(Q41138327)

English

Clinical utility of alpha-1 proteinase inhibitor in the management of adult patients with severe alpha-1 antitrypsin deficiency: a review of the current literature

scientific article published on 14 July 2017

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scholarly article

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Europe PubMed Central

27 September 2017

6 references

24 March 2019

22 April 2019

20 November 2019

27 November 2019

13 December 2019

31 January 2021

Clinical utility of alpha-1 proteinase inhibitor in the management of adult patients with severe alpha-1 antitrypsin deficiency: a review of the current literature (English)

1 reference

Europe PubMed Central

27 September 2017

alpha-1-antitrypsin deficiency

6 references

24 March 2019

22 April 2019

20 November 2019

27 November 2019

13 December 2019

31 January 2021

1 reference

20 November 2019

1 reference

27 November 2019

1 reference

13 December 2019

Serpin family A member 1

1 reference

31 January 2021

2

1 reference

Europe PubMed Central

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:28769553%20AND%20SRC:MED&resulttype=core&format=json

7 June 2020

author name string

David G Parr

1

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Europe PubMed Central

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7 June 2020

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publication date

14 July 2017

7 references

Europe PubMed Central

27 September 2017

24 March 2019

22 April 2019

20 November 2019

27 November 2019

13 December 2019

31 January 2021

Drug Design, Development and Therapy

7 references

24 March 2019

22 April 2019

20 November 2019

27 November 2019

13 December 2019

Europe PubMed Central

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:28769553%20AND%20SRC:MED&resulttype=core&format=json

7 June 2020

31 January 2021

11

1 reference

Europe PubMed Central

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:28769553%20AND%20SRC:MED&resulttype=core&format=json

7 June 2020

2149-2162

1 reference

Europe PubMed Central

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:28769553%20AND%20SRC:MED&resulttype=core&format=json

7 June 2020

copyright license

Creative Commons Attribution-NonCommercial

6 references

24 March 2019

22 April 2019

20 November 2019

27 November 2019

13 December 2019

31 January 2021

on focus list of Wikimedia project

0 references

Intravenous alpha-1 antitrypsin augmentation therapy for treating patients with alpha-1 antitrypsin deficiency and lung disease.

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5529111

27 September 2017

SPARTA clinical trial design: exploring the efficacy and safety of two dose regimens of alpha1-proteinase inhibitor augmentation therapy in alpha1-antitrypsin deficiency

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5529111

27 September 2017

Long-term experience in the treatment of α1-antitrypsin deficiency: 25 years of augmentation therapy

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5529111

27 September 2017

Alpha-1 proteinase inhibitors for the treatment of alpha-1 antitrypsin deficiency: safety, tolerability, and patient outcomes

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5529111

27 September 2017

Indications for active case searches and intravenous alpha-1 antitrypsin treatment for patients with alpha-1 antitrypsin deficiency chronic pulmonary obstructive disease: an update

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5529111

27 September 2017

Production and characterization of a novel human recombinant alpha-1-antitrypsin in PER.C6 cells

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5529111

27 September 2017

Alpha-1 antitrypsin deficiency targeted testing and augmentation therapy: a Canadian Thoracic Society clinical practice guideline

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5529111

27 September 2017

A review of augmentation therapy for alpha-1 antitrypsin deficiency

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5529111

27 September 2017

Efficacy of alpha1-antitrypsin augmentation therapy in conditions other than pulmonary emphysema

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5529111

27 September 2017

The discovery of α1-antitrypsin and its role in health and disease

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5529111

27 September 2017

The role of augmentation therapy in alpha-1 antitrypsin deficiency

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5529111

27 September 2017

Lung deposition of inhaled alpha-1-proteinase inhibitor (alpha 1-PI) - problems and experience of alpha1-PI inhalation therapy in patients with hereditary alpha1-PI deficiency and cystic fibrosis

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5529111

27 September 2017

Therapeutic efficacy of α-1 antitrypsin augmentation therapy on the loss of lung tissue: an integrated analysis of 2 randomised clinical trials using computed tomography densitometry

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5529111

27 September 2017

Pharmacokinetic comparability of Prolastin®-C to Prolastin® in alpha₁-antitrypsin deficiency: a randomized study

