(Q33339275)

25 July 2017

1 reference

title

The wobbler mouse: a neurodegeneration jigsaw puzzle (English)

1 reference

https://api.crossref.org/works/10.1385/MN:28:1:65

25 July 2017

The Wobbler Mouse: A Neurodegeneration Jigsaw Puzzle (English)

1 reference

15 March 2024

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?resulttype=core&format=json&query=SRC%3AMED%20AND%20EXT_ID%3A14514986

15 March 2024

1 reference

https://api.crossref.org/works/10.1385/MN:28:1:65

15 March 2024

1 reference

1

Séverine Boillée

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?resulttype=core&format=json&query=SRC%3AMED%20AND%20EXT_ID%3A14514986

15 March 2024

author name string

Marc Peschanski

series ordinal

2

1 reference

25 July 2017

Marie-Pierre Junier

series ordinal

3

1 reference

25 July 2017

language of work or name

English

1 reference

National Center for Biotechnology Information

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/esummary.fcgi?db=pubmed&retmode=json&id=14514986

15 March 2024

publication date

1 August 2003

1 reference

full work available at URL

25 July 2017

http://www.springerlink.com/index/pdf/10.1385/MN:28:1:65

1 reference

https://api.crossref.org/works/10.1385/MN:28:1:65

15 March 2024

published in

Molecular Neurobiology

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25 July 2017

volume

28

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25 July 2017

issue

1

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25 July 2017

page(s)

65-106

1 reference

https://scigraph.springernature.com/pub.10.1385/mn:28:1:65

25 July 2017

exact match

0 references

cites work

Acetylcholine esterase and peripherin mRNA level decrease in wobbler mouse

1 reference

12 December 2020

Alterations in acetylcholinesterase and choline acetyltransferase activities and neuropeptide levels in the ventral spinal cord of the Wobbler mouse during inherited motoneuron disease

1 reference

12 December 2020

Sec61p and BiP directly facilitate polypeptide translocation into the ER.

1 reference

12 December 2020

Neurofilament distribution is altered in the Mnd (motor neuron degeneration) mouse

1 reference

12 December 2020

'Wasted', a new mutant of the mouse with abnormalities characteristic to ataxia telangiectasia.

1 reference

12 December 2020

Acid protease activity in spinal cord and muscle in wobbler mouse

1 reference

12 December 2020

Transforming growth factor alpha expression as a response of murine motor neurons to axonal injury and mutation-induced degeneration

1 reference

12 December 2020

Effects of cardiotrophin-1 (CT-1) in a mouse motor neuron disease

1 reference

12 December 2020

Polyglutamine length-dependent interaction of Hsp40 and Hsp70 family chaperones with truncated N-terminal huntingtin: their role in suppression of aggregation and cellular toxicity

1 reference

12 December 2020

A controlled trial of recombinant methionyl human BDNF in ALS: The BDNF Study Group (Phase III)

1 reference

12 December 2020

Overexpression of neurofilament subunit NF-L and NF-H extends survival of a mouse model for amyotrophic lateral sclerosis

1 reference

12 December 2020

Reactive astrocytes: cellular and molecular cues to biological function

1 reference

12 December 2020

Chaperone suppression of aggregation and altered subcellular proteasome localization imply protein misfolding in SCA1.

1 reference

12 December 2020

Spatiotemporal progression of neurodegeneration and glia activation in the wobbler neuropathy of the mouse.

1 reference

12 December 2020

Protein fate in neurodegenerative proteinopathies: polyglutamine diseases join the (mis)fold

1 reference

12 December 2020

Increased expression of neurofilament subunit NF-L produces morphological alterations that resemble the pathology of human motor neuron disease

1 reference

12 December 2020

Impaired slow axonal transport in wobbler mouse motor neuron disease

1 reference

12 December 2020

Effects of brain-derived neurotrophic factor on motor dysfunction in wobbler mouse motor neuron disease

1 reference

12 December 2020

Reduced branching and length of dendrites detected in cervical spinal cord motoneurons of wobbler mouse, a model for inherited motoneuron disease

1 reference

12 December 2020

Measurement of neuropeptides in the brain and spinal cord of Wobbler mouse: a model for motoneuron disease

1 reference

12 December 2020

Transgenic mice carrying a human mutant superoxide dismutase transgene develop neuronal cytoskeletal pathology resembling human amyotrophic lateral sclerosis lesions

