(Q34991844)

5 August 2017

1 reference

title

Hyperacidification in cystic fibrosis: links with lung disease and new prospects for treatment (English)

1 reference

5 August 2017

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3

Vojo Deretic

1 reference

5 August 2017

2

Elizabeth Perkett

1 reference

5 August 2017

Jens Poschet

1

1 reference

5 August 2017

1 November 2002

1 reference

Trends in Molecular Medicine

5 August 2017

1 reference

5 August 2017

8

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5 August 2017

11

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5 August 2017

512-519

1 reference

Identification of the cystic fibrosis gene: cloning and characterization of complementary DNA

5 August 2017

1 reference

https://api.crossref.org/works/10.1016%2FS1471-4914%2802%2902414-0

7 January 2021

TGF-beta(1) genotype and accelerated decline in lung function of patients with cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS1471-4914%2802%2902414-0

7 January 2021

HLA class II polymorphism in cystic fibrosis. A possible modifier of pulmonary phenotype

1 reference

https://api.crossref.org/works/10.1016%2FS1471-4914%2802%2902414-0

7 January 2021

CFTR is a conductance regulator as well as a chloride channel

1 reference

https://api.crossref.org/works/10.1016%2FS1471-4914%2802%2902414-0

7 January 2021

Biosynthesis and degradation of CFTR.

1 reference

https://api.crossref.org/works/10.1016%2FS1471-4914%2802%2902414-0

7 January 2021

CFTR as a cAMP-dependent regulator of sodium channels

1 reference

https://api.crossref.org/works/10.1016%2FS1471-4914%2802%2902414-0

7 January 2021

The first-nucleotide binding domain of the cystic-fibrosis transmembrane conductance regulator is important for inhibition of the epithelial Na+ channel.

1 reference

https://api.crossref.org/works/10.1016%2FS1471-4914%2802%2902414-0

7 January 2021

Aberrant CFTR-dependent HCO3- transport in mutations associated with cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS1471-4914%2802%2902414-0

7 January 2021

Regulation of CFTR chloride channels by syntaxin and Munc18 isoforms

1 reference

https://api.crossref.org/works/10.1016%2FS1471-4914%2802%2902414-0

7 January 2021

Effect of high-dose ibuprofen in patients with cystic fibrosis.

1 reference

https://api.crossref.org/works/10.1016%2FS1471-4914%2802%2902414-0

7 January 2021

Inflammatory cytokines in cystic fibrosis lungs

1 reference

https://api.crossref.org/works/10.1016%2FS1471-4914%2802%2902414-0

7 January 2021

Molecular basis for defective glycosylation and Pseudomonas pathogenesis in cystic fibrosis lung

1 reference

https://api.crossref.org/works/10.1016%2FS1471-4914%2802%2902414-0

7 January 2021

Hyperacidification of cellubrevin endocytic compartments and defective endosomal recycling in cystic fibrosis respiratory epithelial cells

1 reference

https://api.crossref.org/works/10.1016%2FS1471-4914%2802%2902414-0

7 January 2021

Human beta-defensin-1 is a salt-sensitive antibiotic in lung that is inactivated in cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS1471-4914%2802%2902414-0

7 January 2021

Cystic fibrosis airway epithelia fail to kill bacteria because of abnormal airway surface fluid.

1 reference

https://api.crossref.org/works/10.1016%2FS1471-4914%2802%2902414-0

7 January 2021

Ion composition of airway surface liquid of patients with cystic fibrosis as compared with normal and disease-control subjects

1 reference

https://api.crossref.org/works/10.1016%2FS1471-4914%2802%2902414-0

7 January 2021

Airway surface liquid osmolality measured using fluorophore-encapsulated liposomes

1 reference

https://api.crossref.org/works/10.1016%2FS1471-4914%2802%2902414-0

7 January 2021

Submucosal gland secretions in airways from cystic fibrosis patients have normal [Na(+)] and pH but elevated viscosity

1 reference

https://api.crossref.org/works/10.1016%2FS1471-4914%2802%2902414-0

7 January 2021

Evidence for periciliary liquid layer depletion, not abnormal ion composition, in the pathogenesis of cystic fibrosis airways disease

1 reference

https://api.crossref.org/works/10.1016%2FS1471-4914%2802%2902414-0

7 January 2021

Mucociliary transport in trachea of patients with cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS1471-4914%2802%2902414-0

7 January 2021

Systemic deficiency of glutathione in cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS1471-4914%2802%2902414-0

7 January 2021

Role of the cystic fibrosis transmembrane conductance regulator in innate immunity to Pseudomonas aeruginosa infections

1 reference

https://api.crossref.org/works/10.1016%2FS1471-4914%2802%2902414-0

7 January 2021

Role of mutant CFTR in hypersusceptibility of cystic fibrosis patients to lung infections.

1 reference

https://api.crossref.org/works/10.1016%2FS1471-4914%2802%2902414-0

7 January 2021

Invasion of human epithelial cells by Pseudomonas aeruginosa involves src-like tyrosine kinases p60Src and p59Fyn.

