(Q26747210)

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:27340661%20AND%20SRC:MED&resulttype=core&format=json

15 March 2020

review article

4 references

28 January 2021

6 February 2021

27 January 2024

Animal Models of Cystic Fibrosis Pathology: Phenotypic Parallels and Divergences (English)

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:27340661%20AND%20SRC:MED&resulttype=core&format=json

15 March 2020

6 references

13 March 2019

21 March 2019

22 April 2019

28 November 2019

15 December 2019

28 January 2021

0 references

1 reference

28 November 2019

1 reference

15 December 2019

1 reference

6 February 2021

1

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:27340661%20AND%20SRC:MED&resulttype=core&format=json

15 March 2020

Michelle M White

2

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:27340661%20AND%20SRC:MED&resulttype=core&format=json

15 March 2020

Niall Browne

3

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:27340661%20AND%20SRC:MED&resulttype=core&format=json

15 March 2020

Emer P Reeves

5

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:27340661%20AND%20SRC:MED&resulttype=core&format=json

15 March 2020

author name string

Noel G McElvaney

4

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:27340661%20AND%20SRC:MED&resulttype=core&format=json

15 March 2020

language of work or name

English

0 references

publication date

1 June 2016

9 references

13 March 2019

21 March 2019

22 April 2019

28 November 2019

15 December 2019

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:27340661%20AND%20SRC:MED&resulttype=core&format=json

15 March 2020

28 January 2021

6 February 2021

27 January 2024

BioMed Research International

10 references

13 March 2019

21 March 2019

22 April 2019

28 November 2019

15 December 2019

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:27340661%20AND%20SRC:MED&resulttype=core&format=json

15 March 2020

28 January 2021

6 February 2021

27 January 2024

2016

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:27340661%20AND%20SRC:MED&resulttype=core&format=json

15 March 2020

page(s)

5258727

1 reference

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:27340661%20AND%20SRC:MED&resulttype=core&format=json

Creative Commons Attribution 4.0 International

15 March 2020

copyright license

8 references

13 March 2019

21 March 2019

22 April 2019

28 November 2019

15 December 2019

28 January 2021

6 February 2021

on focus list of Wikimedia project

27 January 2024

copyright status

copyrighted

0 references

ScienceSource

0 references

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7 April 2017

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Nebulized hypertonic saline decreases IL-8 in sputum of patients with cystic fibrosis

7 April 2017

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Production of CFTR-null and CFTR-DeltaF508 heterozygous pigs by adeno-associated virus-mediated gene targeting and somatic cell nuclear transfer

7 April 2017

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Increased airway epithelial Na+ absorption produces cystic fibrosis-like lung disease in mice

7 April 2017

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CFTR delivery to 25% of surface epithelial cells restores normal rates of mucus transport to human cystic fibrosis airway epithelium

7 April 2017

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CYSTIC FIBROSIS OF THE PANCREAS AND ITS RELATION TO CELIAC DISEASE

7 April 2017

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Identification of the cystic fibrosis gene: genetic analysis

22 April 2017

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Lung infections associated with cystic fibrosis

7 April 2017

1 reference

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Airway acidification initiates host defense abnormalities in cystic fibrosis mice.

25 May 2017

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rAAV-CFTRΔR Rescues the Cystic Fibrosis Phenotype in Human Intestinal Organoids and Cystic Fibrosis Mice

28 September 2017

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Cystic Fibrosis Transmembrane Conductance Regulator in Sarcoplasmic Reticulum of Airway Smooth Muscle. Implications for Airway Contractility

28 September 2017

1 reference

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Targeting ion channels in cystic fibrosis

28 September 2017

1 reference

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Lumacaftor-Ivacaftor in Patients with Cystic Fibrosis Homozygous for Phe508del CFTR.

28 September 2017

1 reference

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Alterations in blood leukocytes of G551D-bearing cystic fibrosis patients undergoing treatment with ivacaftor

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4908263

Defective innate immunity and hyperinflammation in newborn cystic fibrosis transmembrane conductance regulator-knockout ferret lungs

28 September 2017

1 reference

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A neutrophil intrinsic impairment affecting Rab27a and degranulation in cystic fibrosis is corrected by CFTR potentiator therapy

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4908263

Clinical mechanism of the cystic fibrosis transmembrane conductance regulator potentiator ivacaftor in G551D-mediated cystic fibrosis

28 September 2017

1 reference

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Lack of neutrophil elastase reduces inflammation, mucus hypersecretion, and emphysema, but not mucus obstruction, in mice with cystic fibrosis-like lung disease

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4908263

Antibacterial properties of the CFTR potentiator ivacaftor

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4908263

Assessment of influenza virus hemagglutinin stalk-based immunity in ferrets.

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4908263

Synthetic aminoglycosides efficiently suppress cystic fibrosis transmembrane conductance regulator nonsense mutations and are enhanced by ivacaftor

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4908263

Air trapping and airflow obstruction in newborn cystic fibrosis piglets

28 September 2017

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Lung phenotype of juvenile and adult cystic fibrosis transmembrane conductance regulator-knockout ferrets.

