(Q49076261)

18 February 2018

title

Biology and neuropathology of prion diseases. (English)

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18 February 2018

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1

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18 February 2018

Mark W Head

object named as

Mark W Head

series ordinal

2

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publication date

1 January 2008

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18 February 2018

Handbook of clinical neurology / edited by P.J. Vinken and G.W. Bruyn

published in

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18 February 2018

volume

89

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18 February 2018

page(s)

779-797

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18 February 2018

Mammalian prion biology: one century of evolving concepts

cites work

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Fatal familial insomnia: a new Austrian family

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Codon 129 prion protein genotype and sporadic Creutzfeldt-Jakob disease

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Prion protein immunocytochemistry--UK five centre consensus report

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Predicting susceptibility and incubation time of human-to-human transmission of vCJD.

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Distribution of codon 129 genotype in human growth hormone-treated CJD patients in France and the UK

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Normal host prion protein necessary for scrapie-induced neurotoxicity.

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Normal host prion protein (PrPC) is required for scrapie spread within the central nervous system

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Prion and prejudice: normal protein and the synapse

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Human spongiform encephalopathy: the National Institutes of Health series of 300 cases of experimentally transmitted disease

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Iatrogenic Creutzfeldt-Jakob disease: the waning of an era.

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Transmissions to mice indicate that 'new variant' CJD is caused by the BSE agent

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Detection of variant Creutzfeldt-Jakob disease infectivity in extraneural tissues

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Neuropathological diagnostic criteria for Creutzfeldt-Jakob disease (CJD) and other human spongiform encephalopathies (prion diseases).

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Mice devoid of PrP are resistant to scrapie

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Beta PP participates in PrP-amyloid plaques of Gerstmann-Sträussler-Scheinker disease, Indiana kindred.

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Detection of prions in blood

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

In vitro generation of infectious scrapie prions.

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Prions and their partners in crime

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Phenotype-genotype studies in kuru: implications for new variant Creutzfeldt-Jakob disease

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Prion protein is necessary for normal synaptic function

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Molecular analysis of prion strain variation and the aetiology of 'new variant' CJD.

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Kuru in the 21st century--an acquired human prion disease with very long incubation periods

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

RNA molecules stimulate prion protein conversion

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Genotype at codon 129 and susceptibility to Creutzfeldt-Jakob disease

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Letter: Hepatitis with hindsight

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Neurotoxicity of a prion protein fragment.

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Degenerative disease of the central nervous system in New Guinea; the endemic occurrence of kuru in the native population

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Hereditary prion protein amyloidoses

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Extraneural pathologic prion protein in sporadic Creutzfeldt-Jakob disease

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Genetic studies in relation to kuru: an overview

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Severe, early and selective loss of a subpopulation of GABAergic inhibitory neurons in experimental transmissible spongiform encephalopathies.

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Evidence for oxidative stress in experimental prion disease

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

The original Gerstmann-Sträussler-Scheinker family of Austria: divergent clinicopathological phenotypes but constant PrP genotype

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Pathology and immunocytochemistry of a kuru brain

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Sporadic Creutzfeldt-Jakob disease in a young Dutch valine homozygote: atypical molecular phenotype.

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Prion protein heterogeneity in sporadic but not variant Creutzfeldt-Jakob disease: UK cases 1991-2002.

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Peripheral tissue involvement in sporadic, iatrogenic, and variant Creutzfeldt-Jakob disease: an immunohistochemical, quantitative, and biochemical study

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Sporadic Creutzfeldt-Jakob disease: further twists and turns in a convoluted protein.

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Dura mater-associated Creutzfeldt-Jakob disease: experience from surveillance in the UK.

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

A transmembrane form of the prion protein in neurodegenerative disease

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Evidence of presynaptic location and function of the prion protein

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Creutzfeldt-Jakob disease and blood transfusion: results of the UK Transfusion Medicine Epidemiological Review study

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Investigation of variant Creutzfeldt-Jakob disease and other human prion diseases with tonsil biopsy samples.

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Molecular classification of sporadic Creutzfeldt-Jakob disease.

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Prion immunoreactivity in appendix before clinical onset of variant Creutzfeldt-Jakob disease

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Prevalence of lymphoreticular prion protein accumulation in UK tissue samples.

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Linkage of a prion protein missense variant to Gerstmann-Sträussler syndrome

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Review: Creutzfeldt-Jakob disease

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Laboratory diagnosis of variant Creutzfeldt-Jakob disease.