1 reference

12 December 2020

Retardation of fast axonal transport in wobbler mice

1 reference

12 December 2020

GAP-43: an intrinsic determinant of neuronal development and plasticity

1 reference

12 December 2020

Decreased immunoreactive (IR) calcitonin gene-related peptide correlates with sprouting of IR-peptidergic and serotonergic neuronal processes in spinal cord and brain nuclei from the Wobbler mouse during motoneuron disease

1 reference

12 December 2020

Absence of neurofilaments reduces the selective vulnerability of motor neurons and slows disease caused by a familial amyotrophic lateral sclerosis-linked superoxide dismutase 1 mutant

1 reference

12 December 2020

Acid hydrolases and other enzymes in secondary demyelination: a quantitative histochemical study in the wobbler mouse.

1 reference

12 December 2020

A gene encoding a putative GTPase regulator is mutated in familial amyotrophic lateral sclerosis 2

1 reference

12 December 2020

Elevated expression of membrane type 1 metalloproteinase (MT1-MMP) in reactive astrocytes following neurodegeneration in mouse central nervous system

1 reference

12 December 2020

Protective effect of a novel free radical scavenger, OPC-14117, on wobbler mouse motor neuron disease

1 reference

12 December 2020

The motoneuron degeneration in the wobbler mouse is independent of the overexpression of a Bcl2 transgene in neurons

1 reference

12 December 2020

Murine motor neuron disease (the wobbler mouse): degeneration and regeneration of the lower motor neuron.

1 reference

12 December 2020

Chronic inhibition of glutamate uptake produces a model of slow neurotoxicity

1 reference

12 December 2020

Chaperoning brain diseases.

1 reference

12 December 2020

Integrated radiation hybrid map of human chromosome 2p13: possible involvement of dynactin in neuromuscular diseases

1 reference

12 December 2020

Amyotrophic lateral sclerosis: current issues in classification, pathogenesis and molecular pathology

1 reference

12 December 2020

BDNF and NT-4/5 exert neurotrophic influences on injured adult spinal motor neurons

1 reference

12 December 2020

Definition of tumor-associated antigens in hepatocellular carcinoma.

1 reference

12 December 2020

Comparative transcription map of the wobbler critical region on mouse chromosome 11 and the homologous region on human chromosome 2p13-14.

1 reference

12 December 2020

Motoneuron loss in the abducens nucleus of wobbler mice

1 reference

12 December 2020

Polyglutamine-expanded androgen receptors form aggregates that sequester heat shock proteins, proteasome components and SRC-1, and are suppressed by the HDJ-2 chaperone

1 reference

12 December 2020

Abnormal astrocyte differentiation and defective cellular interactions in wobbler mouse spinal cord.

1 reference

12 December 2020

Ubiquitin-dependent degradation of certain protein substrates in vitro requires the molecular chaperone Hsc70

1 reference

12 December 2020

Early defect in the expression of mouse sperm DnaJ 1, a member of the DNAJ/heat shock protein 40 chaperone protein family, in the spinal cord of the wobbler mouse, a murine model of motoneuronal degeneration

1 reference

12 December 2020

Induction of nitric oxide synthase and motoneuron death in newborn and early postnatal rats following spinal root avulsion

1 reference

12 December 2020

Microglia and the early phase of immune surveillance in the axotomized facial motor nucleus: impaired microglial activation and lymphocyte recruitment but no effect on neuronal survival or axonal regeneration in macrophage-colony stimulating factor-

1 reference

12 December 2020

Modulation of HSP25 expression during anterior horn motor neuron degeneration in the paralysé mouse mutant

1 reference

12 December 2020

Reactive microglia in cerebral ischaemia: an early mediator of tissue damage?

1 reference

12 December 2020

Randomized, double-blind, controlled trial of acetylcysteine in amyotrophic lateral sclerosis

1 reference

12 December 2020

Motor neurone disease and animal models

1 reference

12 December 2020

The wobbler mouse mutant: an animal model of hereditary motor system disease

1 reference

12 December 2020

MSJ-1, a mouse testis-specific DnaJ protein, is highly expressed in haploid male germ cells and interacts with the testis-specific heat shock protein Hsp70-2

1 reference

12 December 2020

Spinal muscular atrophies: recent insights and impact on molecular diagnosis

1 reference

12 December 2020

Inhibition of nitric oxide synthase reduces motoneuron death due to spinal root avulsion

1 reference

12 December 2020

Glucocorticoid receptors and actions in the spinal cord of the Wobbler mouse, a model for neurodegenerative diseases

1 reference

12 December 2020

Glycosaminoglycans boost insulin-like growth factor-I-promoted neuroprotection: blockade of motor neuron death in the wobbler mouse

1 reference

12 December 2020

Deletion of the hypoxia-response element in the vascular endothelial growth factor promoter causes motor neuron degeneration.

