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Using pharmacological chaperones to restore proteostasis
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instance of
scholarly article
1 reference
stated in
Europe PubMed Central
PubMed publication ID
24747662
retrieved
29 July 2017
title
Using pharmacological chaperones to restore proteostasis
(English)
1 reference
stated in
Europe PubMed Central
PubMed publication ID
24747662
retrieved
29 July 2017
main subject
molecular chaperones
0 references
author
Ting-Wei Mu
series ordinal
3
1 reference
stated in
Europe PubMed Central
PMC publication ID
4070435
reference URL
https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:24747662%20AND%20SRC:MED&resulttype=core&format=json
retrieved
31 May 2020
author name string
Ya-Juan Wang
series ordinal
1
1 reference
stated in
Europe PubMed Central
PMC publication ID
4070435
reference URL
https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:24747662%20AND%20SRC:MED&resulttype=core&format=json
retrieved
31 May 2020
Xiao-Jing Di
series ordinal
2
1 reference
stated in
Europe PubMed Central
PMC publication ID
4070435
reference URL
https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:24747662%20AND%20SRC:MED&resulttype=core&format=json
retrieved
31 May 2020
publication date
18 April 2014
1 reference
stated in
Europe PubMed Central
PubMed publication ID
24747662
retrieved
29 July 2017
published in
Pharmacological Research
1 reference
stated in
Europe PubMed Central
PMC publication ID
4070435
reference URL
https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:24747662%20AND%20SRC:MED&resulttype=core&format=json
retrieved
31 May 2020
volume
83
1 reference
stated in
Europe PubMed Central
PMC publication ID
4070435
reference URL
https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:24747662%20AND%20SRC:MED&resulttype=core&format=json
retrieved
31 May 2020
page(s)
3-9
1 reference
stated in
Europe PubMed Central
PMC publication ID
4070435
reference URL
https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:24747662%20AND%20SRC:MED&resulttype=core&format=json
retrieved
31 May 2020
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Molecular chaperones and protein quality control
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Specific rescue of cystic fibrosis transmembrane conductance regulator processing mutants using pharmacological chaperones
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Most LQT2 mutations reduce Kv11.1 (hERG) current by a class 2 (trafficking-deficient) mechanism
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4 July 2018
Nicotine acts as a pharmacological chaperone to up-regulate human alpha4beta2 acetylcholine receptors
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4 July 2018
Versatility of the endoplasmic reticulum protein folding factory
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The mammalian unfolded protein response
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4 July 2018
A contradictory treatment for lysosomal storage disorders: inhibitors enhance mutant enzyme activity
1 reference
stated in
PubMed Central
reference URL
https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4070435
retrieved
4 July 2018
Pharmacological chaperone-mediated in vivo folding and stabilization of the P23H-opsin mutant associated with autosomal dominant retinitis pigmentosa
1 reference
stated in
PubMed Central
reference URL
https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4070435
retrieved
4 July 2018
Chemical chaperones increase the cellular activity of N370S beta -glucosidase: a therapeutic strategy for Gaucher disease
1 reference
stated in
PubMed Central
reference URL
https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4070435
retrieved
4 July 2018
Ligands act as pharmacological chaperones and increase the efficiency of delta opioid receptor maturation
1 reference
stated in
PubMed Central
reference URL
https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4070435
retrieved
4 July 2018
The binding site for channel blockers that rescue misprocessed human long QT syndrome type 2 ether-a-gogo-related gene (HERG) mutations
1 reference
stated in
PubMed Central
reference URL
https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4070435
retrieved
4 July 2018
Novel CFTR chloride channel activators identified by screening of combinatorial libraries based on flavone and benzoquinolizinium lead compounds
1 reference
stated in
PubMed Central
reference URL
https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4070435
retrieved
4 July 2018
Autophagy as a regulated pathway of cellular degradation
1 reference
stated in
PubMed Central
reference URL
https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4070435
retrieved
4 July 2018
Pharmacological chaperones rescue cell-surface expression and function of misfolded V2 vasopressin receptor mutants
1 reference
stated in
PubMed Central
reference URL
https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4070435
retrieved
4 July 2018
Correction of defective protein trafficking of a mutant HERG potassium channel in human long QT syndrome. Pharmacological and temperature effects
1 reference
stated in
PubMed Central
reference URL
https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4070435
retrieved
4 July 2018
The Hsp70 and Hsp60 chaperone machines
1 reference
stated in
PubMed Central
reference URL
https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4070435
retrieved
4 July 2018
Molecular chaperones in cellular protein folding
1 reference
stated in
PubMed Central
reference URL
https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4070435
retrieved
4 July 2018
The heat-shock response
1 reference
stated in
PubMed Central
reference URL
https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4070435
retrieved
4 July 2018
A Phase 2 study of migalastat hydrochloride in females with Fabry disease: selection of population, safety and pharmacodynamic effects.