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Pathological diagnosis of variant Creutzfeldt-Jakob disease

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Variant Creutzfeldt-Jakob disease: prion protein genotype analysis of positive appendix tissue samples from a retrospective prevalence study

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Reversible conversion of monomeric human prion protein between native and fibrilogenic conformations.

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Phenotypic variability in the brains of a family with a prion disease characterized by a 144-base pair insertion in the prion protein gene.

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

An amber mutation of prion protein in Gerstmann-Sträussler syndrome with mutant PrP plaques

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Cell-free formation of protease-resistant prion protein.

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Disease-associated prion protein in vessel walls

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Immunohistochemistry for the prion protein: comparison of different monoclonal antibodies in human prion disease subtypes.

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Mutations of the prion protein gene phenotypic spectrum

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Complement activation in human prion disease

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Subcellular localization of disease-associated prion protein in the human brain

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Mortality from Creutzfeldt-Jakob disease and related disorders in Europe, Australia, and Canada

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Ancestral origins and worldwide distribution of the PRNP 200K mutation causing familial Creutzfeldt-Jakob disease

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Synthetic mammalian prions

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Comparative ultrastructural neuropathology of naturally occurring bovine spongiform encephalopathy and experimentally induced scrapie and Creutzfeldt-Jakob disease.

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Possible transmission of variant Creutzfeldt-Jakob disease by blood transfusion.

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Prion protein accumulation and neuroprotection in hypoxic brain damage

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Neurotoxicity and neurodegeneration when PrP accumulates in the cytosol

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Subacute spongiform encephalopathy (Creutzfeldt-Jakob disease). The nature and progression of spongiform change

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Familial and sporadic fatal insomnia

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Signal transduction through prion protein

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Demyelinating peripheral neuropathy in Creutzfeldt-Jakob disease

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Subacute spongiform encephalopathy--a subacute form of encephalopathy attributable to vascular dysfunction (spongiform cerebral atrophy).

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Typing prion isoforms.

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Different patterns of truncated prion protein fragments correlate with distinct phenotypes in P102L Gerstmann-Sträussler-Scheinker disease

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Molecular pathology of fatal familial insomnia

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Classification of sporadic Creutzfeldt-Jakob disease based on molecular and phenotypic analysis of 300 subjects

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Genetic influence on the structural variations of the abnormal prion protein

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Preclinical vCJD after blood transfusion in a PRNP codon 129 heterozygous patient

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Detection and localization of PrPSc in the skeletal muscle of patients with variant, iatrogenic, and sporadic forms of Creutzfeldt-Jakob disease

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Phenotypic variability of Gerstmann-Sträussler-Scheinker disease is associated with prion protein heterogeneity.

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Rapid acquisition of beta-sheet structure in the prion protein prior to multimer formation

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

The human 37-kDa laminin receptor precursor interacts with the prion protein in eukaryotic cells

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Advances in the detection of prion protein in peripheral tissues of variant Creutzfeldt-Jakob disease patients using paraffin-embedded tissue blotting

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Sensitive detection of pathological prion protein by cyclic amplification of protein misfolding

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Prion protein recruits its neuronal receptor NCAM to lipid rafts to activate p59fyn and to enhance neurite outgrowth.

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Association of an 11-12 kDa protease-resistant prion protein fragment with subtypes of dura graft-associated Creutzfeldt-Jakob disease and other prion diseases

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Creutzfeldt-Jakob disease with florid-type plaques after cadaveric dura mater grafting

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

A neuronal isoform of the aplysia CPEB has prion-like properties

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Creutzfeldt-Jakob disease in United Kingdom patients treated with human pituitary growth hormone

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Studies on peptide fragments of prion proteins.

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Evidence for the conformation of the pathologic isoform of the prion protein enciphering and propagating prion diversity

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Coexistence of CJD and Alzheimer's disease: an autopsy case showing typical clinical features of CJD.

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Prion encephalopathy with insertion of octapeptide repeats: the number of repeats determines the type of cerebellar deposits.

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Sporadic Creutzfeldt-Jakob disease and surgery: a case-control study using community controls

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Prions of yeast are genes made of protein: amyloids and enzymes

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

A new variant of Creutzfeldt-Jakob disease in the UK.

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

Increased levels of oxidative stress markers detected in the brains of mice devoid of prion protein

1 reference

https://api.crossref.org/works/10.1016%2FS0072-9752%2807%2901268-7

7 January 2021

10.1016/S0072-9752(07)01268-7

Identifiers

DOI

1 reference

18 February 2018

1 reference

18 February 2018