(Q37819431)

English

Lung deposition of inhaled alpha-1-proteinase inhibitor (alpha 1-PI) - problems and experience of alpha1-PI inhalation therapy in patients with hereditary alpha1-PI deficiency and cystic fibrosis

scientific article

In more languages

Statements

scholarly article

1 reference

Europe PubMed Central

23 August 2017

11 references

13 March 2019

21 March 2019

24 March 2019

22 April 2019

9 October 2019

20 November 2019

27 November 2019

13 December 2019

28 January 2021

31 January 2021

6 February 2021

Lung deposition of inhaled alpha-1-proteinase inhibitor (alpha 1-PI) - problems and experience of alpha1-PI inhalation therapy in patients with hereditary alpha1-PI deficiency and cystic fibrosis (English)

1 reference

Europe PubMed Central

23 August 2017

cystic fibrosis

9 references

13 March 2019

21 March 2019

24 March 2019

22 April 2019

9 October 2019

20 November 2019

27 November 2019

13 December 2019

28 January 2021

alpha-1-antitrypsin deficiency

11 references

13 March 2019

21 March 2019

24 March 2019

22 April 2019

9 October 2019

20 November 2019

27 November 2019

13 December 2019

28 January 2021

31 January 2021

6 February 2021

respiratory system

1 reference

9 October 2019

1 reference

20 November 2019

1 reference

27 November 2019

1 reference

13 December 2019

Serpin family A member 1

1 reference

31 January 2021

perinatal disease

1 reference

6 February 2021

author name string

R Siekmeier

1

1 reference

Europe PubMed Central

23 August 2017

language of work or name

0 references

publication date

1 November 2010

1 reference

Europe PubMed Central

23 August 2017

4 November 2010

11 references

13 March 2019

21 March 2019

24 March 2019

22 April 2019

9 October 2019

20 November 2019

27 November 2019

13 December 2019

28 January 2021

31 January 2021

6 February 2021

European Journal of Medical Research

12 references

Europe PubMed Central

23 August 2017

13 March 2019

21 March 2019

24 March 2019

22 April 2019

9 October 2019

20 November 2019

27 November 2019

13 December 2019

28 January 2021

31 January 2021

6 February 2021

15 Suppl 2

1 reference

Europe PubMed Central

23 August 2017

164-174

1 reference

Europe PubMed Central

23 August 2017

The electrophoretic α1-globulin pattern of serum in α1-antitrypsin deficiency. 1963.

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4360286

6 September 2017

Intravenous alpha-1 antitrypsin augmentation therapy for treating patients with alpha-1 antitrypsin deficiency and lung disease

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4360286

6 September 2017

The changing microbial epidemiology in cystic fibrosis

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4360286

6 September 2017

The I-neb Adaptive Aerosol Delivery System enhances delivery of alpha1-antitrypsin with controlled inhalation

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4360286

6 September 2017

Novel devices for individualized controlled inhalation can optimize aerosol therapy in efficacy, patient care and power of clinical trials

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4360286

6 September 2017

Role of the pulmonary epithelium and inflammatory signals in acute lung injury

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4360286

6 September 2017

Alpha-1 antitrypsin (AAT) deficiency - what are the treatment options?

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4360286

6 September 2017

Emerging treatments in cystic fibrosis

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4360286

6 September 2017

Mechanisms of neutrophil accumulation in the lungs against bacteria

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4360286

6 September 2017

Clinical practice and genetic counseling for cystic fibrosis and CFTR-related disorders

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4360286

6 September 2017

Proteases and cystic fibrosis

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4360286

6 September 2017

Alpha-1 antitrypsin: now available, but do we need it?

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4360286

6 September 2017

Clinical perspectives on pulmonary systemic and macromolecular delivery

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4360286

6 September 2017

Estimated numbers and prevalence of PI*S and PI*Z alleles of alpha1-antitrypsin deficiency in European countries.

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4360286

6 September 2017

Potential role of inhibitors of neutrophil elastase in treating diseases of the airway

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4360286

6 September 2017

Alpha1-antitrypsin deficiency. 2: genetic aspects of alpha(1)-antitrypsin deficiency: phenotypes and genetic modifiers of emphysema risk

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4360286

6 September 2017

Neutrophil elastase inhibitors as treatment for COPD.

