(Q45162912)

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:15564131%20AND%20SRC:MED&resulttype=core&format=json

5 January 2020

title

Dual therapeutic utility of proteasome modulating agents for pharmaco-gene therapy of the cystic fibrosis airway (English)

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:15564131%20AND%20SRC:MED&resulttype=core&format=json

5 January 2020

0 references

0 references

1

1 reference

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5 January 2020

Ziying Yan

7

1 reference

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5 January 2020

Christie Thomas

10

1 reference

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5 January 2020

Joseph Zabner

11

1 reference

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5 January 2020

John F Engelhardt

16

1 reference

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5 January 2020

6

Keith Munson

1 reference

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5 January 2020

author name string

Phil Karp

2

1 reference

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5 January 2020

Christopher J Gerard

3

1 reference

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5 January 2020

Eric Pastor

4

1 reference

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5 January 2020

Douglas Laux

5

1 reference

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5 January 2020

Xiaoming Liu

8

1 reference

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5 January 2020

Simon Godwin

9

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:15564131%20AND%20SRC:MED&resulttype=core&format=json

5 January 2020

Huidong Shi

12

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:15564131%20AND%20SRC:MED&resulttype=core&format=json

5 January 2020

Charles W Caldwell

13

1 reference

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5 January 2020

Richard Peluso

14

1 reference

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5 January 2020

Barrie Carter

15

1 reference

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5 January 2020

publication date

1 December 2004

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5 January 2020

1 reference

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5 January 2020

volume

10

1 reference

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5 January 2020

issue

6

1 reference

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5 January 2020

page(s)

990-1002

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:15564131%20AND%20SRC:MED&resulttype=core&format=json

Cellular heterogeneity of CFTR expression and function in the lung: implications for gene therapy of cystic fibrosis.

5 January 2020

cites work

1 reference

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Cystic fibrosis transmembrane conductance regulator inverts protein kinase A-mediated regulation of epithelial sodium channel single channel kinetics

7 January 2021

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CFTR and outward rectifying chloride channels are distinct proteins with a regulatory relationship

7 January 2021

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Chloride channel and chloride conductance regulator domains of CFTR, the cystic fibrosis transmembrane conductance regulator

7 January 2021

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Identification of the cystic fibrosis transmembrane conductance regulator domains that are important for interactions with ROMK2.

7 January 2021

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The cystic fibrosis transmembrane conductance regulator attenuates the endogenous Ca2+ activated Cl- conductance of Xenopus oocytes.

7 January 2021

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Mucus clearance as a primary innate defense mechanism for mammalian airways

7 January 2021

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Cystic fibrosis and the salt controversy

7 January 2021

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Cystic fibrosis airway epithelia fail to kill bacteria because of abnormal airway surface fluid.

7 January 2021

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Use of nasal potential difference and sweat chloride as outcome measures in multicenter clinical trials in subjects with cystic fibrosis

7 January 2021

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A pilot clinical trial of oral sodium 4-phenylbutyrate (Buphenyl) in deltaF508-homozygous cystic fibrosis patients: partial restoration of nasal epithelial CFTR function

7 January 2021

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A pilot study of aerosolized amiloride for the treatment of lung disease in cystic fibrosis

7 January 2021

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French multicenter randomized double-blind placebo-controlled trial on nebulized amiloride in cystic fibrosis patients. The Amiloride-AFLM Collaborative Study Group

7 January 2021

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A phase I study of aerosolized administration of tgAAVCF to cystic fibrosis subjects with mild lung disease

7 January 2021

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Phase I trial of intranasal and endobronchial administration of a recombinant adeno-associated virus serotype 2 (rAAV2)-CFTR vector in adult cystic fibrosis patients: a two-part clinical study

7 January 2021

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A phase II, double-blind, randomized, placebo-controlled clinical trial of tgAAVCF using maxillary sinus delivery in patients with cystic fibrosis with antrostomies.

7 January 2021

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Safety and biological efficacy of an adeno-associated virus vector-cystic fibrosis transmembrane regulator (AAV-CFTR) in the cystic fibrosis maxillary sinus.

7 January 2021

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Adeno-associated virus type 5 (AAV5) but not AAV2 binds to the apical surfaces of airway epithelia and facilitates gene transfer

7 January 2021

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Polarity influences the efficiency of recombinant adenoassociated virus infection in differentiated airway epithelia.

7 January 2021

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Binding of adeno-associated virus type 5 to 2,3-linked sialic acid is required for gene transfer

7 January 2021

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Endosomal processing limits gene transfer to polarized airway epithelia by adeno-associated virus.

7 January 2021

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Second-strand genome conversion of adeno-associated virus type 2 (AAV-2) and AAV-5 is not rate limiting following apical infection of polarized human airway epithelia

7 January 2021

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Efficient expression of CFTR function with adeno-associated virus vectors that carry shortened CFTR genes

7 January 2021

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CFTR with a partially deleted R domain corrects the cystic fibrosis chloride transport defect in human airway epithelia in vitro and in mouse nasal mucosa in vivo

7 January 2021

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A new dual-vector approach to enhance recombinant adeno-associated virus-mediated gene expression through intermolecular cis activation

7 January 2021

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Noninvasive gene transfer to the lung for systemic delivery of therapeutic proteins.

7 January 2021

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Loss of CFTR chloride channels alters salt absorption by cystic fibrosis airway epithelia in vitro.

7 January 2021

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7 January 2021

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7 January 2021

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7 January 2021

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Distinct classes of proteasome-modulating agents cooperatively augment recombinant adeno-associated virus type 2 and type 5-mediated transduction from the apical surfaces of human airway epithelia

7 January 2021

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Efficiency of gene transfer for restoration of normal airway epithelial function in cystic fibrosis

7 January 2021

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Normalization of raised sodium absorption and raised calcium-mediated chloride secretion by adenovirus-mediated expression of cystic fibrosis transmembrane conductance regulator in primary human cystic fibrosis airway epithelial cells

7 January 2021

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Association of 5' CpG demethylation and altered chromatin structure in the promoter region with transcriptional activation of the multidrug resistance 1 gene in human cancer cells

7 January 2021

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Human amiloride-sensitive epithelial Na+ channel gamma subunit promoter: functional analysis and identification of a polypurine-polypyrimidine tract with the potential for triplex DNA formation

7 January 2021

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7 January 2021

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7 January 2021

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7 January 2021

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