(Q37868451)

24 August 2017

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title

Oxidative stress in phenylketonuria: what is the evidence? (English)

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24 August 2017

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3

Moacir Wajner

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24 August 2017

Graziela S Ribas

1

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PubMed ID

21516352

24 August 2017

Angela Sitta

series ordinal

2

1 reference

PubMed ID

21516352

24 August 2017

Carmen R Vargas

series ordinal

4

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24 August 2017

23 April 2011

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Cellular and Molecular Neurobiology

24 August 2017

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24 August 2017

31

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24 August 2017

5

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24 August 2017

653-662

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https://scigraph.springernature.com/pub.10.1007/s10571-011-9693-2

24 August 2017

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cites work

Oxidative stress in neurodegeneration: cause or consequence?

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Response monitoring in children with phenylketonuria.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Plasma phenylalanine is associated with decreased serum ubiquinone-10 concentrations in phenylketonuria

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

A longitudinal study of antioxidant status in phenylketonuric patients.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Evidence that oxidative stress is increased in plasma from patients with maple syrup urine disease.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Oxidative stress in plasma from maple syrup urine disease patients during treatment.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Morphologic and histoanatomic observations of the brain in untreated human phenylketonuria.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Biochemical and toxicological properties of the oxidation products of catecholamines

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Microglial-produced nitric oxide and reactive nitrogen oxides mediate neuronal cell death

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

alpha-keto acids accumulating in maple syrup urine disease stimulate lipid peroxidation and reduce antioxidant defences in cerebral cortex from young rats.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Tissue-specific functions of individual glutathione peroxidases

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Reduced myelinogenesis and recovery in hyperphenylalaninemic rats. Correlation between brain phenylalanine levels, characteristic brain enzymes for myelination, and brain development.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Basic mechanisms of antioxidant activity

21 January 2018

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https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Low selenium diet increases the dopamine turnover in prefrontal cortex of the rat.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Inhibition of brain and liver 3-hydroxy-3-methylglutaryl-CoA reductase and mevalonate-5-pyrophosphate decarboxylase in experimental hyperphenylalaninemia.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Mitochondria deficient in complex I activity are depolarized by hydrogen peroxide in nerve terminals: relevance to Parkinson's disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Species differences in the generation of reactive oxygen species by microglia

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Hyperphenylalaninemia reduces creatine kinase activity in the cerebral cortex of rats

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Protein carbonyl groups as biomarkers of oxidative stress.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Biomarkers of oxidative damage in human disease.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Glutaric acid induces oxidative stress in brain of young rats

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Mitochondrial function as a determinant of recovery or death in cell response to injury.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Free radical-induced damage to DNA: mechanisms and measurement

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

A review of recent studies on the metabolism of exogenous and endogenous malondialdehyde

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Reactive carbonyls and oxidative stress: potential for therapeutic intervention

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Oxidative stress in a phenylketonuria animal model.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Chemistry and biochemistry of 4-hydroxynonenal, malonaldehyde and related aldehydes

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Free radicals, antioxidants, and nutrition

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Alanine prevents the reduction of pyruvate kinase activity in brain cortex of rats subjected to chemically induced hyperphenylalaninemia.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Experimental evidence that phenylalanine provokes oxidative stress in hippocampus and cerebral cortex of developing rats

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Propionic and L-methylmalonic acids induce oxidative stress in brain of young rats.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Superoxide radical and superoxide dismutases

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Fundamental aspects of reactive oxygen species, or what's the matter with oxygen?

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Cognitive functions and the antioxidant system in phenylketonuric patients

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Phenylketonuria: dietary and therapeutic challenges

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Antioxidant and antiradical activities of L-carnitine

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Role of free radicals in the neurodegenerative diseases: therapeutic implications for antioxidant treatment

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Oxidative stress and neurodegeneration: where are we now?

