(Q39237966)

10 September 2017

Altered expression of carbonic anhydrase-related protein XI in neuronal cells expressing mutant ataxin-3. (English)

1 reference

10 September 2017

Mingli Hsieh

1

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10 September 2017

Wei-Hsiu Chang

2

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10 September 2017

Chi-Fu Hsu

3

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10 September 2017

Isao Nishimori

4

1 reference

10 September 2017

Cheng-Liang Kuo

5

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10 September 2017

Tomoko Minakuchi

6

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10 September 2017

1 June 2013

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10 September 2017

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10 September 2017

12

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10 September 2017

3

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10 September 2017

338-349

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https://scigraph.springernature.com/pub.10.1007/s12311-012-0430-2

10 September 2017

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cites work

CAG expansions in a novel gene for Machado-Joseph disease at chromosome 14q32.1

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Toward understanding Machado-Joseph disease

21 January 2018

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The polyglutamine neurodegenerative protein ataxin-3 binds polyubiquitylated proteins and has ubiquitin protease activity

21 January 2018

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Poly-ubiquitin Binding by the Polyglutamine Disease Protein Ataxin-3 Links Its Normal Function to Protein Surveillance Pathways

21 January 2018

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Ubiquitin-mediated sequestration of normal cellular proteins into polyglutamine aggregates

21 January 2018

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Ataxin-3 interactions with rad23 and valosin-containing protein and its associations with ubiquitin chains and the proteasome are consistent with a role in ubiquitin-mediated proteolysis

21 January 2018

1 reference

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Elucidation of ataxin-3 and ataxin-7 function by integrative bioinformatics

21 January 2018

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Ataxin-3 suppresses polyglutamine neurodegeneration in Drosophila by a ubiquitin-associated mechanism.

21 January 2018

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Cellular defenses against unfolded proteins: a cell biologist thinks about neurodegenerative diseases

21 January 2018

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Proteolytic cleavage of polyglutamine-expanded ataxin-3 is critical for aggregation and sequestration of non-expanded ataxin-3.

21 January 2018

1 reference

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Nuclear aggregation of polyglutamine-expanded ataxin-3: fragments escape the cytoplasmic quality control

21 January 2018

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Polyglutamine disease and neuronal cell death.

21 January 2018

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Sp1 and TAFII130 transcriptional activity disrupted in early Huntington's disease

21 January 2018

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Ataxin-3 is a histone-binding protein with two independent transcriptional corepressor activities

21 January 2018

1 reference

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Down-regulation of heat shock protein 27 in neuronal cells and non-neuronal cells expressing mutant ataxin-3

21 January 2018

1 reference

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Gene Expression Profiling in Ataxin-3 Expressing Cell Lines Reveals Distinct Effects of Normal and Mutant Ataxin-3

21 January 2018

1 reference

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Dynamic expression of Hsp27 in the presence of mutant ataxin-3.

21 January 2018

1 reference

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Proteotoxic stress increases nuclear localization of ataxin-3

21 January 2018

1 reference

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Intranuclear inclusions of expanded polyglutamine protein in spinocerebellar ataxia type 3.

21 January 2018

1 reference

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An isoform of ataxin-3 accumulates in the nucleus of neuronal cells in affected brain regions of SCA3 patients.

21 January 2018

1 reference

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Opinion: What is the role of protein aggregation in neurodegeneration?

21 January 2018

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Inclusion body formation reduces levels of mutant huntingtin and the risk of neuronal death

21 January 2018

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Novel therapeutic strategies for the treatment of protein-misfolding diseases

21 January 2018

1 reference

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Conformational targeting of fibrillar polyglutamine proteins in live cells escalates aggregation and cytotoxicity

21 January 2018

1 reference

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Human carbonic anhydrases and carbonic anhydrase deficiencies

21 January 2018

1 reference

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Characterization of CA XIII, a novel member of the carbonic anhydrase isozyme family

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12311-012-0430-2

Functional diversity, conservation, and convergence in the evolution of the alpha-, beta-, and gamma-carbonic anhydrase gene families

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12311-012-0430-2

cDNA cloning and developmental expression of murine carbonic anhydrase-related proteins VIII, X, and XI.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12311-012-0430-2

Developmental expression of carbonic anhydrase-related proteins VIII, X, and XI in the human brain

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12311-012-0430-2

Carbonic anhydrase-related protein VIII deficiency is associated with a distinctive lifelong gait disorder in waddles mice

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12311-012-0430-2

CA8 mutations cause a novel syndrome characterized by ataxia and mild mental retardation with predisposition to quadrupedal gait

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12311-012-0430-2

Phenotypical spectrum of cerebellar ataxia associated with a novel mutation in the CA8 gene, encoding carbonic anhydrase (CA) VIII.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12311-012-0430-2

Decreased protein synthesis of Hsp27 associated with cellular toxicity in a cell model of Machado-Joseph disease

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12311-012-0430-2

YAC transgenic mice carrying pathological alleles of the MJD1 locus exhibit a mild and slowly progressive cerebellar deficit.

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12311-012-0430-2

Carbonic anhydrase-related protein is a novel binding protein for inositol 1,4,5-trisphosphate receptor type 1

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12311-012-0430-2

Deranged calcium signaling and neurodegeneration in spinocerebellar ataxia type 3

21 January 2018

1 reference

https://api.crossref.org/works/10.1007%2FS12311-012-0430-2

Interference by huntingtin and atrophin-1 with cbp-mediated transcription leading to cellular toxicity

21 January 2018

1 reference

12 December 2020

Evolution and distribution of the carbonic anhydrase gene families

1 reference

12 December 2020

Excitation-induced ataxin-3 aggregation in neurons from patients with Machado-Joseph disease

1 reference

12 December 2020

Dephosphorylation of the small heat shock protein Hsp27 in vivo by protein phosphatase 2A.

1 reference

12 December 2020

Joseph's disease: clinical and pathological studies in a Japanese family

1 reference

12 December 2020

Carbonic anhydrase (CA)-related proteins (CA-RPs), and transmembrane proteins with CA or CA-RP domains

1 reference

12 December 2020

Polyglutamine and CBP: fatal attraction?

1 reference

12 December 2020

10.1007/S12311-012-0430-2

Identifiers

DOI

1 reference

release_p62cmswhsncgjhf4a55gu3aopa

10 September 2017

0 references

1 reference