(Q34399667)

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:22937152%20AND%20SRC:MED&resulttype=core&format=json

12 February 2020

title

CFTR regulates early pathogenesis of chronic obstructive lung disease in βENaC-overexpressing mice (English)

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:22937152%20AND%20SRC:MED&resulttype=core&format=json

12 February 2020

1 reference

chronic obstructive pulmonary disease

1 reference

4

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:22937152%20AND%20SRC:MED&resulttype=core&format=json

12 February 2020

author name string

Bjarki Johannesson

1

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:22937152%20AND%20SRC:MED&resulttype=core&format=json

12 February 2020

Stephanie Hirtz

2

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:22937152%20AND%20SRC:MED&resulttype=core&format=json

12 February 2020

Jolanthe Schatterny

3

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:22937152%20AND%20SRC:MED&resulttype=core&format=json

12 February 2020

Marcus A Mall

5

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:22937152%20AND%20SRC:MED&resulttype=core&format=json

12 February 2020

language of work or name

English

0 references

publication date

24 August 2012

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:22937152%20AND%20SRC:MED&resulttype=core&format=json

12 February 2020

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:22937152%20AND%20SRC:MED&resulttype=core&format=json

12 February 2020

volume

7

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:22937152%20AND%20SRC:MED&resulttype=core&format=json

12 February 2020

page(s)

e44059

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:22937152%20AND%20SRC:MED&resulttype=core&format=json

12 February 2020

issue

8

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:22937152%20AND%20SRC:MED&resulttype=core&format=json

Creative Commons Attribution 4.0 International

12 February 2020

copyright license

start time

24 August 2012

1 reference

April 2022 Public Data File from Crossref

copyright status

copyrighted

0 references

cites work

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1 reference

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6 July 2018

1 reference

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6 July 2018

1 reference

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A CFTR potentiator in patients with cystic fibrosis and the G551D mutation

6 July 2018

1 reference

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Transgenic hCFTR expression fails to correct β-ENaC mouse lung disease

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3427321

Cigarette smoke exposure induces CFTR internalization and insolubility, leading to airway surface liquid dehydration

6 July 2018

1 reference

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The K+ channel opener 1-EBIO potentiates residual function of mutant CFTR in rectal biopsies from cystic fibrosis patients

6 July 2018

1 reference

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The ENaC-overexpressing mouse as a model of cystic fibrosis lung disease

6 July 2018

1 reference

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Pharmacological therapy for cystic fibrosis: from bench to bedside

6 July 2018

1 reference

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Genetics of complex airway disease

6 July 2018

1 reference

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Critical role of CFTR-dependent lipid rafts in cigarette smoke-induced lung epithelial injury.

6 July 2018

1 reference

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Critical modifier role of membrane-cystic fibrosis transmembrane conductance regulator-dependent ceramide signaling in lung injury and emphysema

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3427321

Effect of VX-770 in persons with cystic fibrosis and the G551D-CFTR mutation

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3427321

Regulation of endogenous ENaC functional expression by CFTR and ΔF508-CFTR in airway epithelial cells.

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3427321

Airway surface liquid volume regulation determines different airway phenotypes in liddle compared with betaENaC-overexpressing mice

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3427321

Allergic airway inflammation induces a pro-secretory epithelial ion transport phenotype in mice

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3427321

Use of a new-generation reverse tetracycline transactivator system for quantitative control of conditional gene expression in the murine lung

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3427321

Rescue of CF airway epithelial cell function in vitro by a CFTR potentiator, VX-770

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3427321

The pathology of chronic obstructive pulmonary disease

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3427321

Role of cilia, mucus, and airway surface liquid in mucociliary dysfunction: lessons from mouse models

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3427321

Ceramide accumulation mediates inflammation, cell death and infection susceptibility in cystic fibrosis

6 July 2018

1 reference

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Global Strategy for the Diagnosis, Management, and Prevention of Chronic Obstructive Pulmonary Disease

