(Q36556391)

14 August 2017

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title

Cystic fibrosis mouse models (English)

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14 August 2017

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4

Danuta Radzioch

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Gregory P. Downey

object named as

Gregory P Downey

series ordinal

3

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Sahar Saeed

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author name string

Claudine Guilbault

series ordinal

1

1 reference

PubMed ID

16888286

14 August 2017

Zienab Saeed

series ordinal

2

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14 August 2017

3 August 2006

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American Journal of Respiratory Cell and Molecular Biology

14 August 2017

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14 August 2017

36

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14 August 2017

1-7

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14 August 2017

1

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An animal model for cystic fibrosis made by gene targeting

14 August 2017

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2006-0184TR

Lung disease in mice with cystic fibrosis

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2006-0184TR

Characteristic multiorgan pathology of cystic fibrosis in a long-living cystic fibrosis transmembrane regulator knockout murine model

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2006-0184TR

Cystic fibrosis lung disease following infection with Pseudomonas aeruginosa in Cftr knockout mice using novel non-invasive direct pulmonary infection technique.

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2006-0184TR

Cystic fibrosis in the mouse by targeted insertional mutagenesis

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2006-0184TR

Production of a severe cystic fibrosis mutation in mice by gene targeting

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2006-0184TR

A severe phenotype in mice with a duplication of exon 3 in the cystic fibrosis locus.

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2006-0184TR

Modulation of disease severity in cystic fibrosis transmembrane conductance regulator deficient mice by a secondary genetic factor

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2006-0184TR

Generation and characterization of a delta F508 cystic fibrosis mouse model.

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2006-0184TR

A mouse model for the delta F508 allele of cystic fibrosis.

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2006-0184TR

Genotype-phenotype correlation in cystic fibrosis: the role of modifier genes.

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2006-0184TR

The severe G480C cystic fibrosis mutation, when replicated in the mouse, demonstrates mistrafficking, normal survival and organ-specific bioelectrics.

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2006-0184TR

Mouse models of chronic lung infection with Pseudomonas aeruginosa: models for the study of cystic fibrosis

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2006-0184TR

Talniflumate increases survival in a cystic fibrosis mouse model of distal intestinal obstructive syndrome

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2006-0184TR

A membrane lipid imbalance plays a role in the phenotypic expression of cystic fibrosis in cftr(-/-) mice

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2006-0184TR

Relationship of a non-cystic fibrosis transmembrane conductance regulator-mediated chloride conductance to organ-level disease in Cftr(-/-) mice

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2006-0184TR

Distinct pattern of lung gene expression in the Cftr-KO mice developing spontaneous lung disease compared with their littermate controls

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2006-0184TR

The lung in cystic fibrosis. A quantitative study including prevalence of pathologic findings among different age groups

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2006-0184TR

Murine submucosal glands are clonally derived and show a cystic fibrosis gene-dependent distribution pattern

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2006-0184TR

Cystic fibrosis transmembrane conductance regulator-dependent regulation of epithelial inducible nitric oxide synthase expression

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2006-0184TR

Inducible nitric oxide synthase expression is reduced in cystic fibrosis murine and human airway epithelial cells

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2006-0184TR

Chloride secretory response of cystic fibrosis human airway epithelia. Preservation of calcium but not protein kinase C- and A-dependent mechanisms

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2006-0184TR

Normalization of raised sodium absorption and raised calcium-mediated chloride secretion by adenovirus-mediated expression of cystic fibrosis transmembrane conductance regulator in primary human cystic fibrosis airway epithelial cells

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2006-0184TR

Activation of airway cl- secretion in human subjects by adenosine.

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2006-0184TR

Transcriptional gene silencing in plants: targets, inducers and regulators

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2006-0184TR

Innate lung defenses and compromised Pseudomonas aeruginosa clearance in the malnourished mouse model of respiratory infections in cystic fibrosis

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2006-0184TR

Mapping of genetic factors influencing the weight of cystic fibrosis knockout mice.

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2006-0184TR

Increased rate of fractures and severe kyphosis: sequelae of living into adulthood with cystic fibrosis.

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2006-0184TR

CFTR as a cAMP-dependent regulator of sodium channels

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2006-0184TR

Murine models of chronic Pseudomonas aeruginosa lung infection

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2006-0184TR

Excessive inflammatory response of cystic fibrosis mice to bronchopulmonary infection with Pseudomonas aeruginosa

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2006-0184TR

Nonmucoid Pseudomonas aeruginosa expresses alginate in the lungs of patients with cystic fibrosis and in a mouse model.

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2006-0184TR

Role of Cftr genotype in the response to chronic Pseudomonas aeruginosa lung infection in mice

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2006-0184TR

Response to acute lung infection with mucoid Pseudomonas aeruginosa in cystic fibrosis mice

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2006-0184TR

Gene complementation of airway epithelium in the cystic fibrosis mouse is necessary and sufficient to correct the pathogen clearance and inflammatory abnormalities

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2006-0184TR

Novel mouse model of chronic Pseudomonas aeruginosa lung infection mimicking cystic fibrosis

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2006-0184TR

Intranasal immunization strategy to impede pilin-mediated binding of Pseudomonas aeruginosa to airway epithelial cells

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2006-0184TR

Identification of DNA markers for a transmissible Pseudomonas aeruginosa cystic fibrosis strain

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2006-0184TR

Enhanced susceptibility to pulmonary infection with Burkholderia cepacia in Cftr(-/-) mice

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2006-0184TR

Neutrophil transepithelial migration: role of toll-like receptors in mucosal inflammation

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2006-0184TR

Toll-like receptors in normal and cystic fibrosis airway epithelial cells.

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2006-0184TR

Lung inflammation as a therapeutic target in cystic fibrosis.

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2006-0184TR

Nutritional effects on host response to lung infections with mucoid Pseudomonas aeruginosa in mice

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2006-0184TR

Characterization of LPS-induced lung inflammation in cftr-/- mice and the effect of docosahexaenoic acid

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2006-0184TR

Vitamins and respiratory disease: antioxidant micronutrients in pulmonary health and disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2006-0184TR

Modulation of deltaF508 cystic fibrosis transmembrane regulator trafficking and function with 4-phenylbutyrate and flavonoids

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2006-0184TR

Curcumin, a major constituent of turmeric, corrects cystic fibrosis defects

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2006-0184TR

SERCA pump inhibitors do not correct biosynthetic arrest of deltaF508 CFTR in cystic fibrosis

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2006-0184TR

Embryonic stem cells generate airway epithelial tissue

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2006-0184TR

Successful targeting of the mouse cystic fibrosis transmembrane conductance regulator gene in embryonal stem cells

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2006-0184TR

Altered chloride ion channel kinetics associated with the ΔF508 cystic fibrosis mutation

21 January 2018

1 reference

https://api.crossref.org/works/10.1165%2FRCMB.2006-0184TR

21 January 2018

Identifiers

DOI

10.1165/RCMB.2006-0184TR

1 reference

14 August 2017

1 reference

PubMed ID

16888286