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4360286

6 September 2017

Serine proteinase inhibitor therapy in alpha(1)-antitrypsin inhibitor deficiency and cystic fibrosis

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4360286

6 September 2017

Replacement therapy of alpha 1-antitrypsin deficiency. Reversal of protease-antiprotease imbalance within the alveolar structures of PiZ subjects

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4360286

6 September 2017

Recombinant DNA-produced alpha 1-antitrypsin administered by aerosol augments lower respiratory tract antineutrophil elastase defenses in individuals with alpha 1-antitrypsin deficiency

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4360286

6 September 2017

Pulmonary deposition and clearance of aerosolized alpha-1-proteinase inhibitor administered to dogs and to sheep

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4360286

6 September 2017

Fate of aerosolized recombinant DNA-produced alpha 1-antitrypsin: use of the epithelial surface of the lower respiratory tract to administer proteins of therapeutic importance

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4360286

6 September 2017

Comparative demographics of the European cystic fibrosis population: a cross-sectional database analysis

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4360286

14 September 2017

Replacement therapy for alpha 1-antitrypsin deficiency associated with emphysema

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4360286

28 September 2017

Opportunities for the use of aerosolized alpha 1-antitrypsin for the treatment of cystic fibrosis

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4360286

28 September 2017

Safety and efficacy of recombinant alpha(1)-antitrypsin therapy in cystic fibrosis

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4360286

23 June 2018

The intrapulmonary half-life and safety of aerosolized alpha1-protease inhibitor in normal volunteers.

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4360286

23 June 2018

Strategies for aerosol therapy of alpha 1-antitrypsin deficiency by the aerosol route

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4360286

23 June 2018

alpha1-Antitrypsin deficiency: best clinical practice

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4360286

1 September 2018

Lung deposition of inhaled alpha1-proteinase inhibitor in cystic fibrosis and alpha1-antitrypsin deficiency.

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4360286

1 September 2018

Alpha-1-antitrypsin aerosolised augmentation abrogates neutrophil elastase-induced expression of cathepsin B and matrix metalloprotease 2 in vivo and in vitro.

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4360286

1 September 2018

Inhalation of tobramycin in patients with cystic fibrosis: comparison of two methods

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4360286

1 September 2018

Estimated numbers and prevalence of PI*S and PI*Z deficiency alleles of alpha1-antitrypsin deficiency in Asia.

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4360286

1 September 2018

Optimum peripheral drug deposition in patients with cystic fibrosis.

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4360286

1 September 2018

PULMONARY EMPHYSEMA AND ALPHA1-ANTITRYPSIN DEFICIENCY.

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4360286

1 September 2018

Peripheral deposition of alpha1-protease inhibitor using commercial inhalation devices

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4360286

1 September 2018

Inhalation of alpha(1)-protease inhibitor in cystic fibrosis does not affect surfactant convertase and surface activity

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4360286

1 September 2018

alpha1-Antitrypsin inhalation reduces airway inflammation in cystic fibrosis patients

1 reference

https://pubmed.ncbi.nlm.nih.gov/21147646

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Anti-neutrophil-elastase defenses of the lower respiratory tract in alpha 1-antitrypsin deficiency directly augmented with an aerosol of alpha 1-antitrypsin

1 reference

https://pubmed.ncbi.nlm.nih.gov/21147646

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Inhalation of [123I]alpha1-protease inhibitor: toward a new therapeutic concept of alpha1-protease inhibitor deficiency?

1 reference

https://pubmed.ncbi.nlm.nih.gov/21147646

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Aerosol α1 -antitrypsin treatment for cystic fibrosis

1 reference

https://pubmed.ncbi.nlm.nih.gov/21147646

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Prolastin aerosol therapy and sputum taurine in cystic fibrosis

1 reference

https://pubmed.ncbi.nlm.nih.gov/21147646

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Reduced proteolysis of surfactant protein A and changes of the bronchoalveolar lavage fluid proteome by inhaled alpha 1-protease inhibitor in cystic fibrosis

1 reference

https://pubmed.ncbi.nlm.nih.gov/21147646

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Augmentation therapy for alpha1 antitrypsin deficiency: a meta-analysis

1 reference

https://pubmed.ncbi.nlm.nih.gov/21147646

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Ethnic differences in alpha-1 antitrypsin deficiency in the United States of America

1 reference

https://pubmed.ncbi.nlm.nih.gov/21147646

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

[Update: Alpha-1-antitrypsin deficiency. Summary of a scientific symposium at the conference of the Swiss Pneumologic Society on April 16th, 2009]

1 reference

https://pubmed.ncbi.nlm.nih.gov/21147646

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Augmentation therapy in alpha-1 antitrypsin deficiency

1 reference

https://pubmed.ncbi.nlm.nih.gov/21147646

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Biologic availability of injected or aerosolized alpha 1 proteinase inhibitor

1 reference

https://pubmed.ncbi.nlm.nih.gov/21147646

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Identifiers

1 reference

Europe PubMed Central

23 August 2017

1 reference

Europe PubMed Central

23 August 2017

Sitelinks

Wikipedia(0 entries)

Wikibooks(0 entries)

Wikinews(0 entries)

Wikiquote(0 entries)

Wikisource(0 entries)

Wikiversity(0 entries)

Wikivoyage(0 entries)

Wiktionary(0 entries)

Multilingual sites(0 entries)

Retrieved from "https://www.wikidata.org/w/index.php?title=Q37819431&oldid=1702640984"