1 reference

https://api.crossref.org/works/10.1016%2FS1471-4914%2802%2902414-0

7 January 2021

Role of cystic fibrosis transmembrane conductance regulator in pulmonary clearance of Pseudomonas aeruginosa in vivo

1 reference

https://api.crossref.org/works/10.1016%2FS1471-4914%2802%2902414-0

7 January 2021

Innate lung defenses and compromised Pseudomonas aeruginosa clearance in the malnourished mouse model of respiratory infections in cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS1471-4914%2802%2902414-0

7 January 2021

Decreased concentration of exhaled nitric oxide (NO) in patients with cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS1471-4914%2802%2902414-0

7 January 2021

Inducible nitric oxide synthase expression is reduced in cystic fibrosis murine and human airway epithelial cells

1 reference

https://api.crossref.org/works/10.1016%2FS1471-4914%2802%2902414-0

7 January 2021

Airway nitric oxide levels in cystic fibrosis patients are related to a polymorphism in the neuronal nitric oxide synthase gene

1 reference

https://api.crossref.org/works/10.1016%2FS1471-4914%2802%2902414-0

7 January 2021

Terminal glycosylation in cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS1471-4914%2802%2902414-0

7 January 2021

Additional fucosyl residues on membrane glycoproteins but not a secreted glycoprotein from cystic fibrosis fibroblasts

1 reference

https://api.crossref.org/works/10.1016%2FS1471-4914%2802%2902414-0

7 January 2021

Increased sulfation of glycoconjugates by cultured nasal epithelial cells from patients with cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS1471-4914%2802%2902414-0

7 January 2021

The sialylation of bronchial mucins secreted by patients suffering from cystic fibrosis or from chronic bronchitis is related to the severity of airway infection

1 reference

https://api.crossref.org/works/10.1016%2FS1471-4914%2802%2902414-0

7 January 2021

Heterologous expression of delta F508 CFTR results in decreased sialylation of membrane glycoconjugates

1 reference

https://api.crossref.org/works/10.1016%2FS1471-4914%2802%2902414-0

7 January 2021

CFTR gene transfer reduces the binding of Pseudomonas aeruginosa to cystic fibrosis respiratory epithelium

1 reference

https://api.crossref.org/works/10.1016%2FS1471-4914%2802%2902414-0

7 January 2021

Cystic fibrosis epithelial cells have a receptor for pathogenic bacteria on their apical surface

1 reference

https://api.crossref.org/works/10.1016%2FS1471-4914%2802%2902414-0

7 January 2021

Many pulmonary pathogenic bacteria bind specifically to the carbohydrate sequence GalNAc beta 1-4Gal found in some glycolipids

1 reference

https://api.crossref.org/works/10.1016%2FS1471-4914%2802%2902414-0

7 January 2021

Lack of adherence of clinical isolates of Pseudomonas aeruginosa to asialo-GM(1) on epithelial cells

1 reference

https://api.crossref.org/works/10.1016%2FS1471-4914%2802%2902414-0

7 January 2021

Muc1 mucins on the cell surface are adhesion sites for Pseudomonas aeruginosa

1 reference

https://api.crossref.org/works/10.1016%2FS1471-4914%2802%2902414-0

7 January 2021

Receptors in the Pseudomonas aeruginosa adherence to injured and repairing airway epithelium

1 reference

https://api.crossref.org/works/10.1016%2FS1471-4914%2802%2902414-0

7 January 2021

Pili binding to asialo-GM1 on epithelial cells can mediate cytotoxicity or bacterial internalization by Pseudomonas aeruginosa.

1 reference

https://api.crossref.org/works/10.1016%2FS1471-4914%2802%2902414-0

7 January 2021

Cystic fibrosis pathogens activate Ca2+-dependent mitogen-activated protein kinase signaling pathways in airway epithelial cells

1 reference

https://api.crossref.org/works/10.1016%2FS1471-4914%2802%2902414-0

7 January 2021

Overproduction of the CFTR R domain leads to increased levels of asialoGM1 and increased Pseudomonas aeruginosa binding by epithelial cells

1 reference

https://api.crossref.org/works/10.1016%2FS1471-4914%2802%2902414-0

7 January 2021

Defective acidification of intracellular organelles in cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS1471-4914%2802%2902414-0

7 January 2021

Evidence against defective trans-Golgi acidification in cystic fibrosis

1 reference

https://api.crossref.org/works/10.1016%2FS1471-4914%2802%2902414-0

7 January 2021

Visualizing secretion and synaptic transmission with pH-sensitive green fluorescent proteins

1 reference

https://api.crossref.org/works/10.1016%2FS1471-4914%2802%2902414-0

7 January 2021

Proton leak and CFTR in regulation of Golgi pH in respiratory epithelial cells

1 reference

https://api.crossref.org/works/10.1016%2FS1471-4914%2802%2902414-0

7 January 2021

Bicarbonate and chloride secretion in Calu-3 human airway epithelial cells

1 reference

https://api.crossref.org/works/10.1016%2FS1471-4914%2802%2902414-0

7 January 2021

cAMP stimulates bicarbonate secretion across normal, but not cystic fibrosis airway epithelia

1 reference

https://api.crossref.org/works/10.1016%2FS1471-4914%2802%2902414-0

7 January 2021

Developmental expression of mucin genes in the human respiratory tract.

1 reference

https://api.crossref.org/works/10.1016%2FS1471-4914%2802%2902414-0

7 January 2021

https://api.crossref.org/works/10.1016%2FS1471-4914%2802%2902414-0

1 reference

7 January 2021

Role of growth factors in lung repair and diseases.

1 reference

https://api.crossref.org/works/10.1016%2FS1471-4914%2802%2902414-0

7 January 2021

Expression of transforming growth factor-beta 1, -beta 2, and -beta 3 mRNA and protein in the murine lung.

1 reference

https://api.crossref.org/works/10.1016%2FS1471-4914%2802%2902414-0

7 January 2021

10.1016/S1471-4914(02)02414-0

Identifiers

DOI

1 reference

5 August 2017

1 reference

PubMed ID

12421684