(Q36239823)

13 August 2017

Biogenesis of iron-sulfur proteins in eukaryotes: components, mechanism and pathology (English)

1 reference

13 August 2017

2

Roland Lill

1 reference

13 August 2017

Jana Gerber

1

1 reference

13 August 2017

1 November 2002

1 reference

13 August 2017

1 reference

13 August 2017

2

1 reference

13 August 2017

1-2

1 reference

13 August 2017

71-86

1 reference

Iron-dependent self-assembly of recombinant yeast frataxin: implications for Friedreich ataxia

13 August 2017

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

IscU as a Scaffold for Iron−Sulfur Cluster Biosynthesis: Sequential Assembly of [2Fe-2S] and [4Fe-4S] Clusters in IscU†

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

Modular organization and identification of a mononuclear iron-binding site within the NifU protein

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

Mutation of a putative mitochondrial iron transporter gene (ABC7) in X-linked sideroblastic anemia and ataxia (XLSA/A)

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

The genome sequence of Rickettsia prowazekii and the origin of mitochondria

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

Regulation of mitochondrial iron accumulation by Yfh1p, a putative homolog of frataxin

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

YAH1 of Saccharomyces cerevisiae: a new essential gene that codes for a protein homologous to human adrenodoxin.

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

Spectroscopy of succinate dehydrogenases, a historical perspective

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

Iron-sulfur clusters: nature's modular, multipurpose structures

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

The GAA triplet-repeat expansion in Friedreich ataxia interferes with transcription and may be associated with an unusual DNA structure

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

Friedreich's ataxia: autosomal recessive disease caused by an intronic GAA triplet repeat expansion

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

Assembly and iron-binding properties of human frataxin, the protein deficient in Friedreich ataxia

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

The nitrogenase FeMo-cofactor and P-cluster pair: 2.2 A resolution structures

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

Crystal structure of Escherichia coli CyaY protein reveals a previously unidentified fold for the evolutionarily conserved frataxin family

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

Crystal structure of the cystine C-S lyase from Synechocystis: stabilization of cysteine persulfide for FeS cluster biosynthesis

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

Inactivation of the Friedreich ataxia mouse gene leads to early embryonic lethality without iron accumulation

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

Mitochondrial iron metabolism in the yeast Saccharomyces cerevisiae

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

Identification of a human mitochondrial ABC transporter, the functional orthologue of yeast Atm1p

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

Nitrogenase metalloclusters: structures, organization, and synthesis

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

Crystal structure of human frataxin

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

Clinical and genetic abnormalities in patients with Friedreich's ataxia

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

Low iron concentration and aconitase deficiency in a yeast frataxin homologue deficient strain

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

Deletion of the yeast homologue of the human gene associated with Friedreich's ataxia elicits iron accumulation in mitochondria.

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

Mitochondrial control of iron homeostasis. A genome wide analysis of gene expression in a yeast frataxin-deficient strain

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

nifU gene product from Azotobacter vinelandii is a homodimer that contains two identical [2Fe-2S] clusters.

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

Structure of a NifS homologue: X-ray structure analysis of CsdB, an Escherichia coli counterpart of mammalian selenocysteine lyase

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

Saccharomyces cerevisiae ISU1 and ISU2: members of a well-conserved gene family for iron-sulfur cluster assembly

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

Molecular control of vertebrate iron metabolism: mRNA-based regulatory circuits operated by iron, nitric oxide, and oxidative stress

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

Interaction of the iron-sulfur cluster assembly protein IscU with the Hsc66/Hsc20 molecular chaperone system of Escherichia coli

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

Role of Saccharomyces cerevisiae ISA1 and ISA2 in iron homeostasis

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

Crystal structure of a NifS-like protein from Thermotoga maritima: implications for iron sulphur cluster assembly

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

IscS is a sulfurtransferase for the in vitro biosynthesis of 4-thiouridine in Escherichia coli tRNA

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

Evidence for the transfer of sulfane sulfur from IscS to ThiI during the in vitro biosynthesis of 4-thiouridine in Escherichia coli tRNA

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

Requirement for hsp70 in the mitochondrial matrix for translocation and folding of precursor proteins

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

Isa1p is a component of the mitochondrial machinery for maturation of cellular iron-sulfur proteins and requires conserved cysteine residues for function

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

J-domain protein, Jac1p, of yeast mitochondria required for iron homeostasis and activity of Fe-S cluster proteins

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

The mitochondrial proteins Atm1p and Nfs1p are essential for biogenesis of cytosolic Fe/S proteins

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

Mt-Hsp70 homolog, Ssc2p, required for maturation of yeast frataxin and mitochondrial iron homeostasis

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

The yeast connection to Friedreich ataxia.

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

IscA, an alternate scaffold for Fe-S cluster biosynthesis

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

A mutation of the mitochondrial ABC transporter Sta1 leads to dwarfism and chlorosis in the Arabidopsis mutant starik.

