(Q45345359)

13 December 2017

title

SFTPC mutations cause SP-C degradation and aggregate formation without increasing ER stress (English)

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13 December 2017

Tobias Thurm

1

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13 December 2017

Eva Kaltenborn

2

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13 December 2017

Sunčana Kern

3

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13 December 2017

Matthias Griese

4

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13 December 2017

Ralf Zarbock

5

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13 December 2017

publication date

24 May 2013

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European Journal of Clinical Investigation

13 December 2017

published in

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13 December 2017

volume

43

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13 December 2017

issue

8

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13 December 2017

page(s)

791-800

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Palmitoylation of pulmonary surfactant protein SP-C is critical for its functional cooperation with SP-B to sustain compression/expansion dynamics in cholesterol-containing surfactant films.

13 December 2017

cites work

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Proteomic analysis of lamellar bodies isolated from rat lungs

21 January 2018

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The tetraspanin CD63/lamp3 cycles between endocytic and secretory compartments in human endothelial cells

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Surfactant protein C biosynthesis and its emerging role in conformational lung disease

21 January 2018

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Proteolytic generation and aggregation of peptides from transmembrane regions: lung surfactant protein C and amyloid beta-peptide

21 January 2018

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Heterozygosity for a surfactant protein C gene mutation associated with usual interstitial pneumonitis and cellular nonspecific interstitial pneumonitis in one kindred

21 January 2018

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Surfactant protein C mutations are the basis of a significant portion of adult familial pulmonary fibrosis in a dutch cohort.

21 January 2018

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A common mutation in the surfactant protein C gene associated with lung disease.

21 January 2018

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Endoplasmic reticulum stress induced by surfactant protein C BRICHOS mutants promotes proinflammatory signaling by epithelial cells

21 January 2018

1 reference

A non-BRICHOS surfactant protein c mutation disrupts epithelial cell function and intercellular signaling

21 January 2018

1 reference

A surfactant protein C precursor protein BRICHOS domain mutation causes endoplasmic reticulum stress, proteasome dysfunction, and caspase 3 activation

21 January 2018

1 reference

Misfolded BRICHOS SP-C mutant proteins induce apoptosis via caspase-4- and cytochrome c-related mechanisms

21 January 2018

1 reference

Endoplasmic reticulum stress in alveolar epithelial cells is prominent in IPF: association with altered surfactant protein processing and herpesvirus infection.

21 January 2018

1 reference

Nonspecific interstitial pneumonia, alveolar proteinosis, and abnormal proprotein trafficking resulting from a spontaneous mutation in the surfactant protein C gene

21 January 2018

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Interstitial lung disease in a baby with a de novo mutation in the SFTPC gene

21 January 2018

1 reference

Genetic mutations in surfactant protein C are a rare cause of sporadic cases of IPF

21 January 2018

1 reference

A nonaggregating surfactant protein C mutant is misdirected to early endosomes and disrupts phospholipid recycling.

21 January 2018

1 reference

The Brichos domain of prosurfactant protein C can hold and fold a transmembrane segment

21 January 2018

1 reference

Deletion of exon 4 from human surfactant protein C results in aggresome formation and generation of a dominant negative

21 January 2018

1 reference

Expression of a Human Surfactant Protein C Mutation Associated with Interstitial Lung Disease Disrupts Lung Development in Transgenic Mice

21 January 2018

1 reference

Hydroxychloroquine and surfactant protein C deficiency

21 January 2018

1 reference

The surfactant protein C mutation A116D alters cellular processing, stress tolerance, surfactant lipid composition, and immune cell activation

21 January 2018

1 reference

Some ABCA3 mutations elevate ER stress and initiate apoptosis of lung epithelial cells

21 January 2018

1 reference

4-Phenylbutyric acid treatment rescues trafficking and processing of a mutant surfactant protein-C.

21 January 2018

1 reference

Cell surface relocalization of the endoplasmic reticulum chaperone and unfolded protein response regulator GRP78/BiP.

21 January 2018

1 reference

Improved detection of amyloid in fat pad aspiration: an evaluation of Congo red stain by fluorescent microscopy

21 January 2018

1 reference

Measurement of autophagy in cells and tissues.

21 January 2018

1 reference

New surfactant protein C gene mutations associated with diffuse lung disease

21 January 2018

1 reference

Role of endoplasmic reticulum stress in epithelial-mesenchymal transition of alveolar epithelial cells: effects of misfolded surfactant protein

21 January 2018

1 reference

Adaptation and increased susceptibility to infection associated with constitutive expression of misfolded SP-C.

21 January 2018

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Anti-amyloid activity of the C-terminal domain of proSP-C against amyloid beta-peptide and medin

21 January 2018

1 reference

Mutations linked to interstitial lung disease can abrogate anti-amyloid function of prosurfactant protein C.

21 January 2018

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BRICHOS domain associated with lung fibrosis, dementia and cancer--a chaperone that prevents amyloid fibril formation?

21 January 2018

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Palmitoylation and processing of the lipopeptide surfactant protein C.

21 January 2018

1 reference

21 January 2018

Identifiers

DOI

10.1111/ECI.12107

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13 December 2017

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