(Q80060299)

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:17393522%20AND%20SRC:MED&resulttype=core&format=json

28 December 2019

title

Bile acid treatment alters hepatic disease and bile acid transport in peroxisome-deficient PEX2 Zellweger mice (English)

1 reference

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28 December 2019

6

Ronald J A Wanders

1 reference

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28 December 2019

4

Sacha Ferdinandusse

1 reference

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28 December 2019

author name string

Megan H Keane

1

1 reference

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28 December 2019

Henk Overmars

2

1 reference

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28 December 2019

Thomas M Wikander

3

1 reference

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28 December 2019

Marinus Duran

5

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28 December 2019

Phyllis L Faust

7

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28 December 2019

language of work or name

English

0 references

publication date

1 April 2007

1 reference

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28 December 2019

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28 December 2019

volume

45

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28 December 2019

issue

4

1 reference

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28 December 2019

page(s)

982-997

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The enzymes, regulation, and genetics of bile acid synthesis

28 December 2019

cites work

1 reference

7 January 2021

Bile acid synthetic defects and liver disease: a comprehensive review

1 reference

7 January 2021

The peroxisome deficient PEX2 Zellweger mouse: pathologic and biochemical correlates of lipid dysfunction.

1 reference

7 January 2021

Abnormal cerebellar histogenesis in PEX2 Zellweger mice reflects multiple neuronal defects induced by peroxisome deficiency

1 reference

7 January 2021

Oral bile acid treatment and the patient with zellweger syndrome

1 reference

7 January 2021

Oral bile Acid treatment in two Japanese patients with Zellweger syndrome

1 reference

7 January 2021

Targeted deletion of the PEX2 peroxisome assembly gene in mice provides a model for Zellweger syndrome, a human neuronal migration disorder

1 reference

7 January 2021

Disturbed cholesterol homeostasis in a peroxisome-deficient PEX2 knockout mouse model

1 reference

7 January 2021

Detection of peroxisomal proteins and their mRNAs in serial sections of fetal and newborn mouse organs

1 reference

7 January 2021

Rapid analysis of conjugated bile acids in plasma using electrospray tandem mass spectrometry: application for selective screening of peroxisomal disorders

1 reference

7 January 2021

Disruption of cholesterol 7alpha-hydroxylase gene in mice. II. Bile acid deficiency is overcome by induction of oxysterol 7alpha-hydroxylase.

1 reference

7 January 2021

Peroxisomal and mitochondrial defects in the cerebro-hepato-renal syndrome.

1 reference

7 January 2021

Biochemical studies in the liver and muscle of patients with Zellweger syndrome.

1 reference

7 January 2021

Pathology of hepatic peroxisomes and mitochondria in patients with peroxisomal disorders

1 reference

7 January 2021

Ultrastructure of the Liver in the Cerebrohepatorenal Syndrome of Zellweger

1 reference

7 January 2021

Mitochondrial alterations caused by defective peroxisomal biogenesis in a mouse model for Zellweger syndrome (PEX5 knockout mouse)

1 reference

7 January 2021

Absence of peroxisomes in mouse hepatocytes causes mitochondrial and ER abnormalities

1 reference

7 January 2021

Mitochondrially-mediated toxicity of bile acids.

1 reference

7 January 2021

Hepatic transport of bile salts

1 reference

7 January 2021

Cellular localization and up-regulation of multidrug resistance-associated protein 3 in hepatocytes and cholangiocytes during obstructive cholestasis in rat liver

1 reference

7 January 2021

Analysis of the in vivo functions of Mrp3.

1 reference

7 January 2021

Asynchronous expression and colocalization of Bsep and Mrp2 during development of rat liver

1 reference

7 January 2021

Vectorial transport of unconjugated and conjugated bile salts by monolayers of LLC-PK1 cells doubly transfected with human NTCP and BSEP or with rat Ntcp and Bsep.

1 reference

7 January 2021

Developmental changes of bile acid composition and conjugation in L- and D-bifunctional protein single and double knockout mice

1 reference

7 January 2021

Participation of two members of the very long-chain acyl-CoA synthetase family in bile acid synthesis and recycling

1 reference

7 January 2021

Differential regulation of cytosolic and peroxisomal bile acid amidation by PPAR alpha activation favors the formation of unconjugated bile acids

1 reference

7 January 2021

Complex inheritance of familial hypercholanemia with associated mutations in TJP2 and BAAT.

1 reference

7 January 2021

Restoration of PEX2 peroxisome assembly defects by overexpression of PMP70

1 reference

7 January 2021

Suppression of peroxisomal membrane protein defects by peroxisomal ATP binding cassette (ABC) proteins

1 reference

7 January 2021

A mouse model for alpha-methylacyl-CoA racemase deficiency: adjustment of bile acid synthesis and intolerance to dietary methyl-branched lipids

1 reference

7 January 2021

Identifiers

DOI

10.1002/HEP.21532

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:17393522%20AND%20SRC:MED&resulttype=core&format=json

28 December 2019

1 reference