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

Characterization of recombinant adrenodoxin reductase homologue (Arh1p) from yeast. Implication in in vitro cytochrome p45011beta monooxygenase system

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

The cardiomyopathy of Friedreich's ataxia morphological observations in 3 cases

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

Targeting of a human iron-sulfur cluster assembly enzyme, nifs, to different subcellular compartments is regulated through alternative AUG utilization

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

Mechanism of iron transport to the site of heme synthesis inside yeast mitochondria

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

A mitochondrial ferredoxin is essential for biogenesis of cellular iron-sulfur proteins

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

An essential function of the mitochondrial sulfhydryl oxidase Erv1p/ALR in the maturation of cytosolic Fe/S proteins

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

Erv1p from Saccharomyces cerevisiae is a FAD-linked sulfhydryl oxidase

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

A new pathway for vacuolar cadmium sequestration in Saccharomyces cerevisiae: YCF1-catalyzed transport of bis(glutathionato)cadmium

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

Yeast mitochondrial protein, Nfs1p, coordinately regulates iron-sulfur cluster proteins, cellular iron uptake, and iron distribution

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

Adrenodoxin reductase homolog (Arh1p) of yeast mitochondria required for iron homeostasis

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

Maturation of cellular Fe-S proteins: an essential function of mitochondria

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

Mitochondrial ABC transporters

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

The essential role of mitochondria in the biogenesis of cellular iron-sulfur proteins

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

Dual function of a new nuclear gene for oxidative phosphorylation and vegetative growth in yeast

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

Deficit of in vivo mitochondrial ATP production in patients with Friedreich ataxia

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

The mitochondrial proteins Ssq1 and Jac1 are required for the assembly of iron sulfur clusters in mitochondria

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

The reconstitution of clostridial ferredoxin

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

ARH1 of Saccharomyces cerevisiae: a new essential gene that codes for a protein homologous to the human adrenodoxin reductase

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

Mitochondrial changes associated with glutathione deficiency

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

POSTTRANSLATIONAL ASSEMBLY OF PHOTOSYNTHETIC METALLOPROTEINS.

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

MTABC3, a novel mitochondrial ATP-binding cassette protein involved in iron homeostasis

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

Biogenesis of iron-sulfur proteins in eukaryotes: a novel task of mitochondria that is inherited from bacteria

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

The yeast frataxin homolog Yfh1p plays a specific role in the maturation of cellular Fe/S proteins

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

The genome of Rickettsia prowazekii and some thoughts on the origin of mitochondria and hydrogenosomes

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

Towards a structural understanding of Friedreich's ataxia: the solution structure of frataxin

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

Nuclear localization of yeast Nfs1p is required for cell survival

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

Protein import into mitochondria

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

Transfer of iron-sulfur cluster from NifU to apoferredoxin

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

Iron-sulfur cluster assembly: characterization of IscA and evidence for a specific and functional complex with ferredoxin

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

Mitochondrial Isa2p plays a crucial role in the maturation of cellular iron-sulfur proteins

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

Nitrogenase structure and function: a biochemical-genetic perspective

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

Versatility of the mitochondrial protein import machinery

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

Recent advances in the molecular pathogenesis of Friedreich ataxia

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

Mouse models for Friedreich ataxia exhibit cardiomyopathy, sensory nerve defect and Fe-S enzyme deficiency followed by intramitochondrial iron deposits

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

The yeast frataxin homologue mediates mitochondrial iron efflux. Evidence for a mitochondrial iron cycle

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

Nitrogenase: standing at the crossroads

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

Frataxin activates mitochondrial energy conversion and oxidative phosphorylation

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

Aconitase and mitochondrial iron-sulphur protein deficiency in Friedreich ataxia

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

A second iron-regulatory system in yeast independent of Aft1p

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

Isolation and chromosomal mapping of a novel ATP-binding cassette transporter conserved in mouse and human.

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

The cold sensitivity of a mutant of Saccharomyces cerevisiae lacking a mitochondrial heat shock protein 70 is suppressed by loss of mitochondrial DNA.

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

Evidence for a conserved system for iron metabolism in the mitochondria of Saccharomyces cerevisiae

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

The two mitochondrial heat shock proteins 70, Ssc1 and Ssq1, compete for the cochaperone Mge1.

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

Cloning and chromosomal mapping of a novel ABC transporter gene (hABC7), a candidate for X-linked sideroblastic anemia with spinocerebellar ataxia

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

Maturation of cytosolic iron-sulfur proteins requires glutathione

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

Sulfur transfer from IscS to IscU: the first step in iron-sulfur cluster biosynthesis.

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

Suppressors of superoxide dismutase (SOD1) deficiency in Saccharomyces cerevisiae. Identification of proteins predicted to mediate iron-sulfur cluster assembly

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

Functional assignment of the ORF2-iscS-iscU-iscA-hscB-hscA-fdx-ORF3 gene cluster involved in the assembly of Fe-S clusters in Escherichia coli

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

Distinct iron-sulfur cluster assembly complexes exist in the cytosol and mitochondria of human cells

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

Transfer of sulfur from IscS to IscU during Fe/S cluster assembly

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

Role of the mitochondrial Hsp70s, Ssc1 and Ssq1, in the maturation of Yfh1

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

Jac1, a mitochondrial J-type chaperone, is involved in the biogenesis of Fe/S clusters in Saccharomyces cerevisiae

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

Respiratory deficiency due to loss of mitochondrial DNA in yeast lacking the frataxin homologue

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

Iron-sulfur cluster biosynthesis: characterization of Schizosaccharomyces pombe Isa1.

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

Characterization of an Iron−Sulfur Cluster Assembly Protein (ISU1) fromSchizosaccharomyces pombe†

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

Iron-regulated DNA binding by the AFT1 protein controls the iron regulon in yeast.

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

NifS-directed assembly of a transient [2Fe-2S] cluster within the NifU protein

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

Cysteine desulfurase activity indicates a role for NIFS in metallocluster biosynthesis

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

Mechanism for the desulfurization of L-cysteine catalyzed by the nifS gene product

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

Assembly of iron-sulfur clusters. Identification of an iscSUA-hscBA-fdx gene cluster from Azotobacter vinelandii

1 reference

https://api.crossref.org/works/10.1016%2FS1567-7249%2802%2900041-7

7 January 2021

10.1016/S1567-7249(02)00041-7

Identifiers

DOI

1 reference

13 August 2017

1 reference

PubMed ID

16120310