1 reference

12 December 2020

Astrocyte overgrowth in the brain stem and spinal cord of mice affected by spinal atrophy, wobbler

1 reference

12 December 2020

Tumor necrosis factor alpha induces a metalloprotease-disintegrin, ADAM8 (CD 156): implications for neuron-glia interactions during neurodegeneration

1 reference

12 December 2020

Transforming growth factor alpha: a promoter of motoneuron survival of potential biological relevance.

1 reference

12 December 2020

A double-blind, placebo-controlled randomized clinical trial of alpha-tocopherol (vitamin E) in the treatment of amyotrophic lateral sclerosis. ALS riluzole-tocopherol Study Group

1 reference

12 December 2020

A phase I/II trial of recombinant methionyl human brain derived neurotrophic factor administered by intrathecal infusion to patients with amyotrophic lateral sclerosis.

1 reference

12 December 2020

Neurofilaments and motor neuron disease

1 reference

12 December 2020

Histometric characteristics and regenerative capacity in wobbler mouse motor neuron disease.

1 reference

12 December 2020

Ultrastructural differences during embryonic cell death in normal and peripherally deprived ciliary ganglia

1 reference

12 December 2020

Evidence for down-regulation of GAP-43 mRNA in Wobbler mouse spinal motoneurons by corticosterone and a 21-aminosteroid

1 reference

12 December 2020

A placebo-controlled trial of recombinant human ciliary neurotrophic (rhCNTF) factor in amyotrophic lateral sclerosis. rhCNTF ALS Study Group

1 reference

12 December 2020

Generalized molecular defects of the neuromuscular junction in skeletal muscle of the wobbler mutant mouse

1 reference

12 December 2020

Molecular profile of reactive astrocytes--implications for their role in neurologic disease

1 reference

12 December 2020

Raised thyrotrophin-releasing hormone, pyroglutamylamino peptidase, and proline endopeptidase are present in the spinal cord of wobbler mice but not in human motor neurone disease

1 reference

12 December 2020

What role(s) for TGFalpha in the central nervous system?

1 reference

12 December 2020

Transforming growth factor alpha (TGF alpha) expression in degenerating motoneurons of the murine mutant wobbler: a neuronal signal for astrogliosis?

1 reference

12 December 2020

SOD1 mutation is associated with accumulation of neurofilaments in amyotrophic lateral sclerosis.

1 reference

12 December 2020

Localization of the human UGP2 gene encoding the muscle isoform of UDPglucose pyrophosphorylase to 2p13-p14 by fluorescence in situ hybridization

1 reference

12 December 2020

Overexpression of BCL-2 in transgenic mice protects neurons from naturally occurring cell death and experimental ischemia

1 reference

12 December 2020

Involvement of the molecular chaperone Ydj1 in the ubiquitin-dependent degradation of short-lived and abnormal proteins in Saccharomyces cerevisiae

1 reference

12 December 2020

Spinal muscular atrophy gene wobbler of the mouse: evidence from chimeric spinal cord and testis for cell-autonomous function.

1 reference

12 December 2020

Excitatory amino acid receptor antagonist in murine motoneuron disease (the wobbler mouse)

1 reference

12 December 2020

Brain macrophages: neurotoxic or neurotrophic effector cells?

1 reference

12 December 2020

The Fine Structure of the Cervical Spinal Cord, Ventral Root and Brachial Nerves in the Wobbler (WR) Mouse

1 reference

12 December 2020

Motoneuron morphological alterations before and after the onset of the disease in the wobbler mouse.