1 reference
stated in
PubMed Central
reference URL
https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4070435
retrieved
30 October 2018
Click chemistry approach to new N-substituted aminocyclitols as potential pharmacological chaperones for Gaucher disease
1 reference
stated in
PubMed Central
reference URL
https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4070435
retrieved
30 October 2018
2,5-Dideoxy-2,5-imino-d-altritol as a new class of pharmacological chaperone for Fabry disease.
1 reference
stated in
PubMed Central
reference URL
https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4070435
retrieved
30 October 2018
Correctors promote maturation of cystic fibrosis transmembrane conductance regulator (CFTR)-processing mutants by binding to the protein
1 reference
stated in
PubMed Central
reference URL
https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4070435
retrieved
30 October 2018
Chemical chaperones and permissive temperatures alter localization of Gaucher disease associated glucocerebrosidase variants
1 reference
stated in
PubMed Central
reference URL
https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4070435
retrieved
30 October 2018
Pharmacologic chaperones as a potential treatment for X-linked nephrogenic diabetes insipidus
1 reference
stated in
PubMed Central
reference URL
https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4070435
retrieved
30 October 2018
Retinoids assist the cellular folding of the autosomal dominant retinitis pigmentosa opsin mutant P23H.
1 reference
stated in
PubMed Central
reference URL
https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4070435
retrieved
30 October 2018
Different binding orientations for the same agonist at homologous receptors: a lock and key or a simple wedge?
1 reference
stated in
PubMed Central
reference URL
https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4070435
retrieved
30 October 2018
Rescue of hypogonadotropic hypogonadism-causing and manufactured GnRH receptor mutants by a specific protein-folding template: misrouted proteins as a novel disease etiology and therapeutic target
1 reference
stated in
PubMed Central
reference URL
https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4070435
retrieved
30 October 2018
Accelerated transport and maturation of lysosomal α–galactosidase A in Fabry lymphoblasts by an enzyme inhibitor
1 reference
stated in
PubMed
reference URL
https://pubmed.ncbi.nlm.nih.gov/24747662
retrieved
12 December 2020
based on heuristic
inferred from PubMed ID database lookup
Identifiers
DOI
10.1016/J.PHRS.2014.04.002
1 reference
stated in
Europe PubMed Central
PMC publication ID
4070435
reference URL
https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:24747662%20AND%20SRC:MED&resulttype=core&format=json
retrieved
31 May 2020
Fatcat ID
release_t3to3qvqn5flvob4dkhyqkwsle
1 reference
stated in
Fatcat
reference URL
https://api.fatcat.wiki/v0/release/t3to3qvqn5flvob4dkhyqkwsle
retrieved
24 November 2022
based on heuristic
mapped directly with Wikidata item
PMC publication ID
4070435
1 reference
stated in
Europe PubMed Central
PMC publication ID
4070435
reference URL
https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:24747662%20AND%20SRC:MED&resulttype=core&format=json
retrieved
31 May 2020
PubMed publication ID
24747662
1 reference
stated in
Europe PubMed Central
PMC publication ID
4070435
reference URL
https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:24747662%20AND%20SRC:MED&resulttype=core&format=json
retrieved
31 May 2020
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