(Q35131715)

6 August 2017

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title

Mutant Cu,Zn superoxide dismutases and familial amyotrophic lateral sclerosis: evaluation of oxidative hypotheses (English)

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amyotrophic lateral sclerosis

6 August 2017

main subject

0 references

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2

Irwin Fridovich

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6 August 2017

Stefan I Liochev

1

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6 August 2017

publication date

1 June 2003

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Free Radical Biology and Medicine

6 August 2017

published in

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6 August 2017

volume

34

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6 August 2017

issue

11

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6 August 2017

page(s)

1383-1389

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Epidemiology of mutations in superoxide dismutase in amyotrophic lateral sclerosis

6 August 2017

cites work

1 reference

https://api.crossref.org/works/10.1016%2FS0891-5849%2803%2900153-9

7 January 2021

Identification of a novel mutation in Cu/Zn superoxide dismutase gene associated with familial amyotrophic lateral sclerosis

1 reference

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7 January 2021

Amyotrophic lateral sclerosis. unfolding the toxicity of the misfolded

1 reference

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7 January 2021

Amyotrophic lateral sclerosis

1 reference

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7 January 2021

Motor neuron degeneration in mice that express a human Cu,Zn superoxide dismutase mutation

1 reference

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7 January 2021

Motor neurons in Cu/Zn superoxide dismutase-deficient mice develop normally but exhibit enhanced cell death after axonal injury

1 reference

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7 January 2021

Do oxidatively modified proteins cause ALS?

1 reference

https://api.crossref.org/works/10.1016%2FS0891-5849%2803%2900153-9

7 January 2021

Altered reactivity of superoxide dismutase in familial amyotrophic lateral sclerosis

1 reference

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7 January 2021

A gain-of-function of an amyotrophic lateral sclerosis-associated Cu,Zn-superoxide dismutase mutant: An enhancement of free radical formation due to a decrease in Km for hydrogen peroxide

1 reference

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7 January 2021

Superoxide-dependent peroxidase activity of H48Q: a superoxide dismutase variant associated with familial amyotrophic lateral sclerosis

1 reference

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7 January 2021

Copper- and zinc-containing superoxide dismutase can act as a superoxide reductase and a superoxide oxidase

1 reference

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7 January 2021

Superoxide dismutase and the death of motoneurons in ALS.

1 reference

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7 January 2021

Induction of nitric oxide-dependent apoptosis in motor neurons by zinc-deficient superoxide dismutase

1 reference

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7 January 2021

Oxidation versus aggregation - how do SOD1 mutants cause ALS?

1 reference

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7 January 2021

Aggregation of mutant Cu/Zn superoxide dismutase proteins in a culture model of ALS

1 reference

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7 January 2021

Amyotrophic lateral sclerosis: a proposed mechanism

1 reference

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7 January 2021

Pulse radiolytic investigations of superoxide catalyzed disproportionation. Mechanism for bovine superoxide dismutase

1 reference

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7 January 2021

Copper, zinc superoxide dismutase and H2O2. Effects of bicarbonate on inactivation and oxidations of NADPH and urate, and on consumption of H2O2.

1 reference

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7 January 2021

Reversal of the superoxide dismutase reaction revisited

1 reference

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7 January 2021

Lucigenin luminescence as a measure of intracellular superoxide dismutase activity in Escherichia coli

1 reference

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7 January 2021

Superoxide and nitric oxide: consequences of varying rates of production and consumption: a theoretical treatment

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7 January 2021

Interaction of bovine erythrocyte superoxide dismutase with hydrogen peroxide. Chemiluminescence and peroxidation

1 reference

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7 January 2021

Bicarbonate is required for the peroxidase function of Cu, Zn-superoxide dismutase at physiological pH

1 reference

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7 January 2021

On the role of bicarbonate in peroxidations catalyzed by Cu,Zn superoxide dismutase

1 reference

https://api.crossref.org/works/10.1016%2FS0891-5849%2803%2900153-9

7 January 2021

Bicarbonate enhances the hydroxylation, nitration, and peroxidation reactions catalyzed by copper, zinc superoxide dismutase. Intermediacy of carbonate anion radical

1 reference

https://api.crossref.org/works/10.1016%2FS0891-5849%2803%2900153-9

7 January 2021

Bicarbonate enhances peroxidase activity of Cu,Zn-superoxide dismutase. Role of carbonate anion radical and scavenging of carbonate anion radical by metalloporphyrin antioxidant enzyme mimetics

1 reference

https://api.crossref.org/works/10.1016%2FS0891-5849%2803%2900153-9

7 January 2021

The familial amyotrophic lateral sclerosis-associated amino acid substitutions E100G, G93A, and G93R do not influence the rate of inactivation of copper- and zinc-containing superoxide dismutase by H2O2

1 reference

https://api.crossref.org/works/10.1016%2FS0891-5849%2803%2900153-9

7 January 2021

Reexamination of the mechanism of hydroxyl radical adducts formed from the reaction between familial amyotrophic lateral sclerosis-associated Cu,Zn superoxide dismutase mutants and H2O2.