28 September 2017

1 reference

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Intestinal complications of cystic fibrosis

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4908263

Intestinal CFTR expression alleviates meconium ileus in cystic fibrosis pigs

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4908263

ENaC inhibitors and airway re-hydration in cystic fibrosis: state of the art.

28 September 2017

1 reference

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CFTR regulates early pathogenesis of chronic obstructive lung disease in βENaC-overexpressing mice

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4908263

Pancreatic and biliary secretion are both altered in cystic fibrosis pigs.

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4908263

Ivacaftor in subjects with cystic fibrosis who are homozygous for the F508del-CFTR mutation

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4908263

A CFTR potentiator in patients with cystic fibrosis and the G551D mutation

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4908263

New animal models of cystic fibrosis: what are they teaching us?

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4908263

Mouse models of cystic fibrosis: phenotypic analysis and research applications

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4908263

Comparative biology of cystic fibrosis animal models

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4908263

The ΔF508 mutation causes CFTR misprocessing and cystic fibrosis-like disease in pigs

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4908263

Intestinal obstruction syndromes in cystic fibrosis: meconium ileus, distal intestinal obstruction syndrome, and constipation

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4908263

The cystic fibrosis neutrophil: a specialized yet potentially defective cell

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4908263

Loss of anion transport without increased sodium absorption characterizes newborn porcine cystic fibrosis airway epithelia

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4908263

Disease phenotype of a ferret CFTR-knockout model of cystic fibrosis.

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4908263

Loss of cystic fibrosis transmembrane conductance regulator function produces abnormalities in tracheal development in neonatal pigs and young children

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4908263

Cystic fibrosis pigs develop lung disease and exhibit defective bacterial eradication at birth

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4908263

Regulation of the epithelial sodium channel (ENaC) by membrane trafficking

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4908263

Correction of the Delta phe508 cystic fibrosis transmembrane conductance regulator trafficking defect by the bioavailable compound glafenine.

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4908263

Pathology of gastrointestinal organs in a porcine model of cystic fibrosis

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4908263

The delta-subunit of the epithelial sodium channel (ENaC) enhances channel activity and alters proteolytic ENaC activation

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4908263

Clinical practice and genetic counseling for cystic fibrosis and CFTR-related disorders

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4908263

Disruption of the CFTR gene produces a model of cystic fibrosis in newborn pigs

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4908263

Infertility in females with cystic fibrosis is multifactorial: evidence from mouse models

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4908263

Adeno-associated virus-targeted disruption of the CFTR gene in cloned ferrets.

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4908263

Parallel improvement of sodium and chloride transport defects by miglustat (n-butyldeoxynojyrimicin) in cystic fibrosis epithelial cells.

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4908263

PTC124 is an orally bioavailable compound that promotes suppression of the human CFTR-G542X nonsense allele in a CF mouse model

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4908263

Severe acute respiratory syndrome coronavirus infection in vaccinated ferrets

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4908263

Bioelectric properties of chloride channels in human, pig, ferret, and mouse airway epithelia

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4908263

Cystic fibrosis mouse models

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4908263

Potential difference measurements in the lower airway of children with and without cystic fibrosis.

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4908263

The cholangiopathies: disorders of biliary epithelia

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4908263

Standardized procedure for measurement of nasal potential difference: an outcome measure in multicenter cystic fibrosis clinical trials

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4908263

New concepts of the pathogenesis of cystic fibrosis lung disease

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4908263

Enterohepatic cycling of bilirubin as a cause of 'black' pigment gallstones in adult life.

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4908263

Early pulmonary infection, inflammation, and clinical outcomes in infants with cystic fibrosis

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4908263

Mouse models of cystic fibrosis

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4908263

Enhanced susceptibility to pulmonary infection with Burkholderia cepacia in Cftr(-/-) mice

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4908263

rhDNase therapy for the treatment of cystic fibrosis patients with mild to moderate lung disease

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4908263

Effect of increasing doses of hypertonic saline on mucociliary clearance in patients with cystic fibrosis

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4908263

Excessive inflammatory response of cystic fibrosis mice to bronchopulmonary infection with Pseudomonas aeruginosa

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4908263

Cystic fibrosis mice carrying the missense mutation G551D replicate human genotype-phenotype correlations.

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4908263

Defective fluid transport by cystic fibrosis airway epithelia

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4908263

A mouse model for the delta F508 allele of cystic fibrosis.

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4908263

A mouse model for the cystic fibrosis delta F508 mutation.

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4908263

Relationship of a non-cystic fibrosis transmembrane conductance regulator-mediated chloride conductance to organ-level disease in Cftr(-/-) mice

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4908263

Expression of the cystic fibrosis transmembrane conductance regulator gene in cells of non-epithelial origin

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4908263

An animal model for cystic fibrosis made by gene targeting

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4908263

Modulation of disease severity in cystic fibrosis transmembrane conductance regulator deficient mice by a secondary genetic factor

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4908263

Cystic fibrosis and infertility caused by congenital bilateral absence of the vas deferens and related clinical entities

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4908263

CFTR is required for PKA-regulated ATP sensitivity of Kir1.1 potassium channels in mouse kidney

28 September 2017

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4908263

Lysozyme secretion by submucosal glands protects the airway from bacterial infection.

