(Q28655881)

21 June 2017

5 references

13 March 2019

21 March 2019

22 April 2019

28 January 2021

6 February 2021

Cystic fibrosis related liver disease--another black box in hepatology (English)

1 reference

21 June 2017

0 references

0 references

4 references

13 March 2019

21 March 2019

22 April 2019

28 January 2021

3 references

13 March 2019

21 March 2019

22 April 2019

1 reference

6 February 2021

3

Michael Trauner

1 reference

21 June 2017

Katharina Staufer

1

1 reference

21 June 2017

Emina Halilbasic

series ordinal

2

1 reference

21 June 2017

Lili Kazemi-Shirazi

series ordinal

4

1 reference

21 June 2017

language of work or name

English

0 references

publication date

4 August 2014

6 references

International Journal of Molecular Sciences

21 June 2017

13 March 2019

21 March 2019

22 April 2019

28 January 2021

6 February 2021

6 references

21 June 2017

13 March 2019

21 March 2019

22 April 2019

28 January 2021

6 February 2021

15

1 reference

21 June 2017

issue

8

1 reference

21 June 2017

page(s)

13529-13549

1 reference

Creative Commons Attribution

21 June 2017

copyright license

5 references

13 March 2019

21 March 2019

22 April 2019

28 January 2021

6 February 2021

0 references

on focus list of Wikimedia project

ScienceSource

0 references

cites work

Ursodeoxycholic acid for cystic fibrosis-related liver disease

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4159809

The bile acid receptor GPBAR-1 (TGR5) modulates integrity of intestinal barrier and immune response to experimental colitis

17 March 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4159809

High-dose ursodeoxycholic acid is associated with the development of colorectal neoplasia in patients with ulcerative colitis and primary sclerosing cholangitis

17 March 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4159809

Effect of VX-770 in persons with cystic fibrosis and the G551D-CFTR mutation

17 March 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4159809

Rescue of CF airway epithelial cell function in vitro by a CFTR potentiator, VX-770

17 March 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4159809

High-dose ursodeoxycholic acid for the treatment of primary sclerosing cholangitis

17 March 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4159809

High expression of the bile salt-homeostatic hormone fibroblast growth factor 19 in the liver of patients with extrahepatic cholestasis

17 March 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4159809

Farnesoid X receptor antagonizes nuclear factor kappaB in hepatic inflammatory response

17 March 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4159809

Guidelines for diagnosis of cystic fibrosis in newborns through older adults: Cystic Fibrosis Foundation consensus report

17 March 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4159809

Patterns of GI disease in adulthood associated with mutations in the CFTR gene

17 March 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4159809

Altered hepatobiliary gene expressions in PFIC1: ATP8B1 gene defect is associated with CFTR downregulation

17 March 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4159809

Regulation of antibacterial defense in the small intestine by the nuclear bile acid receptor

17 March 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4159809

Bile acids induce energy expenditure by promoting intracellular thyroid hormone activation

17 March 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4159809

A gene encoding a liver-specific ABC transporter is mutated in progressive familial intrahepatic cholestasis

17 March 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4159809

The clinical significance of the gut microbiota in cystic fibrosis and the potential for dietary therapies

17 March 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4159809

Improvement of digestive health and reduction in proteobacterial populations in the gut microbiota of cystic fibrosis patients using a Lactobacillus reuteri probiotic preparation: a double blind prospective study

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4159809

CFTR genotype and clinical outcomes of adult patients carried as cystic fibrosis disease.

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4159809

Metabolic phenotyping and systems biology approaches to understanding metabolic syndrome and fatty liver disease

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4159809

Combined lung and liver transplantation: analysis of a single-center experience

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4159809

The Gordian Knot of dysbiosis, obesity and NAFLD.

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4159809

Serum proteome profiling identifies novel and powerful markers of cystic fibrosis liver disease

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4159809

Intestinal microbiota determines development of non-alcoholic fatty liver disease in mice.

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4159809

Gastrointestinal complications of cystic fibrosis

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4159809

Cystic fibrosis transmembrane conductance regulator knockout mice exhibit aberrant gastrointestinal microbiota

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4159809

Non-invasive evaluation of cystic fibrosis related liver disease in adults with ARFI, transient elastography and different fibrosis scores

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4159809

Altered de novo lipogenesis contributes to low adipose stores in cystic fibrosis mice

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4159809

The biliary HCO(3)(-) umbrella: experimental evidence revisited.

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4159809

Dual farnesoid X receptor/TGR5 agonist INT-767 reduces liver injury in the Mdr2-/- (Abcb4-/-) mouse cholangiopathy model by promoting biliary HCO⁻₃ output

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4159809

Correction of the F508del-CFTR protein processing defect in vitro by the investigational drug VX-809.

