(Q38088187)

28 August 2017

4 references

9 October 2019

27 November 2019

29 May 2020

14 October 2020

Recent insights into C3 glomerulopathy (English)

1 reference

complement system proteins

28 August 2017

4 references

9 October 2019

27 November 2019

29 May 2020

14 October 2020

1 reference

9 October 2019

1 reference

27 November 2019

1 reference

14 October 2020

Thomas D Barbour

1

0 references

Matthew C Pickering

object named as

Matthew C Pickering

series ordinal

2

0 references

author name string

H Terence Cook

series ordinal

3

1 reference

PMCID

3707523

28 August 2017

language of work or name

English

0 references

publication date

10 March 2013

1 reference

PMCID

3707523

Nephrology Dialysis Transplantation

28 August 2017

1 July 2013

3 references

9 October 2019

27 November 2019

14 October 2020

5 references

28 August 2017

9 October 2019

27 November 2019

29 May 2020

14 October 2020

28

1 reference

28 August 2017

7

1 reference

28 August 2017

1685-1693

1 reference

Creative Commons Attribution-NonCommercial 3.0 Unported

28 August 2017

4 references

9 October 2019

27 November 2019

29 May 2020

Thrombotic microangiopathy and associated renal disorders

14 October 2020

cites work

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3707523

Eculizumab for the Treatment of Dense-Deposit Disease

6 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3707523

Eculizumab in a patient with dense-deposit disease

6 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3707523

Eculizumab for dense deposit disease and C3 glomerulonephritis

6 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3707523

Clinical features and outcomes of 98 children and adults with dense deposit disease.

6 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3707523

Regulating complement in the kidney: insights from CFHR5 nephropathy

6 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3707523

Complement factor H variants I890 and L1007 while commonly associated with atypical hemolytic uremic syndrome are polymorphisms with no functional significance

6 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3707523

Allelic variants of complement genes associated with dense deposit disease

6 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3707523

Glomerulonephritis with isolated C3 deposits and monoclonal gammopathy: a fortuitous association?

6 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3707523

6 September 2017

Dense deposit disease.

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3707523

Familial C3 glomerulopathy associated with CFHR5 mutations: clinical characteristics of 91 patients in 16 pedigrees

6 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3707523

Common polymorphisms in C3, factor B, and factor H collaborate to determine systemic complement activity and disease risk

6 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3707523

Proliferative glomerulonephritis secondary to dysfunction of the alternative pathway of complement

6 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3707523

Genome-wide association study identifies susceptibility loci for IgA nephropathy

6 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3707523

Allograft failure in kidney transplant recipients with membranoproliferative glomerulonephritis

6 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3707523

Recurrence of complement factor H-related protein 5 nephropathy in a renal transplant

6 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3707523

Human C3 mutation reveals a mechanism of dense deposit disease pathogenesis and provides insights into complement activation and regulation

6 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3707523

Dense deposit disease associated with monoclonal gammopathy of undetermined significance

6 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3707523

Identification of a mutation in complement factor H-related protein 5 in patients of Cypriot origin with glomerulonephritis

6 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3707523

C3 glomerulopathy: a new classification

6 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3707523

Treatment with human complement factor H rapidly reverses renal complement deposition in factor H-deficient mice

6 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3707523

Membranoproliferative glomerulonephritis secondary to monoclonal gammopathy.

6 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3707523

Complement regulators and inhibitory proteins

6 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3707523

Structure of complement fragment C3b-factor H and implications for host protection by complement regulators

6 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3707523

The high frequency of complement factor H related CFHR1 gene deletion is restricted to specific subgroups of patients with atypical haemolytic uraemic syndrome.

6 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3707523

Glomeruli of Dense Deposit Disease contain components of the alternative and terminal complement pathway

6 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3707523

Dense deposit disease: clinicopathologic study of 32 pediatric and adult patients

6 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3707523

Factor I is required for the development of membranoproliferative glomerulonephritis in factor H-deficient mice

6 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3707523

Factor H autoantibodies in atypical hemolytic uremic syndrome correlate with CFHR1/CFHR3 deficiency

6 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3707523

New approaches to the treatment of dense deposit disease

6 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3707523

Spontaneous hemolytic uremic syndrome triggered by complement factor H lacking surface recognition domains

6 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3707523

Dense deposit disease is not a membranoproliferative glomerulonephritis

6 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3707523

Deletion of complement factor H-related genes CFHR1 and CFHR3 is associated with atypical hemolytic uremic syndrome

6 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3707523

Primary glomerulonephritis with isolated C3 deposits: a new entity which shares common genetic risk factors with haemolytic uraemic syndrome

6 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3707523

Prevention of C5 activation ameliorates spontaneous and experimental glomerulonephritis in factor H-deficient mice

6 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3707523

Deletion of Lys224 in regulatory domain 4 of Factor H reveals a novel pathomechanism for dense deposit disease (MPGN II)

6 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3707523

Variations in the complement regulatory genes factor H (CFH) and factor H related 5 (CFHR5) are associated with membranoproliferative glomerulonephritis type II (dense deposit disease)

6 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3707523

Membranoproliferative glomerulonephritis type II (dense deposit disease): an update

6 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3707523

Heterozygous and homozygous factor h deficiencies associated with hemolytic uremic syndrome or membranoproliferative glomerulonephritis: report and genetic analysis of 16 cases

6 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3707523

SERUM LEVELS OF BETA-1C GLOBULIN, A COMPLEMENT COMPONENT, IN THE NEPHRITIDES, LIPOID NEPHROSIS, AND OTHER CONDITIONS.