31 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4908263

CFTR gene and male fertility

31 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4908263

Lower airway inflammation in infants and young children with cystic fibrosis.

31 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4908263

Cystic fibrosis in the mouse by targeted insertional mutagenesis

31 May 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4908263

Gastrointestinal Manifestations of Cystic Fibrosis.

31 May 2018

1 reference

https://api.crossref.org/works/10.1155%2F2016%2F5258727

Production of a severe cystic fibrosis mutation in mice by gene targeting

21 January 2018

1 reference

https://api.crossref.org/works/10.1155%2F2016%2F5258727

A severe phenotype in mice with a duplication of exon 3 in the cystic fibrosis locus.

21 January 2018

1 reference

https://api.crossref.org/works/10.1155%2F2016%2F5258727

Generation and characterization of a delta F508 cystic fibrosis mouse model.

21 January 2018

1 reference

https://api.crossref.org/works/10.1155%2F2016%2F5258727

The severe G480C cystic fibrosis mutation, when replicated in the mouse, demonstrates mistrafficking, normal survival and organ-specific bioelectrics.

21 January 2018

1 reference

https://api.crossref.org/works/10.1155%2F2016%2F5258727

Long-term survival of the exon 10 insertional cystic fibrosis mutant mouse is a consequence of low level residual wild-type Cftr gene expression.

21 January 2018

1 reference

https://api.crossref.org/works/10.1155%2F2016%2F5258727

Zero-stress state of intra- and extraparenchymal airways from human, pig, rabbit, and sheep lung.

21 January 2018

1 reference

https://api.crossref.org/works/10.1155%2F2016%2F5258727

Morphometric characterization of the airway and vascular systems of the lung of the domestic pig, Sus scrofa: comparison of the airway, arterial and venous systems

21 January 2018

1 reference

https://api.crossref.org/works/10.1155%2F2016%2F5258727

Evolution of pancreatic function during the first year in infants with cystic fibrosis

21 January 2018

1 reference

https://api.crossref.org/works/10.1155%2F2016%2F5258727

Successful targeting of the mouse cystic fibrosis transmembrane conductance regulator gene in embryonal stem cells

21 January 2018

1 reference

https://api.crossref.org/works/10.1155%2F2016%2F5258727

The CF mouse: an important tool for studying cystic fibrosis.

21 January 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4908263

Normal vas deferens in fetuses with cystic fibrosis.

28 November 2018

1 reference

https://eutils.ncbi.nlm.nih.gov/entrez/eutils/elink.fcgi?dbfrom=pmc&linkname=pmc_refs_pubmed&retmode=json&id=4908263

Guidelines for the physiotherapy management of the adult, medical, spontaneously breathing patient

28 November 2018

1 reference

12 December 2020

Blood basophils from cystic fibrosis patients with allergic bronchopulmonary aspergillosis are primed and hyper-responsive to stimulation by aspergillus allergens

1 reference

12 December 2020

Colonic diverticulitis causing partial bowel obstruction in a child with cystic fibrosis

1 reference

12 December 2020

cAMP- but not Ca(2+)-regulated Cl- conductance is lacking in cystic fibrosis mice epididymides and seminal vesicles

1 reference

12 December 2020

The respiratory tract immune system in the pig. II. associated lymphoid tissues

1 reference

12 December 2020

Severe phenotype in mice with termination mutation in exon 2 of cystic fibrosis gene

1 reference

12 December 2020

The delta F508 mutation decreases the stability of cystic fibrosis transmembrane conductance regulator in the plasma membrane. Determination of functional half-lives on transfected cells

1 reference

12 December 2020

Longitudinal assessment of Pseudomonas aeruginosa in young children with cystic fibrosis

1 reference

12 December 2020

1 reference

12 December 2020

Impaired ability of Cftr knockout mice to control lung infection with Pseudomonas aeruginosa.

1 reference

12 December 2020

Early pulmonary inflammation in infants with cystic fibrosis

1 reference

12 December 2020

Bronchoalveolar lavage findings in cystic fibrosis patients with stable, clinically mild lung disease suggest ongoing infection and inflammation

1 reference

12 December 2020

Submucosal glands are the predominant site of CFTR expression in the human bronchus

1 reference

12 December 2020

True survival benefit of lung transplantation for cystic fibrosis patients: the Zurich experience

1 reference

12 December 2020

Identifiers

DOI

10.1155/2016/5258727

2 references

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:27340661%20AND%20SRC:MED&resulttype=core&format=json

15 March 2020

1 reference

2 references

https://www.ebi.ac.uk/europepmc/webservices/rest/search?query=EXT_ID:27340661%20AND%20SRC:MED&resulttype=core&format=json

15 March 2020

2 references