(Q40116328)

17 September 2017

Misfolded BRICHOS SP-C mutant proteins induce apoptosis via caspase-4- and cytochrome c-related mechanisms (English)

1 reference

17 September 2017

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Surafel Mulugeta

1

1 reference

17 September 2017

Jean Ann Maguire

2

1 reference

17 September 2017

Jennifer L Newitt

3

1 reference

17 September 2017

Scott J Russo

4

1 reference

17 September 2017

Adam Kotorashvili

5

1 reference

17 September 2017

Michael F Beers

6

1 reference

17 September 2017

22 June 2007

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American Journal of Physiology - Lung Cellular and Molecular Physiology

17 September 2017

1 reference

17 September 2017

293

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17 September 2017

3

1 reference

17 September 2017

L720-9

1 reference

Impairment of the ubiquitin-proteasome system by protein aggregation

17 September 2017

1 reference

https://api.crossref.org/works/10.1152%2FAJPLUNG.00025.2007

Interstitial lung disease in a baby with a de novo mutation in the SFTPC gene

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FAJPLUNG.00025.2007

Expression of a Human Surfactant Protein C Mutation Associated with Interstitial Lung Disease Disrupts Lung Development in Transgenic Mice

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FAJPLUNG.00025.2007

Adaptation and increased susceptibility to infection associated with constitutive expression of misfolded SP-C.

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FAJPLUNG.00025.2007

Evidence for proteasome dysfunction in cytotoxicity mediated by anti-Ras intracellular antibodies.

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FAJPLUNG.00025.2007

Ubiquitin-mediated degradation of cellular proteins in health and disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FAJPLUNG.00025.2007

Secretion of surfactant protein C, an integral membrane protein, requires the N-terminal propeptide.

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FAJPLUNG.00025.2007

Deacylated pulmonary surfactant protein SP-C transforms from alpha-helical to amyloid fibril structure via a pH-dependent mechanism: an infrared structural investigation.

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FAJPLUNG.00025.2007

Degradation signals for ubiquitin system proteolysis in Saccharomyces cerevisiae

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FAJPLUNG.00025.2007

Involvement of caspase-4 in endoplasmic reticulum stress-induced apoptosis and Abeta-induced cell death

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FAJPLUNG.00025.2007

A transgenic mouse model for monitoring endoplasmic reticulum stress

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FAJPLUNG.00025.2007

Multiple proteolytic systems, including the proteasome, contribute to CFTR processing.

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FAJPLUNG.00025.2007

The Brichos domain-containing C-terminal part of pro-surfactant protein C binds to an unfolded poly-val transmembrane segment

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FAJPLUNG.00025.2007

Post-translational processing of surfactant protein-C proprotein: targeting motifs in the NH(2)-terminal flanking domain are cleaved in late compartments

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FAJPLUNG.00025.2007

Aggresomes: a cellular response to misfolded proteins

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FAJPLUNG.00025.2007

Orchestrating the unfolded protein response in health and disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FAJPLUNG.00025.2007

Cytochrome C and caspase-9 expression in Huntington's disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FAJPLUNG.00025.2007

Amyloid beta peptide induces cytochrome C release from isolated mitochondria

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FAJPLUNG.00025.2007

The release of cytochrome c from mitochondria: a primary site for Bcl-2 regulation of apoptosis

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FAJPLUNG.00025.2007

Aggresomes, inclusion bodies and protein aggregation

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FAJPLUNG.00025.2007

21 January 2018

Conformational disease

1 reference

https://api.crossref.org/works/10.1152%2FAJPLUNG.00025.2007

XBP-1 Regulates a Subset of Endoplasmic Reticulum Resident Chaperone Genes in the Unfolded Protein Response

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FAJPLUNG.00025.2007

The N-terminal propeptide of lung surfactant protein C is necessary for biosynthesis and prevents unfolding of a metastable alpha-helix.

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FAJPLUNG.00025.2007

Cytochrome c and dATP-dependent formation of Apaf-1/caspase-9 complex initiates an apoptotic protease cascade

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FAJPLUNG.00025.2007

Conversion of PrP to a self-perpetuating PrPSc-like conformation in the cytosol

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FAJPLUNG.00025.2007

Processing of surfactant protein C requires a type II transmembrane topology directed by juxtamembrane positively charged residues

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FAJPLUNG.00025.2007

A surfactant protein C precursor protein BRICHOS domain mutation causes endoplasmic reticulum stress, proteasome dysfunction, and caspase 3 activation

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FAJPLUNG.00025.2007

Cross-talk between two cysteine protease families. Activation of caspase-12 by calpain in apoptosis

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FAJPLUNG.00025.2007

Caspase-12 mediates endoplasmic-reticulum-specific apoptosis and cytotoxicity by amyloid-beta

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FAJPLUNG.00025.2007

ASK1 is essential for endoplasmic reticulum stress-induced neuronal cell death triggered by expanded polyglutamine repeats

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FAJPLUNG.00025.2007

A mutation in the surfactant protein C gene associated with familial interstitial lung disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FAJPLUNG.00025.2007

Caspase-12 and caspase-4 are not required for caspase-dependent endoplasmic reticulum stress-induced apoptosis

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FAJPLUNG.00025.2007

Rapid induction of the intrinsic apoptotic pathway by L-glutamine starvation

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FAJPLUNG.00025.2007

Parkin protects against the toxicity associated with mutant alpha-synuclein: proteasome dysfunction selectively affects catecholaminergic neurons

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FAJPLUNG.00025.2007

Amyloid beta-peptide disrupts mitochondrial membrane lipid and protein structure: protective role of tauroursodeoxycholate.

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FAJPLUNG.00025.2007

A trip to the ER: coping with stress

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FAJPLUNG.00025.2007

BRICHOS: a conserved domain in proteins associated with dementia, respiratory distress and cancer

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FAJPLUNG.00025.2007

Endoplasmic reticulum stress and mitochondrial cell death pathways mediate A53T mutant alpha-synuclein-induced toxicity

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FAJPLUNG.00025.2007

Nonspecific interstitial pneumonia, alveolar proteinosis, and abnormal proprotein trafficking resulting from a spontaneous mutation in the surfactant protein C gene

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FAJPLUNG.00025.2007

Heterozygosity for a surfactant protein C gene mutation associated with usual interstitial pneumonitis and cellular nonspecific interstitial pneumonitis in one kindred

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FAJPLUNG.00025.2007

Deletion of exon 4 from human surfactant protein C results in aggresome formation and generation of a dominant negative

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FAJPLUNG.00025.2007

Biosynthesis of surfactant protein C (SP-C). Sorting of SP-C proprotein involves homomeric association via a signal anchor domain

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FAJPLUNG.00025.2007

Degradation of CFTR by the ubiquitin-proteasome pathway

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FAJPLUNG.00025.2007

Regulation of apoptosis by the ubiquitin and proteasome pathway.

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FAJPLUNG.00025.2007

Neurotoxicity of a fragment of the amyloid precursor associated with Alzheimer's disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FAJPLUNG.00025.2007

Activation of caspase-12, an endoplastic reticulum (ER) resident caspase, through tumor necrosis factor receptor-associated factor 2-dependent mechanism in response to the ER stress

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FAJPLUNG.00025.2007

Patterns of atrophy in pathologically confirmed FTLD with and without motor neuron degeneration

21 January 2018

1 reference

https://api.crossref.org/works/10.1152%2FAJPLUNG.00025.2007

10.1152/AJPLUNG.00025.2007

21 January 2018

Identifiers

DOI

1 reference

17 September 2017

1 reference