1 reference

12 December 2020

Plasminogen activators in the neuromuscular system of the wobbler mutant mouse

1 reference

12 December 2020

Excitotoxic cell death

1 reference

12 December 2020

Alteration in the levels of thyrotropin releasing hormone, substance P and enkephalins in the spinal cord, brainstem, hypothalamus and midbrain of the Wobbler mouse at different stages of the motoneuron disease

1 reference

12 December 2020

Transcriptional networks regulating neuronal identity in the developing spinal cord

1 reference

12 December 2020

The association between neuronal nitric oxide synthase and neuronal sensitivity in the brain after brain injury

1 reference

12 December 2020

Selective inhibitors of neuronal nitric oxide synthase--is no NOS really good NOS for the nervous system?

1 reference

12 December 2020

A comparative study of "denervation" in muscles from mice with inherited progressive neuromuscular disorders

1 reference

12 December 2020

Genetic modifiers that aggravate the neurological phenotype of the wobbler mouse

1 reference

12 December 2020

Transient massive DNA fragmentation in nervous system during the early course of a murine neurodegenerative disease

1 reference

12 December 2020

Increased expression of BDNF and trkB mRNA in rat facial motoneurons after axotomy

1 reference

12 December 2020

A low expressor line of transgenic mice carrying a mutant human Cu,Zn superoxide dismutase (SOD1) gene develops pathological changes that most closely resemble those in human amyotrophic lateral sclerosis

1 reference

12 December 2020

The gene for cytoplasmatic malate dehydrogenase, Mor2, is closely linked to the wobbler spinal muscular atrophy gene (wr).

1 reference

12 December 2020

Neuronal specification in the spinal cord: inductive signals and transcriptional codes

1 reference

12 December 2020

An hereditary motor neurone disease with progressive denervation of muscle in the mouse: the mutant 'wobbler'.

1 reference

12 December 2020

A role for transforming growth factor alpha as an inducer of astrogliosis.

1 reference

12 December 2020

Phase III randomized trial of gabapentin in patients with amyotrophic lateral sclerosis

1 reference

12 December 2020

Neuronal pathology in the wobbler mouse brain revealed by in vivo proton magnetic resonance spectroscopy and immunocytochemistry.

1 reference

12 December 2020

The wobbler mouse: amino acid contents in brain and spinal cord.

1 reference

12 December 2020

From Charcot to Lou Gehrig: deciphering selective motor neuron death in ALS

1 reference

12 December 2020

Development of central nervous system pathology in a murine transgenic model of human amyotrophic lateral sclerosis

1 reference

12 December 2020

Proximal axonal enlargement in motor neuron disease.

1 reference

12 December 2020

Superoxide dismutase activity, oxidative damage, and mitochondrial energy metabolism in familial and sporadic amyotrophic lateral sclerosis

1 reference

12 December 2020

Impairment of retrograde axonal transport in wobbler mouse motor neuron disease

1 reference

12 December 2020

Sperm tail axoneme alterations in the Wobbler mouse

1 reference

12 December 2020

Lesion of the rat entorhinal cortex leads to a rapid microglial reaction in the dentate gyrus. A light and electron microscopical study

1 reference

12 December 2020

Evidence that brain-derived neurotrophic factor is a trophic factor for motor neurons in vivo.

1 reference

12 December 2020

Assignment of homologous genes, Peli1/PELI1 and Peli2/PELI2, for the Pelle adaptor protein Pellino to mouse chromosomes 11 and 14 and human chromosomes 2p13.3 and 14q21, respectively, by physical and radiation hybrid mapping

1 reference

12 December 2020

In vivo and in vitro muscle tensions in wobbler mouse motor neuron disease

1 reference

12 December 2020

Homology between human chromosome 2p13.3 and the wobbler critical region on mouse chromosome 11: comparative high-resolution mapping of STS and EST loci on YAC/BAC contigs.

1 reference

12 December 2020

The effects of ciliary neurotrophic factor on motor dysfunction in wobbler mouse motor neuron disease

1 reference

12 December 2020

Dynamic association of proteasomal machinery with the centrosome

1 reference

12 December 2020

Histometric effects of ciliary neurotrophic factor in wobbler mouse motor neuron disease

1 reference

12 December 2020

Expression of nitric-oxide synthase (NOS) in injured CNS neurons as shown by NADPH diaphorase histochemistry

1 reference

12 December 2020

Up-regulation of protein chaperones preserves viability of cells expressing toxic Cu/Zn-superoxide dismutase mutants associated with amyotrophic lateral sclerosis

1 reference

12 December 2020

Pathoanatomy of Parkinson's disease

1 reference

12 December 2020

Abnormal RNA metabolism in spinal motor neurons in the wobbler mouse

1 reference

12 December 2020

Ultrastructure of chromatolytic motoneurons and anterior spinal roots in a case of Werdnig-Hoffmann disease.

