(Q52599963)

4 May 2018

title

Superoxide dismutase-1 and other proteins in inclusions from transgenic amyotrophic lateral sclerosis model mice. (English)

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4 May 2018

amyotrophic lateral sclerosis

main subject

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5

Peter M Andersen

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4 May 2018

Daniel Bergemalm

1

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4 May 2018

Karin Forsberg

2

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4 May 2018

Vaibhav Srivastava

3

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4 May 2018

Karin S Graffmo

4

1 reference

4 May 2018

Thomas Brännström

6

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4 May 2018

Gunnar Wingsle

7

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4 May 2018

Stefan L Marklund

8

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4 May 2018

language of work or name

English

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publication date

19 April 2010

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4 May 2018

Journal of Neurochemistry

published in

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4 May 2018

volume

114

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4 May 2018

issue

2

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4 May 2018

page(s)

408-418

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4 May 2018

Induction of the unfolded protein response in familial amyotrophic lateral sclerosis and association of protein-disulfide isomerase with superoxide dismutase 1.

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Metal-free superoxide dismutase forms soluble oligomers under physiological conditions: a possible general mechanism for familial ALS

21 January 2018

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Characterization of detergent-insoluble proteins in ALS indicates a causal link between nitrative stress and aggregation in pathogenesis.

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Overloading of stable and exclusion of unstable human superoxide dismutase-1 variants in mitochondria of murine amyotrophic lateral sclerosis models

21 January 2018

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Changes in the spinal cord proteome of an amyotrophic lateral sclerosis murine model determined by differential in-gel electrophoresis

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Onset and progression in inherited ALS determined by motor neurons and microglia

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ALS-linked SOD1 mutant G85R mediates damage to astrocytes and promotes rapidly progressive disease with SOD1-containing inclusions.

21 January 2018

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Initiation and elongation in fibrillation of ALS-linked superoxide dismutase

21 January 2018

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Co-chaperone CHIP associates with mutant Cu/Zn-superoxide dismutase proteins linked to familial amyotrophic lateral sclerosis and promotes their degradation by proteasomes

21 January 2018

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Complete loss of post-translational modifications triggers fibrillar aggregation of SOD1 in the familial form of amyotrophic lateral sclerosis

21 January 2018

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Motor neuron degeneration in mice that express a human Cu,Zn superoxide dismutase mutation

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Natural history of amyotrophic lateral sclerosis in a database population Validation of a scoring system and a model for survival prediction

21 January 2018

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Microglia in ALS: the good, the bad, and the resting

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Formation of high molecular weight complexes of mutant Cu, Zn-superoxide dismutase in a mouse model for familial amyotrophic lateral sclerosis.

21 January 2018

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Minute quantities of misfolded mutant superoxide dismutase-1 cause amyotrophic lateral sclerosis

21 January 2018

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A limited role for disulfide cross-linking in the aggregation of mutant SOD1 linked to familial amyotrophic lateral sclerosis.

21 January 2018

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Role of mutant SOD1 disulfide oxidation and aggregation in the pathogenesis of familial ALS

21 January 2018

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Treatment with arimoclomol, a coinducer of heat shock proteins, delays disease progression in ALS mice

21 January 2018

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Spinal cord endoplasmic reticulum stress associated with a microsomal accumulation of mutant superoxide dismutase-1 in an ALS model

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Toxicity of familial ALS-linked SOD1 mutants from selective recruitment to spinal mitochondria.

21 January 2018

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Astrocytes expressing ALS-linked mutated SOD1 release factors selectively toxic to motor neurons

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Disulfide bond mediates aggregation, toxicity, and ubiquitylation of familial amyotrophic lateral sclerosis-linked mutant SOD1.

21 January 2018

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Loss of metal ions, disulfide reduction and mutations related to familial ALS promote formation of amyloid-like aggregates from superoxide dismutase

21 January 2018

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No widespread induction of cell death genes occurs in pure motoneurons in an amyotrophic lateral sclerosis mouse model.

21 January 2018

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Specificity in intracellular protein aggregation and inclusion body formation

21 January 2018

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The disulfide relay system of mitochondria is required for the biogenesis of mitochondrial Ccs1 and Sod1.

21 January 2018

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Mutations in Cu/Zn superoxide dismutase gene are associated with familial amyotrophic lateral sclerosis

21 January 2018

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A role for motoneuron subtype-selective ER stress in disease manifestations of FALS mice

21 January 2018

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Detergent-insoluble aggregates associated with amyotrophic lateral sclerosis in transgenic mice contain primarily full-length, unmodified superoxide dismutase-1.

21 January 2018

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Mutant Cu/Zn-superoxide dismutase proteins have altered solubility and interact with heat shock/stress proteins in models of amyotrophic lateral sclerosis

21 January 2018

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Alternative splicing studies of the reactive oxygen species gene network in Populus reveal two isoforms of high-isoelectric-point superoxide dismutase

21 January 2018

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Mutant SOD1 linked to familial amyotrophic lateral sclerosis, but not wild-type SOD1, induces ER stress in COS7 cells and transgenic mice.

21 January 2018

1 reference

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Impaired extracellular secretion of mutant superoxide dismutase 1 associates with neurotoxicity in familial amyotrophic lateral sclerosis

21 January 2018

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Chromogranin-mediated secretion of mutant superoxide dismutase proteins linked to amyotrophic lateral sclerosis

21 January 2018

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Selective association of misfolded ALS-linked mutant SOD1 with the cytoplasmic face of mitochondria.

21 January 2018

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Mutant superoxide dismutase 1 forms aggregates in the brain mitochondrial matrix of amyotrophic lateral sclerosis mice.

21 January 2018

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High molecular weight complexes of mutant superoxide dismutase 1: age-dependent and tissue-specific accumulation

21 January 2018

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Fibrillar inclusions and motor neuron degeneration in transgenic mice expressing superoxide dismutase 1 with a disrupted copper-binding site

21 January 2018

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Copper-binding-site-null SOD1 causes ALS in transgenic mice: aggregates of non-native SOD1 delineate a common feature

21 January 2018

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Progressive aggregation despite chaperone associations of a mutant SOD1-YFP in transgenic mice that develop ALS.

21 January 2018

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Histological evidence of protein aggregation in mutant SOD1 transgenic mice and in amyotrophic lateral sclerosis neural tissues

21 January 2018

1 reference

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Expression of an endoplasmic reticulum-resident chaperone, glucose-regulated stress protein 78, in the spinal cord of a mouse model of amyotrophic lateral sclerosis.

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2010.06753.X

Soluble misfolded subfractions of mutant superoxide dismutase-1s are enriched in spinal cords throughout life in murine ALS models

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2010.06753.X

Sixteen novel mutations in the Cu/Zn superoxide dismutase gene in amyotrophic lateral sclerosis: a decade of discoveries, defects and disputes

21 January 2018

1 reference

https://api.crossref.org/works/10.1111%2FJ.1471-4159.2010.06753.X

10.1111/J.1471-4159.2010.06753.X

21 January 2018

Identifiers

DOI

1 reference

4 May 2018

1 reference

4 May 2018