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4159809

A biliary HCO3- umbrella constitutes a protective mechanism against bile acid-induced injury in human cholangiocytes.

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4159809

Non-invasive markers for hepatic fibrosis

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4159809

Metabolic syndrome: is immunosuppression to blame?

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4159809

The G-protein-coupled bile acid receptor, Gpbar1 (TGR5), negatively regulates hepatic inflammatory response through antagonizing nuclear factor κ light-chain enhancer of activated B cells (NF-κB) in mice

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4159809

Best practice guidance for the diagnosis and management of cystic fibrosis-associated liver disease

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4159809

Functional characterization of genetic variants in the apical sodium-dependent bile acid transporter (ASBT; SLC10A2).

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4159809

Liver transplantation in patients with cystic fibrosis: analysis of United Network for Organ Sharing data

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4159809

Nuclear receptors as new perspective for the management of liver diseases

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4159809

Role of nuclear receptors for bile acid metabolism, bile secretion, cholestasis, and gallstone disease

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4159809

Clinical care guidelines for cystic fibrosis-related diabetes: a position statement of the American Diabetes Association and a clinical practice guideline of the Cystic Fibrosis Foundation, endorsed by the Pediatric Endocrine Society

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4159809

Cystic fibrosis-associated liver disease

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4159809

Protective effect of bile acids on the onset of fructose-induced hepatic steatosis in mice

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4159809

The biliary HCO(3)(-) umbrella: a unifying hypothesis on pathogenetic and therapeutic aspects of fibrosing cholangiopathies

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4159809

Nonalcoholic fatty liver disease: US-based acoustic radiation force impulse elastography

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4159809

Evidence of intestinal inflammation in patients with cystic fibrosis

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4159809

CFTR depletion results in changes in fatty acid composition and promotes lipogenesis in intestinal Caco 2/15 cells

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4159809

Bile acids as regulators of hepatic lipid and glucose metabolism

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4159809

Cystic fibrosis is a risk factor for celiac disease.

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4159809

Genetics of cholestatic liver disease in 2010.

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4159809

Prevalence of dyslipidemia in adults with cystic fibrosis

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4159809

Genetic modifiers of liver disease in cystic fibrosis

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4159809

Advanced MRI methods for assessment of chronic liver disease

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4159809

Side chain structure determines unique physiologic and therapeutic properties of norursodeoxycholic acid in Mdr2-/- mice

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4159809

Orthotopic liver transplantation and what to do during follow-up: recommendations for the practitioner

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4159809

Bile acid-induced apoptosis in hepatocytes is caspase-6-dependent

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4159809

Targeting bile-acid signalling for metabolic diseases

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4159809

Expression and function of the bile acid receptor TGR5 in Kupffer cells

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4159809

Cyclic AMP regulates bicarbonate secretion in cholangiocytes through release of ATP into bile

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4159809

Sclerosing cholangitis: a focus on secondary causes

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4159809

Endocrine functions of bile acids

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4159809

Standards of care for patients with cystic fibrosis: a European consensus

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4159809

Bacterial overgrowth in the cystic fibrosis transmembrane conductance regulator null mouse small intestine

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4159809

The phenotypic consequences of CFTR mutations

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4159809

Ultrasound evaluation of liver disease in cystic fibrosis as part of an annual assessment clinic: a 9-year review

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4159809

Transplantation for cystic fibrosis: outcome following early liver transplantation

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4159809

The effect of ursodeoxycholic acid therapy on liver fibrosis progression in primary biliary cirrhosis

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4159809

Sclerosing cholangitis in adults with cystic fibrosis: a magnetic resonance cholangiographic prospective study.

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4159809

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4159809

Intestinal bile acid malabsorption in cystic fibrosis

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4159809

Crohn's disease and cystic fibrosis

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4159809

Inhibition by cyclosporin A of adenosine triphosphate-dependent transport from the hepatocyte into bile

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4159809

Bile acid malabsorption in cystic fibrosis with and without pancreatic insufficiency.

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4159809

Liver disease and common-bile-duct stenosis in cystic fibrosis

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4159809

Cyclosporin A blocks bile acid synthesis in cultured hepatocytes by specific inhibition of chenodeoxycholic acid synthesis

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4159809

Biliary complications of cystic fibrosis

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4159809

Ursodeoxycholic acid therapy in cystic fibrosis-associated liver disease: a dose-response study.