1 reference

12 December 2020

Fine structural study of neurofibrillary changes in a family with amyotrophic lateral sclerosis

1 reference

12 December 2020

Programmed cell death of developing mammalian neurons after genetic deletion of caspases.

1 reference

12 December 2020

Axonal regeneration in wobbler motor neuron disease: quantitative histologic and axonal transport studies

1 reference

12 December 2020

Bcl-2 gene family in the nervous system

1 reference

12 December 2020

Cell death of motoneurons in the chick embryo spinal cord. I. A light and electron microscopic study of naturally occurring and induced cell loss during development

1 reference

12 December 2020

Quantitative autoradiographic distribution of glutamate receptors in the cervical segment of the spinal cord of the wobbler mouse

1 reference

12 December 2020

Amyotrophic lateral sclerosis associated with genetic abnormalities in the gene encoding Cu/Zn superoxide dismutase: molecular pathology of five new cases, and comparison with previous reports and 73 sporadic cases of ALS.

1 reference

12 December 2020

Chaperones Hsp70 and Hsp40 suppress aggregate formation and apoptosis in cultured neuronal cells expressing truncated androgen receptor protein with expanded polyglutamine tract

1 reference

12 December 2020

Cell birth, cell death, cell diversity and DNA breaks: how do they all fit together?

1 reference

12 December 2020

A double-blind placebo-controlled clinical trial of subcutaneous recombinant human ciliary neurotrophic factor (rHCNTF) in amyotrophic lateral sclerosis. ALS CNTF Treatment Study Group

1 reference

12 December 2020

Quantitative measurement of muscle strength in the mouse

1 reference

12 December 2020

A novel behavioral method to detect motoneuron disease in Wobbler mice aged three to seven days old.

1 reference

12 December 2020

Bcl-2 sensitivity differentiates two pathways for motoneuronal death in the wobbler mutant mouse

1 reference

12 December 2020

Early detection of mouse wobbler mutation: a model of pathological motoneurone death

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12 December 2020

Oxidative processes and antioxidative defense mechanisms in the aging brain

1 reference

12 December 2020

Changes in receptor levels for thyrotropin releasing hormone, serotonin, and substance P in cervical spinal cord of Wobbler mouse: a quantitative autoradiography study during early and late stages of the motoneuron disease.

1 reference

12 December 2020

Excitotoxicity hypothesis

1 reference

12 December 2020

Of mice, men and motor neurons

1 reference

12 December 2020

Dose-ranging study of riluzole in amyotrophic lateral sclerosis. Amyotrophic Lateral Sclerosis/Riluzole Study Group II

1 reference

12 December 2020

Early and selective pathology of light chain neurofilament in the spinal cord and sciatic nerve of G86R mutant superoxide dismutase transgenic mice

1 reference

12 December 2020

Regeneration in the CNS: optimism mounts.

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12 December 2020

Mechanisms of programmed cell death in the developing brain

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12 December 2020

Mouse U2af1-rs1 is a neomorphic imprinted gene

1 reference

12 December 2020

MSJ-1, a new member of the DNAJ family of proteins, is a male germ cell-specific gene product.

1 reference

12 December 2020

Mouse sperm cell-specific DnaJ first homologue: an evolutionarily conserved protein for spermiogenesis.

1 reference

12 December 2020

Genetic transfer of the wobbler gene to a C57BL/6J x NZB hybrid stock: natural history of the motor neuron disease and response to CNTF and BDNF cotreatment.

1 reference

12 December 2020

A placebo-controlled trial of insulin-like growth factor-I in amyotrophic lateral sclerosis. European ALS/IGF-I Study Group

1 reference

12 December 2020

Glutamate transporters in the spinal cord of the wobbler mouse

1 reference

12 December 2020

Genetic interactions between KAR2 and SEC63, encoding eukaryotic homologues of DnaK and DnaJ in the endoplasmic reticulum

1 reference

12 December 2020

Fine structural observations of neurofilamentous changes in amyotrophic lateral sclerosis

1 reference

12 December 2020

Neuroprotective effect of cholinergic differentiation factor/leukemia inhibitory factor on wobbler murine motor neuron disease

1 reference

12 December 2020

Glial changes following an excitotoxic lesion in the CNS—I. Microglia/macrophages

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12 December 2020

Modulation of intracellular protein degradation by SSB1-SIS1 chaperon system in yeast S. cerevisiae.

