(Q34055364)

30 July 2017

title

Macroautophagy is regulated by the UPR-mediator CHOP and accentuates the phenotype of SBMA mice (English)

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30 July 2017

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7

Diane M Robins

1 reference

30 July 2017

Hiroaki Adachi

3

0 references

Gen Sobue

5

object named as

Gen Sobue

1 reference

30 July 2017

Zhigang Yu

1

1 reference

30 July 2017

Adrienne M Wang

2

1 reference

30 July 2017

Masahisa Katsuno

4

1 reference

30 July 2017

Zhenyu Yue

6

1 reference

30 July 2017

Andrew P Lieberman

8

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30 July 2017

publication date

13 October 2011

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30 July 2017

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30 July 2017

volume

7

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30 July 2017

issue

10

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30 July 2017

page(s)

e1002321

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Creative Commons Attribution 4.0 International

30 July 2017

copyright license

start time

13 October 2011

1 reference

April 2022 Public Data File from Crossref

copyright status

copyrighted

0 references

describes a project that uses

ImageJ

1 reference

11 June 2022

https://www.ebi.ac.uk/europepmc/webservices/rest/PMC3192827/fullTextXML

inferred from PubMed Central ID database lookup

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5 July 2018

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5 July 2018

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5 July 2018

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5 July 2018

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CHOP is implicated in programmed cell death in response to impaired function of the endoplasmic reticulum

5 July 2018

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The length and location of CAG trinucleotide repeats in the androgen receptor N-terminal domain affect transactivation function

5 July 2018

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5 July 2018

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5 July 2018

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5 July 2018

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Castration restores function and neurofilament alterations of aged symptomatic males in a transgenic mouse model of spinal and bulbar muscular atrophy.

21 January 2018

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Testosterone reduction prevents phenotypic expression in a transgenic mouse model of spinal and bulbar muscular atrophy

21 January 2018

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https://api.crossref.org/works/10.1371%2FJOURNAL.PGEN.1002321

Altered transcriptional regulation in cells expressing the expanded polyglutamine androgen receptor

21 January 2018

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https://api.crossref.org/works/10.1371%2FJOURNAL.PGEN.1002321

Reversible disruption of dynactin 1-mediated retrograde axonal transport in polyglutamine-induced motor neuron degeneration.

21 January 2018

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https://api.crossref.org/works/10.1371%2FJOURNAL.PGEN.1002321

Neuropathogenic forms of huntingtin and androgen receptor inhibit fast axonal transport

21 January 2018

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https://api.crossref.org/works/10.1371%2FJOURNAL.PGEN.1002321

Pharmacologic and genetic inhibition of hsp90-dependent trafficking reduces aggregation and promotes degradation of the expanded glutamine androgen receptor without stress protein induction

21 January 2018

1 reference

https://api.crossref.org/works/10.1371%2FJOURNAL.PGEN.1002321

CHIP overexpression reduces mutant androgen receptor protein and ameliorates phenotypes of the spinal and bulbar muscular atrophy transgenic mouse model.

21 January 2018

1 reference

https://api.crossref.org/works/10.1371%2FJOURNAL.PGEN.1002321

Ablation of the UPR-mediator CHOP restores motor function and reduces demyelination in Charcot-Marie-Tooth 1B mice

21 January 2018

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https://api.crossref.org/works/10.1371%2FJOURNAL.PGEN.1002321

Comparison of gene expression of 2-mo denervated, 2-mo stimulated-denervated, and control rat skeletal muscles

21 January 2018

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https://api.crossref.org/works/10.1371%2FJOURNAL.PGEN.1002321

ER stress (PERK/eIF2alpha phosphorylation) mediates the polyglutamine-induced LC3 conversion, an essential step for autophagy formation.

21 January 2018

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https://api.crossref.org/works/10.1371%2FJOURNAL.PGEN.1002321

Polyglutamine aggregates stimulate ER stress signals and caspase-12 activation

21 January 2018

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https://api.crossref.org/works/10.1371%2FJOURNAL.PGEN.1002321

Novel targets for Huntington's disease in an mTOR-independent autophagy pathway

21 January 2018

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https://api.crossref.org/works/10.1371%2FJOURNAL.PGEN.1002321

Replacing the Mouse Androgen Receptor with Human Alleles Demonstrates Glutamine Tract Length-Dependent Effects on Physiology and Tumorigenesis in Mice

21 January 2018

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PubMed

https://pubmed.ncbi.nlm.nih.gov/22022281

12 December 2020

inferred from PubMed ID database lookup

X-linked recessive bulbospinal neuronopathy. A clinicopathological study

1 reference

PubMed

https://pubmed.ncbi.nlm.nih.gov/22022281

12 December 2020

inferred from PubMed ID database lookup

Reduced transcriptional regulatory competence of the androgen receptor in X-linked spinal and bulbar muscular atrophy

1 reference

PubMed

https://pubmed.ncbi.nlm.nih.gov/22022281

12 December 2020

inferred from PubMed ID database lookup

Identifiers

DOI

10.1371/JOURNAL.PGEN.1002321

1 reference

30 July 2017

1 reference

30 July 2017

1 reference