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4159809

Small intestine bacterial overgrowth

3 June 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4159809

3 June 2018

1 reference

https://api.crossref.org/works/10.3390%2FIJMS150813529

Liver disease in adult patients with cystic fibrosis: a frequent and independent prognostic factor associated with death or lung transplantation.

21 January 2018

1 reference

https://api.crossref.org/works/10.3390%2FIJMS150813529

Surveillance for cystic fibrosis-associated hepatobiliary disease: early ultrasound changes and predisposing factors

21 January 2018

1 reference

https://api.crossref.org/works/10.3390%2FIJMS150813529

Serum markers of hepatic fibrogenesis in cystic fibrosis liver disease.

21 January 2018

1 reference

https://api.crossref.org/works/10.3390%2FIJMS150813529

Non-invasive liver elastography (Fibroscan) for detection of cystic fibrosis-associated liver disease

21 January 2018

1 reference

https://api.crossref.org/works/10.3390%2FIJMS150813529

Transient elastography in patients with cystic fibrosis.

21 January 2018

1 reference

https://api.crossref.org/works/10.3390%2FIJMS150813529

Non-invasive measurement of liver and pancreas fibrosis in patients with cystic fibrosis

21 January 2018

1 reference

https://api.crossref.org/works/10.3390%2FIJMS150813529

ARFI and transient elastography for characterization of cystic fibrosis related liver disease: first longitudinal follow-up data in adult patients

21 January 2018

1 reference

https://api.crossref.org/works/10.3390%2FIJMS150813529

Cystic fibrosis transmembrane conductance regulator gene polymorphisms in patients with primary sclerosing cholangitis.

21 January 2018

1 reference

https://api.crossref.org/works/10.3390%2FIJMS150813529

Diagnosis and management of primary sclerosing cholangitis.

21 January 2018

1 reference

https://api.crossref.org/works/10.3390%2FIJMS150813529

Cancer risk in cystic fibrosis: a 20-year nationwide study from the United States

21 January 2018

1 reference

https://api.crossref.org/works/10.3390%2FIJMS150813529

Immunoglobulin G4-associated cholangitis: clinical profile and response to therapy.

21 January 2018

1 reference

https://api.crossref.org/works/10.3390%2FIJMS150813529

Clinical and genetic risk factors for cystic fibrosis-related liver disease

21 January 2018

1 reference

https://api.crossref.org/works/10.3390%2FIJMS150813529

Cystic fibrosis presenting with neonatal cholestasis simulating biliary atresia in a patient with a novel mutation.

21 January 2018

1 reference

https://api.crossref.org/works/10.3390%2FIJMS150813529

Hypertriglyceridemia is associated with insulin levels in adult cystic fibrosis patients.

21 January 2018

1 reference

https://api.crossref.org/works/10.3390%2FIJMS150813529

Impact of lung transplantation on serum lipids in adults with cystic fibrosis

21 January 2018

1 reference

https://api.crossref.org/works/10.3390%2FIJMS150813529

Endogenous ursodeoxycholic acid and cholic acid in liver disease due to cystic fibrosis.

21 January 2018

1 reference

https://api.crossref.org/works/10.3390%2FIJMS150813529

Targeted disruption of the nuclear receptor FXR/BAR impairs bile acid and lipid homeostasis.

21 January 2018

1 reference

https://api.crossref.org/works/10.3390%2FIJMS150813529

Defects in gallbladder emptying and bile Acid homeostasis in mice with cystic fibrosis transmembrane conductance regulator deficiencies.

21 January 2018

1 reference

https://api.crossref.org/works/10.3390%2FIJMS150813529

Association of cystic fibrosis with abnormalities in fatty acid metabolism.

21 January 2018

1 reference

https://api.crossref.org/works/10.3390%2FIJMS150813529

Nutritional assessment and hepatic fatty acid composition in non-alcoholic fatty liver disease (NAFLD): a cross-sectional study.

21 January 2018

1 reference

https://api.crossref.org/works/10.3390%2FIJMS150813529

Bile salt supplementation acts via the farnesoid X receptor to alleviate lipopolysaccharide-induced intestinal injury.

21 January 2018

1 reference

https://api.crossref.org/works/10.3390%2FIJMS150813529

Farnesoid X receptor expression is decreased in colonic mucosa of patients with primary sclerosing cholangitis and colitis-associated neoplasia.

21 January 2018

1 reference

https://api.crossref.org/works/10.3390%2FIJMS150813529

Cyclosporin a and enterohepatic circulation of bile salts in rats: decreased cholate synthesis but increased intestinal reabsorption.

21 January 2018

1 reference

https://api.crossref.org/works/10.3390%2FIJMS150813529

EASL Clinical Practice Guidelines: management of cholestatic liver diseases.