1 reference

12 December 2020

Deletions of the heavy neurofilament subunit tail in amyotrophic lateral sclerosis

1 reference

12 December 2020

Axotomy induces NADPH diaphorase activity in neonatal but not adult motoneurones.

1 reference

12 December 2020

Progressive neuronopathy in transgenic mice expressing the human neurofilament heavy gene: a mouse model of amyotrophic lateral sclerosis

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12 December 2020

Arrest of motor neuron disease in wobbler mice cotreated with CNTF and BDNF

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12 December 2020

Neuron volume in the ventral horn in Wobbler mouse motoneuron disease: a light microscope stereological study

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12 December 2020

Effects of low doses of glycosaminoglycans and insulin-like growth factor-I on motor neuron disease in wobbler mouse

1 reference

12 December 2020

Proopiomelanocortin-derived peptides in mice with motoneurone disease

1 reference

12 December 2020

Implantation of PNS Graft Inhibits the Induction of Neuronal Nitric Oxide Synthase and Enhances the Survival of Spinal Motoneurons Following Root Avulsion

1 reference

12 December 2020

Quantitative light and electron microscopic studies on the ventral roots of the wobbler mutant mouse

1 reference

12 December 2020

Studies on a murine form of spontaneous lower motor neuron degeneration--the wobbler (wa) mouse

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12 December 2020

Tetramethyl benzidine for horseradish peroxidase neurohistochemistry: a non-carcinogenic blue reaction product with superior sensitivity for visualizing neural afferents and efferents

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12 December 2020

Neuroprotective effect of basic fibroblast growth factor on wobbler mouse motor neuron disease

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12 December 2020

Quantitative reverse transcriptase PCR to gauge increased protease-activated receptor 1 (PAR-1) mRNA copy numbers in the Wobbler mutant mouse

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12 December 2020

Defect of sperm assembly in a neurological mutant of the mouse, wobbler (WR).

1 reference

12 December 2020

Reduction of lower motor neuron degeneration in wobbler mice by N-acetyl-L-cysteine

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12 December 2020

Differential regulation of motor neuron survival and choline acetyltransferase expression following axotomy

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12 December 2020

Ubiquitin in neurodegenerative diseases

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12 December 2020

Mutations in Hsp83 and cdc37 impair signaling by the sevenless receptor tyrosine kinase in Drosophila.

1 reference

12 December 2020

Neuron-specific expression of mutant superoxide dismutase 1 in transgenic mice does not lead to motor impairment.

1 reference

12 December 2020

The mouse mutation muscle deficient (mdf) is characterized by a progressive motoneuron disease

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12 December 2020

T-588, a novel neuroprotective agent, delays progression of neuromuscular dysfunction in wobbler mouse motoneuron disease

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12 December 2020

Muscle lactate dehydrogenase activity is decreased in murine motor neuron disease

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12 December 2020

Role of the protein chaperone YDJ1 in establishing Hsp90-mediated signal transduction pathways

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12 December 2020

Astrocytosis in wobbler mouse spinal cord involves a population of astrocytes which is glutamine synthetase-negative.

1 reference

12 December 2020

Otx genes in the development and evolution of the vertebrate brain.

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12 December 2020

The molecular bases of spinal muscular atrophy

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12 December 2020

Motor neuron cell death in wobbler mutant mice follows overexpression of the G-protein-coupled, protease-activated receptor for thrombin

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12 December 2020

A therapeutic trial of gangliosides and thymosin in the Wobbler mouse model of motor neuron disease

1 reference

12 December 2020

TRPM-2 expression and tunel staining in neurodegenerative diseases: studies in wobbler and rd mice

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12 December 2020

Reduced protein synthesis in spinal anterior horn neurons in wobbler mouse mutant

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12 December 2020

DnaJ-like proteins: molecular chaperones and specific regulators of Hsp70.

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12 December 2020

Loss of motor neurons from the median nerve motor nucleus of the mutant mouse 'wobbler'

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12 December 2020

Spiny interneurons identified in the normal mouse spinal cord show alterations in the Wobbler mouse: a model for inherited motoneuron disease

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12 December 2020

Early upregulation of medium neurofilament gene expression in developing spinal cord of the wobbler mouse mutant.

