(Q34892327)

5 August 2017

title

Glial nuclear aggregates of superoxide dismutase-1 are regularly present in patients with amyotrophic lateral sclerosis (English)

1 reference

amyotrophic lateral sclerosis

5 August 2017

main subject

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2

Peter M Andersen

1 reference

5 August 2017

Karin Forsberg

1

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5 August 2017

Stefan L Marklund

series ordinal

3

1 reference

5 August 2017

Thomas Brännström

series ordinal

4

1 reference

5 August 2017

publication date

3 February 2011

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5 August 2017

published in

Acta Neuropathologica

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5 August 2017

volume

121

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5 August 2017

issue

5

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5 August 2017

page(s)

623-634

1 reference

https://scigraph.springernature.com/pub.10.1007/s00401-011-0805-3

5 August 2017

exact match

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cites work

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Novel antibodies reveal inclusions containing non-native SOD1 in sporadic ALS patients

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Amyotrophic lateral sclerosis is a non-amyloid disease in which extensive misfolding of SOD1 is unique to the familial form

8 July 2018

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Role of mutant SOD1 disulfide oxidation and aggregation in the pathogenesis of familial ALS

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Mutations in FUS, an RNA processing protein, cause familial amyotrophic lateral sclerosis type 6

8 July 2018

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Initiation and elongation in fibrillation of ALS-linked superoxide dismutase

8 July 2018

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Complete loss of post-translational modifications triggers fibrillar aggregation of SOD1 in the familial form of amyotrophic lateral sclerosis

8 July 2018

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Mutant SOD1 in cell types other than motor neurons and oligodendrocytes accelerates onset of disease in ALS mice.

8 July 2018

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TARDBP mutations in individuals with sporadic and familial amyotrophic lateral sclerosis

8 July 2018

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TDP-43 mutations in familial and sporadic amyotrophic lateral sclerosis

8 July 2018

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Astrocytes as determinants of disease progression in inherited amyotrophic lateral sclerosis

8 July 2018

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Crossing the nuclear envelope: hierarchical regulation of nucleocytoplasmic transport

8 July 2018

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Soluble misfolded subfractions of mutant superoxide dismutase-1s are enriched in spinal cords throughout life in murine ALS models

8 July 2018

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TDP-43 is a component of ubiquitin-positive tau-negative inclusions in frontotemporal lobar degeneration and amyotrophic lateral sclerosis

8 July 2018

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The roles of intracellular protein-degradation pathways in neurodegeneration

8 July 2018

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Wild-type microglia extend survival in PU.1 knockout mice with familial amyotrophic lateral sclerosis

8 July 2018

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Onset and progression in inherited ALS determined by motor neurons and microglia

8 July 2018

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Conversion to the amyotrophic lateral sclerosis phenotype is associated with intermolecular linked insoluble aggregates of SOD1 in mitochondria

8 July 2018

1 reference

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Increased susceptibility of cytoplasmic over nuclear polyglutamine aggregates to autophagic degradation

8 July 2018

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Mutant copper-zinc superoxide dismutase binds to and destabilizes human low molecular weight neurofilament mRNA.

8 July 2018

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Sequestosome 1/p62 is a polyubiquitin chain binding protein involved in ubiquitin proteasome degradation

8 July 2018

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El Escorial revisited: revised criteria for the diagnosis of amyotrophic lateral sclerosis

8 July 2018

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Pathological characterization of astrocytic hyaline inclusions in familial amyotrophic lateral sclerosis.

8 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3085063

ALS-linked SOD1 mutant G85R mediates damage to astrocytes and promotes rapidly progressive disease with SOD1-containing inclusions.

8 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3085063

Mutations in Cu/Zn superoxide dismutase gene are associated with familial amyotrophic lateral sclerosis

8 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3085063

Motor neuron degeneration in mice that express a human Cu,Zn superoxide dismutase mutation

8 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3085063

Superoxide dismutase is an abundant component in cell bodies, dendrites, and axons of motor neurons and in a subset of other neurons

8 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3085063

Superoxide dismutase. Organelle specificity.

8 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3085063

Molecular immunocytochemistry of the CuZn superoxide dismutase in rat hepatocytes

8 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3085063

Superoxide dismutase-1 and other proteins in inclusions from transgenic amyotrophic lateral sclerosis model mice.

8 July 2018

1 reference

https://api.crossref.org/works/10.1007%2FS00401-011-0805-3

Wild-Type Nonneuronal Cells Extend Survival of SOD1 Mutant Motor Neurons in ALS Mice

21 January 2018

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https://api.crossref.org/works/10.1007%2FS00401-011-0805-3

Human Cu/Zn superoxide dismutase (SOD1) overexpression in mice causes mitochondrial vacuolization, axonal degeneration, and premature motoneuron death and accelerates motoneuron disease in mice expressing a familial amyotrophic lateral sclerosis mut

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS00401-011-0805-3

Minute quantities of misfolded mutant superoxide dismutase-1 cause amyotrophic lateral sclerosis.

21 January 2018

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https://api.crossref.org/works/10.1007%2FS00401-011-0805-3

Pathological TDP-43 distinguishes sporadic amyotrophic lateral sclerosis from amyotrophic lateral sclerosis with SOD1 mutations.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS00401-011-0805-3

Oxidation-induced misfolding and aggregation of superoxide dismutase and its implications for amyotrophic lateral sclerosis

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS00401-011-0805-3

SOD1 mutation is associated with accumulation of neurofilaments in amyotrophic lateral sclerosis.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS00401-011-0805-3

Restricted expression of mutant SOD1 in spinal motor neurons and interneurons induces motor neuron pathology

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS00401-011-0805-3

ALSOD: The Amyotrophic Lateral Sclerosis Online Database

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS00401-011-0805-3

Lack of evidence of monomer/misfolded superoxide dismutase-1 in sporadic amyotrophic lateral sclerosis

21 January 2018

1 reference

12 December 2020

Nuclear contour irregularity and abnormal transporter protein distribution in anterior horn cells in amyotrophic lateral sclerosis

1 reference

12 December 2020

Transgenic animal models of familial amyotrophic lateral sclerosis

1 reference

12 December 2020

Disulphide-reduced superoxide dismutase-1 in CNS of transgenic amyotrophic lateral sclerosis models

1 reference

12 December 2020

Immunoreactivities of p62, an ubiqutin-binding protein, in the spinal anterior horn cells of patients with amyotrophic lateral sclerosis

1 reference

12 December 2020

Motor neuron disease in mice expressing the wild type-like D90A mutant superoxide dismutase-1

1 reference

12 December 2020

DNA is a template for accelerating the aggregation of copper, zinc superoxide dismutase

1 reference

12 December 2020

Neuron-specific expression of mutant superoxide dismutase is sufficient to induce amyotrophic lateral sclerosis in transgenic mice

1 reference

12 December 2020

10.1007/S00401-011-0805-3

Identifiers

DOI

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5 August 2017

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5 August 2017

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