(Q39162679)

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:23606264%20AND%20SRC:MED&resulttype=core&format=json

29 February 2020

title

Bicyclic derivatives of L-idonojirimycin as pharmacological chaperones for neuronopathic forms of Gaucher disease (English)

1 reference

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29 February 2020

0 references

1 reference

9

1 reference

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29 February 2020

Aurelio A Moya García

4

1 reference

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María Isabel Garcia Moreno

29 February 2020

5

1 reference

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Francisca Sánchez Jiménez

29 February 2020

7

1 reference

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José Manuel García Fernández

29 February 2020

10

1 reference

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29 February 2020

Almudena Pino-Ángeles

3

object named as

Almudena Pino-Angeles

1 reference

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29 February 2020

author name string

Pilar Alfonso

1

1 reference

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29 February 2020

Vanesa Andreu

2

1 reference

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29 February 2020

José C Rodríguez-Rey

6

1 reference

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29 February 2020

Miguel Pocoví

8

1 reference

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29 February 2020

Pilar Giraldo

11

1 reference

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29 February 2020

publication date

18 April 2013

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29 February 2020

1 reference

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29 February 2020

volume

14

1 reference

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29 February 2020

issue

8

1 reference

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29 February 2020

page(s)

943-949

1 reference

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Glycosphingolipids--nature, function, and pharmacological modulation.

29 February 2020

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Rapid assembly of a library of lipophilic iminosugars via the thiol-ene reaction yields promising pharmacological chaperones for the treatment of Gaucher disease

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Binding of 3,4,5,6-Tetrahydroxyazepanes to the Acid-β-glucosidase Active Site: Implications for Pharmacological Chaperone Design for Gaucher Disease

21 January 2018

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Polyhydroxylated bicyclic isoureas and guanidines are potent glucocerebrosidase inhibitors and nanomolar enzyme activity enhancers in Gaucher cells.

21 January 2018

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Pharmacological chaperones facilitate the post-ER transport of recombinant N370S mutant β-glucocerebrosidase in plant cells: evidence that N370S is a folding mutant

21 January 2018

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Decreased glucocerebrosidase activity in Gaucher disease parallels quantitative enzyme loss due to abnormal interaction with TCP1 and c-Cbl.

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The myo-1,2-Diaminocyclitol Scaffold Defines Potent Glucocerebrosidase Activators and Promising Pharmacological Chaperones for Gaucher Disease.

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Castanospermine-trehazolin hybrids: a new family of glycomimetics with tuneable glycosidase inhibitory properties.

21 January 2018

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Synthesis and evaluation of isourea-type glycomimetics related to the indolizidine and trehazolin glycosidase inhibitor families

21 January 2018

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