(Q39508625)

12 September 2017

Hepatocyte transplantation improves phenotype and extends survival in a murine model of intermediate maple syrup urine disease (English)

1 reference

12 September 2017

1 reference

Fabio Marongiu

4

0 references

Ewa C Ellis

Ewa Ellis

5

0 references

Stephen C Strom

Stephen C Strom

10

0 references

Gregg E. Homanics

Gregg E Homanics

9

0 references

Kristen J Skvorak

1

Kristen J Skvorak

1 reference

12 September 2017

3

Kenneth Dorko

1 reference

12 September 2017

Harbhajan S Paul

2

1 reference

12 September 2017

Donald Chace

6

1 reference

12 September 2017

Carolyn Ferguson

7

1 reference

12 September 2017

K Michael Gibson

8

1 reference

12 September 2017

12 May 2009

1 reference

12 September 2017

1 reference

12 September 2017

17

1 reference

12 September 2017

7

1 reference

12 September 2017

1266-1273

1 reference

Dual mechanism of brain injury and novel treatment strategy in maple syrup urine disease

12 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2835204

Animal models of maple syrup urine disease

12 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2835204

Ex vivo gene transfer into hepatocytes

12 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2835204

Hepatocyte transplantation: clinical experience and potential for future use.

12 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2835204

Production and characterization of murine models of classic and intermediate maple syrup urine disease

12 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2835204

Mechanisms responsible for regulation of branched-chain amino acid catabolism

12 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2835204

A new syndrome: progressive familial infantile cerebral dysfunction associated with an unusual urinary substance.

12 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2835204

Isolated hepatocyte transplantation in an infant with a severe urea cycle disorder.

12 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2835204

Amplification of engrafted hepatocytes by preparative manipulation of the host liver

12 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2835204

Liver transplantation in maple syrup urine disease

12 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2835204

Hepatocyte transplantation for the treatment of human disease

12 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2835204

Long-term, near-total liver replacement by transplantation of isolated hepatocytes in rats treated with retrorsine

12 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2835204

Treatment of the Crigler-Najjar syndrome type I with hepatocyte transplantation

12 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2835204

The 2-oxo acid dehydrogenase complexes: recent advances

12 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2835204

Mouse hepatocytes migrate to liver parenchyma and function indefinitely after intrasplenic transplantation

12 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2835204

Promoter traps in embryonic stem cells: a genetic screen to identify and mutate developmental genes in mice

12 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2835204

Correction of hyperbilirubinemia in the glucuronyltransferase-deficient rat by intraportal hepatocyte transplantation

12 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2835204

Hepatocyte transplantation as a bridge to orthotopic liver transplantation in terminal liver failure

25 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2835204

Correction of hyperoxaluria by liver repopulation with hepatocytes in a mouse model of primary hyperoxaluria type-1.

15 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2835204

Hepatocyte transplantation for glycogen storage disease type Ib.

21 August 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2835204

Elective liver transplantation for the treatment of classical maple syrup urine disease.

21 August 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2835204

Administration-route and gender-independent long-term therapeutic correction of phenylketonuria (PKU) in a mouse model by recombinant adeno-associated virus 8 pseudotyped vector-mediated gene transfer

21 August 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2835204

Branched chain amino acids as a parameter for catabolism in treated phenylketonuria

21 August 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2835204

Liver repopulation after cell transplantation in mice treated with retrorsine and carbon tetrachloride

21 August 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2835204

Diagnosis and treatment of maple syrup disease: a study of 36 patients

21 August 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2835204

Hepatocyte transplantation as a treatment for glycogen storage disease type 1a.

21 August 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2835204

Correction of liver disease following transplantation of normal rat hepatocytes into Long-Evans Cinnamon rats modeling Wilson's disease

21 August 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2835204

Defining hepatocellular chimerism in a liver failure patient bridged with hepatocyte infusion

21 August 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2835204

Hepatocytes corrected by gene therapy are selected in vivo in a murine model of hereditary tyrosinaemia type I.

21 August 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2835204

Selective intraportal hepatocyte transplantation in analbuminemic and Gunn rats.

21 August 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=2835204

Hepatocellular transplantation for metabolic deficiencies: decrease of plasms bilirubin in Gunn rats

21 August 2018

1 reference

12 December 2020

Hepatocyte transplantation for enzyme deficiency disease in congenic rats

1 reference

12 December 2020

Human liver cell transplantation. Prolonged function in athymic-Gunn and athymic-analbuminemic hybrid rats

1 reference

12 December 2020

Mechanism of increased conversion of branched chain keto acid dehydrogenase from inactive to active form by a medium chain fatty acid (octanoate) in skeletal muscle

1 reference

12 December 2020

Rapid diagnosis of maple syrup urine disease in blood spots from newborns by tandem mass spectrometry

1 reference

12 December 2020

[Mid-term outcome of 2 cases with maple syrup urine disease: role of liver transplantation in the treatment]

1 reference

12 December 2020

Use of human hepatocytes to study P450 gene induction

1 reference

12 December 2020

Transplantation of human hepatocytes

1 reference

12 December 2020

Restoration of serum albumin levels in nagase analbuminemic rats by hepatocyte transplantation

1 reference

12 December 2020

Metabolism of the white blood cells in maple-syrup-urine disease

1 reference

12 December 2020

Hepatocyte transplantation for inherited factor VII deficiency

1 reference

12 December 2020

Hepatocyte transplantation in acute liver failure

1 reference

12 December 2020

Branched-chain L-amino acid metabolism in classical maple syrup urine disease after orthotopic liver transplantation

1 reference

12 December 2020

Morphology and function of isolated hepatocytes transplanted into rat spleen

1 reference

12 December 2020

Identifiers

DOI

10.1038/MT.2009.99

1 reference

12 September 2017

1 reference

12 September 2017

PubMed publication ID

19436271

1 reference