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

"Hypotyrosinemia" in phenylketonuria

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Cerebral Glucose Metabolism Is Decreased in White Matter Changes in Patients with Phenylketonuria

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Quantification of protein modification by oxidants

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Biological selectivity and functional aspects of protein tyrosine nitration

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Oxidative stress and the pathogenesis of Parkinson's disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Non-linear accumulation of 8-hydroxy-2'-deoxyguanosine, a marker of oxidized DNA damage, during aging

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Experimental hyperphenylalaninemia provokes oxidative stress in rat brain.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Mechanism of mitochondrial uncouplers, inhibitors, and toxins: focus on electron transfer, free radicals, and structure-activity relationships

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Biochemical and neuropsychological effects of elevated plasma phenylalanine in patients with treated phenylketonuria. A model for the study of phenylalanine and brain function in man

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Clinical and nutritional evaluation of phenylketonuric patients on tetrahydrobiopterin monotherapy.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

3-Hydroxyglutaric acid induces oxidative stress and decreases the antioxidant defenses in cerebral cortex of young rats

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Induction of oxidative stress by the metabolites accumulating in 3-methylglutaconic aciduria in cerebral cortex of young rats.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Carbonyl modified proteins in cellular regulation, aging, and disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Alanine prevents the in vitro inhibition of glycolysis caused by phenylalanine in brain cortex of rats

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Oxidative stress induced by phenylketonuria in the rat: Prevention by melatonin, vitamin E, and vitamin C.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Mitochondrial damage induced by fetal hyperphenylalaninemia in the rat brain and liver: its prevention by melatonin, Vitamin E, and Vitamin C.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Novel mechanisms of natural antioxidant compounds in biological systems: involvement of glutathione and glutathione-related enzymes

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

The evolution of free radicals and oxidative stress

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Transition metals as catalysts of "autoxidation" reactions

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

The L-arginine-nitric oxide pathway

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Lipoic acid prevents oxidative stress in vitro and in vivo by an acute hyperphenylalaninemia chemically-induced in rat brain

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

The effect of hyperphenylalaninemia on size and density of synapses in rat neocortex

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Lipid peroxidation: physiological levels and dual biological effects

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Adventiously-bound redox active iron and copper are at the center of oxidative damage in Alzheimer disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Neurological aspects of adult phenylketonuria

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Nutrition, physical growth, and bone density in treated phenylketonuria

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Inhibition of the mitochondrial respiratory chain by phenylalanine in rat cerebral cortex

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Oxidative stress and the pathogenesis of neurodegenerative disorders

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Reduction of lipid and protein damage in patients with disorders of propionate metabolism under treatment: a possible protective role of L-carnitine supplementation

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Methylmalonic acidaemia leads to increased production of reactive oxygen species and induction of apoptosis through the mitochondrial/caspase pathway

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Biophysical consequences of lipid peroxidation in membranes

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Effect of phenylalanine, p-chlorophenylalanine and alpha-methylphenylalanine on glucose uptake in vitro by the brain of young rats.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Effect of diet on plasma total antioxidant status in phenylketonuric patients

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Low total antioxidant status is implicated with high 8-hydroxy-2-deoxyguanosine serum concentrations in phenylketonuria

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Lipid composition of human cerebral white matter and myelin in phenylketonuria

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Oxidative stress in patients with phenylketonuria.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Investigation of oxidative stress parameters in treated phenylketonuric patients.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Evidence that DNA damage is associated to phenylalanine blood levels in leukocytes from phenylketonuric patients

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

L-carnitine blood levels and oxidative stress in treated phenylketonuric patients

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Effect of short- and long-term exposition to high phenylalanine blood levels on oxidative damage in phenylketonuric patients.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Behaviour in early treated phenylketonuria: a systematic review

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Induction of oxidative stress by the metabolites accumulating in isovaleric acidemia in brain cortex of young rats.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Inhibition of rat brain Na+, K+-ATPase activity induced by homocysteine is probably mediated by oxidative stress.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

In vitro effect of homocysteine on some parameters of oxidative stress in rat hippocampus

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Biochemical markers related to Alzheimer's dementia in serum and cerebrospinal fluid

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

4-Hydroxy-2-nonenal: a product and mediator of oxidative stress

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Effect of experimental hyperphenylalaninemia on the postnatal rat brain.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Role of oxygen radicals in DNA damage and cancer incidence.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Free radicals and antioxidants in normal physiological functions and human disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

