(Q28477612)

2

0 references

Xiaodong Gao

3

0 references

Gavin Y Oudit

4

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Robert G Tsushima

Creative Commons Attribution 4.0 International

5

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language of work or name

English

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publication date

31 March 2011

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published in

PLOS One

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volume

6

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issue

3

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page(s)

e18273

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copyright license

start time

31 March 2011

1 reference

April 2022 Public Data File from Crossref

copyright status

copyrighted

0 references

cites work

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Mechanisms of pharmacological rescue of trafficking-defective hERG mutant channels in human long QT syndrome

19 March 2017

1 reference

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Correction of defective protein trafficking of a mutant HERG potassium channel in human long QT syndrome. Pharmacological and temperature effects

19 March 2017

1 reference

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Properties of HERG channels stably expressed in HEK 293 cells studied at physiological temperature

19 March 2017

1 reference

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A family of potassium channel genes related to eag in Drosophila and mammals

19 March 2017

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A mechanistic link between an inherited and an acquired cardiac arrhythmia: HERG encodes the IKr potassium channel

19 March 2017

1 reference

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Extracellular K+ is a prerequisite for the function and plasma membrane stability of HERG channels

19 March 2017

1 reference

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Hsp40 chaperones promote degradation of the HERG potassium channel

29 September 2017

1 reference

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Genetic testing for long-QT syndrome: distinguishing pathogenic mutations from benign variants.

29 September 2017

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Extracellular K+ concentration controls cell surface density of IKr in rabbit hearts and of the HERG channel in human cell lines

29 September 2017

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A new C-terminal hERG mutation A915fs+47X associated with symptomatic LQT2 and auditory-trigger syncope

29 September 2017

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The QT syndromes: long and short

29 September 2017

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Stimulation of N-terminal truncated isoform of androgen receptor stabilizes human ether-á-go-go-related gene-encoded potassium channel protein via activation of extracellular signal regulated kinase 1/2.

29 September 2017

1 reference

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Clinical practice. Long-QT syndrome

29 September 2017

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Improved functional expression of recombinant human ether-a-go-go (hERG) K+ channels by cultivation at reduced temperature

29 September 2017

1 reference

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Co-chaperone FKBP38 promotes HERG trafficking

29 September 2017

1 reference

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HERG trafficking and pharmacological rescue of LQTS-2 mutant channels.

29 September 2017

1 reference

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The ubiquitin-proteasome system: focus on the heart.

29 September 2017

1 reference

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Most LQT2 mutations reduce Kv11.1 (hERG) current by a class 2 (trafficking-deficient) mechanism

29 September 2017

1 reference

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Role of sequence variations in the human ether-a-go-go-related gene (HERG, KCNH2) in the Brugada syndrome

29 September 2017

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Degradation of trafficking-defective long QT syndrome type II mutant channels by the ubiquitin-proteasome pathway.

29 September 2017

1 reference

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Novel C-terminus frameshift mutation, 1122fs/147, of HERG in LQT2: additional amino acids generated by frameshift cause accelerated inactivation

29 September 2017

1 reference

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Pharmacological rescue of trafficking defective HERG channels formed by coassembly of wild-type and long QT mutant N470D subunits

29 September 2017

1 reference

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Clinical and electrophysiological characterization of a novel mutation R863X in HERG C-terminus associated with long QT syndrome

29 September 2017

1 reference

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Defective protein trafficking in hERG-associated hereditary long QT syndrome (LQT2): molecular mechanisms and restoration of intracellular protein processing

29 September 2017

1 reference

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29 September 2017

1 reference

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C-terminal domains implicated in the functional surface expression of potassium channels

29 September 2017

1 reference

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Heteroligomerization of an Aquaporin-2 mutant with wild-type Aquaporin-2 and their misrouting to late endosomes/lysosomes explains dominant nephrogenic diabetes insipidus

29 September 2017

1 reference

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The binding site for channel blockers that rescue misprocessed human long QT syndrome type 2 ether-a-gogo-related gene (HERG) mutations

29 September 2017

1 reference

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Two components of cardiac delayed rectifier K+ current. Differential sensitivity to block by class III antiarrhythmic agents

29 September 2017

1 reference

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Functional characterization of the C-terminus of the human ether-à-go-go-related gene K(+) channel (HERG).

29 September 2017

1 reference

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A K+ channel splice variant common in human heart lacks a C-terminal domain required for expression of rapidly activating delayed rectifier current

2 June 2018

1 reference

https://api.crossref.org/works/10.1371%2FJOURNAL.PONE.0018273

Aminoglycoside antibiotics restore functional expression of truncated HERG channels produced by nonsense mutations.

21 January 2018

1 reference

https://api.crossref.org/works/10.1371%2FJOURNAL.PONE.0018273

Thapsigargin selectively rescues the trafficking defective LQT2 channels G601S and F805C.

21 January 2018

1 reference

https://api.crossref.org/works/10.1371%2FJOURNAL.PONE.0018273

Epinephrine QT stress testing in the evaluation of congenital long-QT syndrome: diagnostic accuracy of the paradoxical QT response

21 January 2018

1 reference

https://api.crossref.org/works/10.1371%2FJOURNAL.PONE.0018273

Defective assembly and trafficking of mutant HERG channels with C-terminal truncations in long QT syndrome

21 January 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3069070

Defective human Ether-à-go-go-related gene trafficking linked to an endoplasmic reticulum retention signal in the C terminus

27 November 2018

1 reference

12 December 2020

Identification of a COOH-terminal segment involved in maturation and stability of human ether-a-go-go-related gene potassium channels

1 reference

12 December 2020

The dominant negative LQT2 mutation A561V reduces wild-type HERG expression

1 reference

12 December 2020

Downregulation of the HERG (KCNH2) K(+) channel by ceramide: evidence for ubiquitin-mediated lysosomal degradation

1 reference

12 December 2020