1 reference

https://api.crossref.org/works/10.1016%2FS0891-5849%2803%2900153-9

7 January 2021

Survival in transgenic ALS mice does not vary with CNS glutathione peroxidase activity.

1 reference

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7 January 2021

Increased mitochondrial antioxidative activity or decreased oxygen free radical propagation prevent mutant SOD1-mediated motor neuron cell death and increase amyotrophic lateral sclerosis-like transgenic mouse survival

1 reference

https://api.crossref.org/works/10.1016%2FS0891-5849%2803%2900153-9

7 January 2021

Common denominator of Cu/Zn superoxide dismutase mutants associated with amyotrophic lateral sclerosis: decreased stability of the apo state

1 reference

https://api.crossref.org/works/10.1016%2FS0891-5849%2803%2900153-9

7 January 2021

Mutations in copper-zinc superoxide dismutase that cause amyotrophic lateral sclerosis alter the zinc binding site and the redox behavior of the protein

1 reference

https://api.crossref.org/works/10.1016%2FS0891-5849%2803%2900153-9

7 January 2021

CCS knockout mice establish an alternative source of copper for SOD in ALS

1 reference

https://api.crossref.org/works/10.1016%2FS0891-5849%2803%2900153-9

7 January 2021

Nitroxyl (NO-): a substrate for superoxide dismutase

1 reference

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7 January 2021

The mode of decomposition of Angeli's salt (Na2N2O3) and the effects thereon of oxygen, nitrite, superoxide dismutase, and glutathione

1 reference

https://api.crossref.org/works/10.1016%2FS0891-5849%2803%2900153-9

7 January 2021

The oxidation of 3-hydroxyanthranilic acid by Cu,Zn superoxide dismutase: mechanism and possible consequences

1 reference

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7 January 2021

The regulation of mitochondrial oxygen uptake by redox reactions involving nitric oxide and ubiquinol

1 reference

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7 January 2021

Human Cu/Zn superoxide dismutase (SOD1) overexpression in mice causes mitochondrial vacuolization, axonal degeneration, and premature motoneuron death and accelerates motoneuron disease in mice expressing a familial amyotrophic lateral sclerosis mut

1 reference

https://api.crossref.org/works/10.1016%2FS0891-5849%2803%2900153-9

7 January 2021

Effect of overexpression of wild-type and mutant Cu/Zn-superoxide dismutases on oxidative damage and antioxidant defences: relevance to Down's syndrome and familial amyotrophic lateral sclerosis

1 reference

https://api.crossref.org/works/10.1016%2FS0891-5849%2803%2900153-9

7 January 2021

The modulation of cellular susceptibility to oxidative stress: protective and destructive actions of Cu,Zn-superoxide dismutase

1 reference

https://api.crossref.org/works/10.1016%2FS0891-5849%2803%2900153-9

7 January 2021

Aggregation and Motor Neuron Toxicity of an ALS-Linked SOD1 Mutant Independent from Wild-Type SOD1

1 reference

https://api.crossref.org/works/10.1016%2FS0891-5849%2803%2900153-9

7 January 2021

Mutant SOD1 causes motor neuron disease independent of copper chaperone-mediated copper loading

1 reference

https://api.crossref.org/works/10.1016%2FS0891-5849%2803%2900153-9

7 January 2021

Reversal of the superoxide dismutase reaction

1 reference

https://api.crossref.org/works/10.1016%2FS0891-5849%2803%2900153-9

7 January 2021

The uniqueness of superoxide dismutase (SOD)--why cannot most copper compounds substitute SOD in vivo?

1 reference

https://api.crossref.org/works/10.1016%2FS0891-5849%2803%2900153-9

7 January 2021

Thiol oxidase activity of copper, zinc superoxide dismutase

1 reference

https://api.crossref.org/works/10.1016%2FS0891-5849%2803%2900153-9

7 January 2021

Interaction of Cu,Zn superoxide dismutase with hydrogen sulfide

1 reference

https://api.crossref.org/works/10.1016%2FS0891-5849%2803%2900153-9

7 January 2021

Decreased metallation and activity in subsets of mutant superoxide dismutases associated with familial amyotrophic lateral sclerosis.

1 reference

https://api.crossref.org/works/10.1016%2FS0891-5849%2803%2900153-9

7 January 2021

?True? sporadic ALS associated with a novel SOD-1 mutation

1 reference

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7 January 2021

10.1016/S0891-5849(03)00153-9

Identifiers

DOI

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6 August 2017

1 reference