(Q34722056)

4 August 2017

title

Persistence of psychosine in brain lipid rafts is a limiting factor in the therapeutic recovery of a mouse model for Krabbe disease (English)

1 reference

4 August 2017

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ChEBI release 2020-05-28

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6

R van Breemen

1 reference

4 August 2017

A B White

1

1 reference

4 August 2017

F Galbiati

2

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4 August 2017

M I Givogri

3

1 reference

4 August 2017

A Lopez Rosas

4

1 reference

4 August 2017

X Qiu

5

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4 August 2017

E R Bongarzone

7

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4 August 2017

language of work or name

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29 December 2010

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4 August 2017

number of pages

13

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Journal of Neuroscience Research

inferred from page(s)

published in

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4 August 2017

volume

89

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4 August 2017

issue

3

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4 August 2017

page(s)

352-364

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describes a project that uses

4 August 2017

ImageJ

1 reference

11 June 2022

https://www.ebi.ac.uk/europepmc/webservices/rest/PMC3064524/fullTextXML

inferred from PubMed Central ID database lookup

cites work

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PKC-alpha modulates TGF-beta signaling and impairs podocyte survival

7 July 2018

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PKC induces internalization and retention of the EAAC1 glutamate transporter in recycling endosomes of MDCK cells.

7 July 2018

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https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3064524

Psychosine accumulates in membrane microdomains in the brain of krabbe patients, disrupting the raft architecture.

7 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3064524

Docosahexaenoic acid alters bilayer elastic properties.

7 July 2018

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Inhibition of caveolar uptake, SV40 infection, and beta1-integrin signaling by a nonnatural glycosphingolipid stereoisomer

7 July 2018

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Phosphorylation of the norepinephrine transporter at threonine 258 and serine 259 is linked to protein kinase C-mediated transporter internalization.

7 July 2018

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Krabbe disease: psychosine-mediated activation of phospholipase A2 in oligodendrocyte cell death

7 July 2018

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Transplantation of umbilical-cord blood in babies with infantile Krabbe's disease

7 July 2018

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Spatial segregation of gamma-secretase and substrates in distinct membrane domains

7 July 2018

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Gbetagamma activation of Src induces caveolae-mediated endocytosis in endothelial cells

7 July 2018

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Endocytosis by random initiation and stabilization of clathrin-coated pits

7 July 2018

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Association of gamma-secretase with lipid rafts in post-Golgi and endosome membranes

7 July 2018

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Role of Src-induced dynamin-2 phosphorylation in caveolae-mediated endocytosis in endothelial cells

7 July 2018

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Globoid Cell Leukodystrophy (Krabbe's Disease): Update

7 July 2018

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Molecular mechanism of psychosine-induced cell death in human oligodendrocyte cell line

7 July 2018

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7 July 2018

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Quantification of galactosylsphingosine in the twitcher mouse using electrospray ionization-tandem mass spectrometry

7 July 2018

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Functional rafts in cell membranes

7 July 2018

1 reference

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Retroviral vector-mediated transfer of the galactocerebrosidase (GALC) cDNA leads to overexpression and transfer of GALC activity to neighboring cells

7 July 2018

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Molecular cloning and expression of cDNA for murine galactocerebrosidase and mutation analysis of the twitcher mouse, a model of Krabbe's disease

7 July 2018

1 reference

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7 July 2018

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7 July 2018

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Progressive accumulation of toxic metabolite in a genetic leukodystrophy

7 July 2018

1 reference

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Donor-derived cells in the central nervous system of twitcher mice after bone marrow transplantation

7 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3064524

Lysosphingolipids inhibit protein kinase C: implications for the sphingolipidoses

7 July 2018

1 reference

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Characterization of 6-hexadecanoylamino-4-methylumbelliferyl-beta-D- galactopyranoside as fluorogenic substrate of galactocerebrosidase for the diagnosis of Krabbe disease

7 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3064524

Substrate-reduction therapy enhances the benefits of bone marrow transplantation in young mice with globoid cell leukodystrophy

7 July 2018

1 reference

Design and optimization of lentiviral vectors for transfer of GALC expression in Twitcher brain.

21 January 2018

1 reference

Autonomic denervation of lymphoid organs leads to epigenetic immune atrophy in a mouse model of Krabbe disease.

21 January 2018

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Notch signaling in astrocytes and neuroblasts of the adult subventricular zone in health and after cortical injury.

21 January 2018

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Oligodendroglial progenitor cell therapy limits central neurological deficits in mice with metachromatic leukodystrophy.

21 January 2018

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Multipotential neural precursors transplanted into the metachromatic leukodystrophy brain fail to generate oligodendrocytes but contribute to limit brain dysfunction

21 January 2018

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Membrane lipid segregation in endocytosis

21 January 2018

1 reference

Prolonged survival and remyelination after hematopoietic cell transplantation in the twitcher mouse

21 January 2018

1 reference

Cellular uptake and lysosomal delivery of galactocerebrosidase tagged with the HIV Tat protein transduction domain

21 January 2018

1 reference

Hereditary leucodystrophy in the mouse: the new mutant twitcher

21 January 2018

1 reference

12 December 2020

Enzyme replacement in grafted nerve of twitcher mouse

1 reference

12 December 2020

A differential effect between the acute and chronic administration of ethanol on the endocytotic rate constant, ke, for the internalisation of asialoglycoproteins by hepatocytes

1 reference

12 December 2020

Hematopoietic stem-cell transplantation in globoid-cell leukodystrophy

1 reference

12 December 2020

Sustained neurological improvement following reduced-intensity conditioning allogeneic haematopoietic stem cell transplantation for late-onset Krabbe disease

1 reference

12 December 2020

Combined hematopoietic and lentiviral gene-transfer therapies in newborn Twitcher mice reveal contemporaneous neurodegeneration and demyelination in Krabbe disease

1 reference

12 December 2020

Identifiers

DOI

10.1002/JNR.22564

1 reference

4 August 2017

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4 August 2017

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