxide dismutase based on tetrazolium salt 3'--1--(phenylamino)-carbonyl--3, 4-tetrazolium]-bis(4-methoxy-6-nitro)benzenesulfonic acid hydrate reduction by xanthine-xanthine oxidase

1 reference

12 December 2020

Heavy metal concentrations in blood cells in patients with amyotrophic lateral sclerosis

1 reference

12 December 2020

Iron, copper, and zinc distribution of the cerebellum

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12 December 2020

Amyotrophic lateral sclerosis

1 reference

12 December 2020

Somatodendritic accumulation of misfolded SOD1-L126Z in motor neurons mediates degeneration: alphaB-crystallin modulates aggregation

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12 December 2020

Identifiers

DOI

10.1074/JBC.M110.186999

1 reference

2 August 2017

1 reference

2 August 2017

1 reference