The role of oxidative damage in the neuropathology of organic acidurias: insights from animal studies.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Selenium, glutathione peroxidase (GSH-Px) and lipid peroxidation products before and after selenium supplementation

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Alanine prevents the decrease of Na+,K+-ATPase activity in experimental phenylketonuria.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Inhibition of Na(+),K(+)-ATPase activity in hippocampus of rats subjected to acute administration of homocysteine is prevented by vitamins E and C treatment

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Redox sensing by prokaryotic transcription factors

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Effect of L-Carnitine derivatives on heart mitochondrial damage induced by lipid peroxidation

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS10571-011-9693-2

Oxidative stress in the context of acute cerebrovascular stroke

21 January 2018

1 reference

12 December 2020

L-propionyl carnitine protects erythrocytes and low density lipoproteins against peroxidation

1 reference

12 December 2020

Antioxidant status in hyperphenylalaninemia

1 reference

12 December 2020

Thought processes as related to brain metabolism in certain abnormal conditions.

1 reference

12 December 2020

Chromatographic determination of 8-oxo-7,8-dihydro-2'-deoxyguanosine in cellular DNA: a validation study

1 reference

12 December 2020

Plasma selenium levels in treated phenylketonuric patients

1 reference

12 December 2020

The roles of free radicals in amyotrophic lateral sclerosis: reactive oxygen species and elevated oxidation of protein, DNA, and membrane phospholipids

1 reference

12 December 2020

Alanine reverses the inhibitory effect of phenylalanine and its metabolites on Na+,K(+)-ATPase in synaptic plasma membranes from cerebral cortex of rats

1 reference

12 December 2020

Lipophilic antioxidants in patients with phenylketonuria

1 reference

12 December 2020

Decreased serum ubiquinone-10 concentrations in phenylketonuria

1 reference

12 December 2020

The comet assay: a comprehensive review

1 reference

12 December 2020

Serotonin and Dopamine Synthesis in Phenylketonuria

1 reference

12 December 2020

Erythrocyte glutathione peroxidase activity and plasma selenium concentration are reduced in maple syrup urine disease patients during treatment

1 reference

12 December 2020

Effect of phenylalanine and alpha-methylphenylalanine on in vitro incorporation of 32P into cytoskeletal cerebral proteins

1 reference

12 December 2020

Mitochondrial damage: an important feature in a number of inborn errors of metabolism?

1 reference

12 December 2020

Tocopherol in inborn errors of intermediary metabolism

1 reference

12 December 2020

Evaluation of total antioxidant potential (TRAP) and total antioxidant reactivity from luminol-enhanced chemiluminescence measurements

1 reference

12 December 2020

Protein status of infants with phenylketonuria undergoing nutrition management

1 reference

12 December 2020

Trace element nutrition status and dietary intake of children with phenylketonuria

1 reference

12 December 2020

Antioxidant and thyroid hormone status in selenium-deficient phenylketonuric and hyperphenylalaninemic patients

1 reference

12 December 2020

Plasma glutathione peroxidase after selenium supplementation in patients with reduced selenium state

1 reference

12 December 2020

Plasma antioxidant capacity in two cases of tyrosinaemia type 1: one case treated with NTBC

1 reference

12 December 2020

Serum selenium levels in individuals on PKU diets

1 reference

12 December 2020

Dietary interventions for phenylketonuria

1 reference

12 December 2020

Micronutrients: oxidant/antioxidant status.

1 reference

12 December 2020

Coenzyme Q10 in the diet--daily intake and relative bioavailability

1 reference

12 December 2020

Serum carnitine level in phenylketonuric children under dietary control in Greece

1 reference

12 December 2020

[Congenital errors of metabolism: cause of oxidative stress?]

1 reference

12 December 2020

Neurological findings in early treated phenylketonuria

1 reference

12 December 2020

10.1007/S10571-011-9693-2

Identifiers

DOI

1 reference

24 August 2017

1 reference

PubMed ID

21516352