21 January 2018

1 reference

https://api.crossref.org/works/10.3390%2FIJMS150813529

Effects of ivacaftor in patients with cystic fibrosis who carry the G551D mutation and have severe lung disease

21 January 2018

1 reference

https://api.crossref.org/works/10.3390%2FIJMS150813529

Liver transplantation in cystic fibrosis: a report from Baylor College of Medicine and the Texas Children's Hospital

21 January 2018

1 reference

https://api.crossref.org/works/10.3390%2FIJMS150813529

Survival of cystic fibrosis patients undergoing liver and liver-lung transplantations.

21 January 2018

1 reference

https://api.crossref.org/works/10.3390%2FIJMS150813529

Liver transplantation for cholestasis associated with cystic fibrosis in the pediatric population

21 January 2018

1 reference

https://api.crossref.org/works/10.3390%2FIJMS150813529

Cystic fibrosis mortality and survival in the UK: 1947-2003

21 January 2018

1 reference

https://api.crossref.org/works/10.3390%2FIJMS150813529

Importance of hepatic fibrosis in cystic fibrosis and the predictive value of liver biopsy

21 January 2018

1 reference

https://api.crossref.org/works/10.3390%2FIJMS150813529

Cyclosporine A versus tacrolimus monotherapy. Comparison on bile lipids in the first 3 months after liver transplant in humans

21 January 2018

1 reference

https://api.crossref.org/works/10.3390%2FIJMS150813529

Small intestine bacterial overgrowth is frequent in cystic fibrosis: combined hydrogen and methane measurements are required for its detection.

21 January 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4159809

Serum bile acids and ursodeoxycholic acid treatment in cystic fibrosis-related liver disease.

27 November 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4159809

Differential effects of cyclosporin A on the transport of bile acids by human hepatocytes

27 November 2018

1 reference

12 December 2020

Inhibition of ileal bile acid transport by cyclosporin A in rat

1 reference

12 December 2020

Cholestatic effects of cyclosporine in the rat

1 reference

12 December 2020

Can the histologic changes of cystic fibrosis-associated hepatobiliary disease be predicted by clinical criteria?

1 reference

12 December 2020

LIGHT AND ELECTRON MICROSCOPIC EXAMINATION OF THE SMALL BOWEL OF CHILDREN WITH CYSTIC FIBROSIS

1 reference

12 December 2020

Lack of association of common cystic fibrosis transmembrane conductance regulator gene mutations with primary sclerosing cholangitis

1 reference

12 December 2020

Outcome in Cystic Fibrosis Liver Disease

1 reference

12 December 2020

Immunoglobin G4-hepatopathy: association of immunoglobin G4-bearing plasma cells in liver with autoimmune pancreatitis

1 reference

12 December 2020

Primary sclerosing cholangitis in childhood is associated with abnormalities in cystic fibrosis-mediated chloride channel function

1 reference

12 December 2020

Comparison of ultrasound and biopsy findings in children with cystic fibrosis related liver disease

1 reference

12 December 2020

Genetics of cystic fibrosis

1 reference

12 December 2020

Evaluation of acoustic radiation force impulse elastography for fibrosis staging of chronic liver disease: a pilot study

1 reference

12 December 2020

Pilot study on the use of acoustic radiation force impulse imaging in the staging of cystic fibrosis associated liver disease

1 reference

12 December 2020

Acoustic radiation force impulse (ARFI) imaging with Virtual Touch Tissue Quantification in liver disease associated with cystic fibrosis in children

1 reference

12 December 2020

A pilot study of the characterization of hepatic tissue strain in children with cystic-fibrosis-associated liver disease (CFLD) by acoustic radiation force impulse imaging

1 reference

12 December 2020

Evidence of chronic inflammation in morphologically normal small intestine of cystic fibrosis patients

1 reference

12 December 2020

Long-term effects of ursodeoxycholic acid in primary biliary cirrhosis: results of a double-blind controlled multicentric trial. UDCA-Cooperative Group from the Spanish Association for the Study of the Liver

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12 December 2020

Cystic fibrosis mutations: report from the French Registry. The Clinical Centers of the CF

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12 December 2020

Liver disease in cystic fibrosis: A prospective study on incidence, risk factors, and outcome

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12 December 2020

Identifiers

DOI

10.3390/IJMS150813529

1 reference

release_6dgukouwnrecfpze5ve6om7grm

21 June 2017

Fatcat ID

1 reference

Fatcat

https://api.fatcat.wiki/v0/release/6dgukouwnrecfpze5ve6om7grm

24 November 2022

mapped directly with Wikidata item

PMC publication ID

4159809

0 references

1 reference