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5529111

27 September 2017

Intravenous alpha-1 antitrypsin augmentation therapy for treating patients with alpha-1 antitrypsin deficiency and lung disease

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5529111

27 September 2017

The I-neb Adaptive Aerosol Delivery System enhances delivery of alpha1-antitrypsin with controlled inhalation

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5529111

27 September 2017

Novel devices for individualized controlled inhalation can optimize aerosol therapy in efficacy, patient care and power of clinical trials

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5529111

27 September 2017

Alpha-1-antitrypsin augmentation therapy in deficient individuals enrolled in the Alpha-1 Foundation DNA and Tissue Bank

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5529111

27 September 2017

Exploring the optimum approach to the use of CT densitometry in a randomised placebo-controlled study of augmentation therapy in alpha 1-antitrypsin deficiency

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5529111

27 September 2017

Conformational pathology of the serpins: themes, variations, and therapeutic strategies

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5529111

27 September 2017

PI S and PI Z alpha-1 antitrypsin deficiency worldwide. A review of existing genetic epidemiological data

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5529111

27 September 2017

Aralast: an alpha 1-protease inhibitor for the treatment of alpha-antitrypsin deficiency

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5529111

27 September 2017

Molecular pathogenesis of alpha-1-antitrypsin deficiency-associated liver disease: a meeting review

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5529111

27 September 2017

Determinants of airflow obstruction in severe alpha-1-antitrypsin deficiency

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5529111

27 September 2017

alpha-1 antitrypsin inhibits caspase-3 activity, preventing lung endothelial cell apoptosis

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5529111

27 September 2017

Alpha-1-antitrypsin deficiency: optimal therapeutic regimen based on population pharmacokinetics

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5529111

27 September 2017

Validation of computed tomographic lung densitometry for monitoring emphysema in alpha1-antitrypsin deficiency

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5529111

27 September 2017

Alpha1-antitrypsin deficiency. 2: genetic aspects of alpha(1)-antitrypsin deficiency: phenotypes and genetic modifiers of emphysema risk

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5529111

27 September 2017

Correlation between annual change in health status and computer tomography derived lung density in subjects with alpha1-antitrypsin deficiency

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5529111

27 September 2017

Predictors of mortality in alpha1-antitrypsin deficiency

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5529111

27 September 2017

Emphysema in nonsmokers: alpha 1-antitrypsin deficiency and other causes.

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5529111

27 September 2017

Augmentation therapy reduces frequency of lung infections in antitrypsin deficiency: a new hypothesis with supporting data

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5529111

27 September 2017

Feasibility of a clinical trial of augmentation therapy for alpha(1)-antitrypsin deficiency. The Alpha 1-Antitrypsin Deficiency Registry Study Group

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5529111

27 September 2017

A randomized clinical trial of alpha(1)-antitrypsin augmentation therapy

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5529111

27 September 2017

Environmental correlates of impaired lung function in non-smokers with severe alpha 1-antitrypsin deficiency (PiZZ)

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5529111

27 September 2017

Survival of patients with severe alpha 1-antitrypsin deficiency with special reference to non-index cases

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5529111

27 September 2017

Replacement therapy of alpha 1-antitrypsin deficiency. Reversal of protease-antiprotease imbalance within the alveolar structures of PiZ subjects

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5529111

27 September 2017

Replacement therapy for alpha 1-antitrypsin deficiency associated with emphysema

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5529111

27 September 2017

Does alpha1-antitrypsin augmentation therapy slow the annual decline in FEV1 in patients with severe hereditary alpha1-antitrypsin deficiency? Wissenschaftliche Arbeitsgemeinschaft zur Therapie von Lungenerkrankungen (WATL) alpha1-AT study group.

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5529111

14 June 2018

Biochemical and biological properties of an alpha 1-antitrypsin concentrate

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5529111

14 June 2018

Quantitation of emphysema by computed tomography using a "density mask" program and correlation with pulmonary function tests

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5529111

14 June 2018

Lung CT density correlates with measurements of airflow limitation and the diffusing capacity

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5529111

14 June 2018

Long-term efficacy and safety of α1 proteinase inhibitor treatment for emphysema caused by severe α1 antitrypsin deficiency: an open-label extension trial (RAPID-OLE).

