(Q39726453)

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20 January 2020

title

Impaired ganglioside metabolism in Huntington's disease and neuroprotective role of GM1 (English)

1 reference

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20 January 2020

0 references

1

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20 January 2020

Alba Di Pardo

3

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20 January 2020

author name string

Paolo Marchi

2

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20 January 2020

Susanne Lingrell

4

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20 January 2020

Melanie Horkey

5

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20 January 2020

Emily Tidmarsh

6

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20 January 2020

Simonetta Sipione

7

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20 January 2020

language of work or name

English

0 references

publication date

1 March 2010

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20 January 2020

published in

Journal of Neuroscience

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20 January 2020

volume

30

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20 January 2020

issue

11

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20 January 2020

page(s)

4072-4080

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Mice lacking complex gangliosides develop Wallerian degeneration and myelination defects

20 January 2020

cites work

1 reference

12 December 2020

Interaction of cholera toxin and membrane GM1 ganglioside of small intestine

1 reference

12 December 2020

Effects of GM1 ganglioside treatment on pre- and postsynaptic dopaminergic markers in the striatum of parkinsonian monkeys

1 reference

12 December 2020

Wild-type huntingtin protects from apoptosis upstream of caspase-3.

1 reference

12 December 2020

Neurotrophin signal transduction in the nervous system

1 reference

12 December 2020

A one-hit model of cell death in inherited neuronal degenerations

1 reference

12 December 2020

A functional role for complex gangliosides: motor deficits in GM2/GD2 synthase knockout mice.

1 reference

12 December 2020

Dominant phenotypes produced by the HD mutation in STHdh(Q111) striatal cells

1 reference

12 December 2020

Expression of full-length polyglutamine-expanded Huntingtin disrupts growth factor receptor signaling in rat pheochromocytoma (PC12) cells

1 reference

12 December 2020

1 reference

12 December 2020

Sp1 and TAFII130 transcriptional activity disrupted in early Huntington's disease

1 reference

12 December 2020

The IGF-1/Akt pathway is neuroprotective in Huntington's disease and involves Huntingtin phosphorylation by Akt.

1 reference

12 December 2020

Early transcriptional profiles in huntingtin-inducible striatal cells by microarray analyses

1 reference

12 December 2020

Selective striatal neuronal loss in a YAC128 mouse model of Huntington disease

1 reference

12 December 2020

Regulation of ganglioside biosynthesis in the nervous system

1 reference

12 December 2020

Ganglioside/glycosphingolipid turnover: new concepts

1 reference

12 December 2020

Infantile-onset symptomatic epilepsy syndrome caused by a homozygous loss-of-function mutation of GM3 synthase.

1 reference

12 December 2020

Susceptibility of cerebellar granule neurons from GM2/GD2 synthase-null mice to apoptosis induced by glutamate excitotoxicity and elevated KCl: rescue by GM1 and LIGA20.

1 reference

12 December 2020

Generation and function of astroglial lipoproteins from Niemann-Pick type C1-deficient mice

1 reference

12 December 2020

Asymmetric membrane ganglioside sialidase activity specifies axonal fate.

1 reference

12 December 2020

Akt is altered in an animal model of Huntington's disease and in patients

1 reference

12 December 2020

Gangliosides for acute spinal cord injury

1 reference

12 December 2020

Cdk5 phosphorylation of huntingtin reduces its cleavage by caspases: implications for mutant huntingtin toxicity

1 reference

12 December 2020

p53 mediates cellular dysfunction and behavioral abnormalities in Huntington's disease

1 reference

12 December 2020

Exogenous gangliosides, neuronal plasticity and repair, and the neurotrophins

1 reference

12 December 2020

Juvenile Huntington's disease: does a dosage-effect pathogenic mechanism differ from the classical adult disease?

1 reference

12 December 2020

Enhanced susceptibility to kainate-induced seizures, neuronal apoptosis, and death in mice lacking gangliotetraose gangliosides: protection with LIGA 20, a membrane-permeant analog of GM1.

1 reference

12 December 2020

Brain white-matter volume loss and glucose hypometabolism precede the clinical symptoms of Huntington's disease.

1 reference

12 December 2020

Sp1 is up-regulated in cellular and transgenic models of Huntington disease, and its reduction is neuroprotective

1 reference

12 December 2020

Huntingtin phosphorylation sites mapped by mass spectrometry. Modulation of cleavage and toxicity

1 reference

12 December 2020

Gangliosides as components of lipid membrane domains.

1 reference

12 December 2020

Context-dependent dysregulation of transcription by mutant huntingtin

1 reference

12 December 2020

1 reference

12 December 2020

Glycolipid and ganglioside metabolism imbalances in Huntington's disease.

1 reference

12 December 2020

Regulation of axonal development by plasma membrane gangliosides

1 reference

12 December 2020

Atrophy and degeneration in sciatic nerve of presymptomatic mice carrying the Huntington's disease mutation

1 reference

12 December 2020

Nuclear sphingolipids: metabolism and signaling

1 reference

12 December 2020

Huntington's disease: from pathology and genetics to potential therapies

1 reference

12 December 2020

Phosphorylation of mutant huntingtin at S421 restores anterograde and retrograde transport in neurons.

1 reference

12 December 2020

Glycosphingolipid behaviour in complex membranes

1 reference

12 December 2020

Phosphorylation of huntingtin reduces the accumulation of its nuclear fragments

1 reference

12 December 2020

Binding of laminin-1 to monosialoganglioside GM1 in lipid rafts is crucial for neurite outgrowth

1 reference

12 December 2020

GM1 ganglioside therapy in acute ischemic stroke

1 reference

12 December 2020

A solvent partition method for microscale ganglioside purification.

1 reference

12 December 2020

Sub-synaptosomal localization of brain particulate neuraminidase

1 reference

12 December 2020

Prevention of apoptotic neuronal death by GM1 ganglioside. Involvement of Trk neurotrophin receptors.

1 reference

12 December 2020

Exon 1 of the HD gene with an expanded CAG repeat is sufficient to cause a progressive neurological phenotype in transgenic mice

1 reference

12 December 2020

Huntingtin protein colocalizes with lesions of neurodegenerative diseases: An investigation in Huntington's, Alzheimer's, and Pick's diseases

1 reference

12 December 2020

GM1 ganglioside in the treatment of Parkinson's disease

1 reference

12 December 2020

GM1 ganglioside for acute ischemic stroke. Trial design issues

1 reference

12 December 2020

Effect of the mono- and tetra-sialogangliosides, GM1 and GQ1b, on long-term potentiation in the CA1 hippocampal neurons of the guinea pig.

1 reference

12 December 2020

Regulation of ganglioside biosynthesis in the nervous system

1 reference

12 December 2020

10.1523/JNEUROSCI.6348-09.2010

Identifiers

DOI

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:20237277%20AND%20SRC:MED&resulttype=core&format=json

20 January 2020

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20 January 2020

PubMed publication ID

20237277

1 reference