6 July 2018

1 reference

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The mouse as a model for human biology: a resource guide for complex trait analysis

6 July 2018

1 reference

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Progress in chronic obstructive pulmonary disease genetics

6 July 2018

1 reference

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Relationship of airway epithelial ion transport to chronic bronchitis

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3427321

Ceramide upregulation causes pulmonary cell apoptosis and emphysema-like disease in mice

6 July 2018

1 reference

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Increased airway epithelial Na+ absorption produces cystic fibrosis-like lung disease in mice

6 July 2018

1 reference

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Mucus clearance as a primary innate defense mechanism for mammalian airways

6 July 2018

1 reference

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Pharmacotherapy of the ion transport defect in cystic fibrosis.

6 July 2018

1 reference

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A new mathematical model for relative quantification in real-time RT-PCR

6 July 2018

1 reference

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The amiloride-inhibitable Na+ conductance is reduced by the cystic fibrosis transmembrane conductance regulator in normal but not in cystic fibrosis airways.

6 July 2018

1 reference

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Diversity of channels generated by different combinations of epithelial sodium channel subunits

6 July 2018

1 reference

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Wild type but not deltaF508 CFTR inhibits Na+ conductance when coexpressed in Xenopus oocytes.

6 July 2018

1 reference

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CFTR as a cAMP-dependent regulator of sodium channels

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3427321

In vivo nasal potential difference: techniques and protocols for assessing efficacy of gene transfer in cystic fibrosis

6 July 2018

1 reference

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Cigarette smoke inhibition of ion transport in canine tracheal epithelium

6 July 2018

1 reference

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Regional differences in quantities of histochemically detectable mucosubstances in nasal, paranasal, and nasopharyngeal epithelium of the bonnet monkey

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3427321

Relationship of smoking history and pulmonary function tests to tracheal mucous velocity in nonsmokers, young smokers, ex-smokers, and patients with chronic bronchitis

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3427321

The CFTR and ENaC debate: how important is ENaC in CF lung disease?

6 July 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3427321

Lung disease at diagnosis in infants with cystic fibrosis detected by newborn screening.

27 October 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3427321

Transmembrane protein 16A (TMEM16A) is a Ca2+-regulated Cl- secretory channel in mouse airways

27 October 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3427321

Role of the amiloride-sensitive epithelial Na+ channel in the pathogenesis and as a therapeutic target for cystic fibrosis lung disease

27 October 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3427321

Preventive but not late amiloride therapy reduces morbidity and mortality of lung disease in betaENaC-overexpressing mice.

27 October 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3427321

Development of chronic bronchitis and emphysema in beta-epithelial Na+ channel-overexpressing mice.

27 October 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3427321

Cystic fibrosis transmembrane conductance regulator function is suppressed in cigarette smokers.

27 October 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3427321

Cystic fibrosis transmembrane conductance regulator inhibits epithelial Na+ channels carrying Liddle's syndrome mutations.

27 October 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=3427321

Correction of lethal intestinal defect in a mouse model of cystic fibrosis by human CFTR

27 October 2018

1 reference

PubMed

https://pubmed.ncbi.nlm.nih.gov/22937152

inferred from PubMed ID database lookup

12 December 2020

based on heuristic

In vivo monitoring of cystic fibrosis-like lung disease in mice by volumetric computed tomography

1 reference

PubMed

https://pubmed.ncbi.nlm.nih.gov/22937152

inferred from PubMed ID database lookup

12 December 2020

based on heuristic

A simple method for volumetry of organs in quantitative stereology

1 reference

PubMed

https://pubmed.ncbi.nlm.nih.gov/22937152

inferred from PubMed ID database lookup

12 December 2020

based on heuristic

Identifiers

DOI

10.1371/JOURNAL.PONE.0044059

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:22937152%20AND%20SRC:MED&resulttype=core&format=json

12 February 2020

0 references

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:22937152%20AND%20SRC:MED&resulttype=core&format=json

12 February 2020

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:22937152%20AND%20SRC:MED&resulttype=core&format=json