6 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3707523

The molecular basis for hereditary porcine membranoproliferative glomerulonephritis type II: point mutations in the factor H coding sequence block protein secretion

6 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3707523

Complement. Second of two parts

6 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3707523

Complement. First of two parts

6 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3707523

Nephritogenic lambda light chain dimer: a unique human miniautoantibody against complement factor H

6 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3707523

Extensive complement activation in hereditary porcine membranoproliferative glomerulonephritis type II (porcine dense deposit disease)

6 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3707523

Hereditary porcine membranoproliferative glomerulonephritis type II is caused by factor H deficiency

6 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3707523

Hypocomplementæmic Membranoproliferative Glomerulonephritis and Nephrotic Syndrome Associated with Partial Lipodystrophy of the Face and Trunk

6 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3707523

Human genes for three complement components that regulate the activation of C3 are tightly linked

6 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3707523

Activation of the alternative pathway of complement by monoclonal lambda light chains in membranoproliferative glomerulonephritis

6 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3707523

Dense deposit disease: a variant of membranoproliferative glomerulonephritis

6 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3707523

Recurrent Glomerulonephritis After Renal Transplantation

6 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3707523

C3 nephritic factor and SLE: report of four cases and review of the literature.

14 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3707523

Idiopathic mesangiocapillary glomerulonephritis. Comparison of types I and II in children and adults and long-term prognosis

14 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3707523

Recurrence of dense deposits in transplanted kidneys: I. Sequential survey of the lesions

14 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3707523

Factor H facilitates the clearance of GBM bound iC3b by controlling C3 activation in fluid phase

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3707523

Isolation and characterization of two beta1-glycoproteins of human serum

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3707523

Porcine membranoproliferative glomerulonephritis type II: an autosomal recessive deficiency of factor H.

23 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3707523

Plasma C3 and C4 concentrations in management of glomerulonephritis.

23 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3707523

Serum C'3 lytic system in patients with glomerulonephritis

23 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3707523

Hypocomplementemic glomerulonephritis in an infant and mother. Evidence for an abnormal form of C3.

23 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3707523

Fundus changes in (type II) mesangiocapillary glomerulonephritis simulating drusen: a histopathological report

23 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3707523

The amplification loop of the complement pathways.

23 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3707523

Genetic deficiency of complement factor H in a patient with age-related macular degeneration and membranoproliferative glomerulonephritis

31 August 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3707523

The localization of in vivo bound complement in tissue section

31 August 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3707523

[Immuno-electrophoretic study of the blood of disseminated lupus erythematosus patients].

31 August 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3707523

Structure and composition of drusen associated with glomerulonephritis: implications for the role of complement activation in drusen biogenesis.

31 August 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3707523

Uncontrolled C3 activation causes membranoproliferative glomerulonephritis in mice deficient in complement factor H

31 August 2018

2 references

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3707523

1 October 2018

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3707523

Acquired and genetic complement abnormalities play a critical role in dense deposit disease and other C3 glomerulopathies

3 December 2018

1 reference

Crossref

https://api.crossref.org/works/10.1093%2FNDT%2FGFS430

Spontaneous clinical improvement in dense deposit disease

21 January 2018

1 reference

12 December 2020

Composition of nephritic factor-generated glomerular deposits in membranoproliferative glomerulonephritis type 2

1 reference

12 December 2020

C3 nephritic factor (C3NeF): stabilization of fluid phase and cell-bound alternative pathway convertase

1 reference

12 December 2020

An inherited defect in the C3 convertase, C3b,Bb, associated with glomerulonephritis

1 reference

12 December 2020

C3 nephritic factor and hypocomplementaemia in a clinically healthy individual

1 reference

12 December 2020

H deficiency in two brothers with atypical dense intramembranous deposit disease

1 reference

12 December 2020

Dense deposit disease in association with monoclonal gammopathy of unknown significance

1 reference

12 December 2020

Eradication of porcine factor H deficiency in Norway

1 reference

12 December 2020

In situ complement activation in porcine membranoproliferative glomerulonephritis type II

1 reference

12 December 2020

Complement analysis in children with idiopathic membranoproliferative glomerulonephritis: a long-term follow-up

1 reference

12 December 2020

Renal transplantation in patients with dense deposit disease: morphological characteristics of recurrent disease and clinical outcome

1 reference

12 December 2020

[Unusual change of the basal membranes of the kidney.]

1 reference

12 December 2020

Mouse podocyte complement factor H: the functional analog to human complement receptor 1

1 reference

12 December 2020

C3 deposition glomerulopathy due to a functional factor H defect

1 reference

12 December 2020

Anti-factor B autoantibody in dense deposit disease

1 reference

12 December 2020

Experimental models of membranoproliferative glomerulonephritis, including dense deposit disease

1 reference

12 December 2020

Complement factor H deficiency and endocapillary glomerulonephritis due to paternal isodisomy and a novel factor H mutation

1 reference

12 December 2020

Membranoproliferative glomerulonephritis with C3NeF and genetic complement dysregulation

1 reference

12 December 2020

Heterogeneous pattern of renal disease associated with homozygous Factor H deficiency

1 reference

12 December 2020

Combined C3b and factor B autoantibodies and MPGN type II

1 reference

12 December 2020

Recurrent dense deposit disease after renal transplantation: an emerging role for complementary therapies

1 reference

12 December 2020

Identifiers

DOI

10.1093/NDT/GFS430

1 reference

28 August 2017

1 reference

28 August 2017

1 reference

PMCID

3707523