(Q35591553)

9 August 2017

title

A CFTR potentiator in patients with cystic fibrosis and the G551D mutation (English)

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9 August 2017

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ChEBI release 2020-05-28

Claire E Wainwright

9

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Felix Ratjen

Felix Ratjen

12

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Stuart Elborn

J Stuart Elborn

19

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Scott Bell

Scott C Bell

5

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Richard Moss

11

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ORCID Public Data File 2021

Isabelle Sermet-Gaudelus

13

Isabelle Sermet-Gaudelus

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9 August 2017

Bonnie W Ramsey

1

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9 August 2017

Jane Davies

2

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9 August 2017

N Gerard McElvaney

3

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9 August 2017

Elizabeth Tullis

4

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9 August 2017

Pavel Dřevínek

6

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9 August 2017

Matthias Griese

7

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9 August 2017

Edward F McKone

8

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9 August 2017

Michael W Konstan

10

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9 August 2017

Steven M Rowe

14

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9 August 2017

Qunming Dong

15

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9 August 2017

Sally Rodriguez

16

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9 August 2017

Karl Yen

17

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9 August 2017

Claudia Ordoñez

18

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9 August 2017

VX08-770-102 Study Group

20

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9 August 2017

language of work or name

English

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publication date

1 November 2011

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The New England Journal of Medicine

9 August 2017

published in

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9 August 2017

volume

365

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9 August 2017

issue

18

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9 August 2017

page(s)

1663-1672

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Effect of VX-770 in persons with cystic fibrosis and the G551D-CFTR mutation

9 August 2017

cites work

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3230303

Failure to recover to baseline pulmonary function after cystic fibrosis pulmonary exacerbation

12 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3230303

Effect of azithromycin on pulmonary function in patients with cystic fibrosis uninfected with Pseudomonas aeruginosa: a randomized controlled trial

12 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3230303

Rescue of CF airway epithelial cell function in vitro by a CFTR potentiator, VX-770

12 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3230303

Determination of the minimal clinically important difference scores for the Cystic Fibrosis Questionnaire-Revised respiratory symptom scale in two populations of patients with cystic fibrosis and chronic Pseudomonas aeruginosa airway infection

12 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3230303

Guidelines for diagnosis of cystic fibrosis in newborns through older adults: Cystic Fibrosis Foundation consensus report

12 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3230303

Cystic fibrosis pulmonary guidelines: chronic medications for maintenance of lung health.

12 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3230303

12 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3230303

Pathophysiology and Management of Pulmonary Infections in Cystic Fibrosis

12 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3230303

Effect of genotype on phenotype and mortality in cystic fibrosis: a retrospective cohort study

12 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3230303

Molecular mechanisms of CFTR chloride channel dysfunction in cystic fibrosis

12 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3230303

Effect of aerosolized recombinant human DNase on exacerbations of respiratory symptoms and on pulmonary function in patients with cystic fibrosis. The Pulmozyme Study Group

12 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3230303

Changes in the normal maximal expiratory flow-volume curve with growth and aging

12 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3230303

A rational approach to the nutritional care of patients with cystic fibrosis.

12 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3230303

Identification of the cystic fibrosis gene: genetic analysis

12 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3230303

Identification of the cystic fibrosis gene: cloning and characterization of complementary DNA

12 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3230303

A controlled trial of long-term inhaled hypertonic saline in patients with cystic fibrosis

12 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3230303

Development and validation of The Cystic Fibrosis Questionnaire in the United States: a health-related quality-of-life measure for cystic fibrosis.

26 September 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3230303

Azithromycin in patients with cystic fibrosis chronically infected with Pseudomonas aeruginosa: a randomized controlled trial

26 September 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3230303

Sweat analysis proficiency testing for cystic fibrosis

26 September 2018

1 reference

12 December 2020

Expression of cystic fibrosis transmembrane conductance regulator corrects defective chloride channel regulation in cystic fibrosis airway epithelial cells

1 reference

12 December 2020

Intermittent administration of inhaled tobramycin in patients with cystic fibrosis. Cystic Fibrosis Inhaled Tobramycin Study Group

1 reference

12 December 2020

Laboratory parameter profiles among patients with cystic fibrosis

1 reference

12 December 2020

The prevalence of cystic fibrosis in the European Union

1 reference

12 December 2020

Identifiers

DOI

10.1056/NEJMOA1105185

1 reference

9 August 2017

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9 August 2017

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