(Q36516376)

English

Two-year follow-up of Sanfilippo Disease patients treated with a genistein-rich isoflavone extract: assessment of effects on cognitive functions and general status of patients

scientific article published on April 2011

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scholarly article

1 reference

Europe PubMed Central

14 August 2017

Two-year follow-up of Sanfilippo Disease patients treated with a genistein-rich isoflavone extract: assessment of effects on cognitive functions and general status of patients (English)

1 reference

Europe PubMed Central

14 August 2017

Sanfilippo syndrome

1 reference

based on heuristic

inferred from title

Anna Tylki-Szymańska

4

object named as

Anna Tylki-Szymanska

1 reference

Europe PubMed Central

14 August 2017

Alicja Węgrzyn

7

object named as

Alicja Wegrzyn

1 reference

Europe PubMed Central

14 August 2017

Grzegorz Węgrzyn

10

object named as

Grzegorz Wegrzyn

1 reference

Europe PubMed Central

14 August 2017

Joanna Jakóbkiewicz-Banecka

2

object named as

Joanna Jakobkiewicz-Banecka

1 reference

Europe PubMed Central

14 August 2017

Agnieszka Maryniak

3

object named as

Agnieszka Maryniak

1 reference

Europe PubMed Central

14 August 2017

6

object named as

Anna Liberek

1 reference

Europe PubMed Central

14 August 2017

author name string

Ewa Piotrowska

1

1 reference

Europe PubMed Central

14 August 2017

Ewa Puk

5

1 reference

Europe PubMed Central

14 August 2017

Barbara Czartoryska

8

1 reference

Europe PubMed Central

14 August 2017

Monika Slominska-Wojewodzka

9

1 reference

Europe PubMed Central

14 August 2017

publication date

1 April 2011

1 reference

Europe PubMed Central

14 August 2017

Medical Science Monitor

1 reference

Europe PubMed Central

14 August 2017

17

1 reference

Europe PubMed Central

14 August 2017

CR196-202

1 reference

Europe PubMed Central

14 August 2017

4

1 reference

Europe PubMed Central

14 August 2017

Genistin-rich soy isoflavone extract in substrate reduction therapy for Sanfilippo syndrome: An open-label, pilot study in 10 pediatric patients

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3539518

30 September 2017

Genistein improves neuropathology and corrects behaviour in a mouse model of neurodegenerative metabolic disease

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3539518

30 September 2017

Genistein reduces glycosaminoglycan levels in a mouse model of mucopolysaccharidosis type II

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3539518

30 September 2017

Therapy for lysosomal storage disorders

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3539518

30 September 2017

Impairment of glycosaminoglycan synthesis in mucopolysaccharidosis type IIIA cells by using siRNA: a potential therapeutic approach for Sanfilippo disease

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3539518

30 September 2017

Gene silencing of EXTL2 and EXTL3 as a substrate deprivation therapy for heparan sulphate storing mucopolysaccharidoses.

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3539518

30 September 2017

Sanfilippo syndrome type B, a lysosomal storage disease, is also a tauopathy

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3539518

30 September 2017

Genistein-mediated inhibition of glycosaminoglycan synthesis, which corrects storage in cells of patients suffering from mucopolysaccharidoses, acts by influencing an epidermal growth factor-dependent pathway.

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3539518

30 September 2017

Sanfilippo syndrome: a mini-review

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3539518

30 September 2017

Treatment of lysosomal storage disorders : progress with enzyme replacement therapy

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3539518

30 September 2017

Substrate deprivation therapy: a new hope for patients suffering from neuronopathic forms of inherited lysosomal storage diseases

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3539518

30 September 2017

Genistein inhibits glutamate-induced apoptotic processes in primary neuronal cell cultures: an involvement of aryl hydrocarbon receptor and estrogen receptor/glycogen synthase kinase-3beta intracellular signaling pathway

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3539518

30 September 2017

Genistein-mediated inhibition of glycosaminoglycan synthesis as a basis for gene expression-targeted isoflavone therapy for mucopolysaccharidoses

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3539518

30 September 2017

Subacute sclerosing panencephalitis: results of the Canadian Paediatric Surveillance Program and review of the literature

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3539518

30 September 2017

Substrate reduction therapy for lysosomal storage diseases

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3539518

30 September 2017

The first 5 years of clinical experience with laronidase enzyme replacement therapy for mucopolysaccharidosis I.

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3539518

30 September 2017

Neuroprotective effect of genistein against beta amyloid-induced neurotoxicity

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3539518

30 September 2017

Estradiol or genistein prevent Alzheimer's disease-associated inflammation correlating with an increase PPAR gamma expression in cultured astrocytes.

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3539518

21 September 2018

Mucopolysaccharidosis IIIB: oxidative damage and cytotoxic cell involvement in the neuronal pathogenesis.

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3539518

21 September 2018

Genistein attenuates oxidative stress and neuronal damage following transient global cerebral ischemia in rat hippocampus.

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3539518

21 September 2018

Mechanisms of neurodegeneration in mucopolysaccharidoses II and IIIB: analysis of human brain tissue

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3539518

21 September 2018

Improvement in behaviour after substrate deprivation therapy with rhodamine B in a mouse model of MPS IIIA.

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3539518

21 September 2018

Anti-inflammatory and neuroprotective effect of a phytoestrogen compound on rat microglia.

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3539518

21 September 2018

Cytokines, neurotrophins, and oxidative stress in brain disease from mucopolysaccharidosis IIIB.

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3539518

21 September 2018

Inhibition of glycosaminoglycan synthesis using rhodamine B in a mouse model of mucopolysaccharidosis type IIIA.

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3539518

21 September 2018

Genistein ameliorates beta-amyloid peptide (25-35)-induced hippocampal neuronal apoptosis

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3539518

21 September 2018

Use of a brief assessment examination in a study of subacute sclerosing panencephalitis.

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3539518

21 September 2018

A general model for genetic regulation of turnover of glycosaminoglycans suggests a possible procedure for prediction of severity and clinical progress of mucopolysaccharidoses

1 reference

https://pubmed.ncbi.nlm.nih.gov/21455105

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Correlation between severity of mucopolysaccharidoses and combination of the residual enzyme activity and efficiency of glycosaminoglycan synthesis

1 reference

https://pubmed.ncbi.nlm.nih.gov/21455105

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

X-linked mental retardation

1 reference

https://pubmed.ncbi.nlm.nih.gov/21455105

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Identifiers

10.12659/MSM.881715

0 references

1 reference

Europe PubMed Central

14 August 2017

1 reference

Europe PubMed Central

14 August 2017

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