(Q46916908)

26 December 2017

title

Role of N-terminal familial mutations in prion protein fibrillization and prion amyloid propagation in vitro (English)

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26 December 2017

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Eric M Jones

1

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26 December 2017

Krystyna Surewicz

series ordinal

2

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26 December 2017

Witold K Surewicz

series ordinal

3

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26 December 2017

language of work or name

English

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publication date

26 January 2006

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26 December 2017

Journal of Biological Chemistry

published in

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26 December 2017

volume

281

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26 December 2017

issue

12

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26 December 2017

page(s)

8190-8196

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26 December 2017

https://api.crossref.org/works/10.1074%2FJBC.M513417200

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Mammalian prion biology: one century of evolving concepts

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M513417200

21 January 2018

The state of the prion

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M513417200

Prion diseases of humans and animals: their causes and molecular basis

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M513417200

Synthetic mammalian prions

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M513417200

In vitro generation of infectious scrapie prions.

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M513417200

Birth of a prion: spontaneous generation revisited

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M513417200

Emerging principles of conformation-based prion inheritance

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M513417200

The most infectious prion protein particles.

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M513417200

Familial mutations and the thermodynamic stability of the recombinant human prion protein.

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M513417200

Influence of amino acid substitutions related to inherited human prion diseases on the thermodynamic stability of the cellular prion protein.

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M513417200

The effect of disease-associated mutations on the folding pathway of human prion protein

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M513417200

Prion protein diversity and disease in the transmissible spongiform encephalopathies

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M513417200

Flexible N-terminal region of prion protein influences conformation of protease-resistant prion protein isoforms associated with cross-species scrapie infection in vivo and in vitro.

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M513417200

Nucleation-dependent conformational conversion of the Y145Stop variant of human prion protein: structural clues for prion propagation.

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M513417200

Seeded conversion of recombinant prion protein to a disulfide-bonded oligomer by a reduction-oxidation process.

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M513417200

Autocatalytic conversion of recombinant prion proteins displays a species barrier

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M513417200

In vitro conversion of full-length mammalian prion protein produces amyloid form with physical properties of PrP(Sc).

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M513417200

Polymorphism at residue 129 modulates the conformational conversion of the D178N variant of human prion protein 90-231.

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M513417200

Molecular basis of barriers for interspecies transmissibility of mammalian prions

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M513417200

Inherited prion disease with 144 base pair gene insertion. 1. Genealogical and molecular studies.

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M513417200

Human prion protein with valine 129 prevents expression of variant CJD phenotype

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M513417200

Fatal familial insomnia and familial Creutzfeldt-Jakob disease: disease phenotype determined by a DNA polymorphism

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M513417200

Seeding "one-dimensional crystallization" of amyloid: a pathogenic mechanism in Alzheimer's disease and scrapie?

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M513417200

FTIR reveals structural differences between native beta-sheet proteins and amyloid fibrils.

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M513417200

Islet amyloid polypeptide: pinpointing amino acid residues linked to amyloid fibril formation

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M513417200

Theoretical studies of sequence effects on the conformational properties of a fragment of the prion protein: implications for scrapie formation

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M513417200

Computational studies on prion proteins: effect of Ala(117)-->Val mutation

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M513417200

Sulfated glycosaminoglycans in amyloid plaques of prion diseases

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M513417200

Chaperone-supervised conversion of prion protein to its protease-resistant form

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M513417200

Conversion of raft associated prion protein to the protease-resistant state requires insertion of PrP-res (PrP(Sc)) into contiguous membranes

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M513417200

Mutant prion proteins are partially retained in the endoplasmic reticulum

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M513417200

Cell surface accumulation of a truncated transmembrane prion protein in Gerstmann-Straussler-Scheinker disease P102L.

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M513417200

A pathogenic PrP mutation and doppel interfere with polarized sorting of the prion protein.

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M513417200

Genetic predisposition to iatrogenic Creutzfeldt-Jakob disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M513417200

Transmissions to mice indicate that 'new variant' CJD is caused by the BSE agent

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M513417200

Compelling transgenetic evidence for transmission of bovine spongiform encephalopathy prions to humans

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M513417200

The residue 129 polymorphism in human prion protein does not confer susceptibility to Creutzfeldt-Jakob disease by altering the structure or global stability of PrPC.

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M513417200

Molecular classification of sporadic Creutzfeldt-Jakob disease.

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M513417200

Evidence that the Transmission of One Source of Scrapie Agent to Hamsters Involves Separation of Agent Strains from a Mixture

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M513417200

BSE prions propagate as either variant CJD-like or sporadic CJD-like prion strains in transgenic mice expressing human prion protein

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M513417200

Generation of prion transmission barriers by mutational control of amyloid conformations

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M513417200

Mechanism of cross-species prion transmission: an infectious conformation compatible with two highly divergent yeast prion proteins

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M513417200

Insulin forms amyloid in a strain-dependent manner: an FT-IR spectroscopic study

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M513417200

Seeding-dependent propagation and maturation of amyloid fibril conformation

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M513417200

Self-propagating, molecular-level polymorphism in Alzheimer's beta-amyloid fibrils

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M513417200

The same prion strain causes vCJD and BSE

21 January 2018

1 reference

https://api.crossref.org/works/10.1074%2FJBC.M513417200

21 January 2018

Identifiers

DOI

10.1074/JBC.M513417200

1 reference

26 December 2017

PubMed ID

16443601

1 reference

26 December 2017