1 reference

12 December 2020

Cutting edge: mouse pellino-2 modulates IL-1 and lipopolysaccharide signaling

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12 December 2020

Bip/GRP78 but not calnexin associates with a precursor of glycosylphosphatidylinositol-anchored protein

1 reference

12 December 2020

Dependence of postnatal motoneurones on their targets: review and hypothesis

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12 December 2020

The gene encoding alsin, a protein with three guanine-nucleotide exchange factor domains, is mutated in a form of recessive amyotrophic lateral sclerosis

1 reference

12 December 2020

Influence of factors secreted by wobbler astrocytes on neuronal and motoneuronal survival

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12 December 2020

Differential microglial response to progressive neurodegeneration in the murine mutant Wobbler

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12 December 2020

Superoxide dismutase in familial amyotrophic lateral sclerosis: models for gain of function

1 reference

12 December 2020

The lethal mutation of the mouse wasted (wst) is a deletion that abolishes expression of a tissue-specific isoform of translation elongation factor 1alpha, encoded by the Eef1a2 gene

1 reference

12 December 2020

The Bcl2 family: regulators of the cellular life-or-death switch

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12 December 2020

Wobbler, a mutation affecting motoneuron survival and gonadal functions in the mouse, maps to proximal chromosome 11

1 reference

12 December 2020

Thyrotropin-releasing hormone (TRH) neurons sprout in cervical spinal cord of Wobbler mouse

1 reference

12 December 2020

Roles of molecular chaperones in protein degradation

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12 December 2020

Effects of assisted feeding on Wobbler mouse motoneuron disease and on serotonergic and peptidergic sprouting in the cervical spinal ventral horn

1 reference

12 December 2020

Thyrotropin-releasing hormone (TRH) in murine motor neuron disease (the wobbler mouse).

1 reference

12 December 2020

Increased 3-nitrotyrosine in both sporadic and familial amyotrophic lateral sclerosis

1 reference

12 December 2020

Suppression of polyglutamine-mediated neurodegeneration in Drosophila by the molecular chaperone HSP70.

1 reference

12 December 2020

The 21-aminosteroid U-74389F attenuates hyperexpression of GAP-43 and NADPH-diaphorase in the spinal cord of wobbler mouse, a model for amyotrophic lateral sclerosis

1 reference

12 December 2020

A simple method for organotypic cultures of nervous tissue

1 reference

12 December 2020

Decrease of enkephalins in cerebellum during Wobbler mouse motoneuron disease

1 reference

12 December 2020

Lou Gehrig and amyotrophic lateral sclerosis. Is vitamin E to be revisited?

1 reference

12 December 2020

Regionalized neurofilament accumulation and motoneuron degeneration are linked phenotypes in wobbler neuromuscular disease

1 reference

12 December 2020

Regulation of Growth Factor Gene Expression in Degenerating Motoneurons of the Murine Mutantwobbler: A Cellular Patch-Sampling/RT–PCR Study

1 reference

12 December 2020

Expression of nitric oxide synthase by motor neurones in the spinal cord of the mutant mouse wobbler

1 reference

12 December 2020

Lecithinized superoxide dismutase retards wobbler mouse motoneuron disease

1 reference

12 December 2020

YAC contigs of the Rab1 and wobbler (wr) spinal muscular atrophy gene region on proximal mouse chromosome 11 and of the homologous region on human chromosome 2p

1 reference

12 December 2020

Role of brain-derived neurotrophic factor in wobbler mouse motor neuron disease

1 reference

12 December 2020

Microglia: a sensor for pathological events in the CNS

1 reference

12 December 2020

Neuropathological changes in two lines of mice carrying a transgene for mutant human Cu,Zn SOD, and in mice overexpressing wild type human SOD: a model of familial amyotrophic lateral sclerosis (FALS).

1 reference

12 December 2020

Thrombin perturbs neurite outgrowth and induces apoptotic cell death in enriched chick spinal motoneuron cultures through caspase activation

1 reference

12 December 2020

Neurodegeneration: new clues on inclusions

1 reference

12 December 2020

Developmental cell death: morphological diversity and multiple mechanisms

1 reference

12 December 2020

Neuronal nitric oxide synthase inhibitor, 7-nitroindazole, delays motor dysfunction and spinal motoneuron degeneration in the wobbler mouse.