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5529111

19 August 2018

Intravenous augmentation treatment and lung density in severe α1 antitrypsin deficiency (RAPID): a randomised, double-blind, placebo-controlled trial.

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5529111

19 August 2018

Health-related quality of life in patients with alpha-1 antitrypsin deficiency: the French experience.

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5529111

19 August 2018

Mortality by level of emphysema and airway wall thickness

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5529111

19 August 2018

Successful α1-antitrypsin replacement therapy in a patient with α1-antitrypsin deficiency and granulomatosis with polyangiitis

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5529111

19 August 2018

Exploring the role of CT densitometry: a randomised study of augmentation therapy in alpha1-antitrypsin deficiency.

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5529111

19 August 2018

Monitoring the progress of emphysema by repeat computed tomography scans with focus on noise reduction.

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5529111

19 August 2018

Volume correction in computed tomography densitometry for follow-up studies on pulmonary emphysema.

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5529111

19 August 2018

Alpha1-antitrypsin inhibits the activity of the matriptase catalytic domain in vitro

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5529111

19 August 2018

Multi-center study: the biochemical efficacy, safety and tolerability of a new alpha1-proteinase inhibitor, Zemaira.

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5529111

19 August 2018

Antibody response to aerosolized transgenic human alpha1-antitrypsin.

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5529111

19 August 2018

Volume adjustment of lung density by computed tomography scans in patients with emphysema.

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5529111

19 August 2018

Characterization of the interstitial lung diseases via density-based and texture-based analysis of computed tomography images of lung structure and function.

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5529111

19 August 2018

American Thoracic Society/European Respiratory Society statement: standards for the diagnosis and management of individuals with alpha-1 antitrypsin deficiency.

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5529111

19 August 2018

Comparison of spirometric-gated and -ungated HRCT in COPD.

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5529111

19 August 2018

Biochemical efficacy and safety of a new pooled human plasma alpha(1)-antitrypsin, Respitin.

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5529111

19 August 2018

Decline in FEV1 among patients with severe hereditary alpha 1-antitrypsin deficiency type PiZ.

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5529111

19 August 2018

The 1981 catalogue of assigned human genetic markers and report of the nomenclature committee. Oslo Conference (1981): Sixth International Workshop on Human Gene Mapping.

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5529111

19 August 2018

Measurement of pulmonary parenchymal attenuation: use of spirometric gating with quantitative CT.

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5529111

19 August 2018

Actualización sobre indicaciones de búsqueda activa de casos y tratamiento con alfa-1 antitripsina por vía intravenosa en pacientes con enfermedad pulmonar obstructiva crónica asociada a déficit de alfa-1 antitripsina

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5529111

2 December 2018

CT Measurements of Lung Density in Life Can Quantitate Distal Airspace Enlargement—An Essential Defining Feature of Human Emphysema

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=5529111

2 December 2018

Emphysema of early onset associated with a complete deficiency of alpha-1-antitrypsin (null homozygotes)

1 reference

https://pubmed.ncbi.nlm.nih.gov/28769553

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Anti-neutrophil-elastase defenses of the lower respiratory tract in alpha 1-antitrypsin deficiency directly augmented with an aerosol of alpha 1-antitrypsin

1 reference

https://pubmed.ncbi.nlm.nih.gov/28769553

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Survival and FEV1 decline in individuals with severe deficiency of alpha1-antitrypsin. The Alpha-1-Antitrypsin Deficiency Registry Study Group

1 reference

https://pubmed.ncbi.nlm.nih.gov/28769553

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Reduction of severe exacerbations and hospitalization-derived costs in alpha-1-antitrypsin-deficient patients treated with alpha-1-antitrypsin augmentation therapy

1 reference

https://pubmed.ncbi.nlm.nih.gov/28769553

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Longitudinal changes in physiological, radiological, and health status measurements in alpha(1)-antitrypsin deficiency and factors associated with decline

1 reference

https://pubmed.ncbi.nlm.nih.gov/28769553

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

"Density mask". An objective method to quantitate emphysema using computed tomography

1 reference

https://pubmed.ncbi.nlm.nih.gov/28769553

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

The effect of augmentation therapy on bronchial inflammation in alpha1-antitrypsin deficiency

1 reference

https://pubmed.ncbi.nlm.nih.gov/28769553

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Repeatability of lung density measurements with low-dose computed tomography in subjects with alpha-1-antitrypsin deficiency-associated emphysema

