(Q34339563)

1 August 2017

title

Efficacy and safety of ivacaftor in patients aged 6 to 11 years with cystic fibrosis with a G551D mutation (English)

1 reference

1 August 2017

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Jochen G Mainz

7

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Claire Wainwright

object named as

Claire E Wainwright

2

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author name string

Jane C Davies

1

1 reference

1 August 2017

Gerard J Canny

3

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1 August 2017

Mark A Chilvers

4

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1 August 2017

Michelle S Howenstine

5

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1 August 2017

Anne Munck

6

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1 August 2017

Sally Rodriguez

8

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1 August 2017

Haihong Li

9

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1 August 2017

Karl Yen

10

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1 August 2017

Claudia L Ordoñez

11

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1 August 2017

Richard Ahrens

12

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1 August 2017

VX08-770-103 (ENVISION) Study Group

13

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1 August 2017

language of work or name

English

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publication date

1 June 2013

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American Journal of Respiratory and Critical Care Medicine

1 August 2017

published in

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1 August 2017

volume

187

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1 August 2017

issue

11

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1 August 2017

page(s)

1219-1225

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A CFTR potentiator in patients with cystic fibrosis and the G551D mutation

1 August 2017

cites work

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3734608

Effect of VX-770 in persons with cystic fibrosis and the G551D-CFTR mutation

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3734608

Rescue of CF airway epithelial cell function in vitro by a CFTR potentiator, VX-770

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3734608

Determination of the minimal clinically important difference scores for the Cystic Fibrosis Questionnaire-Revised respiratory symptom scale in two populations of patients with cystic fibrosis and chronic Pseudomonas aeruginosa airway infection

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3734608

Guidelines for diagnosis of cystic fibrosis in newborns through older adults: Cystic Fibrosis Foundation consensus report

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3734608

Sodium channels and cystic fibrosis

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3734608

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3734608

Pathophysiology and Management of Pulmonary Infections in Cystic Fibrosis

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3734608

Consensus report on nutrition for pediatric patients with cystic fibrosis

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3734608

Pathogenesis of malnutrition in cystic fibrosis, and its treatment

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3734608

Evidence for periciliary liquid layer depletion, not abnormal ion composition, in the pathogenesis of cystic fibrosis airways disease

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3734608

Changes in the normal maximal expiratory flow-volume curve with growth and aging

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3734608

Identification of the cystic fibrosis gene: genetic analysis

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3734608

Identification of the cystic fibrosis gene: cloning and characterization of complementary DNA

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3734608

Validation of a Disease-Specific Measure of Health-Related Quality of Life for Children with Cystic Fibrosis

6 July 2018

1 reference

https://api.crossref.org/works/10.1164%2FRCCM.201301-0153OC

A two-year randomized, placebo-controlled trial of dornase alfa in young patients with cystic fibrosis with mild lung function abnormalities

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FRCCM.201301-0153OC

Longitudinal relationship among growth, nutritional status, and pulmonary function in children with cystic fibrosis: analysis of the Cystic Fibrosis Foundation National CF Patient Registry.

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FRCCM.201301-0153OC

Longitudinal changes in growth parameters are correlated with changes in pulmonary function in children with cystic fibrosis

21 January 2018

1 reference

https://api.crossref.org/works/10.1164%2FRCCM.201301-0153OC

Intermittent administration of inhaled tobramycin in patients with cystic fibrosis. Cystic Fibrosis Inhaled Tobramycin Study Group

21 January 2018

1 reference

PubMed

https://pubmed.ncbi.nlm.nih.gov/23590265

inferred from PubMed ID database lookup

12 December 2020

based on heuristic

The prevalence of cystic fibrosis in the European Union

1 reference

PubMed

https://pubmed.ncbi.nlm.nih.gov/23590265

inferred from PubMed ID database lookup

12 December 2020

based on heuristic

Identifiers

DOI

10.1164/RCCM.201301-0153OC

1 reference

1 August 2017

1 reference

1 August 2017

1 reference