(Q35645325)

9 August 2017

title

Equilibria and kinetics of folding of gelsolin domain 2 and mutants involved in familial amyloidosis-Finnish type (English)

1 reference

9 August 2017

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3

Fersht AR

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9 August 2017

Isaacson RL

1

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9 August 2017

Weeds AG

series ordinal

2

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9 August 2017

language of work or name

English

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publication date

1 September 1999

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Proceedings of the National Academy of Sciences of the United States of America

9 August 2017

published in

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9 August 2017

volume

96

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9 August 2017

issue

20

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9 August 2017

page(s)

11247-11252

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9 August 2017

cites work

Tissue sulfhydryl groups

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Designing conditions for in vitro formation of amyloid protofilaments and fibrils

12 July 2018

1 reference

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Functions of gelsolin: motility, signaling, apoptosis, cancer

12 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=18019

Folding kinetics of villin 14T, a protein domain with a central beta-sheet and two hydrophobic cores

12 July 2018

1 reference

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The alternative conformations of amyloidogenic proteins and their multi-step assembly pathways

12 July 2018

1 reference

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The crystal structure of plasma gelsolin: implications for actin severing, capping, and nucleation

12 July 2018

1 reference

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Amyloid fibril formation and protein misassembly: a structural quest for insights into amyloid and prion diseases

12 July 2018

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Instability, unfolding and aggregation of human lysozyme variants underlying amyloid fibrillogenesis

12 July 2018

1 reference

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For protein misassembly, it's the "I" decade

12 July 2018

1 reference

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Over-production of proteins in Escherichia coli: mutant hosts that allow synthesis of some membrane proteins and globular proteins at high levels

12 July 2018

1 reference

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Alternative conformations of amyloidogenic proteins govern their behavior

12 July 2018

1 reference

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The acid-mediated denaturation pathway of transthyretin yields a conformational intermediate that can self-assemble into amyloid

12 July 2018

1 reference

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Engineered disulfide bonds as probes of the folding pathway of barnase: increasing the stability of proteins against the rate of denaturation

12 July 2018

1 reference

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Application of physical organic chemistry to engineered mutants of proteins: Hammond postulate behavior in the transition state of protein folding

12 July 2018

1 reference

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The machinery of cell crawling

12 July 2018

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Hemostatic, inflammatory, and fibroblast responses are blunted in mice lacking gelsolin

12 July 2018

1 reference

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1H NMR of A beta amyloid peptide congeners in water solution. Conformational changes correlate with plaque competence

12 July 2018

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Familial systemic paramyloidosis with lattice dystrophy of the cornea, progressive cranial neuropathy, skin changes and various internal symptoms. A previously unrecognized heritable syndrome.

12 July 2018

1 reference

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Plasma and cytoplasmic gelsolins are encoded by a single gene and contain a duplicated actin-binding domain

12 July 2018

1 reference

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Calculation of protein extinction coefficients from amino acid sequence data

12 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=18019

Expression of human plasma gelsolin in Escherichia coli and dissection of actin binding sites by segmental deletion mutagenesis

12 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=18019

Folding of chymotrypsin inhibitor 2. 1. Evidence for a two-state transition

12 July 2018

1 reference

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The folding of an enzyme. II. Substructure of barnase and the contribution of different interactions to protein stability

12 July 2018

1 reference

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The Extracellular Actin-Scavenger System and Actin Toxicity

12 July 2018

1 reference

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Cells of the neuronal lineage play a major role in the generation of amyloid precursor fragments in gelsolin-related amyloidosis

12 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=18019

Gelsolin–derived familial amyloidosis caused by asparagine or tyrosine substitution for aspartic acid at residue 187

25 September 2018

1 reference

Crossref

https://api.crossref.org/works/10.1073%2FPNAS.96.20.11247

Synchrotron X-ray studies suggest that the core of the transthyretin amyloid fibril is a continuous β-sheet helix

21 January 2018

1 reference

Crossref

https://api.crossref.org/works/10.1073%2FPNAS.96.20.11247

Movement of the position of the transition state in protein folding

21 January 2018

1 reference

Crossref

https://api.crossref.org/works/10.1073%2FPNAS.96.20.11247

Variant plasma gelsolin responsible for familial amyloidosis (Finnish type) has defective actin severing activity

21 January 2018

1 reference

12 December 2020

Reduction in viscosity of cystic fibrosis sputum in vitro by gelsolin

1 reference

12 December 2020

Amyloid protein in familial amyloidosis (Finnish type) is homologous to gelsolin, an actin-binding protein

1 reference

12 December 2020

In vitro expression analysis shows that the secretory form of gelsolin is the sole source of amyloid in gelsolin-related amyloidosis

1 reference

12 December 2020

Gelsolin activates DNase I in vitro and cystic fibrosis sputum

1 reference

12 December 2020

Identification of the circulating amyloid precursor and other gelsolin metabolites in patients with G654A mutation in the gelsolin gene (Finnish familial amyloidosis): pathogenetic and diagnostic implications

1 reference

12 December 2020

The amyloidogenicity of gelsolin is controlled by proteolysis and pH

1 reference

12 December 2020

Identifiers

DOI

10.1073/PNAS.96.20.11247

1 reference

9 August 2017

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1 reference

9 August 2017

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