1 reference

https://pubmed.ncbi.nlm.nih.gov/28769553

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Comparison of computed density and macroscopic morphometry in pulmonary emphysema

1 reference

https://pubmed.ncbi.nlm.nih.gov/28769553

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

High-resolution computed tomography scanning in alpha1-antitrypsin deficiency: relationship to lung function and health status

1 reference

https://pubmed.ncbi.nlm.nih.gov/28769553

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Biochemical efficacy and safety of monthly augmentation therapy for alpha 1-antitrypsin deficiency

1 reference

https://pubmed.ncbi.nlm.nih.gov/28769553

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Clinical course and prognosis of never-smokers with severe alpha-1-antitrypsin deficiency (PiZZ)

1 reference

https://pubmed.ncbi.nlm.nih.gov/28769553

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Augmentation therapy for alpha1 antitrypsin deficiency: a meta-analysis

1 reference

https://pubmed.ncbi.nlm.nih.gov/28769553

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

[Guidelines for the diagnosis and management of alpha-1 antitrypsin deficiency]

1 reference

https://pubmed.ncbi.nlm.nih.gov/28769553

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Alpha-1 antitrypsin augmentation therapy and biomarkers of elastin degradation

1 reference

https://pubmed.ncbi.nlm.nih.gov/28769553

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Augmentation therapy with alpha1-antitrypsin: patterns of use and adverse events

1 reference

https://pubmed.ncbi.nlm.nih.gov/28769553

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

From the NIH: Intravenous replacement therapy for patients with severe alpha 1-antitrypsin deficiency

1 reference

https://pubmed.ncbi.nlm.nih.gov/28769553

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

DIAGNOSIS OF PULMONARY EMPHYSEMA BY COMPUTERISED TOMOGRAPHY

1 reference

https://pubmed.ncbi.nlm.nih.gov/28769553

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Longitudinal follow-up of patients with alpha(1)-protease inhibitor deficiency before and during therapy with IV alpha(1)-protease inhibitor

1 reference

https://pubmed.ncbi.nlm.nih.gov/28769553

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Clinical features of individuals with PI*SZ phenotype of alpha 1-antitrypsin deficiency. alpha 1-Antitrypsin Deficiency Registry Study Group

1 reference

https://pubmed.ncbi.nlm.nih.gov/28769553

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Exercise capacity predicts health status in alpha(1)-antitrypsin deficiency

1 reference

https://pubmed.ncbi.nlm.nih.gov/28769553

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

High level expression of active human alpha-1-antitrypsin in the milk of transgenic sheep

1 reference

https://pubmed.ncbi.nlm.nih.gov/28769553

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Acute allergic reaction and demonstration of specific IgE antibodies against alpha-1-protease inhibitor

1 reference

https://pubmed.ncbi.nlm.nih.gov/28769553

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

High resolution computed tomography of inflation-fixed lungs. Pathologic-radiologic correlation of centrilobular emphysema

1 reference

https://pubmed.ncbi.nlm.nih.gov/28769553

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Preparation and properties of alpha 1-proteinase inhibitor concentrate from human plasma

1 reference

https://pubmed.ncbi.nlm.nih.gov/28769553

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Comparison of computed density and microscopic morphometry in pulmonary emphysema

1 reference

https://pubmed.ncbi.nlm.nih.gov/28769553

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Long-term treatment of alpha1-antitrypsin deficiency-related pulmonary emphysema with human alpha1-antitrypsin. Wissenschaftliche Arbeitsgemeinschaft zur Therapie von Lungenerkrankungen (WATL)-alpha1-AT-study group

1 reference

https://pubmed.ncbi.nlm.nih.gov/28769553

12 December 2020

based on heuristic

inferred from PubMed ID database lookup

Identifiers

10.2147/DDDT.S105207

1 reference

Europe PubMed Central

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:28769553%20AND%20SRC:MED&resulttype=core&format=json

7 June 2020

1 reference

Europe PubMed Central

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:28769553%20AND%20SRC:MED&resulttype=core&format=json

7 June 2020

1 reference

Europe PubMed Central

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:28769553%20AND%20SRC:MED&resulttype=core&format=json

7 June 2020

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