1 reference

12 December 2020

Effect of recombinant human insulin-like growth factor-I on progression of ALS. A placebo-controlled study. The North America ALS/IGF-I Study Group

1 reference

12 December 2020

Coadministration of interleukin-6 (IL-6) and soluble IL-6 receptor delays progression of wobbler mouse motor neuron disease.

1 reference

12 December 2020

Restricted expression of G86R Cu/Zn superoxide dismutase in astrocytes results in astrocytosis but does not cause motoneuron degeneration

1 reference

12 December 2020

Cytoskeletal pathology in motor neuron diseases

1 reference

12 December 2020

Mechanisms of selective motor neuron death in ALS: insights from transgenic mouse models of motor neuron disease

1 reference

12 December 2020

Identification and characterization of a spinal muscular atrophy-determining gene

1 reference

12 December 2020

The loss of motorneurons corresponding to specific muscles in the wobbler mutant mouse

1 reference

12 December 2020

Characterization of immunologic and neuropathologic abnormalities in wasted mice

1 reference

12 December 2020

A controlled trial of riluzole in amyotrophic lateral sclerosis. ALS/Riluzole Study Group

1 reference

12 December 2020

Reactive mononuclear phagocytes release neurotoxins after ischemic and traumatic injury to the central nervous system

1 reference

12 December 2020

Neuronal nitric oxide synthase is induced in spinal neurons by traumatic injury

1 reference

12 December 2020

Analysis of the role of heat shock protein (Hsp) molecular chaperones in polyglutamine disease

1 reference

12 December 2020

Abnormal neuromuscular junctions in the lateral rectus muscle of wobbler mice

1 reference

12 December 2020

In vitro differences between astrocytes of control and wobbler mice spinal cord

1 reference

12 December 2020

JTP-2942, a novel thyrotropin-releasing hormone analogue, protects against spinal motor neuron degeneration in the wobbler mouse

1 reference

12 December 2020

Reactive microgliosis

1 reference

12 December 2020

Mutant Cu/Zn-superoxide dismutase proteins have altered solubility and interact with heat shock/stress proteins in models of amyotrophic lateral sclerosis

1 reference

12 December 2020

Astrocyte proliferation induced by wobbler astrocyte conditioned medium is blocked by tumor necrosis factor-alpha (TNF-alpha) and interleukin-1beta (IL-1beta) neutralizing antibodies in vitro

1 reference

12 December 2020

Beneficial effects of insulin-like growth factor-I on wobbler mouse motoneuron disease

1 reference

12 December 2020

Heterogeneity of the glial fibrillary acidic protein in gliosed human brains.

1 reference

12 December 2020

Expression of nerve-regulated genes in muscles of mouse mutants affected by spinal muscular atrophies and muscular dystrophies.

1 reference

12 December 2020

Alterations in contractile properties and expression of myofibrillar proteins in wobbler mouse muscles

1 reference

12 December 2020

Neurotrophins promote motor neuron survival and are present in embryonic limb bud.

1 reference

12 December 2020

Cellular defenses against unfolded proteins: a cell biologist thinks about neurodegenerative diseases

1 reference

12 December 2020

Studies on the localization of the lesion in the Wobbler mutant mouse [proceedings]

1 reference

12 December 2020

Vacuolated anterior horn cells in wobbler mouse motor neuron disease: peripheral axons and regenerative capacity

1 reference

12 December 2020

POMC neuropeptides and their receptors in the neuromuscular system of wobbler mice

1 reference

12 December 2020

The selective vulnerability of nerve cells in Huntington's disease

1 reference

12 December 2020

Decreased Spinal Cord cGMP in Murine (Wobbler) Spontaneous Lower Motor Neuron Degeneration

1 reference

12 December 2020

Ablation of NF1 function in neurons induces abnormal development of cerebral cortex and reactive gliosis in the brain

1 reference

12 December 2020

Astrocyte responses to CNS injury

1 reference

12 December 2020

Extracellular matrix degradation by metalloproteinases and central nervous system diseases

1 reference

12 December 2020

Identifiers

DOI

10.1385/MN:28:1:65

1 reference

Dimensions Publication ID

25 July 2017

1032041335

0 references

1 reference